Class information for:
Level 1: PRIMARY CILIARY DYSKINESIA//KARTAGENERS SYNDROME//CILIARY DYSKINESIA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
10718 1040 30.1 63%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
365 3       MICROTUBULES//MITOSIS//KINETOCHORE 34118
1653 2             PRIMARY CILIARY DYSKINESIA//KARTAGENERS SYNDROME//DYNEIN 6886
10718 1                   PRIMARY CILIARY DYSKINESIA//KARTAGENERS SYNDROME//CILIARY DYSKINESIA 1040

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PRIMARY CILIARY DYSKINESIA authKW 4103573 18% 73% 191
2 KARTAGENERS SYNDROME authKW 2450201 11% 74% 113
3 CILIARY DYSKINESIA authKW 479527 2% 78% 21
4 IMMOTILE CILIA SYNDROME authKW 417015 2% 57% 25
5 CILIARY ULTRASTRUCTURE authKW 412864 1% 94% 15
6 CILIARY MOTILITY DISORDERS authKW 319685 1% 78% 14
7 DANISH PCD address 234875 1% 100% 8
8 SITUS INVERSUS authKW 193918 4% 15% 44
9 RESPIRATORY CILIA authKW 182926 1% 69% 9
10 NASAL NITRIC OXIDE authKW 168207 2% 30% 19

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Respiratory System 13616 30% 0% 311
2 Otorhinolaryngology 2749 11% 0% 116
3 Pediatrics 1549 14% 0% 146
4 Pathology 729 8% 0% 84
5 Genetics & Heredity 512 10% 0% 109
6 Critical Care Medicine 480 5% 0% 47
7 Microscopy 468 2% 0% 25
8 Andrology 321 1% 0% 12
9 Medicine, General & Internal 203 8% 0% 84
10 Anatomy & Morphology 187 2% 0% 21

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PRIMARY CILIARY DYSKINESIA 319685 1% 78% 14
2 DANISH PCD 234875 1% 100% 8
3 REFERENCE MALAD P RA 132108 1% 50% 9
4 PEDIAT PULM SERV 97851 1% 33% 10
5 SERV WOMEN CHILDREN 88078 0% 100% 3
6 UNITE MIXTE RECH S933 88078 0% 100% 3
7 UMR S933 65382 1% 32% 7
8 DANISH PCD PEDIAT PULM SERV 58719 0% 100% 2
9 DISCIPLINE ADULT MED 58719 0% 100% 2
10 KLIN POLIKLIN KINDER JUGENDMED ALLGEMEINE PAE 58719 0% 100% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 EUROPEAN JOURNAL OF RESPIRATORY DISEASES 49443 5% 3% 49
2 PERSPECTIVES IN PEDIATRIC PATHOLOGY 9783 0% 17% 2
3 PAEDIATRIC RESPIRATORY REVIEWS 7130 1% 2% 12
4 ULTRASTRUCTURAL PATHOLOGY 4769 2% 1% 18
5 EUROPEAN RESPIRATORY JOURNAL 4390 4% 0% 37
6 PEDIATRIC PULMONOLOGY 4186 3% 1% 26
7 THORAX 2764 3% 0% 26
8 JOURNAL OF SUBMICROSCOPIC CYTOLOGY AND PATHOLOGY 2449 1% 1% 11
9 AMERICAN JOURNAL OF HUMAN GENETICS 2069 2% 0% 24
10 RHINOLOGY 1403 1% 1% 7

