Class information for:
Level 1: PROTEUS SYNDROME//MACRODACTYLY//MACRODYSTROPHIA LIPOMATOSA

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
15682 628 19.3 59%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
1088 9330 STURGE WEBER SYNDROME//INFANTILE HEMANGIOMA//HEMANGIOMA

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 PROTEUS SYNDROME Author keyword 190 79% 19% 120
2 MACRODACTYLY Author keyword 89 79% 9% 57
3 MACRODYSTROPHIA LIPOMATOSA Author keyword 41 85% 4% 22
4 LIPOFIBROMATOUS HAMARTOMA Author keyword 32 85% 3% 17
5 FIBROLIPOMATOUS HAMARTOMA Author keyword 32 78% 3% 21
6 LIPOMATOSIS OF NERVE Author keyword 17 79% 2% 11
7 NEURAL FIBROLIPOMA Author keyword 14 100% 1% 7
8 HEMIHYPERTROPHY Author keyword 11 33% 5% 29
9 CLOVES SYNDROME Author keyword 8 75% 1% 6
10 ASYMMETRIC OVERGROWTH Author keyword 6 80% 1% 4

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 PROTEUS SYNDROME 190 79% 19% 120 Search PROTEUS+SYNDROME Search PROTEUS+SYNDROME
2 MACRODACTYLY 89 79% 9% 57 Search MACRODACTYLY Search MACRODACTYLY
3 MACRODYSTROPHIA LIPOMATOSA 41 85% 4% 22 Search MACRODYSTROPHIA+LIPOMATOSA Search MACRODYSTROPHIA+LIPOMATOSA
4 LIPOFIBROMATOUS HAMARTOMA 32 85% 3% 17 Search LIPOFIBROMATOUS+HAMARTOMA Search LIPOFIBROMATOUS+HAMARTOMA
5 FIBROLIPOMATOUS HAMARTOMA 32 78% 3% 21 Search FIBROLIPOMATOUS+HAMARTOMA Search FIBROLIPOMATOUS+HAMARTOMA
6 LIPOMATOSIS OF NERVE 17 79% 2% 11 Search LIPOMATOSIS+OF+NERVE Search LIPOMATOSIS+OF+NERVE
7 NEURAL FIBROLIPOMA 14 100% 1% 7 Search NEURAL+FIBROLIPOMA Search NEURAL+FIBROLIPOMA
8 HEMIHYPERTROPHY 11 33% 5% 29 Search HEMIHYPERTROPHY Search HEMIHYPERTROPHY
9 CLOVES SYNDROME 8 75% 1% 6 Search CLOVES+SYNDROME Search CLOVES+SYNDROME
10 ASYMMETRIC OVERGROWTH 6 80% 1% 4 Search ASYMMETRIC+OVERGROWTH Search ASYMMETRIC+OVERGROWTH

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 LIPOFIBROMATOUS HAMARTOMA 53 78% 6% 35
2 MACRODYSTROPHIA LIPOMATOSA 27 72% 3% 21
3 HEMIHYPERTROPHY 27 38% 9% 56
4 FIBROLIPOMATOUS HAMARTOMA 25 54% 5% 32
5 PROTEUS SYNDROME 18 27% 9% 58
6 FIBRO FATTY PROLIFERATION 17 100% 1% 8
7 NEURAL FIBROLIPOMA 14 100% 1% 7
8 INTRANEURAL LIPOMA 11 100% 1% 6
9 ELEPHANT MAN 11 78% 1% 7
10 ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS 10 38% 4% 22

Journals

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
Proteus syndrome review: molecular, clinical, and pathologic features 2014 7 22 91%
Reassessment of the proteus syndrome literature: Application of diagnostic criteria to published cases 2004 76 100 89%
Lipofibromatous hamartoma of the median nerve 2010 10 12 92%
Lipofibromatous hamartoma of the upper extremity: A review of the radiologic findings for 15 patients 2006 21 23 96%
Lipofibromatous Hamartoma of the Median Nerve: A Comprehensive Review and Systematic Approach to Evaluation, Diagnosis, and Treatment 2013 3 76 87%
Congenital infiltrating lipomatosis of the face with exophytic temporomandibular joint ankylosis: a case report and review of the literature 2013 3 25 76%
Genital tract tumors in proteus syndrome: Report of a case of bilateral paraovarian endometrioid cystic tumors of borderline malignancy and review of the literature 2002 10 12 100%
Macrodactyly: Report of eight cases and review of the literature 2000 25 14 86%
Intrinsic haemangioma of the median nerve: Report of a case and review of the literature 2008 3 4 100%
Neural lipofibromatous hamartoma - A report of two cases and review of the literature 2007 6 27 100%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ.
in class
1 CHARLES E SEAY JR HAND 2 67% 0.3% 2
2 STOMATOL MAXILLO IAL SURG PLAST SURG 1 100% 0.3% 2
3 CHIRURG MEMBRE SUPER 1 50% 0.2% 1
4 GEN PEDIATR 1 50% 0.2% 1
5 GRP C S COMP AIDED PLAST SURG 1 50% 0.2% 1
6 INSERMUMRS 903 1 50% 0.2% 1
7 LU 51 1 50% 0.2% 1
8 MANCHESTER GENOM MEDMAHSC 1 50% 0.2% 1
9 NEONATOL NICU SECT 1 50% 0.2% 1
10 NORTH SHORE LIJ HEALTHCARE SYST 1 50% 0.2% 1

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000267442 KLIPPEL TRENAUNAY SYNDROME//KLIPPEL TRENAUNAY WEBER SYNDROME//RASA1
2 0.0000140271 ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS//EPIDERMAL NEVUS SYNDROME//OCULOCEREBROCUTANEOUS SYNDROME
3 0.0000099302 LIPOBLASTOMA//LIPOBLASTOMATOSIS//LIPOFIBROMATOSIS
4 0.0000096549 INTRAOSSEOUS LIPOMA//CHONDROLIPOMA//SIALOLIPOMA
5 0.0000068149 MADELUNGS DISEASE//ADIPOSIS DOLOROSA//DERCUMS DISEASE
6 0.0000065553 ADAMS OLIVER SYNDROME//APLASIA CUTIS CONGENITA//SETLEIS SYNDROME
7 0.0000062869 SOTOS SYNDROME//WEAVER SYNDROME//CEREBRAL GIGANTISM
8 0.0000058976 BRACHYMETATARSIA//CONGENITAL BRACHYMETATARSIA//METATARSAL LENGTHENING
9 0.0000056287 MEDULLARY SPONGE KIDNEY//NEPHROCALCINOSIS//RENAL HYPERECHOGENICITY
10 0.0000056097 NEUROMUSCULAR HAMARTOMA//RHABDOMYOMA//FETAL RHABDOMYOMA