Class information for: |
Basic class information |
ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
---|---|---|---|
25247 | 238 | 28.5 | 65% |
Classes in level above (level 2) |
ID, lev. above |
Publications | Label for level above |
---|---|---|
330 | 17366 | FABRY DISEASE//GAUCHER DISEASE//MUCOPOLYSACCHARIDOSES |
Terms with highest relevance score |
Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|---|
1 | ASPARTYLGLUCOSAMINURIA | Author keyword | 67 | 89% | 13% | 31 |
2 | GLYCOSYLASPARAGINASE | Author keyword | 35 | 86% | 8% | 18 |
3 | ASPARTYLGLUCOSAMINIDASE | Author keyword | 35 | 81% | 9% | 21 |
4 | ASPARTYLGLYCOSAMINURIA | Author keyword | 6 | 71% | 2% | 5 |
5 | GLYCOPROTEIN DEGRADATION | Author keyword | 3 | 57% | 2% | 4 |
6 | ISOASPARTYL PEPTIDASE | Author keyword | 3 | 100% | 1% | 3 |
7 | NEUREGULIN EGF LIKE MOTIF | Author keyword | 1 | 100% | 1% | 2 |
8 | NTN HYDROLASE | Author keyword | 1 | 21% | 2% | 5 |
9 | ENZYME BIOCHEM GRP | Address | 1 | 40% | 1% | 2 |
10 | GLYCOPROTEINOSIS | Author keyword | 1 | 40% | 1% | 2 |
Web of Science journal categories |
Author Key Words |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | ASPARTYLGLUCOSAMINURIA | 67 | 89% | 13% | 31 | Search ASPARTYLGLUCOSAMINURIA | Search ASPARTYLGLUCOSAMINURIA |
2 | GLYCOSYLASPARAGINASE | 35 | 86% | 8% | 18 | Search GLYCOSYLASPARAGINASE | Search GLYCOSYLASPARAGINASE |
3 | ASPARTYLGLUCOSAMINIDASE | 35 | 81% | 9% | 21 | Search ASPARTYLGLUCOSAMINIDASE | Search ASPARTYLGLUCOSAMINIDASE |
4 | ASPARTYLGLYCOSAMINURIA | 6 | 71% | 2% | 5 | Search ASPARTYLGLYCOSAMINURIA | Search ASPARTYLGLYCOSAMINURIA |
5 | GLYCOPROTEIN DEGRADATION | 3 | 57% | 2% | 4 | Search GLYCOPROTEIN+DEGRADATION | Search GLYCOPROTEIN+DEGRADATION |
6 | ISOASPARTYL PEPTIDASE | 3 | 100% | 1% | 3 | Search ISOASPARTYL+PEPTIDASE | Search ISOASPARTYL+PEPTIDASE |
7 | NEUREGULIN EGF LIKE MOTIF | 1 | 100% | 1% | 2 | Search NEUREGULIN+EGF+LIKE+MOTIF | Search NEUREGULIN+EGF+LIKE+MOTIF |
8 | NTN HYDROLASE | 1 | 21% | 2% | 5 | Search NTN+HYDROLASE | Search NTN+HYDROLASE |
9 | GLYCOPROTEINOSIS | 1 | 40% | 1% | 2 | Search GLYCOPROTEINOSIS | Search GLYCOPROTEINOSIS |
10 | N TERMINAL NUCLEOPHILE | 1 | 40% | 1% | 2 | Search N+TERMINAL+NUCLEOPHILE | Search N+TERMINAL+NUCLEOPHILE |
Key Words Plus |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | ASPARTYLGLYCOSAMINURIA | 65 | 81% | 16% | 39 |
2 | GLYCOSYLASPARAGINASE | 32 | 70% | 11% | 26 |
3 | N TERMINAL NUCLEOPHILE | 18 | 52% | 10% | 24 |
4 | ASPARTYLGLUCOSAMINURIA | 17 | 63% | 7% | 17 |
5 | GLYCOASPARAGINASE | 17 | 100% | 3% | 8 |
