Class information for:
Level 1: LIPOID PROTEINOSIS//HYALINOSIS CUTIS ET MUCOSAE//EXTRACELLULAR MATRIX PROTEIN 1

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
26556 206 21.9 61%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
3341 1266 DUPUYTRENS DISEASE//LIPOID PROTEINOSIS//DUPUYTRENS CONTRACTURE

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 LIPOID PROTEINOSIS Author keyword 144 93% 26% 54
2 HYALINOSIS CUTIS ET MUCOSAE Author keyword 29 88% 7% 14
3 EXTRACELLULAR MATRIX PROTEIN 1 Author keyword 26 80% 8% 16
4 URBACH WIETHE DISEASE Author keyword 21 73% 8% 16
5 ECM1 GENE Author keyword 6 100% 2% 4
6 ECM1 Author keyword 4 47% 3% 7
7 EXTRACELLULAR MATRIX PROTEIN 1 ECM1 Author keyword 3 100% 1% 3
8 EXTRACELLULAR MATRIX PROTEIN 1 GENE Author keyword 2 67% 1% 2
9 HYALINE MATERIAL Author keyword 1 50% 1% 2
10 MONILIFORM BLEPHAROSIS Author keyword 1 100% 1% 2

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 LIPOID PROTEINOSIS 144 93% 26% 54 Search LIPOID+PROTEINOSIS Search LIPOID+PROTEINOSIS
2 HYALINOSIS CUTIS ET MUCOSAE 29 88% 7% 14 Search HYALINOSIS+CUTIS+ET+MUCOSAE Search HYALINOSIS+CUTIS+ET+MUCOSAE
3 EXTRACELLULAR MATRIX PROTEIN 1 26 80% 8% 16 Search EXTRACELLULAR+MATRIX+PROTEIN+1 Search EXTRACELLULAR+MATRIX+PROTEIN+1
4 URBACH WIETHE DISEASE 21 73% 8% 16 Search URBACH+WIETHE+DISEASE Search URBACH+WIETHE+DISEASE
5 ECM1 GENE 6 100% 2% 4 Search ECM1+GENE Search ECM1+GENE
6 ECM1 4 47% 3% 7 Search ECM1 Search ECM1
7 EXTRACELLULAR MATRIX PROTEIN 1 ECM1 3 100% 1% 3 Search EXTRACELLULAR+MATRIX+PROTEIN+1+ECM1 Search EXTRACELLULAR+MATRIX+PROTEIN+1+ECM1
8 EXTRACELLULAR MATRIX PROTEIN 1 GENE 2 67% 1% 2 Search EXTRACELLULAR+MATRIX+PROTEIN+1+GENE Search EXTRACELLULAR+MATRIX+PROTEIN+1+GENE
9 HYALINE MATERIAL 1 50% 1% 2 Search HYALINE+MATERIAL Search HYALINE+MATERIAL
10 MONILIFORM BLEPHAROSIS 1 100% 1% 2 Search MONILIFORM+BLEPHAROSIS Search MONILIFORM+BLEPHAROSIS

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 GENE ECM1 36 77% 12% 24
2 LIPOID PROTEINOSIS 27 51% 18% 38
3 CUTIS ET MUCOSAE 21 78% 7% 14
4 EXTRACELLULAR MATRIX PROTEIN 1 18 44% 15% 31
5 HYALINOSIS CUTIS 14 100% 3% 7
6 ECM1 12 58% 7% 14
7 ORAL DIMETHYL SULFOXIDE 12 86% 3% 6
8 URBACH WIETHE DISEASE 11 46% 9% 18
9 MUCOSAE 5 28% 7% 15
10 URBACH WIETHE 3 100% 1% 3

Journals

Reviews


Title Publ. year Cit. Active
references		 % act. ref.
to same field
The molecular basis of lipoid proteinosis: mutations in extracellular matrix protein 1 2007 47 58 72%
Lipoid proteinosis 2002 56 24 96%
Marathon of eponyms: 21 Urbach-Wiethe disease (Lipoid proteinosis) 2011 1 1 100%
Lipoid proteinosis of larynx: review of four cases 2004 7 3 100%
Lipoid proteinosis: Report of four siblings and brief review of the literature 2001 17 19 95%
Oral mucosal manifestations in some genodermatoses: correlation with cutaneous lesions 2013 0 27 19%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ.
in class
1 GENET SKIN DIS GRP 1 11% 3.9% 8
2 CELL GROWTH DIFFERENTIAT DEV VIB 07 1 50% 0.5% 1
3 DERMATOL DERMATOALLERGOL CLIN 1 50% 0.5% 1
4 ORBIT OCULOPLASTY RECONSTRUCT SURG 1 50% 0.5% 1
5 SKELETAL DEV JOINT DIS 1 50% 0.5% 1
6 SIGNALING PROGRAM 0 25% 0.5% 1
7 CHINA EDUC MINIST CELL BIOL TUMOR CELL 0 20% 0.5% 1
8 FREE RADICAL RADIAT BIOL 0 20% 0.5% 1
9 NEUROL IDENCY PROGRAM 0 20% 0.5% 1
10 CHILDS 0 17% 0.5% 1

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000230873 JUVENILE HYALINE FIBROMATOSIS//INFANTILE SYSTEMIC HYALINOSIS//SYSTEMIC HYALINOSIS
2 0.0000086162 MACULAR AMYLOIDOSIS//CUTANEOUS AMYLOIDOSIS//PRIMARY CUTANEOUS AMYLOIDOSIS
3 0.0000077474 LICHEN SCLEROSUS//LICHEN SCLEROSUS ET ATROPHICUS//BALANITIS XEROTICA OBLITERANS
4 0.0000072586 FIBULIN 1//EFEMP1//FIBULIN 3
5 0.0000072042 LIGNEOUS CONJUNCTIVITIS//PLASMINOGEN DEFICIENCY//HYPOPLASMINOGENEMIA
6 0.0000068459 NEUHAUSER SYNDROME//MEGALOCORNEA//ANTERIOR MEGALOPHTHALMOS
7 0.0000066998 HUMAN PLACENTAL EXTRACT//PLACENTA EXTRACT//PORCINE PLACENTA EXTRACT
8 0.0000062229 KWASHIORKOR//HOSP UNIV TROUSSEAU//NACL NUTR
9 0.0000053602 PONTOSUBICULAR NECROSIS//INFANTILE BILATERAL STRIATAL NECROSIS//BRAINSTEM NECROSIS
10 0.0000053076 SCHWARTZ JAMPEL SYNDROME//PERLECAN//STUVE WIEDEMANN SYNDROME