Class information for:
Level 1: LEBERS HEREDITARY OPTIC NEUROPATHY//LHON//LEBER HEREDITARY OPTIC NEUROPATHY

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
8216 1207 33.4 75%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
201 20439 MELAS//MITOCHONDRIAL DNA//LEBERS HEREDITARY OPTIC NEUROPATHY

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 LEBERS HEREDITARY OPTIC NEUROPATHY Author keyword 308 85% 14% 163
2 LHON Author keyword 178 84% 8% 98
3 LEBER HEREDITARY OPTIC NEUROPATHY Author keyword 127 83% 6% 72
4 AUTOSOMAL DOMINANT OPTIC ATROPHY Author keyword 41 87% 2% 20
5 DOMINANT OPTIC ATROPHY Author keyword 33 75% 2% 24
6 TOBACCO ALCOHOL AMBLYOPIA Author keyword 24 91% 1% 10
7 OPA1 Author keyword 20 36% 4% 44
8 ADOA Author keyword 19 80% 1% 12
9 11778 MUTATION Author keyword 12 86% 0% 6
10 G11778A Author keyword 11 100% 0% 6

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 LEBERS HEREDITARY OPTIC NEUROPATHY 308 85% 14% 163 Search LEBERS+HEREDITARY+OPTIC+NEUROPATHY Search LEBERS+HEREDITARY+OPTIC+NEUROPATHY
2 LHON 178 84% 8% 98 Search LHON Search LHON
3 LEBER HEREDITARY OPTIC NEUROPATHY 127 83% 6% 72 Search LEBER+HEREDITARY+OPTIC+NEUROPATHY Search LEBER+HEREDITARY+OPTIC+NEUROPATHY
4 AUTOSOMAL DOMINANT OPTIC ATROPHY 41 87% 2% 20 Search AUTOSOMAL+DOMINANT+OPTIC+ATROPHY Search AUTOSOMAL+DOMINANT+OPTIC+ATROPHY
5 DOMINANT OPTIC ATROPHY 33 75% 2% 24 Search DOMINANT+OPTIC+ATROPHY Search DOMINANT+OPTIC+ATROPHY
6 TOBACCO ALCOHOL AMBLYOPIA 24 91% 1% 10 Search TOBACCO+ALCOHOL+AMBLYOPIA Search TOBACCO+ALCOHOL+AMBLYOPIA
7 OPA1 20 36% 4% 44 Search OPA1 Search OPA1
8 ADOA 19 80% 1% 12 Search ADOA Search ADOA
9 11778 MUTATION 12 86% 0% 6 Search 11778+MUTATION Search 11778+MUTATION
10 G11778A 11 100% 0% 6 Search G11778A Search G11778A

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 NEURORETINOPATHY 293 89% 11% 134
2 MITOCHONDRIAL DNA MUTATION 154 59% 14% 171
3 LHON 137 91% 5% 58
4 CHROMOSOME 3Q REGION 106 95% 3% 36
5 11778 MUTATION 79 87% 3% 39
6 FUNDUS FINDINGS 61 88% 2% 29
7 KJER TYPE 58 88% 2% 28
8 G11778A MUTATION 44 100% 1% 16
9 VISUAL LOSS SUSCEPTIBILITY 41 100% 1% 15
10 MTDNA MUTATIONS 40 39% 7% 81

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Inherited mitochondrial optic neuropathies 2009 105 214 79%
Drug-Related Mitochondrial Optic Neuropathies 2013 12 52 69%
Leber's hereditary optic neuropathy: A multifactorial disease 2006 68 124 87%
Treatment strategies for inherited optic neuropathies: past, present and future 2014 5 82 65%
Leber hereditary optic neuropathy 2002 158 110 91%
Mitochondrial dysfunction as a cause of optic neuropathies 2004 290 272 45%
Leber's Hereditary Optic Neuropathy 2011 20 33 85%
The Neuro-ophthalmology of Mitochondrial Disease 2010 52 228 38%
The optic nerve: A "mito-window" on mitochondrial neurodegeneration 2013 15 241 34%
OPA1-associated disorders: Phenotypes and pathophysiology 2009 35 66 79%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 SIRIRAJ NEUROGENET NETWORK 9 83% 0.4% 5
2 U694 4 23% 1.3% 16
3 AUGENKLIN 2 3 60% 0.2% 3
4 ATTARDI MITOCHONDRIAL BIOMED 2 24% 0.7% 8
5 ZHEJIANG PROV MED GENET 2 10% 1.7% 20
6 MINS 2 67% 0.2% 2
7 SCUOLA SUPER PERFEZIONAMENTO S ANNA 2 67% 0.2% 2
8 SERV NEUROFTALMOL 2 67% 0.2% 2
9 E0018 2 50% 0.2% 3
10 CARDIFF EYE UNIT 2 18% 0.7% 9

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000128138 MELAS//MITOCHONDRIAL ENCEPHALOMYOPATHY//KEARNS SAYRE SYNDROME
2 0.0000084189 MITOCHONDRIAL FISSION//MITOCHONDRIAL DYNAMICS//DRP1
3 0.0000072725 D310//MITOCHONDRIAL MICROSATELLITE INSTABILITY//MITOCHONDRIAL HAPLOGROUPS
4 0.0000068055 COMPLEX I//NADH UBIQUINONE OXIDOREDUCTASE//NADH UBIQUINONE OXIDOREDUCTASE
5 0.0000065878 WOLFRAM SYNDROME//WFS1//WOLFRAMIN
6 0.0000057700 AUDITORY NEUROPATHY//AUDITORY NEUROPATHY SPECTRUM DISORDER//OTOF
7 0.0000056007 OPTIC NEURITIS//RETINAL SEGMENTATION//LOW CONTRAST LETTER ACUITY
8 0.0000054447 PONTOSUBICULAR NECROSIS//INFANTILE BILATERAL STRIATAL NECROSIS//BRAINSTEM NECROSIS
9 0.0000053429 SMON VIRUS//IMV//GRP STUDY EPIDEM NEUROPATHY
10 0.0000049921 ECUAC DIFERENCIALES//UNIDADE SISTEMAS SAUDE//CUBAN DOCTORS