Class information for:
Level 2: OSTEOGENESIS IMPERFECTA//EHLERS DANLOS SYNDROME//EHLERS DANLOS SYNDROME TYPE IV

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
1091 9322 34.0 64%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)



ID, lev.
above
Publications Label for level above
474 21638 JOURNAL OF THE AMERICAN LEATHER CHEMISTS ASSOCIATION//OSTEOGENESIS IMPERFECTA//JOURNAL OF THE SOCIETY OF LEATHER TECHNOLOGISTS AND CHEMISTS

Classes in level below (level 1)



ID, lev. below Publications Label for level below
3500 1892 OSTEOGENESIS IMPERFECTA//BONE EXTRACELLULAR MATRIX BRANCH//BRUCK SYNDROME
7359 1297 COLLAGEN XVI//TYPE XI COLLAGEN//COLLAGEN XII
7505 1281 EHLERS DANLOS SYNDROME//EHLERS DANLOS SYNDROME TYPE IV//JOINT HYPERMOBILITY
7824 1246 TRIPLE HELIX//COLLAGEN LIKE PEPTIDE//COLLAGEN LIKE PEPTIDES
13148 793 LARP6//ALPHA 2I COLLAGEN//DERIVATIVE OF ERYTHROMYCIN
13707 755 SERUM LAMININ//7S COLLAGEN//SERUM TYPE IV COLLAGEN
15876 618 BETHLEM MYOPATHY//COLLAGEN VI//TYPE VI COLLAGEN
18152 501 LYSYL HYDROXYLASE//EHLERS DANLOS SYNDROME TYPE VI//AGEN UNIT
23910 276 HSP47//HEAT SHOCK PROTEIN 47//UMB GREENEBAUM CANC
29101 158 POSTERIOR SCLERAL REINFORCEMENT//ABOVE KNEE FEMOROPOPLITEAL BYPASS//CELLULES TISSUS
30351 139 POLARIZATION COLORS//MED LUMEZZANE//GLOBULE LEUKOCYTE
30445 138 TOYOOKA JR//TOYO OKA JR//LIVING SCI PROGRAM PROC
31211 126 ELECTRON OPTICAL DATA//AXIAL OSTEOMALACIA//FIBROGENESIS IMPERFECTA OSSIUM
32832 102 CUTANEOUS ASTHENIA//DERMATOSPARAXIS//HEREDITARY EQUINE REGIONAL DERMAL ASTHENIA

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 OSTEOGENESIS IMPERFECTA Author keyword 768 71% 7% 619
2 EHLERS DANLOS SYNDROME Author keyword 296 66% 3% 278
3 EHLERS DANLOS SYNDROME TYPE IV Author keyword 111 100% 0% 32
4 JOINT HYPERMOBILITY Author keyword 98 74% 1% 72
5 BENIGN JOINT HYPERMOBILITY SYNDROME Author keyword 73 96% 0% 23
6 BONE EXTRACELLULAR MATRIX BRANCH Address 73 86% 0% 37
7 BETHLEM MYOPATHY Author keyword 69 91% 0% 29
8 VASCULAR EHLERS DANLOS SYNDROME Author keyword 53 95% 0% 18
9 HYPERMOBILITY Author keyword 52 46% 1% 84
10 HSP47 Author keyword 51 60% 1% 56

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 OSTEOGENESIS IMPERFECTA 768 71% 7% 619 Search OSTEOGENESIS+IMPERFECTA Search OSTEOGENESIS+IMPERFECTA
2 EHLERS DANLOS SYNDROME 296 66% 3% 278 Search EHLERS+DANLOS+SYNDROME Search EHLERS+DANLOS+SYNDROME
3 EHLERS DANLOS SYNDROME TYPE IV 111 100% 0% 32 Search EHLERS+DANLOS+SYNDROME+TYPE+IV Search EHLERS+DANLOS+SYNDROME+TYPE+IV
4 JOINT HYPERMOBILITY 98 74% 1% 72 Search JOINT+HYPERMOBILITY Search JOINT+HYPERMOBILITY
5 BENIGN JOINT HYPERMOBILITY SYNDROME 73 96% 0% 23 Search BENIGN+JOINT+HYPERMOBILITY+SYNDROME Search BENIGN+JOINT+HYPERMOBILITY+SYNDROME
6 BETHLEM MYOPATHY 69 91% 0% 29 Search BETHLEM+MYOPATHY Search BETHLEM+MYOPATHY
7 VASCULAR EHLERS DANLOS SYNDROME 53 95% 0% 18 Search VASCULAR+EHLERS+DANLOS+SYNDROME Search VASCULAR+EHLERS+DANLOS+SYNDROME
8 HYPERMOBILITY 52 46% 1% 84 Search HYPERMOBILITY Search HYPERMOBILITY
9 HSP47 51 60% 1% 56 Search HSP47 Search HSP47
10 COLLAGEN VI 49 59% 1% 55 Search COLLAGEN+VI Search COLLAGEN+VI

