Class information for:
Level 1: HEREDITARY HEMORRHAGIC TELANGIECTASIA//PULMONARY ARTERIOVENOUS MALFORMATION//HEREDITARY HAEMORRHAGIC TELANGIECTASIA

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
6397 1425 23.2 67%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
880 10788 HEREDITARY HEMORRHAGIC TELANGIECTASIA//ENDOGLIN//TGF BETA

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 HEREDITARY HEMORRHAGIC TELANGIECTASIA Author keyword 300 72% 17% 237
2 PULMONARY ARTERIOVENOUS MALFORMATION Author keyword 102 72% 6% 80
3 HEREDITARY HAEMORRHAGIC TELANGIECTASIA Author keyword 98 76% 5% 69
4 RENDU OSLER WEBER SYNDROME Author keyword 58 88% 2% 28
5 PULMONARY ARTERIOVENOUS FISTULA Author keyword 58 73% 3% 44
6 RENDU OSLER WEBER DISEASE Author keyword 52 71% 3% 42
7 HEREDITARY HEMORRHAGIC TELANGIECTASIA HHT Author keyword 32 88% 1% 15
8 OSLER WEBER RENDU Author keyword 32 88% 1% 15
9 PULMONARY ARTERIOVENOUS MALFORMATIONS Author keyword 32 63% 2% 32
10 OSLER WEBER RENDU SYNDROME Author keyword 29 77% 1% 20

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 HEREDITARY HEMORRHAGIC TELANGIECTASIA 300 72% 17% 237 Search HEREDITARY+HEMORRHAGIC+TELANGIECTASIA Search HEREDITARY+HEMORRHAGIC+TELANGIECTASIA
2 PULMONARY ARTERIOVENOUS MALFORMATION 102 72% 6% 80 Search PULMONARY+ARTERIOVENOUS+MALFORMATION Search PULMONARY+ARTERIOVENOUS+MALFORMATION
3 HEREDITARY HAEMORRHAGIC TELANGIECTASIA 98 76% 5% 69 Search HEREDITARY+HAEMORRHAGIC+TELANGIECTASIA Search HEREDITARY+HAEMORRHAGIC+TELANGIECTASIA
4 RENDU OSLER WEBER SYNDROME 58 88% 2% 28 Search RENDU+OSLER+WEBER+SYNDROME Search RENDU+OSLER+WEBER+SYNDROME
5 PULMONARY ARTERIOVENOUS FISTULA 58 73% 3% 44 Search PULMONARY+ARTERIOVENOUS+FISTULA Search PULMONARY+ARTERIOVENOUS+FISTULA
6 RENDU OSLER WEBER DISEASE 52 71% 3% 42 Search RENDU+OSLER+WEBER+DISEASE Search RENDU+OSLER+WEBER+DISEASE
7 HEREDITARY HEMORRHAGIC TELANGIECTASIA HHT 32 88% 1% 15 Search HEREDITARY+HEMORRHAGIC+TELANGIECTASIA+HHT Search HEREDITARY+HEMORRHAGIC+TELANGIECTASIA+HHT
8 OSLER WEBER RENDU 32 88% 1% 15 Search OSLER+WEBER+RENDU Search OSLER+WEBER+RENDU
9 PULMONARY ARTERIOVENOUS MALFORMATIONS 32 63% 2% 32 Search PULMONARY+ARTERIOVENOUS+MALFORMATIONS Search PULMONARY+ARTERIOVENOUS+MALFORMATIONS
10 OSLER WEBER RENDU SYNDROME 29 77% 1% 20 Search OSLER+WEBER+RENDU+SYNDROME Search OSLER+WEBER+RENDU+SYNDROME

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 WEBER RENDU DISEASE 192 88% 6% 92
2 PULMONARY ARTERIOVENOUS MALFORMATIONS 82 44% 10% 144
3 HEREDITARY HEMORRHAGIC TELANGIECTASIA 59 22% 17% 239
4 HEPATIC VASCULAR MALFORMATIONS 55 87% 2% 27
5 HEMORRHAGIC TELANGIECTASIA 50 65% 3% 48
6 EMBOLOTHERAPY 48 30% 10% 137
7 HHT 46 67% 3% 42
8 ENDOGLIN 43 31% 8% 114
9 WEBER RENDU SYNDROME 40 82% 2% 23
10 OSLERS DISEASE 38 93% 1% 14

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Evidence-based management of epistaxis in hereditary haemorrhagic telangiectasia 2015 1 39 95%
Hereditary haemorrhagic telangiectasia: a clinical and scientific review 2009 109 51 71%
Hereditary haemorrhagic telangiectasia Pathophysiology, diagnosis and treatment 2010 102 160 63%
Hereditary hemorrhagic telangiectasia: An overview of diagnosis, management, and pathogenesis 2011 49 85 84%
Pulmonary arteriovenous malformations - A state of the art review 1998 208 74 86%
Pulmonary arteriovenous malformations in hereditary hemorrhagic telangiectasia - A Series of 126 patients 2007 65 98 87%
CURRENT CONCEPTS - HEREDITARY HEMORRHAGIC TELANGIECTASIA 1995 501 34 76%
Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (Rendu-Osler disease) 2007 59 128 84%
Liver involvement in hereditary hemorrhagic telangiectasia (HHT) 2007 51 66 94%
Hereditary haemorrhagic telangiectasia (Osier-Weber-Rendu syndrome): a view from the 21st century 2003 126 37 84%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 HHT 22 81% 0.9% 13
2 NHLI CARDIOVASC SCI 18 83% 0.7% 10
3 UNIV INTER HHT 14 100% 0.5% 7
4 REFERENCE MALAD RENDU OSLER 12 86% 0.4% 6
5 HHTIC LONDON 6 100% 0.3% 4
6 TORONTO HHT PIROL 3 100% 0.2% 3
7 UNIV INTERDEPARTMENTAL HHT 3 100% 0.2% 3
8 CLIN MED A MURRIPOLICLIN 2 67% 0.1% 2
9 HHT EXCELLENCE 2 67% 0.1% 2
10 HHT SOLUT 2 67% 0.1% 2

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000233699 ENDOGLIN//CD105//TRC105
2 0.0000106318 ANGIOMA SERPIGINOSUM//HEREDITARY BENIGN TELANGIECTASIA//GENERALIZED ESSENTIAL TELANGIECTASIA
3 0.0000063166 PANCREATIC ARTERIOVENOUS MALFORMATION//HIGH RESOLUTION MULTIPLANAR REFORMATTED IMAGES//INT ENVIRONM MED SCI
4 0.0000061413 HEMOPTYSIS//BRONCHIAL ARTERY EMBOLIZATION//BRONCHIAL ARTERY
5 0.0000054701 ARTERIOPORTAL FISTULA//SPLENIC ARTERIOVENOUS FISTULA//EXTRAHEPATIC ARTERIOPORTAL FISTULA
6 0.0000052108 HEPATOPULMONARY SYNDROME//PORTOPULMONARY HYPERTENSION//PORTO PULMONARY HYPERTENSION
7 0.0000048658 EPISTAXIS//NASAL PACKING//SPHENOPALATINE ARTERY
8 0.0000045592 MYOMATOUS ERYTHROCYTOSIS SYNDROME//EXTRAPULMONARY UPTAKE//LOWER EXTREMITY SWELLING
9 0.0000045274 VEIN OF GALEN//VEIN OF GALEN ANEURYSMAL MALFORMATION//VEIN OF GALEN MALFORMATION
10 0.0000036010 PATENT FORAMEN OVALE//PARADOXICAL EMBOLISM//ATRIAL SEPTAL ANEURYSM