Class information for:
Level 1: SCHNITZLER SYNDROME//SCHNITZLERS SYNDROME//NEUTROPHILIC URTICARIAL DERMATOSIS

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
31701 119 23.0 79%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
2172 4495 FAMILIAL MEDITERRANEAN FEVER//CHRONIC URTICARIA//MEFV

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 SCHNITZLER SYNDROME Author keyword 49 82% 24% 28
2 SCHNITZLERS SYNDROME Author keyword 38 76% 22% 26
3 NEUTROPHILIC URTICARIAL DERMATOSIS Author keyword 3 60% 3% 3
4 MONOCLONAL DYSPROTEINEMIA Author keyword 1 100% 2% 2
5 MONOCLONAL IGM GAMMOPATHY Author keyword 1 100% 2% 2
6 MACROGLOBULINEMIA Author keyword 1 13% 7% 8
7 MACROGLOBULINAEMIA Author keyword 1 27% 3% 3
8 ARTROGRP Address 1 50% 1% 1
9 AUTO INFLAMMATION Author keyword 1 50% 1% 1
10 HUMV Address 1 50% 1% 1

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 SCHNITZLER SYNDROME 49 82% 24% 28 Search SCHNITZLER+SYNDROME Search SCHNITZLER+SYNDROME
2 SCHNITZLERS SYNDROME 38 76% 22% 26 Search SCHNITZLERS+SYNDROME Search SCHNITZLERS+SYNDROME
3 NEUTROPHILIC URTICARIAL DERMATOSIS 3 60% 3% 3 Search NEUTROPHILIC+URTICARIAL+DERMATOSIS Search NEUTROPHILIC+URTICARIAL+DERMATOSIS
4 MONOCLONAL DYSPROTEINEMIA 1 100% 2% 2 Search MONOCLONAL+DYSPROTEINEMIA Search MONOCLONAL+DYSPROTEINEMIA
5 MONOCLONAL IGM GAMMOPATHY 1 100% 2% 2 Search MONOCLONAL+IGM+GAMMOPATHY Search MONOCLONAL+IGM+GAMMOPATHY
6 MACROGLOBULINEMIA 1 13% 7% 8 Search MACROGLOBULINEMIA Search MACROGLOBULINEMIA
7 MACROGLOBULINAEMIA 1 27% 3% 3 Search MACROGLOBULINAEMIA Search MACROGLOBULINAEMIA
8 AUTO INFLAMMATION 1 50% 1% 1 Search AUTO+INFLAMMATION Search AUTO+INFLAMMATION
9 IL 17E IL 25 1 50% 1% 1 Search IL+17E+IL+25 Search IL+17E+IL+25
10 SCLEROTIC BONE DISEASE 1 50% 1% 1 Search SCLEROTIC+BONE+DISEASE Search SCLEROTIC+BONE+DISEASE

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 MACROGLOBULINEMIA 13 23% 40% 48
2 WALDENSTROMS DISEASE 11 100% 5% 6
3 SYNDROME URTICARIA 8 100% 4% 5
4 IGG KAPPA GAMMOPATHY 4 67% 3% 4
5 MONOCLONAL IGM GAMMOPATHY 2 67% 2% 2
6 SCHNITZLER SYNDROME 2 23% 6% 7
7 KAPPA GAMMOPATHY 1 100% 2% 2
8 BENEFICIAL RESPONSE 1 27% 3% 4
9 DRAMATIC IMPROVEMENT 1 25% 2% 2
10 SCHNITZLERS SYNDROME 0 11% 2% 2

Journals

Reviews


Title Publ. year Cit. Active
references		 % act. ref.
to same field
Schnitzler syndrome: Beyond the case reports: Review and follow-up of 94 patients with an emphasis on prognosis and treatment 2007 93 63 78%
Schnitzler's syndrome: diagnosis, treatment, and follow-up 2013 24 24 88%
Long-term effectiveness and safety of interleukin-1 receptor antagonist (anakinra) in Schnitzler's syndrome: A french multicenter study 2014 3 28 68%
The Schnitzler syndrome 2010 30 48 92%
Treatment of Schnitzler's syndrome with anakinra: report of three cases and review of the literature 2011 15 10 80%
Schnitzler syndrome, an autoimmune-autoinflammatory syndrome: Report of two new cases and review of the literature 2011 13 38 87%
Clinical and histopathologic review of Schnitzler syndrome: The Mayo Clinic experience (1972-2011) 2012 11 28 64%
Schnitzler syndrome 2008 10 30 87%
Malignant evolution of Schnitzler's syndrome - Chronic urticaria and IgM monoclonal gammopathy: Report of a new case and review of the literature 2002 20 30 93%
Schnitzler's syndrome associated with pancreatitis: a disease of IL-1 dysregulation 2012 6 22 68%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ.
in class
1 ARTROGRP 1 50% 0.8% 1
2 HUMV 1 50% 0.8% 1
3 URINARY TRACT INFECT 1 50% 0.8% 1
4 CLIN INFECT IMMUNOL DISORDERS 0 33% 0.8% 1
5 PSEUDOMONAS AERUGINOSA HOST PATHOGEN TRANSLAT 0 33% 0.8% 1
6 REFERENCE RARE AUTOIMMUNE SYST DIS 0 33% 0.8% 1
7 SERV MED INTERNE MED GEN 0 33% 0.8% 1
8 MED CLIN DERMATOL 0 18% 1.7% 2
9 MED INTERDISCIPLINARY MED 0 13% 0.8% 1
10 ETABLISSMENT TRANSFUS SANGUINE 0 100% 0.8% 1

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000228723 CHRONIC URTICARIA//AUTOLOGOUS SERUM SKIN TEST//CHRONIC IDIOPATHIC URTICARIA
2 0.0000180737 FAMILIAL MEDITERRANEAN FEVER//MEFV//MEFV GENE
3 0.0000178999 WALDENSTROMS MACROGLOBULINEMIA//WALDENSTROM MACROGLOBULINEMIA//BING WALDENSTROMS MACROGLOBULINEMIA
4 0.0000140623 ADULT ONSET STILLS DISEASE//ADULT STILLS DISEASE//STILLS DISEASE
5 0.0000139774 POEMS SYNDROME//CROW FUKASE SYNDROME//OSTEOSCLEROTIC MYELOMA
6 0.0000114977 IL 37//TIR8//INTERLEUKIN 37
7 0.0000086811 SYSTEMIC CAPILLARY LEAK SYNDROME//PAPULOERYTHRODERMA//DECK CHAIR SIGN
8 0.0000076626 PULMONARY VENO OCCLUSIVE DISEASE//PULMONARY CAPILLARY HEMANGIOMATOSIS//PULMONARY CAPILLARY HAEMANGIOMATOSIS
9 0.0000067071 ANTI CYTOKINE VACCINATION//ANTI IFN ALPHA IMMUNIZATION//INTERFERON ANTIBODIES
10 0.0000064871 PYODERMA GANGRENOSUM//SWEETS SYNDROME//NEUTROPHILIC DERMATOSIS