Class information for:
Level 1: MYOCLONUS//UNVERRICHT LUNDBORG DISEASE//PROGRESSIVE MYOCLONUS EPILEPSY

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
11956 942 29.2 64%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
11 4 NEUROSCIENCES//CLINICAL NEUROLOGY//NEUROL 1112395
124 3       PARKINSONS DISEASE//MOVEMENT DISORDERS//DEEP BRAIN STIMULATION 67777
2520 2             ESSENTIAL TREMOR//TREMOR//ORTHOSTATIC TREMOR 3825
11956 1                   MYOCLONUS//UNVERRICHT LUNDBORG DISEASE//PROGRESSIVE MYOCLONUS EPILEPSY 942

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MYOCLONUS authKW 1160603 17% 22% 164
2 UNVERRICHT LUNDBORG DISEASE authKW 964653 4% 80% 37
3 PROGRESSIVE MYOCLONUS EPILEPSY authKW 721254 5% 49% 45
4 EPM1 authKW 675282 3% 83% 25
5 PROPRIOSPINAL MYOCLONUS authKW 635067 2% 85% 23
6 SPINAL MYOCLONUS authKW 617407 2% 95% 20
7 CORTICAL TREMOR authKW 563716 2% 87% 20
8 CYSTATIN B authKW 502385 3% 50% 31
9 ASTERIXIS authKW 448222 2% 63% 22
10 NEGATIVE MYOCLONUS authKW 447077 2% 69% 20

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 25356 70% 0% 663
2 Neurosciences 1849 27% 0% 256
3 Psychiatry 164 6% 0% 55
4 Genetics & Heredity 68 5% 0% 47
5 Pharmacology & Pharmacy 31 6% 0% 58
6 Engineering, Biomedical 31 2% 0% 19
7 Neuroimaging 30 1% 0% 8
8 Medicine, General & Internal 19 4% 0% 37
9 Anesthesiology 13 1% 0% 10
10 Biophysics 13 3% 0% 24

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 DIAG CARE EPILEPSY 162070 1% 100% 5
2 BIOCHEM MOL STRUCT BIOL 106842 3% 13% 26
3 IPS GRP 97242 0% 100% 3
4 PARKINSONS DIS OTHER MOVEMENT DISORDER 64828 0% 100% 2
5 AZIENDA OSPEDAL UNIV CONSORZIALE 32414 0% 100% 1
6 BELLARIS HOSP NEUROL 32414 0% 100% 1
7 C BESTA FDN NEUROL 32414 0% 100% 1
8 CDC POLICLIN ITALIA 32414 0% 100% 1
9 CENIC 32414 0% 100% 1
10 CERVEAU MOELLE EPINIERE CRICMCNRS 32414 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MOVEMENT DISORDERS 52792 11% 2% 103
2 ADVANCES IN NEUROLOGY 42915 3% 5% 26
3 EPILEPSIA 9789 6% 1% 52
4 CLINICAL NEUROSCIENCE 9115 1% 4% 7
5 NEUROPHYSIOLOGIE CLINIQUE-CLINICAL NEUROPHYSIOLOGY 5912 1% 2% 11
6 NEUROLOGY 4571 6% 0% 55
7 CLINICAL NEUROPHARMACOLOGY 3442 2% 1% 16
8 REVUE NEUROLOGIQUE 3273 2% 0% 22
9 ACTA NEUROLOGICA SCANDINAVICA 3047 3% 0% 24
10 ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY 2676 2% 0% 17

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 MYOCLONUS 1160603 17% 22% 164 Search MYOCLONUS Search MYOCLONUS
2 UNVERRICHT LUNDBORG DISEASE 964653 4% 80% 37 Search UNVERRICHT+LUNDBORG+DISEASE Search UNVERRICHT+LUNDBORG+DISEASE
3 PROGRESSIVE MYOCLONUS EPILEPSY 721254 5% 49% 45 Search PROGRESSIVE+MYOCLONUS+EPILEPSY Search PROGRESSIVE+MYOCLONUS+EPILEPSY
4 EPM1 675282 3% 83% 25 Search EPM1 Search EPM1
5 PROPRIOSPINAL MYOCLONUS 635067 2% 85% 23 Search PROPRIOSPINAL+MYOCLONUS Search PROPRIOSPINAL+MYOCLONUS
6 SPINAL MYOCLONUS 617407 2% 95% 20 Search SPINAL+MYOCLONUS Search SPINAL+MYOCLONUS
7 CORTICAL TREMOR 563716 2% 87% 20 Search CORTICAL+TREMOR Search CORTICAL+TREMOR
8 CYSTATIN B 502385 3% 50% 31 Search CYSTATIN+B Search CYSTATIN+B
9 ASTERIXIS 448222 2% 63% 22 Search ASTERIXIS Search ASTERIXIS
10 NEGATIVE MYOCLONUS 447077 2% 69% 20 Search NEGATIVE+MYOCLONUS Search NEGATIVE+MYOCLONUS

