Class information for:
Level 2: HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//JUVENILE IDIOPATHIC ARTHRITIS//ADULT ONSET STILLS DISEASE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
1918 5294 29.2 72%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)



ID, lev.
above
Publications Label for level above
384 29024 RHEUMATOID ARTHRITIS//RHEUMATOLOGY//RHEUMATOL

Classes in level below (level 1)



ID, lev. below Publications Label for level below
2244 2237 JUVENILE IDIOPATHIC ARTHRITIS//JUVENILE RHEUMATOID ARTHRITIS//CROSS CULTURAL ADAPTATION AND PSYCHOMETRIC
4317 1732 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//HEMOPHAGOCYTIC SYNDROME//HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS
14760 682 ADULT ONSET STILLS DISEASE//ADULT STILLS DISEASE//STILLS DISEASE
15417 643 FEVER OF UNKNOWN ORIGIN//INFLAMMATION OF UNKNOWN ORIGIN//NEOPLASTIC FEVER

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Author keyword 442 77% 6% 302
2 JUVENILE IDIOPATHIC ARTHRITIS Author keyword 362 48% 11% 559
3 ADULT ONSET STILLS DISEASE Author keyword 280 74% 4% 209
4 HEMOPHAGOCYTIC SYNDROME Author keyword 218 60% 5% 241
5 MACROPHAGE ACTIVATION SYNDROME Author keyword 210 79% 3% 136
6 HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Author keyword 125 88% 1% 59
7 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Author keyword 125 87% 1% 61
8 JUVENILE RHEUMATOID ARTHRITIS Author keyword 124 43% 4% 223
9 HEMOPHAGOCYTOSIS Author keyword 116 60% 2% 126
10 STILLS DISEASE Author keyword 91 73% 1% 70

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 442 77% 6% 302 Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
2 JUVENILE IDIOPATHIC ARTHRITIS 362 48% 11% 559 Search JUVENILE+IDIOPATHIC+ARTHRITIS Search JUVENILE+IDIOPATHIC+ARTHRITIS
3 ADULT ONSET STILLS DISEASE 280 74% 4% 209 Search ADULT+ONSET+STILLS+DISEASE Search ADULT+ONSET+STILLS+DISEASE
4 HEMOPHAGOCYTIC SYNDROME 218 60% 5% 241 Search HEMOPHAGOCYTIC+SYNDROME Search HEMOPHAGOCYTIC+SYNDROME
5 MACROPHAGE ACTIVATION SYNDROME 210 79% 3% 136 Search MACROPHAGE+ACTIVATION+SYNDROME Search MACROPHAGE+ACTIVATION+SYNDROME
6 HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 125 88% 1% 59 Search HAEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search HAEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
7 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 125 87% 1% 61 Search FAMILIAL+HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search FAMILIAL+HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
8 JUVENILE RHEUMATOID ARTHRITIS 124 43% 4% 223 Search JUVENILE+RHEUMATOID+ARTHRITIS Search JUVENILE+RHEUMATOID+ARTHRITIS
9 HEMOPHAGOCYTOSIS 116 60% 2% 126 Search HEMOPHAGOCYTOSIS Search HEMOPHAGOCYTOSIS
10 STILLS DISEASE 91 73% 1% 70 Search STILLS+DISEASE Search STILLS+DISEASE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 LYMPHOHISTIOCYTOSIS 391 70% 6% 323
2 MACROPHAGE ACTIVATION SYNDROME 269 69% 4% 231
3 ERYTHROPHAGOCYTIC LYMPHOHISTIOCYTOSIS 178 94% 1% 63
4 PERFORIN GENE MUTATIONS 129 100% 1% 36
5 SELECT CATEGORIES 122 86% 1% 62
6 KILLER CELL DYSFUNCTION 107 93% 1% 40
7 IDIOPATHIC ARTHRITIS 105 52% 3% 143
8 USSR DOUBLE BLIND 81 81% 1% 48
9 DISABILITY MEASUREMENT TOOL 72 91% 1% 30
10 FUO 72 91% 1% 30

Journals



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PEDIATRIC RHEUMATOLOGY 16 23% 1% 60

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
HLH-2004: Diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis 2007 769 51 92%
Familial and Acquired Hemophagocytic Lymphohistiocytosis 2012 103 56 91%
Adult-onset Still's disease 2014 21 170 87%
Macrophage activation syndrome in Kawasaki Disease: More common than we thought? 2015 2 19 84%
Macrophage activation syndrome as part of systemic juvenile idiopathic arthritis: diagnosis, genetics, pathophysiology and treatment 2012 58 112 79%
Juvenile idiopathic arthritis 2007 329 110 62%
Hemophagocytic syndromes 2007 211 43 88%
Hemophagocytic Lymphohistiocytosis An Update on Diagnosis and Pathogenesis 2013 27 121 81%
Advances in understanding the pathogenesis of HLH 2013 24 110 87%
Is There a Window of Opportunity for Treatment of Systemic Juvenile Idiopathic Arthritis? 2014 8 1 100%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PEDIAT RHEUMATOL 31 21% 2.6% 135
2 PAEDIAT PAEDIAT RHEUMATOL 19 74% 0.3% 14
3 PEDIAT HEMATOL IMMUNOL RHEUMATOL INFECT DI 15 88% 0.1% 7
4 PRINTO 15 73% 0.2% 11
5 PAEDIAT RHEUMATOL 14 25% 0.9% 50
6 SERV EPIDEMIOL CLIN BIOMETRIA 8 75% 0.1% 6
7 IRCCS G GASLINI 8 28% 0.5% 24
8 IST RICOVERO CURA CARATTERE SCI G GASLINI 8 62% 0.2% 8
9 INFORMAT MED 6 16% 0.7% 38
10 OXFORD REG PAEDIAT RHEUMATOL UNIT 6 100% 0.1% 4

Related classes at same level (level 2)



Rank Relatedness score Related classes
1 0.0000015365 CUTANEOUS TUBERCULOSIS//PANNICULITIS//SUBCUTANEOUS FAT NECROSIS
2 0.0000014307 RHEUMATOID ARTHRITIS//RHEUMATOLOGY//RHEUMATOL
3 0.0000013700 HERMANSKY PUDLAK SYNDROME//CHEDIAK HIGASHI SYNDROME//GRISCELLI SYNDROME
4 0.0000011476 LANGERHANS CELL HISTIOCYTOSIS//ROSAI DORFMAN DISEASE//HISTIOCYTOSIS
5 0.0000010874 FAMILIAL MEDITERRANEAN FEVER//CHRONIC URTICARIA//MEFV
6 0.0000008623 ARTHRITIS CARE AND RESEARCH//ARTHRITIS & RHEUMATISM-ARTHRITIS CARE & RESEARCH//HEALTH ASSESSMENT QUESTIONNAIRE
7 0.0000008389 ANKYLOSING SPONDYLITIS//HLA B27//SPONDYLOARTHRITIS
8 0.0000008277 INFECTION IMAGING//LEFT VENTRICULAR THROMBUS//NMRL
9 0.0000007763 MUSCULOSKELETAL EXAMINATION//AMBULATORY NEUROLOGICAL CARE//NEUROLOGICAL CARE
10 0.0000007606 DERMATOMYOSITIS//POLYMYOSITIS//INCLUSION BODY MYOSITIS