Class information for: |
Basic class information |
| ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
|---|---|---|---|
| 22256 | 331 | 27.6 | 75% |
Classes in level above (level 2) |
| ID, lev. above |
Publications | Label for level above |
|---|---|---|
| 2161 | 4516 | ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX |
Terms with highest relevance score |
| Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
|---|---|---|---|---|---|---|
| 1 | BIRT HOGG DUBE SYNDROME | Author keyword | 94 | 76% | 20% | 65 |
| 2 | FOLLICULIN | Author keyword | 58 | 83% | 10% | 33 |
| 3 | FIBROFOLLICULOMA | Author keyword | 44 | 81% | 8% | 26 |
| 4 | FLCN | Author keyword | 24 | 82% | 4% | 14 |
| 5 | BHD | Author keyword | 19 | 68% | 5% | 17 |
| 6 | BIRT HOGG DUBE | Author keyword | 16 | 58% | 5% | 18 |
| 7 | FOLLICULIN GENE | Author keyword | 14 | 100% | 2% | 7 |
| 8 | PERIFOLLICULAR FIBROMA | Author keyword | 13 | 80% | 2% | 8 |
| 9 | TRICHODISCOMA | Author keyword | 11 | 69% | 3% | 9 |
| 10 | FLCN GENE | Author keyword | 8 | 100% | 2% | 5 |
Web of Science journal categories |
Author Key Words |
| Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
|---|---|---|---|---|---|---|---|
| 1 | BIRT HOGG DUBE SYNDROME | 94 | 76% | 20% | 65 | Search BIRT+HOGG+DUBE+SYNDROME | Search BIRT+HOGG+DUBE+SYNDROME |
| 2 | FOLLICULIN | 58 | 83% | 10% | 33 | Search FOLLICULIN | Search FOLLICULIN |
| 3 | FIBROFOLLICULOMA | 44 | 81% | 8% | 26 | Search FIBROFOLLICULOMA | Search FIBROFOLLICULOMA |
| 4 | FLCN | 24 | 82% | 4% | 14 | Search FLCN | Search FLCN |
| 5 | BHD | 19 | 68% | 5% | 17 | Search BHD | Search BHD |
| 6 | BIRT HOGG DUBE | 16 | 58% | 5% | 18 | Search BIRT+HOGG+DUBE | Search BIRT+HOGG+DUBE |
| 7 | FOLLICULIN GENE | 14 | 100% | 2% | 7 | Search FOLLICULIN+GENE | Search FOLLICULIN+GENE |
| 8 | PERIFOLLICULAR FIBROMA | 13 | 80% | 2% | 8 | Search PERIFOLLICULAR+FIBROMA | Search PERIFOLLICULAR+FIBROMA |
| 9 | TRICHODISCOMA | 11 | 69% | 3% | 9 | Search TRICHODISCOMA | Search TRICHODISCOMA |
| 10 | FLCN GENE | 8 | 100% | 2% | 5 | Search FLCN+GENE | Search FLCN+GENE |
Key Words Plus |
| Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
|---|---|---|---|---|---|
| 1 | BHD GENE | 127 | 92% | 15% | 49 |
| 2 | FIBROFOLLICULOMAS | 108 | 88% | 15% | 51 |
| 3 | TRICHODISCOMAS | 94 | 89% | 13% | 42 |
| 4 | ACROCHORDONS | 93 | 81% | 17% | 56 |
| 5 | KIDNEY NEOPLASIA | 92 | 92% | 11% | 36 |
| 6 | MTOR ACTIVATION | 73 | 96% | 7% | 23 |
| 7 | BHD | 52 | 100% | 5% | 18 |
| 8 | PERIFOLLICULAR FIBROMAS | 26 | 100% | 3% | 11 |
| 9 | FOLLICULIN | 26 | 80% | 5% | 16 |
| 10 | FLCN | 21 | 90% | 3% | 9 |
Journals |
Reviews |
| Title | Publ. year | Cit. | Active references |
% act. ref. to same field |
