Class information for:
Level 2: GALACTOSEMIA//GALACTOSE 1 PHOSPHATE URIDYLTRANSFERASE//GALACTOSE 1 PHOSPHATE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
2915 2265 32.6 62%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 3)



ID, lev.
above
Publications Label for level above
295 37066 CORYNEBACTERIUM GLUTAMICUM//ACTA CRYSTALLOGRAPHICA SECTION D-BIOLOGICAL CRYSTALLOGRAPHY//DIHYDRODIPICOLINATE SYNTHASE

Classes in level below (level 1)



ID, lev. below Publications Label for level below
11725 895 GALACTOSEMIA//GALACTOSE 1 PHOSPHATE URIDYLTRANSFERASE//GALACTOSE 1 PHOSPHATE
15041 666 GLMU//UDP GLUCOSE PYROPHOSPHORYLASE//UDP SUGAR PYROPHOSPHORYLASE
22111 336 UDP SUGAR HYDROLASE//PHOSPHOHEXOMUTASE//HAD SUPERFAMILY
26064 218 HISTIDINE BIOSYNTHESIS//IMIDAZOLEGLYCEROL PHOSPHATE DEHYDRATASE//HISTIDINOL DEHYDROGENASE
29583 150 UDP GLUCOSE DEHYDROGENASE//UDP GLCA//UDP GLUCURONATE

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 GALACTOSEMIA Author keyword 145 64% 6% 143
2 GALACTOSE 1 PHOSPHATE URIDYLTRANSFERASE Author keyword 69 91% 1% 29
3 GALACTOSE 1 PHOSPHATE Author keyword 69 93% 1% 26
4 GALACTOSAEMIA Author keyword 44 67% 2% 39
5 CLASSIC GALACTOSEMIA Author keyword 38 93% 1% 14
6 GLMU Author keyword 31 92% 1% 12
7 UDP GLUCOSE PYROPHOSPHORYLASE Author keyword 24 52% 1% 32
8 GALACTONATE Author keyword 21 90% 0% 9
9 UDP SUGAR PYROPHOSPHORYLASE Author keyword 20 100% 0% 9
10 GALACTOSE 1 PHOSPHATE URIDYL TRANSFERASE Author keyword 17 79% 0% 11

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 GALACTOSEMIA 145 64% 6% 143 Search GALACTOSEMIA Search GALACTOSEMIA
2 GALACTOSE 1 PHOSPHATE URIDYLTRANSFERASE 69 91% 1% 29 Search GALACTOSE+1+PHOSPHATE+URIDYLTRANSFERASE Search GALACTOSE+1+PHOSPHATE+URIDYLTRANSFERASE
3 GALACTOSE 1 PHOSPHATE 69 93% 1% 26 Search GALACTOSE+1+PHOSPHATE Search GALACTOSE+1+PHOSPHATE
4 GALACTOSAEMIA 44 67% 2% 39 Search GALACTOSAEMIA Search GALACTOSAEMIA
5 CLASSIC GALACTOSEMIA 38 93% 1% 14 Search CLASSIC+GALACTOSEMIA Search CLASSIC+GALACTOSEMIA
6 GLMU 31 92% 1% 12 Search GLMU Search GLMU
7 UDP GLUCOSE PYROPHOSPHORYLASE 24 52% 1% 32 Search UDP+GLUCOSE+PYROPHOSPHORYLASE Search UDP+GLUCOSE+PYROPHOSPHORYLASE
8 GALACTONATE 21 90% 0% 9 Search GALACTONATE Search GALACTONATE
9 UDP SUGAR PYROPHOSPHORYLASE 20 100% 0% 9 Search UDP+SUGAR+PYROPHOSPHORYLASE Search UDP+SUGAR+PYROPHOSPHORYLASE
10 GALACTOSE 1 PHOSPHATE URIDYL TRANSFERASE 17 79% 0% 11 Search GALACTOSE+1+PHOSPHATE+URIDYL+TRANSFERASE Search GALACTOSE+1+PHOSPHATE+URIDYL+TRANSFERASE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 CLASSICAL GALACTOSEMIA 99 87% 2% 48
2 URIDYL TRANSFERASE 84 87% 2% 41
3 CYTIDINE DIPHOSPHATE 3 6 DIDEOXYHEXOSES 83 94% 1% 30
4 GALACTOSE 1 PHOSPHATE 67 87% 1% 33
5 URIDYLTRANSFERASE 67 80% 2% 41
6 URIDINE DIPHOSPHOGLUCOSE DEHYDROGENASE 64 86% 1% 32
7 HUMAN UDP GALACTOSE 4 EPIMERASE 64 100% 1% 21
8 EPIMERASE DEFICIENCY GALACTOSEMIA 62 90% 1% 27
9 GALACTOSEMIA 58 47% 4% 90
10 GALACTOSE 1 PHOSPHATE URIDYLTRANSFERASE DEFICIENCY 58 83% 1% 33

