Class information for:
Level 1: HUMAN GENET INFECT DIS//PEDIAT HEMATOL IMMUNOL UNIT//NECKER MED

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
11862 884 33.3 76%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1398 7605 COMMON VARIABLE IMMUNODEFICIENCY//PRIMARY IMMUNODEFICIENCY//IGA DEFICIENCY

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 HUMAN GENET INFECT DIS Address 44 36% 11% 99
2 PEDIAT HEMATOL IMMUNOL UNIT Address 30 49% 5% 44
3 NECKER MED Address 29 39% 7% 58
4 PEDIAT IMMUNOL HEMATOL UNIT Address 28 64% 3% 27
5 ST GILES HUMAN GENET INFECT DIS Address 27 35% 7% 62
6 ROCKEFELLER BRANCH Address 26 34% 7% 64
7 NECKER BRANCH Address 21 35% 5% 48
8 MENDELIAN SUSCEPTIBILITY TO MYCOBACTERIAL DISEASE Author keyword 21 85% 1% 11
9 STUDY PRIMARY IMMUNODEFICIENCIES Address 20 44% 4% 35
10 FRENCH CHINESE GENET LIFE SCI Address 17 100% 1% 8

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 MENDELIAN SUSCEPTIBILITY TO MYCOBACTERIAL DISEASE 21 85% 1% 11 Search MENDELIAN+SUSCEPTIBILITY+TO+MYCOBACTERIAL+DISEASE Search MENDELIAN+SUSCEPTIBILITY+TO+MYCOBACTERIAL+DISEASE
2 DISSEMINATED BCG INFECTION 12 86% 1% 6 Search DISSEMINATED+BCG+INFECTION Search DISSEMINATED+BCG+INFECTION
3 INTERFERON GAMMA RECEPTOR 1 DEFICIENCY 12 86% 1% 6 Search INTERFERON+GAMMA+RECEPTOR+1+DEFICIENCY Search INTERFERON+GAMMA+RECEPTOR+1+DEFICIENCY
4 MENDELIAN SUSCEPTIBILITY TO MYCOBACTERIAL DISEASES 12 86% 1% 6 Search MENDELIAN+SUSCEPTIBILITY+TO+MYCOBACTERIAL+DISEASES Search MENDELIAN+SUSCEPTIBILITY+TO+MYCOBACTERIAL+DISEASES
5 IL 12R BETA 1 DEFICIENCY 11 100% 1% 6 Search IL+12R+BETA+1+DEFICIENCY Search IL+12R+BETA+1+DEFICIENCY
6 MSMD 10 73% 1% 8 Search MSMD Search MSMD
7 BCG LYMPHADENITIS 6 100% 0% 4 Search BCG+LYMPHADENITIS Search BCG+LYMPHADENITIS
8 NUCLEAR FACTOR KAPPA B ESSENTIAL MODULATOR 4 67% 0% 4 Search NUCLEAR+FACTOR+KAPPA+B+ESSENTIAL+MODULATOR Search NUCLEAR+FACTOR+KAPPA+B+ESSENTIAL+MODULATOR
9 DISSEMINATED MYCOBACTERIUM AVIUM COMPLEX INFECTION 3 57% 0% 4 Search DISSEMINATED+MYCOBACTERIUM+AVIUM+COMPLEX+INFECTION Search DISSEMINATED+MYCOBACTERIUM+AVIUM+COMPLEX+INFECTION
10 INTERFERON GAMMA RECEPTOR DEFICIENCY 3 57% 0% 4 Search INTERFERON+GAMMA+RECEPTOR+DEFICIENCY Search INTERFERON+GAMMA+RECEPTOR+DEFICIENCY

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 CALMETTE GUERIN INFECTION 49 47% 9% 77
2 ESSENTIAL MODULATOR MUTATION 39 74% 3% 29
3 SMALL DELETION HOTSPOT 37 100% 2% 14
4 INHERITED INTERLEUKIN 12 DEFICIENCY 35 67% 4% 32
5 RECEPTOR BETA 1 DEFICIENCY 30 62% 4% 31
6 ANHIDROTIC ECTODERMAL DYSPLASIA 25 39% 6% 51
7 DISSEMINATED BCG INFECTION 23 79% 2% 15
8 IRAK 4 DEFICIENCY 21 69% 2% 18
9 MYCOBACTERIAL INFECTION 21 27% 8% 68
10 IL 12R BETA 1 DEFICIENCY 21 90% 1% 9

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Inborn errors of IL-12/23- and IFN-gamma-mediated immunity: molecular, cellular, and clinical features 2006 131 126 75%
Mendelian susceptibility to mycobacterial disease: Genetic, immunological, and clinical features of inborn errors of IFN-gamma immunity 2014 6 265 72%
Infectious Diseases in Patients with IRAK-4, MyD88, NEMO, or I kappa B alpha Deficiency 2011 73 64 73%
Genetic deficiencies of innate immune signalling in human infectious disease 2009 45 128 65%
The genetic heterogeneity of mendelian susceptibility to mycobacterial diseases 2008 81 89 75%
Inborn errors of interferon (IFN)-mediated immunity in humans: insights into the respective roles of IFN-alpha/beta, IFN-gamma, and IFN-lambda in host defense 2008 119 112 53%
Novel primary immunodeficiencies revealed by the investigation of paediatric infectious diseases 2008 59 77 77%
Genetic dissection of immunity to mycobacteria: The human model 2002 479 162 33%
Human interferon-gamma-mediated immunity is a genetically controlled continuous trait that determines the outcome of mycobacterial invasion 2000 88 21 100%
Primary immunodeficiencies of protective immunity to primary infections 2010 37 43 56%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 HUMAN GENET INFECT DIS 44 36% 11% 99
2 PEDIAT HEMATOL IMMUNOL UNIT 30 49% 5.0% 44
3 NECKER MED 29 39% 6.6% 58
4 PEDIAT IMMUNOL HEMATOL UNIT 28 64% 3.1% 27
5 ST GILES HUMAN GENET INFECT DIS 27 35% 7.0% 62
6 ROCKEFELLER BRANCH 26 34% 7.2% 64
7 NECKER BRANCH 21 35% 5.4% 48
8 STUDY PRIMARY IMMUNODEFICIENCIES 20 44% 4.0% 35
9 FRENCH CHINESE GENET LIFE SCI 17 100% 0.9% 8
10 GENET HUMAINE MALAD INFECT 16 37% 4.0% 35

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000131082 HYPER IGE SYNDROME//JOBS SYNDROME//JOB SYNDROME
2 0.0000130222 SLC11A1//NRAMP1//MCGILL STUDY HOST ISTANCE
3 0.0000110379 BCG//TUBERCULOSIS//LANZHOU TB
4 0.0000106503 TUBERCULIN SCREENING//HLTH EDUC HUMAN SERV//EX JEFE UNIDAD 9
5 0.0000094296 OMENN SYNDROME//SEVERE COMBINED IMMUNODEFICIENCY//T CELL LYMPHOPENIA
6 0.0000085899 INCONTINENTIA PIGMENTI//HYPOMELANOSIS OF ITO//BLOCH SULZBERGER SYNDROME
7 0.0000068042 COMMON VARIABLE IMMUNODEFICIENCY//IGA DEFICIENCY//CVID
8 0.0000065227 TIR DOMAIN//PELLINO//INNATE IMMUN INFLAMMAT
9 0.0000063270 ICES UOTTAWA//VACCINATION AGE//TUBERCULIN RESPONSE
10 0.0000058179 CHILDHOOD TUBERCULOSIS//DESMOND TUTU TB//TUBERCULOSIS IN CHILDREN