Class information for:
Level 1: ASPARTYLGLUCOSAMINURIA//GLYCOSYLASPARAGINASE//ASPARTYLGLUCOSAMINIDASE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
25247 238 28.5 65%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
330 17366 FABRY DISEASE//GAUCHER DISEASE//MUCOPOLYSACCHARIDOSES

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ASPARTYLGLUCOSAMINURIA Author keyword 67 89% 13% 31
2 GLYCOSYLASPARAGINASE Author keyword 35 86% 8% 18
3 ASPARTYLGLUCOSAMINIDASE Author keyword 35 81% 9% 21
4 ASPARTYLGLYCOSAMINURIA Author keyword 6 71% 2% 5
5 GLYCOPROTEIN DEGRADATION Author keyword 3 57% 2% 4
6 ISOASPARTYL PEPTIDASE Author keyword 3 100% 1% 3
7 NEUREGULIN EGF LIKE MOTIF Author keyword 1 100% 1% 2
8 NTN HYDROLASE Author keyword 1 21% 2% 5
9 ENZYME BIOCHEM GRP Address 1 40% 1% 2
10 GLYCOPROTEINOSIS Author keyword 1 40% 1% 2

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 ASPARTYLGLUCOSAMINURIA 67 89% 13% 31 Search ASPARTYLGLUCOSAMINURIA Search ASPARTYLGLUCOSAMINURIA
2 GLYCOSYLASPARAGINASE 35 86% 8% 18 Search GLYCOSYLASPARAGINASE Search GLYCOSYLASPARAGINASE
3 ASPARTYLGLUCOSAMINIDASE 35 81% 9% 21 Search ASPARTYLGLUCOSAMINIDASE Search ASPARTYLGLUCOSAMINIDASE
4 ASPARTYLGLYCOSAMINURIA 6 71% 2% 5 Search ASPARTYLGLYCOSAMINURIA Search ASPARTYLGLYCOSAMINURIA
5 GLYCOPROTEIN DEGRADATION 3 57% 2% 4 Search GLYCOPROTEIN+DEGRADATION Search GLYCOPROTEIN+DEGRADATION
6 ISOASPARTYL PEPTIDASE 3 100% 1% 3 Search ISOASPARTYL+PEPTIDASE Search ISOASPARTYL+PEPTIDASE
7 NEUREGULIN EGF LIKE MOTIF 1 100% 1% 2 Search NEUREGULIN+EGF+LIKE+MOTIF Search NEUREGULIN+EGF+LIKE+MOTIF
8 NTN HYDROLASE 1 21% 2% 5 Search NTN+HYDROLASE Search NTN+HYDROLASE
9 GLYCOPROTEINOSIS 1 40% 1% 2 Search GLYCOPROTEINOSIS Search GLYCOPROTEINOSIS
10 N TERMINAL NUCLEOPHILE 1 40% 1% 2 Search N+TERMINAL+NUCLEOPHILE Search N+TERMINAL+NUCLEOPHILE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ASPARTYLGLYCOSAMINURIA 65 81% 16% 39
2 GLYCOSYLASPARAGINASE 32 70% 11% 26
3 N TERMINAL NUCLEOPHILE 18 52% 10% 24
4 ASPARTYLGLUCOSAMINURIA 17 63% 7% 17
5 GLYCOASPARAGINASE 17 100% 3% 8
6 ASPARTYLGLUCOSAMINIDASE 15 68% 5% 13
7 HUMAN LYSOSOMAL ASPARTYLGLUCOSAMINIDASE 15 56% 8% 18
8 LYSOSOMAL ASPARTYLGLUCOSAMINIDASE 12 75% 4% 9
9 INTRAMOLECULAR PROTEOLYSIS 12 59% 5% 13
10 LYSOSOMAL GLYCOSYLASPARAGINASE 11 100% 3% 6

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Progressive nature of aspartylglucosaminuria 2002 11 13 100%
Molecular genetics of the Finnish disease heritage 1999 219 90 17%
Aspartylglycosaminuria: biochemistry and molecular biology 1999 17 75 80%
ASPARTYLGLYCOSAMINURIA - PROTEIN CHEMISTRY AND MOLECULAR-BIOLOGY OF THE MOST COMMON LYSOSOMAL STORAGE DISORDER OF GLYCOPROTEIN DEGRADATION 1993 26 61 67%
ASPARTYLGLUCOSAMINURIA (AGU) - PROTEIN AND GENE STRUCTURE OF NORMAL AND MUTATED ASPARTYLGLUCOSAMINIDASE 1993 2 33 76%
Messages from an isolate: Lessons from the Finnish gene pool 1995 58 38 11%
ASPARTYLGLYCOSAMINURIA - AN INBORN ERROR OF GLYCOPROTEIN CATABOLISM 1982 16 6 83%
Structural analysis of proteins by mass spectrometry 1996 0 128 1%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 ENZYME BIOCHEM GRP 1 40% 0.8% 2
2 PAAJARVI 1 40% 0.8% 2
3 PROTE SCI 1 40% 0.8% 2
4 TURKU SITE 1 50% 0.4% 1
5 WILLINK BIOCHEM GENET 1 50% 0.4% 1
6 EXCELLENCE DIS GENET 0 33% 0.4% 1
7 HUMAN MOLEC GENET 0 18% 0.8% 2
8 BAMS 0 25% 0.4% 1
9 BIOCRYSTALLOGR H 0 25% 0.4% 1
10 SO DERBYSHIRE ACUTE HOSP NHS TRUST 0 17% 0.4% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000173455 AMINOPOLYSTYRENE//BETA GLYCOPYRANOSYLAMINES//BETA N ACETYLGLUCOSAMINYL L ASPARAGINE ANALOGUES
2 0.0000140791 L ASPARAGINASE//ASPARAGINASE//ERWINIA ASPARAGINASE
3 0.0000127944 PENICILLIN ACYLASE//PENICILLIN G ACYLASE//PENICILLIN V ACYLASE
4 0.0000081050 PROTEIN SPLICING//INTEIN//HOMING ENDONUCLEASE
5 0.0000068585 FUCOSIDOSIS//ALPHA L FUCOSIDASE//FUCOSE DEHYDROGENASE
6 0.0000068152 CYANOPHYCIN//CYANOPHYCIN SYNTHETASE//CYANOPHYCINASE
7 0.0000068004 HIGH MR GLYCOPROTEIN//NEUROCHORDIN//P EPITOPE
8 0.0000065505 CYSTINOSIS//SALLA DISEASE//NEPHROPATHIC CYSTINOSIS
9 0.0000061764 SWAINSONINE//LOCOWEED//ALPHA MANNOSIDOSIS
10 0.0000057603 MUCOPOLYSACCHARIDOSES//HUNTER SYNDROME//MAROTEAUX LAMY SYNDROME