Class information for:
Level 1: MACHADO JOSEPH DISEASE//SPINOCEREBELLAR ATAXIA//SCA2

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
2837 2060 34.2 82%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
1789 5796 HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA//FRIEDREICH ATAXIA

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 MACHADO JOSEPH DISEASE Author keyword 198 72% 7% 154
2 SPINOCEREBELLAR ATAXIA Author keyword 183 54% 11% 233
3 SCA2 Author keyword 125 83% 3% 70
4 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA Author keyword 100 85% 3% 52
5 SPINOCEREBELLAR ATAXIA TYPE 2 Author keyword 90 83% 2% 50
6 SPINOCEREBELLAR ATAXIAS Author keyword 85 73% 3% 65
7 SCA6 Author keyword 50 76% 2% 35
8 SCA3 Author keyword 48 65% 2% 45
9 DENTATORUBRAL PALLIDOLUYSIAN ATROPHY Author keyword 43 69% 2% 37
10 SPINOCEREBELLAR ATAXIA TYPE 3 Author keyword 34 56% 2% 41

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 MACHADO JOSEPH DISEASE 198 72% 7% 154 Search MACHADO+JOSEPH+DISEASE Search MACHADO+JOSEPH+DISEASE
2 SPINOCEREBELLAR ATAXIA 183 54% 11% 233 Search SPINOCEREBELLAR+ATAXIA Search SPINOCEREBELLAR+ATAXIA
3 SCA2 125 83% 3% 70 Search SCA2 Search SCA2
4 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA 100 85% 3% 52 Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA
5 SPINOCEREBELLAR ATAXIA TYPE 2 90 83% 2% 50 Search SPINOCEREBELLAR+ATAXIA+TYPE+2 Search SPINOCEREBELLAR+ATAXIA+TYPE+2
6 SPINOCEREBELLAR ATAXIAS 85 73% 3% 65 Search SPINOCEREBELLAR+ATAXIAS Search SPINOCEREBELLAR+ATAXIAS
7 SCA6 50 76% 2% 35 Search SCA6 Search SCA6
8 SCA3 48 65% 2% 45 Search SCA3 Search SCA3
9 DENTATORUBRAL PALLIDOLUYSIAN ATROPHY 43 69% 2% 37 Search DENTATORUBRAL+PALLIDOLUYSIAN+ATROPHY Search DENTATORUBRAL+PALLIDOLUYSIAN+ATROPHY
10 SPINOCEREBELLAR ATAXIA TYPE 3 34 56% 2% 41 Search SPINOCEREBELLAR+ATAXIA+TYPE+3 Search SPINOCEREBELLAR+ATAXIA+TYPE+3

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 DOMINANT CEREBELLAR ATAXIA 411 72% 16% 325
2 MACHADO JOSEPH DISEASE 326 52% 22% 449
3 SCA2 192 84% 5% 105
4 DRPLA 125 83% 3% 70
5 HEREDITARY ATAXIA 98 82% 3% 58
6 SPINOCEREBELLAR ATAXIA 95 33% 11% 232
7 CHROMOSOME 3P12 P211 94 97% 1% 28
8 DOMINANT CEREBELLAR ATAXIAS 89 69% 4% 76
9 CAG REPEAT 85 25% 14% 292
10 CAG REPEAT EXPANSION 84 68% 4% 75

Journals


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 CEREBELLUM 10 11% 4% 86

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
Autosomal dominant cerebellar ataxias: polyglutamine expansions and beyond 2010 151 99 80%
Autosomal dominant cerebellar ataxias: clinical features, genetics, and pathogenesis 2004 425 135 68%
Brain pathology of spinocerebellar ataxias 2012 51 182 82%
The Global Epidemiology of Hereditary Ataxia and Spastic Paraplegia: A Systematic Review of Prevalence Studies 2014 9 48 65%
The preclinical stage of spinocerebellar ataxias 2015 1 57 81%
Clinical features, neurogenetics and neuropathology of the polyglutamine spinocerebellar ataxias type 1, 2, 3, 6 and 7 2013 27 305 55%
Spinocerebellar ataxia 2 (SCA2) 2008 72 97 80%
Movement Disorders in Spinocerebellar Ataxias 2011 30 100 85%
The autosomal dominant spinocerebellar ataxias: emerging mechanistic themes suggest pervasive Purkinje cell vulnerability 2015 1 100 66%
SCA3: Neurological features, pathogenesis and animal models 2008 60 113 52%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 ENFERMEDADES NEUROL 11 100% 0.3% 6
2 ROSE MOSS PARKINSON NEURODEGENERAT DIS 11 100% 0.3% 6
3 UNIGENE 11 31% 1.4% 29
4 IBMC UNIGENE 8 100% 0.2% 5
5 HLTH SCI GERMANS TRIAS PUJOL IGTP 7 67% 0.3% 6
6 ROSE MOSS PARKINSONS NEURODEGENERAT DIS 5 55% 0.3% 6
7 CLIN NEUROANAT 4 13% 1.6% 32
8 HOP BEN AKNOUM 4 75% 0.1% 3
9 MONTREAL GEN HOSP NEUROSCI 4 75% 0.1% 3
10 NAT OURCES CIRN 4 33% 0.5% 10

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000138912 FRIEDREICH ATAXIA//FRIEDREICHS ATAXIA//FRATAXIN
2 0.0000132438 HUNTINGTIN//POLYGLUTAMINE//HUNTINGTONS DISEASE
3 0.0000125921 NEUROBEHAV NEUROBIOL NEUROPSYCHOL UNIT//TANDOSPIRONE CITRATE//3 MT
4 0.0000108272 SPINAL AND BULBAR MUSCULAR ATROPHY//KENNEDYS DISEASE//KENNEDY DISEASE
5 0.0000097888 MULTIPLE SYSTEM ATROPHY//STRIATONIGRAL DEGENERATION//OLIVOPONTOCEREBELLAR ATROPHY
6 0.0000077273 AOA2//ARSACS//APRATAXIN
7 0.0000067789 FEN1//BRAUN S//CREAT INITIAT CELL CYCLE CONTROL
8 0.0000054931 CEREBELLAR MUTISM//POSTERIOR FOSSA SYNDROME//MUTISM
9 0.0000052964 HEREDITARY SPASTIC PARAPLEGIA//SPG4//SPASTIN
10 0.0000051617 HUNTINGTONS DISEASE//HUNTINGTON DISEASE//NEUROGENET RARE DIS