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PROCOLLAGEN 183 38% 4% 387
2 SYNDROME TYPE IV 155 55% 2% 193
3 TRIPLE HELIX 124 30% 4% 349
4 INTRAVENOUS PAMIDRONATE TREATMENT 99 87% 1% 48
5 BRITTLE BONE DISEASE 91 70% 1% 75
6 IX COLLAGEN 89 52% 1% 120
7 SYNDROME TYPE VI 85 70% 1% 71
8 EHLERS DANLOS SYNDROME 84 27% 3% 262
9 XAA POSITION 80 100% 0% 25
10 BETHLEM MYOPATHY 76 62% 1% 78

Journals



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 COLLAGEN AND RELATED RESEARCH 30 29% 1% 90
2 MATRIX BIOLOGY 17 11% 2% 141
3 MATRIX 8 17% 0% 42

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Collagen Structure and Stability 2009 376 134 77%
New perspectives on osteogenesis imperfecta 2011 119 190 79%
COLLAGENS - MOLECULAR-BIOLOGY, DISEASES, AND POTENTIALS FOR THERAPY 1995 941 191 47%
Fibrillar, Fibril-associated and Basement Membrane Collagens of the Arterial Wall: Architecture, Elasticity and Remodeling Under Stress 2015 4 131 38%
Osteogenesis imperfecta 2004 400 115 68%
Collagens, modifying enzymes and their mutations in humans, flies and worms 2004 457 72 47%
COLLAGEN FAMILY OF PROTEINS 1991 696 49 73%
Ziploc-ing the structure: Triple helix formation is coordinated by rough endoplasmic reticulum resident PPIases 2015 2 149 48%
Consortium for osteogeneslis imperfecta mutations in the helical domain of type I collagen: Regions rich in lethal mutations align with collagen binding sites for integrins and proteoglycans 2007 158 60 60%
Collagen VI related muscle disorders 2005 174 114 86%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BONE EXTRACELLULAR MATRIX BRANCH 73 86% 0.4% 37
2 SECT CONNECT TISSUE DISORDERS 38 93% 0.2% 14
3 AGEN UNIT 35 35% 0.9% 80
4 HYPERMOBIL CLIN 18 83% 0.1% 10
5 TOYOOKA JR 17 70% 0.2% 14
6 CONNECT TISSUE UNIT 12 59% 0.1% 13
7 BEMB 8 100% 0.1% 5
8 TOYO OKA JR 8 62% 0.1% 8
9 BONE OSTEOGENESIS IMPERFECTA 6 80% 0.0% 4
10 UMB GREENEBAUM CANC 6 80% 0.0% 4

Related classes at same level (level 2)



Rank Relatedness score Related classes
1 0.0000021033 GELATIN//ACID SOLUBLE COLLAGEN//PEPSIN SOLUBLE COLLAGEN
2 0.0000018507 ACHONDROPLASIA//HYPOCHONDROPLASIA//THANATOPHORIC DYSPLASIA
3 0.0000014672 MARFAN SYNDROME//FIBRILLIN//LYSYL OXIDASE
4 0.0000012255 MICRODAMAGE//CORTICAL BONE//VIBROARTHROGRAPHY
5 0.0000008032 JOURNAL OF THE AMERICAN LEATHER CHEMISTS ASSOCIATION//JOURNAL OF THE SOCIETY OF LEATHER TECHNOLOGISTS AND CHEMISTS//LEATHER ENGN
6 0.0000007541 LAMININ//FIBRONECTIN//INVASION & METASTASIS
7 0.0000007387 SPARC//GROWTH DIFFERENTIATION FACTOR 15//GDF 15
8 0.0000007147 HEPARANASE//HEPARAN SULFATE//DECORIN
9 0.0000006317 ANTERIOR CRUCIATE LIGAMENT//ACL RECONSTRUCTION//DOUBLE BUNDLE
10 0.0000005704 PEDF//PIGMENT EPITHELIUM DERIVED FACTOR//PIGMENT EPITHELIUM DERIVED FACTOR PEDF