Class information for:
Level 1: SEVERE CONGENITAL NEUTROPENIA//HAX 1//CYCLIC NEUTROPENIA

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
11365 920 36.7 77%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
1830 5658 SEVERE CONGENITAL NEUTROPENIA//CYCLIC NEUTROPENIA//HAX 1

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 SEVERE CONGENITAL NEUTROPENIA Author keyword 166 82% 11% 98
2 HAX 1 Author keyword 58 75% 5% 42
3 CYCLIC NEUTROPENIA Author keyword 52 75% 4% 38
4 ELANE Author keyword 30 100% 1% 12
5 ELA2 Author keyword 27 92% 1% 11
6 CONGENITAL NEUTROPENIA Author keyword 26 56% 3% 31
7 G6PC3 Author keyword 25 77% 2% 17
8 KOSTMANN SYNDROME Author keyword 22 68% 2% 19
9 CHRONIC IDIOPATHIC NEUTROPENIA Author keyword 19 71% 2% 15
10 KOSTMANNS SYNDROME Author keyword 13 80% 1% 8

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 SEVERE CONGENITAL NEUTROPENIA 166 82% 11% 98 Search SEVERE+CONGENITAL+NEUTROPENIA Search SEVERE+CONGENITAL+NEUTROPENIA
2 HAX 1 58 75% 5% 42 Search HAX+1 Search HAX+1
3 CYCLIC NEUTROPENIA 52 75% 4% 38 Search CYCLIC+NEUTROPENIA Search CYCLIC+NEUTROPENIA
4 ELANE 30 100% 1% 12 Search ELANE Search ELANE
5 ELA2 27 92% 1% 11 Search ELA2 Search ELA2
6 CONGENITAL NEUTROPENIA 26 56% 3% 31 Search CONGENITAL+NEUTROPENIA Search CONGENITAL+NEUTROPENIA
7 G6PC3 25 77% 2% 17 Search G6PC3 Search G6PC3
8 KOSTMANN SYNDROME 22 68% 2% 19 Search KOSTMANN+SYNDROME Search KOSTMANN+SYNDROME
9 CHRONIC IDIOPATHIC NEUTROPENIA 19 71% 2% 15 Search CHRONIC+IDIOPATHIC+NEUTROPENIA Search CHRONIC+IDIOPATHIC+NEUTROPENIA
10 KOSTMANNS SYNDROME 13 80% 1% 8 Search KOSTMANNS+SYNDROME Search KOSTMANNS+SYNDROME

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 SEVERE CONGENITAL NEUTROPENIA 93 41% 19% 178
2 CYCLIC NEUTROPENIA 53 51% 8% 74
3 ELA2 50 88% 3% 23
4 INFANTILE GENETIC AGRANULOCYTOSIS 40 77% 3% 27
5 G CSF RECEPTOR 39 54% 5% 49
6 ORIGINAL KOSTMANN FAMILY 32 88% 2% 15
7 KOSTMANN SYNDROME 25 75% 2% 18
8 G CSF THERAPY 21 65% 2% 20
9 DISTINCT CYTOPLASMIC REGIONS 20 63% 2% 20
10 HAX1 MUTATIONS 18 89% 1% 8

Journals

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
Chronic neutrophilic leukemia: novel mutations and their impact on clinical practice 2015 2 15 67%
The diversity of mutations and clinical outcomes for ELANE-associated neutropenia 2015 1 24 83%
Clinical implications of ELA2-, HAX1-, and G-CSF-receptor (CSF3R) mutations in severe congenital neutropenia 2009 41 55 89%
Granulocyte colony-stimulating factor: Molecular mechanisms of action during steady state and 'emergency' hematopoiesis 2008 91 176 40%
Hematopoietic stem cell transplantation for severe congenital neutropenia 2012 7 46 91%
How we evaluate and treat neutropenia in adults 2014 4 44 45%
Neutrophil elastase in cyclic and severe congenital neutropenia 2007 104 82 52%
Genetic Defects in Severe Congenital Neutropenia: Emerging Insights into Life and Death of Human Neutrophil Granulocytes 2011 35 101 43%
A clinical and molecular review of ubiquitous glucose-6-phosphatase deficiency caused by G6PC3 mutations 2013 9 34 50%
CYCLIC NEUTROPENIA - A CLINICAL REVIEW 1988 124 20 95%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 UNIV CRETE 6 80% 0.4% 4
2 SEVERE CHRON NEUTROPENIA INT REGISTRY 6 71% 0.5% 5
3 MOL HEMATOPOIESIS 2 21% 1.1% 10
4 G SALESI WOMENS CHILDRENS HOSP 2 67% 0.2% 2
5 SECT PEDIAT LEUKEMIA LYMPHOMA 2 67% 0.2% 2
6 ABT MOL HAMATOPOESE 1 100% 0.2% 2
7 MOFID PEDIAT HOSP 1 100% 0.2% 2
8 SCNIR 1 100% 0.2% 2
9 SERV HEMATO ONCOL PEDIAT 1 21% 0.5% 5
10 ZELLULARE MOL ANAT ANAT 3 1 40% 0.2% 2

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000247754 CYCLIC THROMBOCYTOPENIA//CYCLICAL NEUTROPENIA//ACQUIRED AMEGAKARYOCYTIC THROMBOCYTOPENIA
2 0.0000172866 GFI1B//GFI1//ZELLBIOL TUMORFOR
3 0.0000129955 SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME
4 0.0000128758 G CSF//GM CSF//GRANULOCYTE COLONY STIMULATING FACTOR
5 0.0000127850 TRALI//TRANSFUSION RELATED ACUTE LUNG INJURY//HUMAN NEUTROPHIL ANTIGENS
6 0.0000094591 COHEN SYNDROME//COH1//VPS13B
7 0.0000073880 HYPOXIA ISCHEMIA HI//NEUROPROTECTIVE THERAPY//INHA NEURAL REPAIR
8 0.0000067594 LITHIUM RESISTANCE//4C4//BLOOD LITHIUM
9 0.0000066571 G CSF PRODUCING TUMOR//LEUKEMOID REACTION//LEUKOCYTOSIS
10 0.0000061405 GLYCOGEN STORAGE DISEASE TYPE III//SECT CELLULAR DIFFERENTIAT//GLUCOSE 6 PHOSPHATASE