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 PRIMARY CILIARY DYSKINESIA 4103573 18% 73% 191 Search PRIMARY+CILIARY+DYSKINESIA Search PRIMARY+CILIARY+DYSKINESIA
2 KARTAGENERS SYNDROME 2450201 11% 74% 113 Search KARTAGENERS+SYNDROME Search KARTAGENERS+SYNDROME
3 CILIARY DYSKINESIA 479527 2% 78% 21 Search CILIARY+DYSKINESIA Search CILIARY+DYSKINESIA
4 IMMOTILE CILIA SYNDROME 417015 2% 57% 25 Search IMMOTILE+CILIA+SYNDROME Search IMMOTILE+CILIA+SYNDROME
5 CILIARY ULTRASTRUCTURE 412864 1% 94% 15 Search CILIARY+ULTRASTRUCTURE Search CILIARY+ULTRASTRUCTURE
6 CILIARY MOTILITY DISORDERS 319685 1% 78% 14 Search CILIARY+MOTILITY+DISORDERS Search CILIARY+MOTILITY+DISORDERS
7 SITUS INVERSUS 193918 4% 15% 44 Search SITUS+INVERSUS Search SITUS+INVERSUS
8 RESPIRATORY CILIA 182926 1% 69% 9 Search RESPIRATORY+CILIA Search RESPIRATORY+CILIA
9 NASAL NITRIC OXIDE 168207 2% 30% 19 Search NASAL+NITRIC+OXIDE Search NASAL+NITRIC+OXIDE
10 CILIA 167720 8% 7% 84 Search CILIA Search CILIA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 LUCAS, JS , PAFF', T , GOGGIN, P , HAARMAN, E , (2016) DIAGNOSTIC METHODS IN PRIMARY CILIARY DYSKINESIA.PAEDIATRIC RESPIRATORY REVIEWS. VOL. 18. ISSUE . P. 8 -17 79 92% 3
2 OLIVIER, KN , MILLA, C , DANIEL, SJ , KIMPLE, AJ , MANION, M , KNOWLES, MR , LEIGH, MW , SHAPIRO, AJ , ZARIWALA, MA , FERKOL, T , ET AL (2016) DIAGNOSIS, MONITORING, AND TREATMENT OF PRIMARY CILIARY DYSKINESIA: PCD FOUNDATION CONSENSUS RECOMMENDATIONS BASED ON STATE OF THE ART REVIEW.PEDIATRIC PULMONOLOGY. VOL. 51. ISSUE 2. P. 115 -132 87 69% 5
3 BOON, M , JORISSEN, M , PROESMANS, M , DE BOECK, K , (2013) PRIMARY CILIARY DYSKINESIA, AN ORPHAN DISEASE.EUROPEAN JOURNAL OF PEDIATRICS. VOL. 172. ISSUE 2. P. 151-162 81 80% 31
4 KNOWLES, MR , DANIELS, LA , DAVIS, SD , ZARIWALA, MA , LEIGH, MW , (2013) PRIMARY CILIARY DYSKINESIA RECENT ADVANCES IN DIAGNOSTICS, GENETICS, AND CHARACTERIZATION OF CLINICAL DISEASE.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 188. ISSUE 8. P. 913-922 64 77% 82
5 DEHLINK, E , HOGG, C , CARR, SB , BUSH, A , (2016) CLINICAL PHENOTYPE AND CURRENT DIAGNOSTIC CRITERIA FOR PRIMARY CILIARY DYSKINESIA.EXPERT REVIEW OF RESPIRATORY MEDICINE. VOL. 10. ISSUE 11. P. 1163 -1175 75 79% 0
6 KURKOWIAK, M , ZIETKIEWICZ, E , WITT, M , (2015) RECENT ADVANCES IN PRIMARY CILIARY DYSKINESIA GENETICS.JOURNAL OF MEDICAL GENETICS. VOL. 52. ISSUE 1. P. 1 -9 62 71% 20
7 HONORE, I , BURGEL, PR , (2016) PRIMARY CILIARY DYSKINESIA IN ADULTS.REVUE DES MALADIES RESPIRATOIRES. VOL. 33. ISSUE 2. P. 165 -189 86 66% 0
8 GOUTAKI, M , MEIER, AB , HALBEISEN, FS , LUCAS, JS , DELL, SD , MAURER, E , CASAULTA, C , JURCA, M , SPYCHER, BD , KUEHNI, CE , (2016) CLINICAL MANIFESTATIONS IN PRIMARY CILIARY DYSKINESIA: SYSTEMATIC REVIEW AND META-ANALYSIS.EUROPEAN RESPIRATORY JOURNAL. VOL. 48. ISSUE 4. P. 1081 -1095 63 86% 0
9 SHA, YW , DING, L , LI, P , (2014) MANAGEMENT OF PRIMARY CILIARY DYSKINESIA/KARTAGENERS SYNDROME IN INFERTILE MALE PATIENTS AND CURRENT PROGRESS IN DEFINING THE UNDERLYING GENETIC MECHANISM.ASIAN JOURNAL OF ANDROLOGY. VOL. 16. ISSUE 1. P. 101-106 61 73% 7
10 BARBATO, A , FRISCHER, T , KUEHNI, CE , SNIJDERS, D , AZEVEDO, I , BAKTAI, G , BARTOLONI, L , EBER, E , ESCRIBANO, A , HAARMAN, E , ET AL (2009) PRIMARY CILIARY DYSKINESIA: A CONSENSUS STATEMENT ON DIAGNOSTIC AND TREATMENT APPROACHES IN CHILDREN.EUROPEAN RESPIRATORY JOURNAL. VOL. 34. ISSUE 6. P. 1264-1276 61 62% 173

Classes with closest relation at Level 1



Rank Class id link
1 7235 CILIARY BEAT FREQUENCY//MUCOCILIARY CLEARANCE//MUCOCILIARY TRANSPORT
2 11071 LEFT RIGHT ASYMMETRY//LEFT RIGHT PATTERNING//NODAL
3 14406 BRONCHIECTASIS//MIDDLE LOBE SYNDROME//ADULT BRONCHIECTASIS SERV
4 4221 DYNEIN//AXONEME//FLAGELLA
5 13335 GLOBOZOOSPERMIA//MANCHETTE//OUTER DENSE FIBERS
6 1635 JOUBERT SYNDROME//CILIOPATHY//BARDET BIEDL SYNDROME
7 37315 BRONCHOLITHIASIS//LITHOPTYSIS//BRONCHOLITH
8 34764 DEXTROCARDIA//SITUS INVERSUS//SITUS SOLITUS
9 3589 EXHALED NITRIC OXIDE//FRACTIONAL EXHALED NITRIC OXIDE//EXHALED NO
10 33114 TEKTIN//DEV ANAT//CHONGQING PIG IND SCI

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