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Mutations in hereditary phosphoglucomutase 1 deficiency map to key regions of enzyme structure and function 2015 1 30 50%
The Leloir pathway: A mechanistic imperative for three enzymes to change the stereochemical configuration of a single carbon in galactose 1996 212 13 100%
The structural biology of enzymes involved in natural product glycosylation 2012 27 226 47%
A re-evaluation of life-long severe galactose restriction for the nutrition management of classic galactosemia 2014 3 52 75%
Structure and function of enzymes of the Leloir pathway for galactose metabolism 2003 168 45 62%
Enzyme Promiscuity: Engine of Evolutionary Innovation 2014 10 66 24%
Galactose Toxicity in Animals 2009 22 152 75%
Chemical and Stereochemical Actions of UDP-Galactose 4-Epimerase 2013 5 34 85%
An updated review of the long-term neurological effects of galactosemia 2005 37 67 91%
Gonadal function in male and female patients with classic galactosemia 2010 21 93 62%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 BIOCHEM DEV MOL DIS 13 69% 0.5% 11
2 PEDIAT CLIN NAKA KU 4 75% 0.1% 3
3 PEDIATMETAB 3 100% 0.1% 3
4 PROGRAM GENET MOL BIOL 2 12% 0.8% 18
5 BIOL MOL CELULAR PLANTAS EDUARDO PRIMO YUF 2 67% 0.1% 2
6 NCIMD 2 67% 0.1% 2
7 BIOSYNTHET CHEM 2 19% 0.4% 9
8 AGROBIOTECNOL LITORAL UNL CONICET 1 50% 0.1% 2
9 CHILDRENS HOSP PHILADELPHIAMETAB 1 100% 0.1% 2
10 DIPARTIMENTO BIOL CELLULARE SVILUPPO VIALE SCI 1 100% 0.1% 2

Related classes at same level (level 2)



Rank Relatedness score Related classes
1 0.0000022898 O ANTIGEN//BACTERIAL POLYSACCHARIDE STRUCTURE//O SPECIFIC POLYSACCHARIDE
2 0.0000012819 ACTA CRYSTALLOGRAPHICA SECTION D-BIOLOGICAL CRYSTALLOGRAPHY//ACTA CRYSTALLOGRAPHICA SECTION A//JOURNAL OF APPLIED CRYSTALLOGRAPHY
3 0.0000010302 O GLCNAC//O GLCNACASE//O GLCNAC TRANSFERASE
4 0.0000010185 ALANINE RACEMASE//TYROSINE PHENOL LYASE//MURD
5 0.0000009864 CONGENITAL DISORDERS OF GLYCOSYLATION//GLYCOPROTEOMICS//OLIGOSACCHARYLTRANSFERASE
6 0.0000008492 STREPTOMYCES//ISOPENICILLIN N SYNTHASE//STREPTOMYCES CLAVULIGERUS
7 0.0000008436 L ARABINOSE ISOMERASE//RARE SUGAR//D PSICOSE
8 0.0000008324 STARCH SYNTHESIS//ADP GLUCOSE PYROPHOSPHORYLASE//SUCROSE SYNTHASE
9 0.0000008162 CORYNEBACTERIUM GLUTAMICUM//SHIKIMATE PATHWAY//SHIKIMATE KINASE
10 0.0000007025 XYLOGLUCAN//PECTIN//PECTIN LYASE