Class information for:
Level 1: BEST VITELLIFORM MACULAR DYSTROPHY//VMD2//BEST1

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
19469 439 29.0 70%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
334 17318 RETINITIS PIGMENTOSA//RETINAL DEGENERATION//RETINA

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BEST VITELLIFORM MACULAR DYSTROPHY Author keyword 28 81% 4% 17
2 VMD2 Author keyword 27 92% 3% 11
3 BEST1 Author keyword 26 87% 3% 13
4 BEST DISEASE Author keyword 26 80% 4% 16
5 ADULT ONSET FOVEOMACULAR VITELLIFORM DYSTROPHY Author keyword 21 78% 3% 14
6 VITELLIFORM MACULAR DYSTROPHY Author keyword 19 80% 3% 12
7 BESTROPHIN Author keyword 19 58% 5% 22
8 BESTS DISEASE Author keyword 17 79% 3% 11
9 PATTERN DYSTROPHY Author keyword 14 65% 3% 13
10 BEST1 GENE Author keyword 14 100% 2% 7

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 BEST VITELLIFORM MACULAR DYSTROPHY 28 81% 4% 17 Search BEST+VITELLIFORM+MACULAR+DYSTROPHY Search BEST+VITELLIFORM+MACULAR+DYSTROPHY
2 VMD2 27 92% 3% 11 Search VMD2 Search VMD2
3 BEST1 26 87% 3% 13 Search BEST1 Search BEST1
4 BEST DISEASE 26 80% 4% 16 Search BEST+DISEASE Search BEST+DISEASE
5 ADULT ONSET FOVEOMACULAR VITELLIFORM DYSTROPHY 21 78% 3% 14 Search ADULT+ONSET+FOVEOMACULAR+VITELLIFORM+DYSTROPHY Search ADULT+ONSET+FOVEOMACULAR+VITELLIFORM+DYSTROPHY
6 VITELLIFORM MACULAR DYSTROPHY 19 80% 3% 12 Search VITELLIFORM+MACULAR+DYSTROPHY Search VITELLIFORM+MACULAR+DYSTROPHY
7 BESTROPHIN 19 58% 5% 22 Search BESTROPHIN Search BESTROPHIN
8 BESTS DISEASE 17 79% 3% 11 Search BESTS+DISEASE Search BESTS+DISEASE
9 PATTERN DYSTROPHY 14 65% 3% 13 Search PATTERN+DYSTROPHY Search PATTERN+DYSTROPHY
10 BEST1 GENE 14 100% 2% 7 Search BEST1+GENE Search BEST1+GENE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 VMD2 GENE 137 93% 12% 52
2 BEST DISEASE 128 88% 14% 60
3 VITELLIFORM MACULAR DYSTROPHY 92 64% 20% 89
4 VMD2 89 90% 9% 38
5 BESTROPHIN 70 86% 8% 36
6 MOUSE BESTROPHIN 2 61 88% 7% 29
7 BESTS DISEASE 33 83% 4% 19
8 VITELLIFORM DYSTROPHY 23 86% 3% 12
9 AUTOSOMAL DOMINANT VITREORETINOCHOROIDOPATHY 21 85% 3% 11
10 ELECTRO OCULOGRAPHY 18 89% 2% 8

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
The spectrum of ocular phenotypes caused by mutations in the BEST1 gene 2009 53 197 61%
Molecular physiology of bestrophins: Multifunctional membrane proteins linked to best disease and other retinopathies 2008 128 176 40%
Bestrophins and retinopathies 2010 34 78 53%
Functional roles of bestrophins in ocular epithelia 2009 46 158 41%
High-resolution Spectral Domain Optical Coherence Tomography Findings in Multifocal Vitelliform Macular Dystrophy 2009 10 11 91%
BEST1 SHOT THROUGH THE EYE - STRUCTURE, FUNCTIONS AND CLINICAL IMPLICATIONS OF BESTROPHIN-1 PROTEIN 2013 1 59 83%
Bestrophin I - Phenotypes and Functional Aspects in Bestrophinopathies 2015 0 126 86%
Calcium-dependent chloride conductance in epithelia: is there a contribution by Bestrophin? 2007 41 63 30%
Best vitelliform macular dystrophy: literature review 2014 0 51 59%
Hereditary Macular Dystrophies in Differential Diagnosis of AMD 2012 1 35 46%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 CIC 1423 1 50% 0.2% 1
2 EQUIPE ACCUEIL MENRT 2502 1 50% 0.2% 1
3 EXCELLENCE PREVENT TREATMENT VISUAL LOSS 1 50% 0.2% 1
4 HOP ROBERT SALENGRO 1 50% 0.2% 1
5 MANCHESTER HLTH SCI BIOMED 1 50% 0.2% 1
6 MONTGOMERY OPHTHALM PATHOL 1 50% 0.2% 1
7 UNITE FONCTIONNELLE RECH CLIN 1 50% 0.2% 1
8 UNIV HOSP NHS FDN TRUST 1 50% 0.2% 1
9 SPECIALIZED SURG SCI 1 29% 0.5% 2
10 HOP INTERCOMMUNAL CRETEIL 1 12% 1.1% 5

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000289894 TMEM16A//CALCIUM ACTIVATED CHLORIDE CHANNELS//CALCIUM ACTIVATED CHLORIDE CHANNEL
2 0.0000260018 ABCA4//STARGARDT DISEASE//A2E
3 0.0000153092 STANDING POTENTIAL//INTERPHOTORECEPTOR MATRIX//C WAVE
4 0.0000102693 RETINITIS PIGMENTOSA//PERIPHERIN RDS//AUTOSOMAL DOMINANT RETINITIS PIGMENTOSA
5 0.0000090455 RETINOSCHISIS//X LINKED RETINOSCHISIS//RETINOSCHISIN
6 0.0000082127 PIGMENTED PARAVENOUS RETINOCHOROIDAL ATROPHY//ATYPICAL RETINITIS PIGMENTOSA//PARAVENOUS
7 0.0000076943 CANCER ASSOCIATED RETINOPATHY//MELANOMA ASSOCIATED RETINOPATHY//BILATERAL DIFFUSE UVEAL MELANOCYTIC PROLIFERATION
8 0.0000074609 ELECTRORETINOGRAM//MULTIFOCAL ELECTRORETINOGRAM//OSCILLATORY POTENTIALS
9 0.0000071277 NORRIE DISEASE//FAMILIAL EXUDATIVE VITREORETINOPATHY//FRIZZLED 4
10 0.0000066136 FIBULIN 1//EFEMP1//FIBULIN 3