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 ANTELMI, E , PROVINI, F , (2015) PROPRIOSPINAL MYOCLONUS: THE SPECTRUM OF CLINICAL AND NEUROPHYSIOLOGICAL PHENOTYPES.SLEEP MEDICINE REVIEWS. VOL. 22. ISSUE . P. 54 -63 42 78% 3
2 VAN DER SALM, SMA , ERRO, R , CORDIVARI, C , EDWARDS, MJ , KOELMAN, JHTM , VAN DEN ENDE, T , BHATIA, KP , VAN ROOTSELAAR, AF , BROWN, P , TIJSSEN, MAJ , (2014) PROPRIOSPINAL MYOCLONUS CLINICAL REAPPRAISAL AND REVIEW OF LITERATURE.NEUROLOGY. VOL. 83. ISSUE 20. P. 1862 -1870 36 82% 9
3 SHIBASAKI, H , HALLETT, M , (2005) ELECTROPHYSIOLOGICAL STUDIES OF MYOCLONUS.MUSCLE & NERVE. VOL. 31. ISSUE 2. P. 157-174 51 70% 68
4 KALVIAINEN, R , KHYUPPENEN, J , KOSKENKORVA, P , ERIKSSON, K , VANNINEN, R , MERVAALA, E , (2008) CLINICAL PICTURE OF EPM1-UNVERRICHT-LUNDBORG DISEASE.EPILEPSIA. VOL. 49. ISSUE 4. P. 549 -556 36 84% 56
5 HYPPONEN, J , AIKIA, M , JOENSUU, T , JULKUNEN, P , DANNER, N , KOSKENKORVA, P , VANNINEN, R , LEHESJOKI, AE , MERVAALA, E , KALVIAINEN, R , (2015) REFINING THE PHENOTYPE OF UNVERRICHT-LUNDBORG DISEASE (EPM1) A POPULATION-WIDE FINNISH STUDY.NEUROLOGY. VOL. 84. ISSUE 15. P. 1529 -1536 32 86% 2
6 POLAJNAR, M , ZAVASNIK-BERGANT, T , KOPITAR-JERALA, N , TUSEK-ZNIDARIC, M , ZEROVNIK, E , (2014) GAIN IN TOXIC FUNCTION OF STEFIN B EPM1 MUTANTS AGGREGATES: CORRELATION BETWEEN CELL DEATH, AGGREGATE NUMBER/SIZE AND OXIDATIVE STRESS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1843. ISSUE 9. P. 2089 -2099 39 68% 2
7 SHIBASAKI, H , (2000) ELECTROPHYSIOLOGICAL STUDIES OF MYOCLONUS.MUSCLE & NERVE. VOL. 23. ISSUE 3. P. 321-335 46 79% 45
8 SHIBASAKI, H , THOMPSON, PD , (2011) MILESTONES IN MYOCLONUS.MOVEMENT DISORDERS. VOL. 26. ISSUE 6. P. 1142-1148 45 56% 12
9 ZEROVNIK, E , (2017) PUTATIVE ALTERNATIVE FUNCTIONS OF HUMAN STEFIN B (CYSTATIN B): BINDING TO AMYLOID-BETA, MEMBRANES, AND COPPER.JOURNAL OF MOLECULAR RECOGNITION. VOL. 30. ISSUE 1. P. - 43 54% 0
10 CEN, ZD , HUANG, CP , YIN, HM , DING, XP , XIE, F , LU, XJ , OUYANG, ZY , LOU, YT , QIU, X , WANG, ZJ , ET AL (2016) CLINICAL AND NEUROPHYSIOLOGICAL FEATURES OF FAMILIAL CORTICAL MYOCLONIC TREMOR WITH EPILEPSY.MOVEMENT DISORDERS. VOL. 31. ISSUE 11. P. 1704 -1710 22 96% 0

Classes with closest relation at Level 1



Rank Class id link
1 23802 PALATAL MYOCLONUS//PALATAL TREMOR//HYPERTROPHIC OLIVARY DEGENERATION
2 16803 LAFORA DISEASE//POLYGLUCOSAN BODIES//LAFORIN
3 31102 HEPP//BRAIN CHIMERA//GABA WITHDRAWAL
4 5865 JUVENILE MYOCLONIC EPILEPSY//IDIOPATHIC GENERALIZED EPILEPSY//REFLEX EPILEPSY
5 36440 PAINFUL LEGS//MOVING TOES//PAINFUL LEGS AND MOVING TOES
6 16357 HEMICHOREA//HEMIBALLISM//HOLMES TREMOR
7 7012 SOMATOSENSORY EVOKED POTENTIALS//ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY//FAR FIELD POTENTIALS
8 12755 LEVETIRACETAM//SV2A//BRIVARACETAM
9 18445 SEROTONIN SYNDROME//SEROTONIN TOXICITY//5 HT ENHANCING DRUG
10 34759 NONKETOTIC HYPERGLYCEMIA//MOVEMENT INDUCED SEIZURES//NON KETOTIC HYPERGLYCAEMIA

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