Class information for: |
Basic class information |
| ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
|---|---|---|---|
| 12382 | 846 | 26.1 | 62% |
Classes in level above (level 2) |
| ID, lev. above |
Publications | Label for level above |
|---|---|---|
| 3340 | 1269 | ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID |
Terms with highest relevance score |
| Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
|---|---|---|---|---|---|---|
| 1 | TYROSINEMIA | Author keyword | 58 | 68% | 6% | 50 |
| 2 | NTBC | Author keyword | 53 | 89% | 3% | 24 |
| 3 | SUCCINYLACETONE | Author keyword | 44 | 77% | 4% | 30 |
| 4 | TYROSINEMIA TYPE II | Author keyword | 30 | 100% | 1% | 12 |
| 5 | TYROSINEMIA TYPE I | Author keyword | 30 | 79% | 2% | 19 |
| 6 | FUMARYLACETOACETATE HYDROLASE | Author keyword | 23 | 69% | 2% | 20 |
| 7 | TYROSINEMIA TYPE 1 | Author keyword | 21 | 85% | 1% | 11 |
| 8 | 4 HYDROXYPHENYLPYRUVATE DIOXYGENASE | Author keyword | 17 | 57% | 2% | 20 |
| 9 | HEREDITARY TYROSINEMIA TYPE 1 | Author keyword | 17 | 79% | 1% | 11 |
| 10 | HEREDITARY TYROSINEMIA | Author keyword | 15 | 77% | 1% | 10 |
Web of Science journal categories |
Author Key Words |
| Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
|---|---|---|---|---|---|---|---|
| 1 | TYROSINEMIA | 58 | 68% | 6% | 50 | Search TYROSINEMIA | Search TYROSINEMIA |
| 2 | NTBC | 53 | 89% | 3% | 24 | Search NTBC | Search NTBC |
| 3 | SUCCINYLACETONE | 44 | 77% | 4% | 30 | Search SUCCINYLACETONE | Search SUCCINYLACETONE |
| 4 | TYROSINEMIA TYPE II | 30 | 100% | 1% | 12 | Search TYROSINEMIA+TYPE+II | Search TYROSINEMIA+TYPE+II |
| 5 | TYROSINEMIA TYPE I | 30 | 79% | 2% | 19 | Search TYROSINEMIA+TYPE+I | Search TYROSINEMIA+TYPE+I |
| 6 | FUMARYLACETOACETATE HYDROLASE | 23 | 69% | 2% | 20 | Search FUMARYLACETOACETATE+HYDROLASE | Search FUMARYLACETOACETATE+HYDROLASE |
| 7 | TYROSINEMIA TYPE 1 | 21 | 85% | 1% | 11 | Search TYROSINEMIA+TYPE+1 | Search TYROSINEMIA+TYPE+1 |
| 8 | 4 HYDROXYPHENYLPYRUVATE DIOXYGENASE | 17 | 57% | 2% | 20 | Search 4+HYDROXYPHENYLPYRUVATE+DIOXYGENASE | Search 4+HYDROXYPHENYLPYRUVATE+DIOXYGENASE |
| 9 | HEREDITARY TYROSINEMIA TYPE 1 | 17 | 79% | 1% | 11 | Search HEREDITARY+TYROSINEMIA+TYPE+1 | Search HEREDITARY+TYROSINEMIA+TYPE+1 |
| 10 | HEREDITARY TYROSINEMIA | 15 | 77% | 1% | 10 | Search HEREDITARY+TYROSINEMIA | Search HEREDITARY+TYROSINEMIA |
Key Words Plus |
| Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
|---|---|---|---|---|---|
| 1 | HEREDITARY TYROSINEMIA | 166 | 65% | 19% | 159 |
| 2 | 4 HYDROXYPHENYLPYRUVATE DIOXYGENASE | 107 | 59% | 14% | 119 |
| 3 | 2 2 NITRO 4 TRIFLUOROMETHYLBENZOYL 1 3 CYCLOHEXANEDIONE | 57 | 95% | 2% | 19 |
| 4 | FUMARYLACETOACETATE | 50 | 88% | 3% | 23 |
| 5 | NTBC | 44 | 77% | 4% | 30 |
| 6 | FUMARYLACETOACETATE HYDROLASE GENE | 35 | 89% | 2% | 16 |
| 7 | HEPATORENAL TYROSINEMIA | 33 | 77% | 3% | 23 |