|---|---|---|---|---|
| Birt-Hogg-Dube syndrome: clinicopathological features of the lung | 2013 | 13 | 40 | 95% |
| Birt-Hogg-Dube syndrome: diagnosis and management | 2009 | 89 | 72 | 81% |
| Birt-Hogg-Dube syndrome: A review of the literature and the differential diagnosis of firm facial papules | 2003 | 42 | 23 | 96% |
| Birt-Hogg-Dube syndrome clinicopathologic - Findings and genetic alterations | 2006 | 49 | 34 | 85% |
| Association Between Birt Hogg Dube Syndrome and Cancer Predisposition | 2010 | 9 | 46 | 100% |
| Clinical features, genetics and potential therapeutic approaches for Birt-Hogg-Dube syndrome | 2015 | 0 | 88 | 91% |
| Spontaneous pneumothorax due to Birt-Hogg-Dube syndrome in a Chinese family | 2009 | 2 | 8 | 88% |
| Birt-Hogg-Dube syndrome. State-of-the-art review with emphasis on pulmonary involvement | 2015 | 0 | 37 | 81% |
| Birt-Hogg-Dubllb syndrome, a genodermatosis that increases risk for renal carcinoma | 2004 | 14 | 38 | 68% |
| REVIEW OF RENAL TUMORS ASSOCIATED WITH BIRT-HOGG-DUBE SYNDROME WITH FOCUS ON CLINICAL AND PATHOBIOLOGICAL ASPECTS | 2014 | 0 | 68 | 68% |
Address terms |
| Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
|---|---|---|---|---|---|
| 1 | GENET EAU INCA | 2 | 67% | 0.6% | 2 |
| 2 | PNEUMOTHORAX | 2 | 33% | 1.5% | 5 |
| 3 | UROL MOL GENET | 1 | 31% | 1.2% | 4 |
| 4 | TOXICOL TERATOL | 1 | 38% | 0.9% | 3 |
| 5 | UNIT SKIN HISTOPATHOL | 1 | 100% | 0.6% | 2 |
| 6 | GENET ONCOL EPHE | 1 | 17% | 1.8% | 6 |
| 7 | PILOTE TUMEURS RA INCA | 1 | 40% | 0.6% | 2 |
| 8 | BIOCHIM HORMONOL GENET B | 1 | 50% | 0.3% | 1 |
| 9 | EAU INCA | 1 | 50% | 0.3% | 1 |
| 10 | INTERVENT PNEUMOL UNIT | 1 | 50% | 0.3% | 1 |
Related classes at same level (level 1) |
| Rank | Relatedness score | Related classes |
|---|---|---|
| 1 | 0.0000229598 | LIPEDEMATOUS ALOPECIA//LIPEDEMATOUS SCALP//SCALP THICKENING |
| 2 | 0.0000197341 | FUMARATE HYDRATASE//HLRCC//CUTANEOUS LEIOMYOSARCOMA |
| 3 | 0.0000138304 | RENAL ONCOCYTOMA//CHROMOPHOBE RENAL CELL CARCINOMA//COLLECTING DUCT CARCINOMA |
| 4 | 0.0000118504 | LYMPHANGIOLEIOMYOMATOSIS//MULTIFOCAL MICRONODULAR PNEUMOCYTE HYPERPLASIA//PULMONARY LYMPHANGIOLEIOMYOMATOSIS |
| 5 | 0.0000086116 | TRICHOBLASTOMA//FOLLICULOSEBACEOUS CYSTIC HAMARTOMA//PROLIFERATING TRICHILEMMAL CYST |
| 6 | 0.0000079485 | HEMANGIOBLASTOMAS//VON HIPPEL LINDAU DISEASE//HAEMANGIOBLASTOMA |
| 7 | 0.0000078140 | SKIN TAGS//CLEAR CELL ACANTHOMA//ACROCHORDON |
| 8 | 0.0000074070 | BAP1//BRCA1 ASSOCIATED PROTEIN 1//SETD2 |
| 9 | 0.0000071316 | TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX//SUBEPENDYMAL GIANT CELL ASTROCYTOMA |
| 10 | 0.0000064629 | SMITH MAGENIS SYNDROME//RAI1//POTOCKI LUPSKI SYNDROME |