Class information for:
Level 1: CADASIL//NOTCH3//NOTCH3 GENE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
13024 802 32.3 85%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1798 5763 BILIARY ATRESIA//CADASIL//NOTCH3

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 CADASIL Author keyword 643 83% 46% 367
2 NOTCH3 Author keyword 88 56% 13% 108
3 NOTCH3 GENE Author keyword 86 96% 3% 26
4 CARASIL Author keyword 31 92% 1% 12
5 U740 Address 26 67% 3% 24
6 COL4A1 Author keyword 22 68% 2% 19
7 CEREBRAL AUTOSOMAL DOMINANT ARTERIOPATHY WITH SUBCORTICAL INFARCTS AND LEUKOENCEPHALOPATHY Author keyword 19 80% 1% 12
8 CEREBRAL AUTOSOMAL DOMINANT ARTERIOPATHY WITH SUBCORTICAL INFARCTS AND LEUKOENCEPHALOPATHY CADASIL Author keyword 15 88% 1% 7
9 GRANULAR OSMIOPHILIC MATERIAL Author keyword 14 100% 1% 7
10 NOTCH 3 GENE Author keyword 14 100% 1% 7

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 CADASIL 643 83% 46% 367 Search CADASIL Search CADASIL
2 NOTCH3 88 56% 13% 108 Search NOTCH3 Search NOTCH3
3 NOTCH3 GENE 86 96% 3% 26 Search NOTCH3+GENE Search NOTCH3+GENE
4 CARASIL 31 92% 1% 12 Search CARASIL Search CARASIL
5 COL4A1 22 68% 2% 19 Search COL4A1 Search COL4A1
6 CEREBRAL AUTOSOMAL DOMINANT ARTERIOPATHY WITH SUBCORTICAL INFARCTS AND LEUKOENCEPHALOPATHY 19 80% 1% 12 Search CEREBRAL+AUTOSOMAL+DOMINANT+ARTERIOPATHY+WITH+SUBCORTICAL+INFARCTS+AND+LEUKOENCEPHALOPATHY Search CEREBRAL+AUTOSOMAL+DOMINANT+ARTERIOPATHY+WITH+SUBCORTICAL+INFARCTS+AND+LEUKOENCEPHALOPATHY
7 CEREBRAL AUTOSOMAL DOMINANT ARTERIOPATHY WITH SUBCORTICAL INFARCTS AND LEUKOENCEPHALOPATHY CADASIL 15 88% 1% 7 Search CEREBRAL+AUTOSOMAL+DOMINANT+ARTERIOPATHY+WITH+SUBCORTICAL+INFARCTS+AND+LEUKOENCEPHALOPATHY+CADASIL Search CEREBRAL+AUTOSOMAL+DOMINANT+ARTERIOPATHY+WITH+SUBCORTICAL+INFARCTS+AND+LEUKOENCEPHALOPATHY+CADASIL
8 GRANULAR OSMIOPHILIC MATERIAL 14 100% 1% 7 Search GRANULAR+OSMIOPHILIC+MATERIAL Search GRANULAR+OSMIOPHILIC+MATERIAL
9 NOTCH 3 GENE 14 100% 1% 7 Search NOTCH+3+GENE Search NOTCH+3+GENE
10 GOM 10 61% 1% 11 Search GOM Search GOM

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 SUBCORTICAL INFARCTS 469 78% 38% 307
2 AUTOSOMAL DOMINANT ARTERIOPATHY 367 69% 39% 311
3 LEUKOENCEPHALOPATHY CADASIL 285 93% 13% 107
4 NOTCH3 MUTATIONS 202 82% 15% 118
5 CADASIL 66 45% 14% 112
6 LEUKOENCEPHALOPATHY 43 20% 24% 195
7 CADASIL PATIENTS 33 67% 4% 29
8 CONDITION CAUSING STROKE 25 73% 2% 19
9 NOTCH3 GENE 24 82% 2% 14
10 COLLAGEN IV A1 22 81% 2% 13

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
CADASIL 2009 195 114 91%
COL4A1 Mutations as a Monogenic Cause of Cerebral Small Vessel Disease A Systematic Review 2010 43 21 90%
Diagnostic strategies in CADASIL 2002 134 19 95%
Interpretation of NOTCH3 mutations in the diagnosis of CADASIL 2014 5 81 96%
Cerebral hemorrhages in CADASIL: Report of four cases and a brief review 2013 12 20 85%
Molecular genetics and pathology of hereditary small vessel diseases of the brain 2011 28 151 71%
Notch and disease: A growing field 2012 44 109 30%
Hereditary cerebral small vessel diseases: A review 2012 16 31 65%
Pathogenesis of CADASIL Transgenic and knock-out mice to probe function and dysfunction of the mutated gene, Notch3, in the cerebrovasculature 2011 23 55 65%
Lacunar Infarction and Small Vessel Disease: Pathology and Pathophysiology 2015 2 12 25%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 U740 26 67% 3.0% 24
2 UMR S 1161 4 75% 0.4% 3
3 STROKE DEMENTIA 3 12% 3.2% 26
4 GRP HOSP LARIBOISIERE FERNAND WIDAL 3 35% 0.9% 7
5 E365 3 50% 0.5% 4
6 UMR740 3 60% 0.4% 3
7 IMSEB 2 67% 0.2% 2
8 NEUROVASC TREATMENT UNIT 2 67% 0.2% 2
9 SITE LARIBOISIERE 2 67% 0.2% 2
10 UMR S740 2 36% 0.5% 4

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000120199 CHROMOSOME 12P13//PRKCH//PDE4D
2 0.0000115945 LEUKOARAIOSIS//WHITE MATTER LESIONS//WHITE MATTER HYPERINTENSITIES
3 0.0000088841 VASCULAR DEMENTIA//POSTSTROKE DEMENTIA//VASCULAR COGNITIVE IMPAIRMENT
4 0.0000072614 CEREBRAL AMYLOID ANGIOPATHY//CEREBRAL MICROBLEEDS//MICROBLEEDS
5 0.0000065734 FAMILIAL HEMIPLEGIC MIGRAINE//HEMIPLEGIC MIGRAINE//ALTERNATING HEMIPLEGIA OF CHILDHOOD
6 0.0000064444 MIGRAINE WITH AURA//SERV CLIN GOVERNANCE//MIGRAINOUS INFARCT
7 0.0000059981 NOTCH//NOTCH SIGNALING//NOTCH1
8 0.0000054810 ALEXANDER DISEASE//LEUKODYSTROPHY//VANISHING WHITE MATTER DISEASE
9 0.0000051265 SUSAC SYNDROME//SUSACS SYNDROME//ENDOTHELIOPATHY
10 0.0000045395 AICARDI GOUTIERES SYNDROME//TREX1//RIBONUCLEASE H