Class information for:
Level 1: GIANT AXONAL NEUROPATHY//GIGAXONIN//GAN MUTATIONS

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
32467 108 29.1 62%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
2469 3523 2 5 HEXANEDIONE//NEUROFILAMENT//NEUROFILAMENTS

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 GIANT AXONAL NEUROPATHY Author keyword 60 83% 31% 34
2 GIGAXONIN Author keyword 23 86% 11% 12
3 GAN MUTATIONS Author keyword 3 100% 3% 3
4 ALUYA5 Author keyword 2 67% 2% 2
5 NEUROPATHOL NEUROBIOL MOL Address 2 67% 2% 2
6 GAN GENE Author keyword 1 100% 2% 2
7 ALGER Address 1 50% 1% 1
8 GIANT AXONAL DEGENERATION Author keyword 1 50% 1% 1
9 HOSP UNIV MUST HA Address 1 50% 1% 1
10 NEUROPATHOL NEURODEGENERAT DIS Address 1 50% 1% 1

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 GIANT AXONAL NEUROPATHY 60 83% 31% 34 Search GIANT+AXONAL+NEUROPATHY Search GIANT+AXONAL+NEUROPATHY
2 GIGAXONIN 23 86% 11% 12 Search GIGAXONIN Search GIGAXONIN
3 GAN MUTATIONS 3 100% 3% 3 Search GAN+MUTATIONS Search GAN+MUTATIONS
4 ALUYA5 2 67% 2% 2 Search ALUYA5 Search ALUYA5
5 GAN GENE 1 100% 2% 2 Search GAN+GENE Search GAN+GENE
6 GIANT AXONAL DEGENERATION 1 50% 1% 1 Search GIANT+AXONAL+DEGENERATION Search GIANT+AXONAL+DEGENERATION
7 TUBULAR LIKE STRUCTURE 1 50% 1% 1 Search TUBULAR+LIKE+STRUCTURE Search TUBULAR+LIKE+STRUCTURE
8 GIANT AXONS 1 19% 3% 3 Search GIANT+AXONS Search GIANT+AXONS
9 BCL 2 ASSOCIATED ATHANOGENE 0 25% 1% 1 Search BCL+2+ASSOCIATED+ATHANOGENE Search BCL+2+ASSOCIATED+ATHANOGENE
10 GENETIC NEUROPATHY 0 25% 1% 1 Search GENETIC+NEUROPATHY Search GENETIC+NEUROPATHY

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 GENERALIZED DISORDER 49 94% 16% 17
2 GIGAXONIN 25 70% 19% 21
3 CHROMOSOME 16Q241 20 100% 8% 9
4 ALGERIAN FAMILY 17 100% 7% 8
5 GENOTYPE PHENOTYPE 2 15% 11% 12
6 MICROTUBULE ASSOCIATED PROTEIN 8 1 100% 2% 2
7 MOLECULAR FINDINGS 1 16% 6% 6
8 GIANT AXONAL NEUROPATHY 1 11% 7% 8
9 NEUROFILAMENT ACCUMULATION 1 33% 2% 2
10 FOLDING COFACTOR D 0 20% 2% 2

Journals

Reviews



Title Publ. year Cit. Active
references
% act. ref.
to same field
Clinical and molecular findings in patients with giant axonal neuropathy (GAN) 2004 36 15 93%
The giant axonal neuropathy - clinical and histological aspects, differential diagnosis and a new case 2001 10 42 79%
GIANT AXONAL NEUROPATHY: AN UPDATED PERSPECTIVE ON ITS PATHOLOGY AND PATHOGENESIS 2014 0 56 66%
GIANT AXONAL NEUROPATHY - A REVIEW 1989 34 12 83%
CHILDHOOD GIANT AXONAL NEUROPATHY - CASE-REPORT AND REVIEW OF THE LITERATURE 1987 18 36 39%
"Personalizing" academic medicine: opportunities and challenges in implementing genomic profiling 2009 6 18 6%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 NEUROPATHOL NEUROBIOL MOL 2 67% 1.9% 2
2 ALGER 1 50% 0.9% 1
3 HOSP UNIV MUST HA 1 50% 0.9% 1
4 NEUROPATHOL NEURODEGENERAT DIS 1 50% 0.9% 1
5 GENET BIOL MOL CELLULARIE 0 33% 0.9% 1
6 ABT NEUROPADIAT MUSKELERKRANKUNGEN 0 25% 0.9% 1
7 PROJECT ALS JENIFER ESTESS STEM CELL 0 25% 0.9% 1
8 COLUMBIA STEM CELL INITIAT 0 11% 1.9% 2
9 NEUROL NEUROMUSCULAR 0 20% 0.9% 1
10 CLIN CHILD NEUROL PSYCHIAT 0 10% 1.9% 2

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000210736 2 5 HEXANEDIONE//GAMMA DIKETONE NEUROPATHY//1 2 DIACETYLBENZENE
2 0.0000176647 NEUROFILAMENT//NEUROFILAMENTS//PERIPHERIN
3 0.0000111806 CHARCOT MARIE TOOTH DISEASE//PMP22//CHARCOT MARIE TOOTH
4 0.0000104971 POKEMON//BCL6//HIC1
5 0.0000091418 MICROTUBULE ASSOCIATED PROTEIN 1B//MAP1B//MAP1A
6 0.0000090453 MYOFIBRILLAR MYOPATHY//DESMINOPATHY//PLECTIN
7 0.0000076387 ALEXANDER DISEASE//LEUKODYSTROPHY//VANISHING WHITE MATTER DISEASE
8 0.0000070691 PROGRESSIVE STATE SELECTION//SPONTANEOUS TRANSFORMATION//GROWTH CONSTRAINT
9 0.0000064613 SEBACEOUS ADENITIS//COMPARAT NEUROMUSCULAR//LYMPHOCYTIC MURAL FOLLICULITIS
10 0.0000060985 PKAN//HALLERVORDEN SPATZ SYNDROME//NBIA