Class information for:
Level 1: WIEDEMANN RAUTENSTRAUCH SYNDROME//NEONATAL PROGEROID SYNDROME//HALLERMANN STREIFF SYNDROME

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
31123 127 19.4 45%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
2846 2447 ORAL MUCOSITIS//MUCOSITIS//WIEDEMANN RAUTENSTRAUCH SYNDROME

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 WIEDEMANN RAUTENSTRAUCH SYNDROME Author keyword 52 100% 14% 18
2 NEONATAL PROGEROID SYNDROME Author keyword 21 85% 9% 11
3 HALLERMANN STREIFF SYNDROME Author keyword 19 70% 13% 16
4 NEONATAL PROGERIA Author keyword 8 75% 5% 6
5 OCULOMANDIBULODYSCEPHALY Author keyword 3 100% 2% 3
6 FRANCOIS SYNDROME Author keyword 2 67% 2% 2
7 PROGRAMA MAESTRIA NEUROCIENCIAS Address 1 100% 2% 2
8 BENEFITS OF QUALITY MANAGEMENT Author keyword 1 50% 1% 1
9 CHRONIC OBSTRUCTIVE SLEEP APNEA Author keyword 1 50% 1% 1
10 CONGENITAL SYNDROMES Author keyword 1 50% 1% 1

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 WIEDEMANN RAUTENSTRAUCH SYNDROME 52 100% 14% 18 Search WIEDEMANN+RAUTENSTRAUCH+SYNDROME Search WIEDEMANN+RAUTENSTRAUCH+SYNDROME
2 NEONATAL PROGEROID SYNDROME 21 85% 9% 11 Search NEONATAL+PROGEROID+SYNDROME Search NEONATAL+PROGEROID+SYNDROME
3 HALLERMANN STREIFF SYNDROME 19 70% 13% 16 Search HALLERMANN+STREIFF+SYNDROME Search HALLERMANN+STREIFF+SYNDROME
4 NEONATAL PROGERIA 8 75% 5% 6 Search NEONATAL+PROGERIA Search NEONATAL+PROGERIA
5 OCULOMANDIBULODYSCEPHALY 3 100% 2% 3 Search OCULOMANDIBULODYSCEPHALY Search OCULOMANDIBULODYSCEPHALY
6 FRANCOIS SYNDROME 2 67% 2% 2 Search FRANCOIS+SYNDROME Search FRANCOIS+SYNDROME
7 BENEFITS OF QUALITY MANAGEMENT 1 50% 1% 1 Search BENEFITS+OF+QUALITY+MANAGEMENT Search BENEFITS+OF+QUALITY+MANAGEMENT
8 CHRONIC OBSTRUCTIVE SLEEP APNEA 1 50% 1% 1 Search CHRONIC+OBSTRUCTIVE+SLEEP+APNEA Search CHRONIC+OBSTRUCTIVE+SLEEP+APNEA
9 CONGENITAL SYNDROMES 1 50% 1% 1 Search CONGENITAL+SYNDROMES Search CONGENITAL+SYNDROMES
10 CRANIOFACIAL RECONSTRUCTIVE SURGERY 1 50% 1% 1 Search CRANIOFACIAL+RECONSTRUCTIVE+SURGERY Search CRANIOFACIAL+RECONSTRUCTIVE+SURGERY

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 NEONATAL PROGEROID SYNDROME 10 61% 9% 11
2 WIEDEMANN RAUTENSTRAUCH SYNDROME 8 100% 4% 5
3 FRANCOIS DYSCEPHALIC SYNDROME 3 100% 2% 3
4 WIEDEMANN RAUTENSTRAUCH 3 50% 3% 4
5 FRANCOIS SYNDROME 1 100% 2% 2
6 KUGELKERN 1 100% 2% 2
7 RAUTENSTRAUCH SYNDROME 1 100% 2% 2
8 SKIN DIMPLES 1 100% 2% 2
9 SYNDROME WIEDEMANN RAUTENSTRAUCH 1 50% 1% 1
10 HEREDITARY RETINOCHOROIDAL DYSTROPHIES 0 33% 1% 1

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Hallermann-Streiff syndrome: Experience with 15 patients and review of the literature 1999 12 17 88%
Hallermann-Streiff syndrome: A case review 2004 5 4 100%
The neonatal progeroid syndrome (Wiedemann-Rautenstrauch syndrome): Case report and review of the literature 2000 4 15 93%
THE NEONATAL PSEUDO-HYDROCEPHALIC PROGEROID SYNDROME (WIEDEMANN-RAUTENSTRAUCH) - REPORT OF A NEW PATIENT AND REVIEW OF THE LITERATURE 1988 26 3 67%
Classification of biomedical research reports as a reference for evidence-based medicine in ophthalmology. A survey considering as example the journal Der Ophthalmologe 2005 1 301 4%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 PROGRAMA MAESTRIA NEUROCIENCIAS 1 100% 1.6% 2
2 KLIN POLIKLIN IELBEHANDLUNG NEUROOPHTHALMO 1 50% 0.8% 1
3 GRP PATOL MOL 0 33% 0.8% 1
4 PEDIAT DIABETOL BIRTH DEFECTS 0 25% 0.8% 1
5 SEZIONE DERMATOL 0 20% 0.8% 1
6 MED GENET SERV WALES 0 17% 0.8% 1
7 HOSP PESQUISA REABILITACAO LESOES IO PALATAI 0 11% 0.8% 1
8 POLIKLIN RECHTS ISAR 0 100% 0.8% 1
9 REFERENCE CONGENITAL ANOMALIES DEV 0 100% 0.8% 1
10 REFERENCE CONGENITAL HEREDITARY DEAFNE 0 100% 0.8% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000246359 REGIONAL ODONTODYSPLASIA//ENAMEL PEARLS//GHOST TEETH
2 0.0000100753 ARTHROGRYPOSIS//NEU LAXOVA SYNDROME//AMYOPLASIA
3 0.0000096837 NANOPHTHALMOS//ANOPHTHALMIA//MICROPHTHALMIA
4 0.0000073723 BASALOID FOLLICULAR HAMARTOMA//MILIA EN PLAQUE//INFUNDIBULOCYSTIC BASAL CELL CARCINOMA
5 0.0000073715 NUCLEAR LAMINA//EMERIN//NUCLEAR ENVELOPE
6 0.0000070657 AXENFELD RIEGER SYNDROME//PETERS ANOMALY//FOXC1
7 0.0000068629 INVOLUTIONAL ENTROPION//MEDIAL CANTHAL TENDON//LATERAL TARSAL STRIP
8 0.0000066452 SECKEL SYNDROME//FLOATING HARBOR SYNDROME//MOPD II
9 0.0000065411 CONGENITAL GENERALIZED LIPODYSTROPHY//SEIPIN//BSCL2
10 0.0000063077 EOSINOPHILIC ULCER//RIGA FEDE DISEASE//NEONATAL TEETH