Class information for:
Level 1: BATTEN DISEASE//NEURONAL CEROID LIPOFUSCINOSIS//NEURONAL CEROID LIPOFUSCINOSES

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
6198 1452 34.4 72%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
330 17366 FABRY DISEASE//GAUCHER DISEASE//MUCOPOLYSACCHARIDOSES

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 BATTEN DISEASE Author keyword 573 93% 15% 218
2 NEURONAL CEROID LIPOFUSCINOSIS Author keyword 517 90% 15% 222
3 NEURONAL CEROID LIPOFUSCINOSES Author keyword 161 91% 5% 68
4 CLN3 Author keyword 119 79% 5% 76
5 INFANTILE NEURONAL CEROID LIPOFUSCINOSIS Author keyword 91 94% 2% 32
6 JNCL Author keyword 65 95% 1% 21
7 TRIPEPTIDYL PEPTIDASE I Author keyword 65 95% 1% 21
8 CLN6 Author keyword 64 100% 1% 21
9 CEROID LIPOFUSCINOSIS Author keyword 64 79% 3% 41
10 LATE INFANTILE NEURONAL CEROID LIPOFUSCINOSIS Author keyword 61 95% 1% 20

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 BATTEN DISEASE 573 93% 15% 218 Search BATTEN+DISEASE Search BATTEN+DISEASE
2 NEURONAL CEROID LIPOFUSCINOSIS 517 90% 15% 222 Search NEURONAL+CEROID+LIPOFUSCINOSIS Search NEURONAL+CEROID+LIPOFUSCINOSIS
3 NEURONAL CEROID LIPOFUSCINOSES 161 91% 5% 68 Search NEURONAL+CEROID+LIPOFUSCINOSES Search NEURONAL+CEROID+LIPOFUSCINOSES
4 CLN3 119 79% 5% 76 Search CLN3 Search CLN3
5 INFANTILE NEURONAL CEROID LIPOFUSCINOSIS 91 94% 2% 32 Search INFANTILE+NEURONAL+CEROID+LIPOFUSCINOSIS Search INFANTILE+NEURONAL+CEROID+LIPOFUSCINOSIS
6 JNCL 65 95% 1% 21 Search JNCL Search JNCL
7 TRIPEPTIDYL PEPTIDASE I 65 95% 1% 21 Search TRIPEPTIDYL+PEPTIDASE+I Search TRIPEPTIDYL+PEPTIDASE+I
8 CLN6 64 100% 1% 21 Search CLN6 Search CLN6
9 CEROID LIPOFUSCINOSIS 64 79% 3% 41 Search CEROID+LIPOFUSCINOSIS Search CEROID+LIPOFUSCINOSIS
10 LATE INFANTILE NEURONAL CEROID LIPOFUSCINOSIS 61 95% 1% 20 Search LATE+INFANTILE+NEURONAL+CEROID+LIPOFUSCINOSIS Search LATE+INFANTILE+NEURONAL+CEROID+LIPOFUSCINOSIS

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 BATTEN DISEASE 522 81% 22% 319
2 JANSKY BIELSCHOWSKY DISEASE 186 100% 3% 48
3 NEURONAL CEROID LIPOFUSCINOSIS 167 42% 21% 302
4 MITOCHONDRIAL ATP SYNTHASE 136 54% 12% 174
5 PALMITOYL PROTEIN THIOESTERASE 116 73% 6% 89
6 CLN3 PROTEIN 107 97% 2% 31
7 TRIPEPTIDYL PEPTIDASE I 98 84% 4% 53
8 GRANULAR OSMIOPHILIC DEPOSITS 85 100% 2% 26
9 LATE INFANTILE 83 84% 3% 46
10 BATTEN DISEASE GENE 81 96% 2% 25

Journals

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
Neuronal ceroid lipofuscinoses 2009 128 220 86%
Human pathology in NCL 2013 20 67 91%
New nomenclature and classification scheme for the neuronal ceroid lipofuscinoses 2012 34 24 100%
Genetic basis and phenotypic correlations of the neuronal ceroid lipofusinoses 2013 21 26 81%
Correlations between genotype, ultrastructural morphology and clinical phenotype in the neuronal ceroid lipofuscinoses 2005 126 141 94%
The neuronal ceroid-lipofuscinoses: A historical introduction 2013 13 36 97%
NCL diseases - clinical perspectives 2013 12 17 94%
Cell biology and function of neuronal ceroid lipofuscinosis-related proteins 2013 17 319 62%
Use of model organisms for the study of neuronal ceroid lipofuscinosis 2013 12 285 80%
CLN3, the protein associated with batten disease: Structure, function and localization 2005 65 38 95%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 PEDIAT STORAGE DISORDERS 46 78% 2.1% 31
2 PATHOL NEUROBIOL 13 36% 1.9% 28
3 MOL NEUROGENET DIAGNOST 11 100% 0.4% 6
4 KINGS HLTH PARTNERS NEURODEGENERAT 10 58% 0.8% 11
5 MRC NEURODEGENERAT PSYCHIAT 6 80% 0.3% 4
6 NEUROL VISUAL SCI NEUROL 6 80% 0.3% 4
7 AGING DEV BIOL 6 14% 2.5% 37
8 CELLULAR BASIS BEHAV PSYCHIAT 6 100% 0.3% 4
9 NEUROSCI CELLULAR BASIS BEHAV 4 67% 0.3% 4
10 SECT DEV GENET 4 20% 1.1% 16

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000073634 GLUTAMIC PEPTIDASE//CARBOXYL PROTEINASE//PEPSTATIN INSENSITIVE
2 0.0000072711 CYSTEINE STRING PROTEIN//CYSTEINE STRING PROTEINS//CSP ALPHA
3 0.0000067232 MUCOLIPIDOSIS TYPE IV//MUCOLIPIN//MUCOLIPIDOSIS IV
4 0.0000066465 LIPOFUSCIN//AGE PIGMENT//BROWN BOWEL SYNDROME
5 0.0000062546 TNFAIP1//KCTD7//KCTD10
6 0.0000061754 LAFORA DISEASE//POLYGLUCOSAN BODIES//UNVERRICHT LUNDBORG DISEASE
7 0.0000056178 ASPARTYLGLUCOSAMINURIA//GLYCOSYLASPARAGINASE//ASPARTYLGLUCOSAMINIDASE
8 0.0000044898 KLUVER BUCY SYNDROME//HYPERORALITY//POSTICTAL BEHAVIOR
9 0.0000044143 PKAN//HALLERVORDEN SPATZ SYNDROME//NBIA
10 0.0000042674 WOBBLER MOUSE//T 588//WOBBLER MICE