Class information for: |
Basic class information |
ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
---|---|---|---|
3340 | 1269 | 23.8 | 59% |
Classes in level above (level 3) |
ID, lev. above |
Publications | Label for level above |
---|---|---|
371 | 29923 | HEPATIC ENCEPHALOPATHY//KETOGENIC DIET//CARNITINE |
Classes in level below (level 1) |
ID, lev. below | Publications | Label for level below |
---|---|---|
12382 | 846 | TYROSINEMIA//NTBC//SUCCINYLACETONE |
21710 | 351 | ALKAPTONURIA//OCHRONOSIS//HOMOGENTISIC ACID |
34414 | 72 | PURPLE URINE BAG SYNDROME//PURPLE URINE//FD C BLUE NO 1 |
Terms with highest relevance score |
Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|---|
1 | ALKAPTONURIA | Author keyword | 258 | 85% | 11% | 136 |
2 | OCHRONOSIS | Author keyword | 184 | 83% | 8% | 105 |
3 | HOMOGENTISIC ACID | Author keyword | 77 | 71% | 5% | 62 |
4 | NTBC | Author keyword | 65 | 93% | 2% | 25 |
5 | TYROSINEMIA | Author keyword | 58 | 68% | 4% | 50 |
6 | SUCCINYLACETONE | Author keyword | 44 | 77% | 2% | 30 |
7 | OCHRONOTIC ARTHROPATHY | Author keyword | 32 | 88% | 1% | 15 |
8 | TYROSINEMIA TYPE II | Author keyword | 30 | 100% | 1% | 12 |
9 | TYROSINEMIA TYPE I | Author keyword | 30 | 79% | 1% | 19 |
10 | NITISINONE | Author keyword | 26 | 87% | 1% | 13 |
Web of Science journal categories |
Author Key Words |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | ALKAPTONURIA | 258 | 85% | 11% | 136 | Search ALKAPTONURIA | Search ALKAPTONURIA |
2 | OCHRONOSIS | 184 | 83% | 8% | 105 | Search OCHRONOSIS | Search OCHRONOSIS |
3 | HOMOGENTISIC ACID | 77 | 71% | 5% | 62 | Search HOMOGENTISIC+ACID | Search HOMOGENTISIC+ACID |
4 | NTBC | 65 | 93% | 2% | 25 | Search NTBC | Search NTBC |
5 | TYROSINEMIA | 58 | 68% | 4% | 50 | Search TYROSINEMIA | Search TYROSINEMIA |
6 | SUCCINYLACETONE | 44 | 77% | 2% | 30 | Search SUCCINYLACETONE | Search SUCCINYLACETONE |
7 | OCHRONOTIC ARTHROPATHY | 32 | 88% | 1% | 15 | Search OCHRONOTIC+ARTHROPATHY | Search OCHRONOTIC+ARTHROPATHY |
8 | TYROSINEMIA TYPE II | 30 | 100% | 1% | 12 | Search TYROSINEMIA+TYPE+II | Search TYROSINEMIA+TYPE+II |
9 | TYROSINEMIA TYPE I | 30 | 79% | 1% | 19 | Search TYROSINEMIA+TYPE+I | Search TYROSINEMIA+TYPE+I |
10 | NITISINONE | 26 | 87% | 1% | 13 | Search NITISINONE | Search NITISINONE |
Key Words Plus |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | HEREDITARY TYROSINEMIA | 175 | 66% | 13% | 162 |
2 | ALKAPTONURIA | 151 | 79% | 8% | 96 |
3 | 4 HYDROXYPHENYLPYRUVATE DIOXYGENASE | 116 | 61% | 10% | 123 |
4 | NTBC | 92 | 92% | 3% | 36 |
5 | 2 2 NITRO 4 TRIFLUOROMETHYLBENZOYL 1 3 CYCLOHEXANEDIONE | 60 | 100% | 2% | 20 |
