Class information for:
Level 1: SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
19009 459 25.7 69%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
507 14507 ACUTE PANCREATITIS//CHRONIC PANCREATITIS//PANCREATITIS

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 SHWACHMAN DIAMOND SYNDROME Author keyword 96 73% 16% 73
2 SBDS Author keyword 41 85% 5% 22
3 SHWACHMAN SYNDROME Author keyword 26 100% 2% 11
4 LIPOMATOUS PSEUDOHYPERTROPHY Author keyword 9 83% 1% 5
5 PANCREAS VOLUME Author keyword 6 80% 1% 4
6 PANCREATIC STEATOSIS Author keyword 6 80% 1% 4
7 SHWACHMAN DIAMOND Author keyword 6 80% 1% 4
8 FATTY PANCREAS Author keyword 6 71% 1% 5
9 SBDS GENE Author keyword 6 100% 1% 4
10 SCHWACHMAN DIAMOND SYNDROME Author keyword 6 100% 1% 4

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 SHWACHMAN DIAMOND SYNDROME 96 73% 16% 73 Search SHWACHMAN+DIAMOND+SYNDROME Search SHWACHMAN+DIAMOND+SYNDROME
2 SBDS 41 85% 5% 22 Search SBDS Search SBDS
3 SHWACHMAN SYNDROME 26 100% 2% 11 Search SHWACHMAN+SYNDROME Search SHWACHMAN+SYNDROME
4 LIPOMATOUS PSEUDOHYPERTROPHY 9 83% 1% 5 Search LIPOMATOUS+PSEUDOHYPERTROPHY Search LIPOMATOUS+PSEUDOHYPERTROPHY
5 PANCREAS VOLUME 6 80% 1% 4 Search PANCREAS+VOLUME Search PANCREAS+VOLUME
6 PANCREATIC STEATOSIS 6 80% 1% 4 Search PANCREATIC+STEATOSIS Search PANCREATIC+STEATOSIS
7 SHWACHMAN DIAMOND 6 80% 1% 4 Search SHWACHMAN+DIAMOND Search SHWACHMAN+DIAMOND
8 FATTY PANCREAS 6 71% 1% 5 Search FATTY+PANCREAS Search FATTY+PANCREAS
9 SBDS GENE 6 100% 1% 4 Search SBDS+GENE Search SBDS+GENE
10 SCHWACHMAN DIAMOND SYNDROME 6 100% 1% 4 Search SCHWACHMAN+DIAMOND+SYNDROME Search SCHWACHMAN+DIAMOND+SYNDROME

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 SBDS 38 66% 8% 35
2 DIAMOND SYNDROME 27 92% 2% 11
3 EXOCRINE PANCREATIC DYSFUNCTION 24 68% 5% 21
4 SBDS MUTATIONS 18 89% 2% 8
5 SBDS GENE 17 79% 2% 11
6 INTRAPANCREATIC LIPOMA 11 67% 2% 10
7 HYPERECHOGENIC PANCREAS 11 100% 1% 6
8 BLACKFAN ANEMIA 5 37% 2% 10
9 SHWACHMAN DIAMOND SYNDROME 5 17% 5% 25
10 LIPOMATOUS PSEUDOHYPERTROPHY 3 60% 1% 3

Journals

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
Shwachman-Diamond syndrome 2002 79 56 82%
Shwachman-Diamond Syndrome: A Review of the Clinical Presentation,, Molecular Pathogenesis, Diagnosis, and Treatment 2009 35 65 83%
Shwachman-Diamond syndrome 2005 52 71 80%
Bone marrow transplantation in Shwachman-Diamond syndrome: Report of two cases and review of the literature 1998 30 11 91%
Shwachman - Diamond syndrome: UK perspective 2006 17 20 90%
Primary Leiomyosarcoma of the Pancreas Study of 9 Cases and Review of Literature 2010 10 16 88%
The clinical significance of pancreatic steatosis 2011 21 108 44%
A clinical algorithm predicts hematological complications in Shwachman-Diamond syndrome? 2012 1 16 94%
Marrow failure: a window into ribosome biology 2014 6 120 30%
Focal Fatty Infiltration in the Head of the Pancreas: Evaluation With Multidetector Computed Tomography With Multiplanar Reformation Imaging 2009 8 20 70%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ.
in class
1 MARROW FAILURE MYELODYSPLASIA PROGRAM 1 31% 0.9% 4
2 GASTROENTEROL NUTR PAEDIAT 1 100% 0.4% 2
3 PROGRAM INTEGRAT BIOL 1 18% 1.5% 7
4 INFECT IMMUNOL INJURY REPAIR PROGRAM 1 40% 0.4% 2
5 AFFILIATED HOSP 1MINIST PUBL HLTH ORGAN 1 50% 0.2% 1
6 COPROL FONCTIONNELLE 1 50% 0.2% 1
7 LIFESPAN MED CYTOGENET 1 50% 0.2% 1
8 NUTR SCI BRANCH 1 50% 0.2% 1
9 RADYOL ANA BILIM DALI 1 50% 0.2% 1
10 SCI MED LAVORO 1 50% 0.2% 1

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000129955 SEVERE CONGENITAL NEUTROPENIA//HAX 1//CYCLIC NEUTROPENIA
2 0.0000120196 DISTAL INTESTINAL OBSTRUCTION SYNDROME//FIBROSING COLONOPATHY//MECONIUM ILEUS EQUIVALENT
3 0.0000119608 DIAMOND BLACKFAN ANEMIA//RPS19//TRANSIENT ERYTHROBLASTOPENIA OF CHILDHOOD
4 0.0000098252 DYSKERATOSIS CONGENITA//HOYERAAL HREIDARSSON SYNDROME//DYSKERIN
5 0.0000097920 PANCREAS DIVISUM//ACCESSORY PANCREATIC DUCT//SANTORINICELE
6 0.0000073219 ARGINYLATION//JOHANSON BLIZZARD SYNDROME//N END RULE
7 0.0000069805 EXOCRINE PANCREATIC INSUFFICIENCY//STEATORRHEA//FECAL ELASTASE 1
8 0.0000067536 WATER FAT SEPARATION//FAT SUPPRESSION//FAT QUANTIFICATION
9 0.0000063027 HEART WEIGHT//NORMAL ORGAN WEIGHT//CARDIAC WEIGHT
10 0.0000061038 JUVENILE MYELOMONOCYTIC LEUKEMIA//JMML//JUVENILE MYELOMONOCYTIC LEUKAEMIA