Class information for:
Level 2: HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA//FRIEDREICH ATAXIA

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
1789 5796 36.9 81%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)


ID, lev.
above		 Publications Label for level above
588 12909 HUNTINGTONS DISEASE//POLYGLUTAMINE//HUNTINGTIN

Classes in level below (level 1)


ID, lev. below Publications Label for level below
2837 2060 MACHADO JOSEPH DISEASE//SPINOCEREBELLAR ATAXIA//SCA2
7601 1269 FRIEDREICH ATAXIA//FRIEDREICHS ATAXIA//FRATAXIN
9970 1039 HEREDITARY SPASTIC PARAPLEGIA//SPG4//SPASTIN
13666 758 CYSTEINE DESULFURASE//ISCU//ZYTOBIOL ZYTOPATHOL
19037 458 AOA2//ARSACS//APRATAXIN
26312 212 MARINESCO SJOGREN SYNDROME//MICRO SYNDROME//WARBURG MICRO SYNDROME

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 HEREDITARY SPASTIC PARAPLEGIA Author keyword 381 81% 4% 227
2 FRIEDREICHS ATAXIA Author keyword 307 73% 4% 234
3 FRIEDREICH ATAXIA Author keyword 305 81% 3% 182
4 FRATAXIN Author keyword 263 82% 3% 154
5 SPINOCEREBELLAR ATAXIA Author keyword 232 60% 4% 256
6 MACHADO JOSEPH DISEASE Author keyword 198 72% 3% 154
7 SPG4 Author keyword 176 96% 1% 53
8 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA Author keyword 140 92% 1% 56
9 SCA2 Author keyword 125 83% 1% 70
10 SPASTIN Author keyword 121 82% 1% 70

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 HEREDITARY SPASTIC PARAPLEGIA 381 81% 4% 227 Search HEREDITARY+SPASTIC+PARAPLEGIA Search HEREDITARY+SPASTIC+PARAPLEGIA
2 FRIEDREICHS ATAXIA 307 73% 4% 234 Search FRIEDREICHS+ATAXIA Search FRIEDREICHS+ATAXIA
3 FRIEDREICH ATAXIA 305 81% 3% 182 Search FRIEDREICH+ATAXIA Search FRIEDREICH+ATAXIA
4 FRATAXIN 263 82% 3% 154 Search FRATAXIN Search FRATAXIN
5 SPINOCEREBELLAR ATAXIA 232 60% 4% 256 Search SPINOCEREBELLAR+ATAXIA Search SPINOCEREBELLAR+ATAXIA
6 MACHADO JOSEPH DISEASE 198 72% 3% 154 Search MACHADO+JOSEPH+DISEASE Search MACHADO+JOSEPH+DISEASE
7 SPG4 176 96% 1% 53 Search SPG4 Search SPG4
8 AUTOSOMAL DOMINANT CEREBELLAR ATAXIA 140 92% 1% 56 Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA Search AUTOSOMAL+DOMINANT+CEREBELLAR+ATAXIA
9 SCA2 125 83% 1% 70 Search SCA2 Search SCA2
10 SPASTIN 121 82% 1% 70 Search SPASTIN Search SPASTIN

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 DOMINANT CEREBELLAR ATAXIA 438 73% 6% 332
2 MACHADO JOSEPH DISEASE 342 53% 8% 458
3 YEAST FRATAXIN 282 81% 3% 170
4 SPINOCEREBELLAR ATAXIA 281 53% 6% 369
5 FRATAXIN 215 76% 3% 151
6 PARAPARESIS 193 70% 3% 162
7 SCA2 192 84% 2% 105
8 TRIPLET REPEAT EXPANSION 187 69% 3% 160
9 CYSTEINE DESULFURASE 177 78% 2% 117
10 FRIEDREICH ATAXIA 170 54% 4% 218

Journals


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 CEREBELLUM 20 15% 2% 118
2 NEUROGENETICS 8 12% 1% 66

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
Function and biogenesis of iron-sulphur proteins 2009 305 99 74%
Iron/sulfur proteins biogenesis in prokaryotes: Formation, regulation and diversity 2013 54 197 75%
Autosomal dominant cerebellar ataxias: polyglutamine expansions and beyond 2010 151 99 83%
The role of mitochondria in cellular iron-sulfur protein biogenesis and iron metabolism 2012 121 235 54%
Friedreich's ataxia: Pathology, pathogenesis, and molecular genetics 2011 97 64 91%
Structure, function, and formation of biological iron-sulfur clusters 2005 554 202 57%
Mammalian iron-sulphur proteins: novel insights into biogenesis and function 2015 3 102 70%
Autosomal dominant cerebellar ataxias: clinical features, genetics, and pathogenesis 2004 425 135 68%
Hereditary spastic paraplegias with autosomal dominant, recessive, X-linked, or maternal trait of inheritance 2012 60 145 85%
Iron-sulfur cluster biogenesis in mammalian cells: New insights into the molecular mechanisms of cluster delivery 2015 3 311 57%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 ZYTOBIOL ZYTOPATHOL 42 56% 0.9% 51
2 UNIGENE 23 44% 0.7% 41
3 BRUCE LEFROY GENET HLTH 19 34% 0.8% 44
4 GENET CYTOGENET 16 23% 1.0% 59
5 ZYTOBIOL 12 42% 0.4% 22
6 ENFERMEDADES NEUROL 11 100% 0.1% 6
7 ROSE MOSS PARKINSON NEURODEGENERAT DIS 11 100% 0.1% 6
8 GENET CYTOGENET EMBRYOL 11 25% 0.6% 36
9 EVANS CHEM 10 31% 0.4% 26
10 NEUROGENET BRANCH 9 19% 0.7% 43

Related classes at same level (level 2)


Rank Relatedness score Related classes
1 0.0000033333 HUNTINGTONS DISEASE//HUNTINGTIN//HUNTINGTON DISEASE
2 0.0000007928 CEREBELLUM//PURKINJE CELL//CLIMBING FIBERS
3 0.0000007705 AMYOTROPHIC LATERAL SCLEROSIS//SPINAL MUSCULAR ATROPHY//MOTOR NEURON DISEASE
4 0.0000007175 COENZYME Q10//UBIQUINONE//COENZYME Q
5 0.0000006912 FAMILIAL DYSAUTONOMIA//ANKYLOGLOSSIA//TONGUE TIE
6 0.0000005829 FRAGILE X SYNDROME//FRAGILE X//FMR1
7 0.0000005761 RHOMBENCEPHALOSYNAPSIS//PONTOCEREBELLAR HYPOPLASIA//ARTHROGRYPOSIS
8 0.0000005195 CYSTINOSIS//PANTOTHENATE KINASE//PKAN
9 0.0000004636 SIDEROPHORE//SIDEROPHORES//PYOVERDINS
10 0.0000004571 BIOTIN//HOLOCARBOXYLASE SYNTHETASE//BIOTINIDASE DEFICIENCY