Class information for:
Level 1: BETHLEM MYOPATHY//COLLAGEN VI//TYPE VI COLLAGEN

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
15876 618 38.5 80%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1091 9322 OSTEOGENESIS IMPERFECTA//EHLERS DANLOS SYNDROME//EHLERS DANLOS SYNDROME TYPE IV

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BETHLEM MYOPATHY Author keyword 50 84% 4% 27
2 COLLAGEN VI Author keyword 47 58% 9% 54
3 TYPE VI COLLAGEN Author keyword 39 49% 10% 59
4 ULLRICH CONGENITAL MUSCULAR DYSTROPHY Author keyword 27 76% 3% 19
5 NG2 PROTEOGLYCAN Author keyword 11 52% 2% 15
6 COLLAGEN TYPE VI Author keyword 8 41% 3% 16
7 COL6A2 Author keyword 8 100% 1% 5
8 ULLRICHS DISEASE Author keyword 8 100% 1% 5
9 MED SURG CLIN CARE Address 4 75% 0% 3
10 TRIPLE HELICAL DOMAIN Author keyword 4 75% 0% 3

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 BETHLEM MYOPATHY 50 84% 4% 27 Search BETHLEM+MYOPATHY Search BETHLEM+MYOPATHY
2 COLLAGEN VI 47 58% 9% 54 Search COLLAGEN+VI Search COLLAGEN+VI
3 TYPE VI COLLAGEN 39 49% 10% 59 Search TYPE+VI+COLLAGEN Search TYPE+VI+COLLAGEN
4 ULLRICH CONGENITAL MUSCULAR DYSTROPHY 27 76% 3% 19 Search ULLRICH+CONGENITAL+MUSCULAR+DYSTROPHY Search ULLRICH+CONGENITAL+MUSCULAR+DYSTROPHY
5 NG2 PROTEOGLYCAN 11 52% 2% 15 Search NG2+PROTEOGLYCAN Search NG2+PROTEOGLYCAN
6 COLLAGEN TYPE VI 8 41% 3% 16 Search COLLAGEN+TYPE+VI Search COLLAGEN+TYPE+VI
7 COL6A2 8 100% 1% 5 Search COL6A2 Search COL6A2
8 ULLRICHS DISEASE 8 100% 1% 5 Search ULLRICHS+DISEASE Search ULLRICHS+DISEASE
9 TRIPLE HELICAL DOMAIN 4 75% 0% 3 Search TRIPLE+HELICAL+DOMAIN Search TRIPLE+HELICAL+DOMAIN
10 LONG SPACING COLLAGEN 4 56% 1% 5 Search LONG+SPACING+COLLAGEN Search LONG+SPACING+COLLAGEN

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BETHLEM MYOPATHY 69 60% 12% 75
2 GLOBULAR DOMAINS 50 52% 11% 68
3 COL6A1 GENE 48 100% 3% 17
4 ULLRICH DISEASE 41 100% 2% 15
5 INTIMA COLLAGEN 40 82% 4% 23
6 ALPHA 3VI CHAIN 38 93% 2% 14
7 LIMB GIRDLE MYOPATHY 20 100% 1% 9
8 ALPHA 2VI CHAINS 14 100% 1% 7
9 ALPHA 3 CHAIN 13 26% 7% 45
10 IN FRAME DELETION 12 47% 3% 18

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Ullrich congenital muscular dystrophy: clinicopathological features, natural history and pathomechanism(s) 2015 1 56 77%
The collagen VI-related myopathies: muscle meets its matrix 2011 43 110 75%
Collagen VI related muscle disorders 2005 174 114 81%
ColVI myopathies: where do we stand, where do we go? 2011 26 103 76%
The expanded collagen VI family: new chains and new questions 2013 5 40 70%
Collagen VI in cancer and its biological mechanisms 2013 9 81 35%
Therapy of collagen VI-related myopathies (Bethlem and Ullrich) 2008 14 30 67%
CSPG4 in Cancer: Multiple Roles 2010 34 55 27%
Theranostic Impact of NG2/CSPG4 Proteoglycan in Cancer 2015 0 150 37%
Functional and Clinical Relevance of Chondroitin Sulfate Proteoglycan 4 2010 22 162 22%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 MED SURG CLIN CARE 4 75% 0.5% 3
2 COMT MOL TRANSLAT ONCOL 3 50% 0.6% 4
3 MUSCULOSKELETAL CELL BIOL 2 19% 1.5% 9
4 NEUROMUSCULAR NEUROGENET DISORDERS CHILDHOOD SE 2 26% 1.0% 6
5 CARDIOGENET MYOGENET FUNCT UNIT 1 50% 0.3% 2
6 NEUROSCI MOL MED 1 50% 0.3% 2
7 SOC EXPT ONCOL 2 1 50% 0.3% 2
8 CANC AVIANO 1 33% 0.5% 3
9 NEUROMUSCULAR PATHOL 1 20% 0.8% 5
10 EXPT NEUROONCOL GRP 1 30% 0.5% 3

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000195789 COLLAGEN XVI//TYPE XI COLLAGEN//COLLAGEN XII
2 0.0000192264 RIGID SPINE SYNDROME//RIGID SPINE//EMERINOPATHY
3 0.0000102288 CONGENITAL MUSCULAR DYSTROPHY//DYSTROGLYCAN//MUSCLE EYE BRAIN DISEASE
4 0.0000067506 LARP6//ALPHA 2I COLLAGEN//DERIVATIVE OF ERYTHROMYCIN
5 0.0000060679 POLYVALENT ANTIGEN//AUTOLOGOUS ANTIBODY//B700
6 0.0000059484 PERICYTES//PERICYTE//BOVINE RETINAL PERICYTES
7 0.0000055774 JUVENILE HYALINE FIBROMATOSIS//INFANTILE SYSTEMIC HYALINOSIS//SYSTEMIC HYALINOSIS
8 0.0000052875 DECORIN//LUMICAN//BIGLYCAN
9 0.0000052761 FRASER SYNDROME//CRYPTOPHTHALMOS//FRAS1
10 0.0000051441 MARFAN SYNDROME//FIBRILLIN//FBN1