| 8 | P HYDROXYPHENYLPYRUVATE DIOXYGENASE | 31 | 46% | 6% | 50 |
| 9 | NTBC TREATMENT | 31 | 92% | 1% | 12 |
| 10 | TYROSINEMIA TYPE I | 30 | 31% | 10% | 81 |
Journals |
Reviews |
| Title | Publ. year | Cit. | Active references |
% act. ref. to same field |
|---|---|---|---|---|
| Recommendations for the management of tyrosinaemia type 1 | 2013 | 13 | 31 | 94% |
| 4-Hydroxyphenylpyruvate dioxygenase and hydroxymandelate synthase: Exemplars of the alpha-keto acid dependent oxygenases | 2014 | 4 | 88 | 44% |
| 4-Hydroxyphenylpyruvate dioxygenase | 2005 | 82 | 86 | 42% |
| Hepatorenal tyrosinemia | 2012 | 3 | 12 | 100% |
| Experience of nitisinone for the pharmacological treatment of hereditary tyrosinaemia type 1 | 2008 | 16 | 49 | 94% |
| Tyrosinemia: A review | 2001 | 67 | 70 | 81% |
| A review of the mode of toxicity and relevance to humans of the triketone herbicide 2-(4-methylsulfonyl-2-nitrobenzoyl)-1, 3-cyclohexanedione | 2013 | 2 | 16 | 81% |
| The pathophysiology and treatment of hereditary tyrosinemia type 1 | 2001 | 59 | 69 | 70% |
| Diagnosis and treatment of hereditary tyrosinemia in Japan | 2015 | 0 | 11 | 100% |
| Hereditary tyrosinaemia type I: from basics to progress in treatment | 2000 | 8 | 72 | 86% |
Address terms |
| Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
|---|---|---|---|---|---|
| 1 | ERROS INATOS METAB | 2 | 18% | 0.9% | 8 |
| 2 | LCBE | 1 | 40% | 0.2% | 2 |
| 3 | CELL DEV GENET | 1 | 12% | 0.9% | 8 |
| 4 | CELLULAR DEV GENET | 1 | 17% | 0.6% | 5 |
| 5 | ARTHUR F SCOTT CHEM | 1 | 33% | 0.2% | 2 |
| 6 | PHYSIOL GENET PLANTES INTERET AGRON | 1 | 33% | 0.2% | 2 |
| 7 | CIBERERIDIPAZ | 1 | 50% | 0.1% | 1 |
| 8 | CIENCIAS MEDCATEDRA CLIN PEDIAT | 1 | 50% | 0.1% | 1 |
| 9 | INFIQC ORGAN CHEM | 1 | 50% | 0.1% | 1 |
| 10 | KEY DISCIPLINE BIOL ENGN HEBEI PROV | 1 | 50% | 0.1% | 1 |
Related classes at same level (level 1) |
| Rank | Relatedness score | Related classes |
|---|---|---|
| 1 | 0.0000173747 | ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID |
| 2 | 0.0000077459 | HOMOGENTISATE PHYTYLTRANSFERASE//GAMMA TOCOPHEROL METHYLTRANSFERASE//PLASTOCHROMANOL |
| 3 | 0.0000070226 | POLYUNSATURATED FREE FATTY ACID//BRUSH BORDERS//ISF PHARM |
| 4 | 0.0000047265 | PHOSPHOENOLPYRUVATE CARBOXYKINASE//GLYCERONEOGENESIS//PHOSPHOENOLPYRUVATE CARBOXYKINASE GENE |
| 5 | 0.0000045227 | 8 AZASTEROIDS//8 AZASTEROID//1 ALKYL 3 4 DIHYDROISOQUINOLINES |
| 6 | 0.0000042449 | MET BIOCATALYSIS//BIOMIMET SYST//NONHEME IRON ENZYMES |
| 7 | 0.0000039917 | IMINE ENAMINE//MINDO FORCES//KETO ENOL EQUILIBRIA |
| 8 | 0.0000036481 | MCAD DEFICIENCY//MEDIUM CHAIN ACYL COA DEHYDROGENASE DEFICIENCY//UNIT MOL MED |
| 9 | 0.0000031805 | URINARY DELTA AMINOLEVULINIC ACID//URINOMETER//URINE SPECIFIC GRAVITY |
| 10 | 0.0000031795 | METHYLMALONIC ACIDEMIA//PROPIONIC ACIDEMIA//METHYLMALONIC ACIDURIA |