Class information for:
Level 1: FRONTONASAL DYSPLASIA//MACROSTOMIA//PROBOSCIS LATERALIS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
15793 691 18.6 48%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
14 4 ORTHOPEDICS//DENTISTRY, ORAL SURGERY & MEDICINE//SPORT SCIENCES 808941
474 3       CLEFT PALATE-CRANIOFACIAL JOURNAL//CLEFT PALATE//CRANIOSYNOSTOSIS 23888
1564 2             DISTRACTION OSTEOGENESIS//HEMIFACIAL MICROSOMIA//PIERRE ROBIN SEQUENCE 7357
15793 1                   FRONTONASAL DYSPLASIA//MACROSTOMIA//PROBOSCIS LATERALIS 691

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FRONTONASAL DYSPLASIA authKW 1566297 7% 74% 48
2 MACROSTOMIA authKW 795386 3% 75% 24
3 PROBOSCIS LATERALIS authKW 707020 2% 100% 16
4 TESSIER CLEFT authKW 638523 2% 85% 17
5 CRANIOFACIAL CLEFT authKW 590809 3% 70% 19
6 SUPERNUMERARY NOSTRIL authKW 530265 2% 100% 12
7 FACIAL CLEFT authKW 474541 4% 38% 28
8 ARHINIA authKW 454510 2% 86% 12
9 PAI SYNDROME authKW 445568 2% 92% 11
10 CRANIOFRONTONASAL DYSPLASIA authKW 424207 2% 80% 12

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Surgery 6661 52% 0% 361
2 Dentistry, Oral Surgery & Medicine 4425 20% 0% 140
3 Genetics & Heredity 1846 22% 0% 154
4 Otorhinolaryngology 674 7% 0% 48
5 Pediatrics 339 9% 0% 59
6 Medical Ethics 87 1% 0% 5
7 Anatomy & Morphology 59 1% 0% 10
8 Developmental Biology 55 2% 0% 15
9 Neuroimaging 23 1% 0% 6
10 Radiology, Nuclear Medicine & Medical Imaging 21 3% 0% 24

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 10TH FLOOR 44189 0% 100% 1
2 ABT PADIATRI NEUROCHIRURG 44189 0% 100% 1
3 AZIENDA OSPED NAZL SS ANTONIO BIAGIO CESAR AR 44189 0% 100% 1
4 CLEFT LIP PALATEPEOPLES HOSP 9 44189 0% 100% 1
5 CLIN GENET PEDIAT UNIT 44189 0% 100% 1
6 CRANIOMAXILLO IAL SURG IAL PLAST RE 44189 0% 100% 1
7 DAVID GEFFEN MEDSTEVEN SPIELBERG PEDIAT 44189 0% 100% 1
8 GENET PATHOPHYSIOL NEURODEV EPILEPTOGEN DIS 44189 0% 100% 1
9 GLOBAL SMILE FDN 44189 0% 100% 1
10 HELLEN CRANIO IAL 44189 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF CRANIOFACIAL SURGERY 36583 11% 1% 78
2 CLEFT PALATE-CRANIOFACIAL JOURNAL 35649 6% 2% 44
3 CLINICAL DYSMORPHOLOGY 31044 4% 3% 28
4 JOURNAL OF CRANIO-MAXILLOFACIAL SURGERY 13807 4% 1% 31
5 PLASTIC AND RECONSTRUCTIVE SURGERY 13159 9% 0% 64
6 AMERICAN JOURNAL OF MEDICAL GENETICS PART A 6411 4% 1% 29
7 BRITISH JOURNAL OF PLASTIC SURGERY 5908 3% 1% 20
8 AMERICAN JOURNAL OF MEDICAL GENETICS 5462 5% 0% 33
9 ANNALS OF PLASTIC SURGERY 4379 4% 0% 28
10 INTERNATIONAL JOURNAL OF PEDIATRIC OTORHINOLARYNGOLOGY 2878 3% 0% 21

