Class information for:
Level 1: PAROXYSMAL NOCTURNAL HEMOGLOBINURIA//PNH//PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
11312 925 33.7 75%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
332 17329 COMPLEMENT//MANNOSE BINDING LECTIN//PAROXYSMAL NOCTURNAL HEMOGLOBINURIA

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PAROXYSMAL NOCTURNAL HEMOGLOBINURIA Author keyword 303 74% 24% 222
2 PNH Author keyword 124 77% 9% 84
3 PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA Author keyword 71 68% 7% 63
4 PIG A Author keyword 25 58% 3% 29
5 ECULIZUMAB Author keyword 21 29% 7% 62
6 PAROXYSMAL NOCTURNAL HEMOGLOBINURIA PNH Author keyword 19 74% 2% 14
7 FLAER Author keyword 15 82% 1% 9
8 PIG A GENE Author keyword 15 63% 2% 15
9 PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA PNH Author keyword 11 78% 1% 7
10 HEMOGLOBINURIA Author keyword 9 36% 2% 21

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 PAROXYSMAL NOCTURNAL HEMOGLOBINURIA 303 74% 24% 222 Search PAROXYSMAL+NOCTURNAL+HEMOGLOBINURIA Search PAROXYSMAL+NOCTURNAL+HEMOGLOBINURIA
2 PNH 124 77% 9% 84 Search PNH Search PNH
3 PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA 71 68% 7% 63 Search PAROXYSMAL+NOCTURNAL+HAEMOGLOBINURIA Search PAROXYSMAL+NOCTURNAL+HAEMOGLOBINURIA
4 PIG A 25 58% 3% 29 Search PIG+A Search PIG+A
5 ECULIZUMAB 21 29% 7% 62 Search ECULIZUMAB Search ECULIZUMAB
6 PAROXYSMAL NOCTURNAL HEMOGLOBINURIA PNH 19 74% 2% 14 Search PAROXYSMAL+NOCTURNAL+HEMOGLOBINURIA+PNH Search PAROXYSMAL+NOCTURNAL+HEMOGLOBINURIA+PNH
7 FLAER 15 82% 1% 9 Search FLAER Search FLAER
8 PIG A GENE 15 63% 2% 15 Search PIG+A+GENE Search PIG+A+GENE
9 PAROXYSMAL NOCTURNAL HAEMOGLOBINURIA PNH 11 78% 1% 7 Search PAROXYSMAL+NOCTURNAL+HAEMOGLOBINURIA+PNH Search PAROXYSMAL+NOCTURNAL+HAEMOGLOBINURIA+PNH
10 HEMOGLOBINURIA 9 36% 2% 21 Search HEMOGLOBINURIA Search HEMOGLOBINURIA

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PIG A GENE 202 73% 17% 155
2 PNH 133 81% 9% 79
3 COMPLEMENT INHIBITOR ECULIZUMAB 72 55% 10% 90
4 HEMOGLOBINURIA 50 55% 7% 63
5 PIG A 45 56% 6% 54
6 PATHOGENETIC LINK 44 78% 3% 29
7 HEMOGLOBINURIA PNH 30 100% 1% 12
8 MINOR POPULATION 26 61% 3% 28
9 ANCHOR BIOSYNTHESIS 19 49% 3% 28
10 PAROXYSMAL NOCTURNAL HEMOGLOBINURIA 17 11% 16% 144

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Diagnosis and management of paroxysmal nocturnal hemoglobinuria 2005 251 69 77%
Anticomplement 05 therapy with eculizumab for the treatment of paroxysmal nocturnal hemoglobinuria and atypical hemolytic uremic syndrome 2015 2 98 46%
Paroxysmal nocturnal hemoglobinuria 2012 18 23 87%
Thrombosis in paroxysmal nocturnal hemoglobinuria 2013 32 110 48%
How I treat paroxysmal nocturnal hemoglobinuria 2009 53 47 74%
Management of Paroxysmal Nocturnal Haemoglobinuria: a personal view 2011 24 53 79%
Paroxysmal nocturnal hemoglobinuria 2014 6 75 76%
Mechanisms and clinical implications of thrombosis in paroxysmal nocturnal hemoglobinuria 2012 15 75 57%
Paroxysmal nocturnal hemoglobinuria and other complement-mediated hematological disorders 2012 16 46 50%
Advances in the diagnosis and therapy of paroxysmal nocturnal hemoglobinuria 2008 37 43 65%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 GENET GENE TRANSFER 4 75% 0.3% 3
2 HAEMATOL MALIGNANCY DIAGNOST SERV 2 16% 1.4% 13
3 PREVENT ENVIRONM UNIT 2 67% 0.2% 2
4 GERMAN RED CROSS BLOOD TRANSFUS SERV BADEN WURTTE 2 36% 0.4% 4
5 LANGONE CANC 2 43% 0.3% 3
6 BONE MARROW TRANSPLANTAT CLIN UNIT 1 100% 0.2% 2
7 CANC GENET GENE TRANSFER CORE 1 100% 0.2% 2
8 HEMATOL ONCOL SECT 111H 1 100% 0.2% 2
9 INSERM 728 1 100% 0.2% 2
10 CANC GENET GENE TRANSFER 1 40% 0.2% 2

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000242332 CD59//CRRY//CD55
2 0.0000147165 APLASTIC ANEMIA//SEVERE APLASTIC ANEMIA//APLASTIC ANAEMIA
3 0.0000133158 GLYCOSYLPHOSPHATIDYLINOSITOL//INOSITOL PHOSPHOGLYCAN//TRANSAMIDASE
4 0.0000073673 BUDD CHIARI SYNDROME//HEPATIC VEIN THROMBOSIS//HEPATIC VEINS THROMBOSIS
5 0.0000047674 ATYPICAL HEMOLYTIC UREMIC SYNDROME//FACTOR H//C3 GLOMERULOPATHY
6 0.0000043642 C8 ALPHA//C8 GAMMA//PROPERDIN DEFICIENCY
7 0.0000042833 CYCLIC THROMBOCYTOPENIA//CYCLICAL NEUTROPENIA//ACQUIRED AMEGAKARYOCYTIC THROMBOCYTOPENIA
8 0.0000041680 COMPSTATIN//COBRA VENOM FACTOR//STELLAR CHANCE S 401
9 0.0000032965 LIVER MICRONUCLEUS ASSAY//CD71 ANTIGEN//IWGT
10 0.0000028059 MR RENOGRAPHY//FUNCTIONAL RENAL IMAGING//CORTICOMEDULLARY DIFFERENTIATION