Class information for:
Level 1: ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS//EPIDERMAL NEVUS SYNDROME//OCULOCEREBROCUTANEOUS SYNDROME

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
12109 867 21.3 58%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
896 10655 BASAL CELL CARCINOMA//EXTRAMAMMARY PAGETS DISEASE//SEBACEOUS CARCINOMA

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS Author keyword 62 92% 3% 24
2 EPIDERMAL NEVUS SYNDROME Author keyword 35 74% 3% 26
3 OCULOCEREBROCUTANEOUS SYNDROME Author keyword 27 83% 2% 15
4 LICHEN STRIATUS Author keyword 25 73% 2% 19
5 NEVUS SEBACEUS Author keyword 21 57% 3% 25
6 EPIDERMAL NEVUS Author keyword 19 51% 3% 27
7 BLASCHKITIS Author keyword 18 89% 1% 8
8 SCHIMMELPENNING FEUERSTEIN MIMS SYNDROME Author keyword 18 89% 1% 8
9 INFLAMMATORY LINEAR VERRUCOUS EPIDERMAL NEVUS Author keyword 14 100% 1% 7
10 DELLEMAN SYNDROME Author keyword 12 86% 1% 6

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS 62 92% 3% 24 Search ENCEPHALOCRANIOCUTANEOUS+LIPOMATOSIS Search ENCEPHALOCRANIOCUTANEOUS+LIPOMATOSIS
2 EPIDERMAL NEVUS SYNDROME 35 74% 3% 26 Search EPIDERMAL+NEVUS+SYNDROME Search EPIDERMAL+NEVUS+SYNDROME
3 OCULOCEREBROCUTANEOUS SYNDROME 27 83% 2% 15 Search OCULOCEREBROCUTANEOUS+SYNDROME Search OCULOCEREBROCUTANEOUS+SYNDROME
4 LICHEN STRIATUS 25 73% 2% 19 Search LICHEN+STRIATUS Search LICHEN+STRIATUS
5 NEVUS SEBACEUS 21 57% 3% 25 Search NEVUS+SEBACEUS Search NEVUS+SEBACEUS
6 EPIDERMAL NEVUS 19 51% 3% 27 Search EPIDERMAL+NEVUS Search EPIDERMAL+NEVUS
7 BLASCHKITIS 18 89% 1% 8 Search BLASCHKITIS Search BLASCHKITIS
8 SCHIMMELPENNING FEUERSTEIN MIMS SYNDROME 18 89% 1% 8 Search SCHIMMELPENNING+FEUERSTEIN+MIMS+SYNDROME Search SCHIMMELPENNING+FEUERSTEIN+MIMS+SYNDROME
9 INFLAMMATORY LINEAR VERRUCOUS EPIDERMAL NEVUS 14 100% 1% 7 Search INFLAMMATORY+LINEAR+VERRUCOUS+EPIDERMAL+NEVUS Search INFLAMMATORY+LINEAR+VERRUCOUS+EPIDERMAL+NEVUS
10 DELLEMAN SYNDROME 12 86% 1% 6 Search DELLEMAN+SYNDROME Search DELLEMAN+SYNDROME

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 JADASSOHN 63 63% 7% 63
2 FOCAL DERMAL MALFORMATIONS 24 82% 2% 14
3 SEBACEUS 21 61% 3% 23
4 OCULOCEREBROCUTANEOUS SYNDROME 19 76% 1% 13
5 ORBITAL CYST 17 68% 2% 15
6 ENCEPHALOCRANIOCUTANEOUS LIPOMATOSIS 17 47% 3% 27
7 RARE NEUROCUTANEOUS SYNDROME 17 100% 1% 8
8 SEBACEOUS SYNDROME 17 75% 1% 12
9 EPIDERMAL NEVUS 16 38% 4% 34
10 ILVEN 15 62% 2% 16

Journals

Reviews



Title Publ. year Cit. Active
references
% act. ref.
to same field
Encephalocraniocutaneous lipomatosis 2009 21 49 90%
Nevus Sebaceous Revisited 2012 15 58 86%
Mosaic RASopathies 2013 11 60 45%
Naevus sebaceus: a mosaic RASopathy 2014 2 23 70%
Familial Disseminated Comedones without Dyskeratosis: Report of an Affected Family and Review of the Literature 2014 2 13 69%
Clinical manifestation and neurosurgical intervention of encephalocraniocutaneous lipomatosis-a case report and review of the literature 2014 1 12 92%
Progressive Growth in Epibulbar Complex Choristomas: Report of 2 Cases and Review of Literature 2011 3 7 86%
Management of Nevus Sebaceous and the Risk of Basal Cell Carcinoma: An 18-Year Review 2009 10 14 64%
Encephalocraniocutaneous lipomatosis: a case with unilateral odontom as and review of the literature 2003 12 22 100%
Facial Blaschkitis: Case and Review 2011 1 8 100%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 GRP CARCINOGENESIS EPITELIAL 4 67% 0.5% 4
2 MALATTIE CUTANEE EREDITARIE 2 50% 0.3% 3
3 GRP CITOGENET MOL 1 50% 0.2% 2
4 IMAGIOL NEURORADIOL 1 100% 0.2% 2
5 PROGRAMA GENET CANC HUMANO 1 33% 0.2% 2
6 ABT PLAST ASTHET WIEDERHERSTELLUNG IRURG 1 50% 0.1% 1
7 ALEMAN HOSP 1 50% 0.1% 1
8 CHILDRENS CRANO IAL 1 50% 0.1% 1
9 CUTANEOUS AGING DERMATOL 1 50% 0.1% 1
10 KIEROWN KATEDRY KLIN PROF DR HAB N MED WOJCIECH 1 50% 0.1% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000160401 BASALOID FOLLICULAR HAMARTOMA//MILIA EN PLAQUE//INFUNDIBULOCYSTIC BASAL CELL CARCINOMA
2 0.0000146579 INCONTINENTIA PIGMENTI//HYPOMELANOSIS OF ITO//BLOCH SULZBERGER SYNDROME
3 0.0000140271 PROTEUS SYNDROME//MACRODACTYLY//MACRODYSTROPHIA LIPOMATOSA
4 0.0000139158 NEUROCUTANEOUS MELANOSIS//NEUROCUTANEOUS MELANOCYTOSIS//TWIN SPOTTING
5 0.0000133786 VERRUCIFORM XANTHOMA//EPIDERMOLYTIC ACANTHOMA//EPIDERMOLYTIC
6 0.0000121488 TRICHOBLASTOMA//FOLLICULOSEBACEOUS CYSTIC HAMARTOMA//PROLIFERATING TRICHILEMMAL CYST
7 0.0000119589 DACRYOCYSTORHINOGRAPHY//ORBITAL FAT PROLAPSE//LIMBAL DERMOID
8 0.0000106280 HAIR FOLLICLE NEVUS//ACCESSORY AURICLE//POLYOTIA
9 0.0000105393 POROKERATOSIS//CORNOID LAMELLA//DISSEMINATED SUPERFICIAL ACTINIC POROKERATOSIS
10 0.0000103565 LICHEN PLANUS PIGMENTOSUS//IDIOPATHIC ERUPTIVE MACULAR PIGMENTATION//ASHY DERMATOSIS