6 | ASPARTYLGLUCOSAMINIDASE | 15 | 68% | 5% | 13 |
7 | HUMAN LYSOSOMAL ASPARTYLGLUCOSAMINIDASE | 15 | 56% | 8% | 18 |
8 | LYSOSOMAL ASPARTYLGLUCOSAMINIDASE | 12 | 75% | 4% | 9 |
9 | INTRAMOLECULAR PROTEOLYSIS | 12 | 59% | 5% | 13 |
10 | LYSOSOMAL GLYCOSYLASPARAGINASE | 11 | 100% | 3% | 6 |
Journals |
Reviews |
Title | Publ. year | Cit. | Active references | % act. ref. to same field |
---|---|---|---|---|
Progressive nature of aspartylglucosaminuria | 2002 | 11 | 13 | 100% |
Molecular genetics of the Finnish disease heritage | 1999 | 219 | 90 | 17% |
Aspartylglycosaminuria: biochemistry and molecular biology | 1999 | 17 | 75 | 80% |
ASPARTYLGLYCOSAMINURIA - PROTEIN CHEMISTRY AND MOLECULAR-BIOLOGY OF THE MOST COMMON LYSOSOMAL STORAGE DISORDER OF GLYCOPROTEIN DEGRADATION | 1993 | 26 | 61 | 67% |
ASPARTYLGLUCOSAMINURIA (AGU) - PROTEIN AND GENE STRUCTURE OF NORMAL AND MUTATED ASPARTYLGLUCOSAMINIDASE | 1993 | 2 | 33 | 76% |
Messages from an isolate: Lessons from the Finnish gene pool | 1995 | 58 | 38 | 11% |
ASPARTYLGLYCOSAMINURIA - AN INBORN ERROR OF GLYCOPROTEIN CATABOLISM | 1982 | 16 | 6 | 83% |
Structural analysis of proteins by mass spectrometry | 1996 | 0 | 128 | 1% |
Address terms |
Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | ENZYME BIOCHEM GRP | 1 | 40% | 0.8% | 2 |
2 | PAAJARVI | 1 | 40% | 0.8% | 2 |
3 | PROTE SCI | 1 | 40% | 0.8% | 2 |
4 | TURKU SITE | 1 | 50% | 0.4% | 1 |
5 | WILLINK BIOCHEM GENET | 1 | 50% | 0.4% | 1 |
6 | EXCELLENCE DIS GENET | 0 | 33% | 0.4% | 1 |
7 | HUMAN MOLEC GENET | 0 | 18% | 0.8% | 2 |
8 | BAMS | 0 | 25% | 0.4% | 1 |
9 | BIOCRYSTALLOGR H | 0 | 25% | 0.4% | 1 |
10 | SO DERBYSHIRE ACUTE HOSP NHS TRUST | 0 | 17% | 0.4% | 1 |
Related classes at same level (level 1) |
Rank | Relatedness score | Related classes |
---|---|---|
1 | 0.0000173455 | AMINOPOLYSTYRENE//BETA GLYCOPYRANOSYLAMINES//BETA N ACETYLGLUCOSAMINYL L ASPARAGINE ANALOGUES |
2 | 0.0000140791 | L ASPARAGINASE//ASPARAGINASE//ERWINIA ASPARAGINASE |
3 | 0.0000127944 | PENICILLIN ACYLASE//PENICILLIN G ACYLASE//PENICILLIN V ACYLASE |
4 | 0.0000081050 | PROTEIN SPLICING//INTEIN//HOMING ENDONUCLEASE |
5 | 0.0000068585 | FUCOSIDOSIS//ALPHA L FUCOSIDASE//FUCOSE DEHYDROGENASE |
6 | 0.0000068152 | CYANOPHYCIN//CYANOPHYCIN SYNTHETASE//CYANOPHYCINASE |
7 | 0.0000068004 | HIGH MR GLYCOPROTEIN//NEUROCHORDIN//P EPITOPE |
8 | 0.0000065505 | CYSTINOSIS//SALLA DISEASE//NEPHROPATHIC CYSTINOSIS |
9 | 0.0000061764 | SWAINSONINE//LOCOWEED//ALPHA MANNOSIDOSIS |
10 | 0.0000057603 | MUCOPOLYSACCHARIDOSES//HUNTER SYNDROME//MAROTEAUX LAMY SYNDROME |