6 | OCHRONOTIC ARTHROPATHY | 51 | 91% | 2% | 21 |
7 | FUMARYLACETOACETATE | 50 | 88% | 2% | 23 |
8 | OCHRONOSIS | 48 | 70% | 3% | 40 |
9 | HOMOGENTISATE 1 2 DIOXYGENASE GENE | 42 | 94% | 1% | 15 |
10 | FUMARYLACETOACETATE HYDROLASE GENE | 35 | 89% | 1% | 16 |
Journals |
Reviews |
Title | Publ. year | Cit. | Active references |
% act. ref. to same field |
---|---|---|---|---|
Recommendations for the management of tyrosinaemia type 1 | 2013 | 13 | 31 | 94% |
Alkaptonuria - a review of surgical and autopsy pathology | 2008 | 29 | 18 | 94% |
4-Hydroxyphenylpyruvate dioxygenase and hydroxymandelate synthase: Exemplars of the alpha-keto acid dependent oxygenases | 2014 | 4 | 88 | 49% |
4-Hydroxyphenylpyruvate dioxygenase | 2005 | 82 | 86 | 45% |
New developments in ochronosis: review of the literature | 2005 | 29 | 18 | 100% |
Experience of nitisinone for the pharmacological treatment of hereditary tyrosinaemia type 1 | 2008 | 16 | 49 | 98% |
Hepatorenal tyrosinemia | 2012 | 3 | 12 | 100% |
Tyrosinemia: A review | 2001 | 67 | 70 | 81% |
Alkaptonuria, ochronosis, and ochronotic arthropathy | 2004 | 30 | 24 | 92% |
Alkaptonuria-Associated Aortic Stenosis | 2013 | 2 | 12 | 92% |
Address terms |
Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | INTERDIPARTIMENTALE STUDIO BIOCHIM PATOL OSTE | 18 | 89% | 0.6% | 8 |
2 | ALK TONURIA OFF | 3 | 100% | 0.2% | 3 |
3 | ERROS INATOS METAB | 2 | 18% | 0.6% | 8 |
4 | UNIDAD PATOL MOL | 1 | 23% | 0.4% | 5 |
5 | LCBE | 1 | 40% | 0.2% | 2 |
6 | CELL DEV GENET | 1 | 12% | 0.6% | 8 |
7 | CELLULAR DEV GENET | 1 | 17% | 0.4% | 5 |
8 | ARTHUR F SCOTT CHEM | 1 | 33% | 0.2% | 2 |
9 | PHYSIOL GENET PLANTES INTERET AGRON | 1 | 33% | 0.2% | 2 |
10 | REFERENCE INHERITED METAB DIS | 1 | 14% | 0.4% | 5 |
Related classes at same level (level 2) |
Rank | Relatedness score | Related classes |
---|---|---|
1 | 0.0000014571 | 8 AZASTEROIDS//THE RITTER REACTION//8 AZASTEROID |
2 | 0.0000013356 | MAPLE SYRUP URINE DISEASE//METHYLMALONIC ACIDEMIA//JOURNAL OF INHERITED METABOLIC DISEASE |
3 | 0.0000007759 | MODY//MATURITY ONSET DIABETES OF THE YOUNG//NEONATAL DIABETES |
4 | 0.0000006526 | VITILIGO//TYROSINASE//MELANOGENESIS |
5 | 0.0000006184 | HEME OXYGENASE//PORPHYRIA//ACUTE INTERMITTENT PORPHYRIA |
6 | 0.0000005669 | WEED TECHNOLOGY//WEED SCIENCE//HERBICIDE RESISTANCE |
7 | 0.0000005243 | DIFFUSE IDIOPATHIC SKELETAL HYPEROSTOSIS//FORESTIERS DISEASE//DISH |
8 | 0.0000005146 | PHENYLKETONURIA//TETRAHYDROBIOPTERIN//HYPERPHENYLALANINEMIA |
9 | 0.0000004359 | GLYPHOSATE//INTERDIPARTIMENTALE NATRISK//ATRAZINE |
10 | 0.0000004112 | BIOARTIFICIAL LIVER//LIVER REGENERATION//HEPATOCYTE TRANSPLANTATION |