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 FRONTONASAL DYSPLASIA 1566297 7% 74% 48 Search FRONTONASAL+DYSPLASIA Search FRONTONASAL+DYSPLASIA
2 MACROSTOMIA 795386 3% 75% 24 Search MACROSTOMIA Search MACROSTOMIA
3 PROBOSCIS LATERALIS 707020 2% 100% 16 Search PROBOSCIS+LATERALIS Search PROBOSCIS+LATERALIS
4 TESSIER CLEFT 638523 2% 85% 17 Search TESSIER+CLEFT Search TESSIER+CLEFT
5 CRANIOFACIAL CLEFT 590809 3% 70% 19 Search CRANIOFACIAL+CLEFT Search CRANIOFACIAL+CLEFT
6 SUPERNUMERARY NOSTRIL 530265 2% 100% 12 Search SUPERNUMERARY+NOSTRIL Search SUPERNUMERARY+NOSTRIL
7 FACIAL CLEFT 474541 4% 38% 28 Search FACIAL+CLEFT Search FACIAL+CLEFT
8 ARHINIA 454510 2% 86% 12 Search ARHINIA Search ARHINIA
9 PAI SYNDROME 445568 2% 92% 11 Search PAI+SYNDROME Search PAI+SYNDROME
10 CRANIOFRONTONASAL DYSPLASIA 424207 2% 80% 12 Search CRANIOFRONTONASAL+DYSPLASIA Search CRANIOFRONTONASAL+DYSPLASIA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 VARGEVIK, K , SLAVOTINEK, AM , WIN, E , (2007) SUBTYPES OF FRONTONASAL DYSPLASIA ARE USEFUL IN DETERMINING CLINICAL PROGNOSIS.AMERICAN JOURNAL OF MEDICAL GENETICS PART A. VOL. 143A. ISSUE 24. P. 3069 -3078 45 83% 0
2 WINTERS, R , (2016) TESSIER CLEFTS AND HYPERTELORISM.FACIAL PLASTIC SURGERY CLINICS OF NORTH AMERICA. VOL. 24. ISSUE 4. P. 545 -+ 25 83% 0
3 VAN DEN ELZEN, MEP , TWIGG, SRF , GOOS, JAC , HOOGEBOOM, AJM , VAN DEN OUWELAND, AMW , WILKIE, AOM , MATHIJSSEN, IMJ , (2014) PHENOTYPES OF CRANIOFRONTONASAL SYNDROME IN PATIENTS WITH A PATHOGENIC MUTATION IN EFNB1.EUROPEAN JOURNAL OF HUMAN GENETICS. VOL. 22. ISSUE 8. P. - 24 86% 5
4 KOBRAEI, EM , LENTZ, AK , EBERLIN, KR , HACHACH-HARAM, N , HAMDAN, US , (2016) MACROSTOMIA: A PRACTICAL GUIDE FOR PLASTIC AND RECONSTRUCTIVE SURGEONS.JOURNAL OF CRANIOFACIAL SURGERY. VOL. 27. ISSUE 1. P. 118 -123 20 91% 0
5 GUION-ALMEIDA, ML , RICHIERI-COSTA, A , (2009) FRONTONASAL DYSPLASIA, SEVERE NEUROPSYCHOLOGICAL DELAY, AND MIDLINE CENTRAL NERVOUS SYSTEM ANOMALIES: REPORT OF 10 BRAZILIAN MALE PATIENTS.AMERICAN JOURNAL OF MEDICAL GENETICS PART A. VOL. 149A. ISSUE 5. P. 1006-1011 20 100% 6
6 WOOD, BC , YI, S , OH, AK , ROGERS, GF , MAGGE, SN , (2015) FRONTAL ENCEPHALOCELE ASSOCIATED WITH A BILATERAL TESSIER NUMBER THREE CLEFT AND FRASER SYNDROME.JOURNAL OF CRANIOFACIAL SURGERY. VOL. 26. ISSUE 6. P. 1947 -1950 20 83% 0
7 BORZABADI-FARAHANI, A , YEN, SLK , FRANCIS, C , LARA-SANCHEZ, PA , HAMMOUDEH, J , (2013) A RARE CASE OF ACCESSORY MAXILLA AND BILATERAL TESSIER NO. 7 CLEFTS, A 10-YEAR FOLLOW-UP.JOURNAL OF CRANIO-MAXILLOFACIAL SURGERY. VOL. 41. ISSUE 6. P. 527-531 21 75% 4
8 VERSNEL, SL , VAN DEN ELZEN, MEP , WOLVIUS, EB , BIESMEIJER, CS , VAANDRAGER, JM , VAN DER MEULEN, JC , MATHIJSSEN, IMJ , (2011) LONG-TERM RESULTS AFTER 40 YEARS EXPERIENCE WITH TREATMENT OF RARE FACIAL CLEFTS: PART 1-OBLIQUE AND PARAMEDIAN CLEFTS.JOURNAL OF PLASTIC RECONSTRUCTIVE AND AESTHETIC SURGERY. VOL. 64. ISSUE 10. P. 1334 -1343 20 77% 7
9 FREITAS, RD , ALONSO, N , AZZOLINI, TD , BUSATO, L , TOLAZZI, ARD , CRUZ, GADE , GOLDENBERG, D , (2010) THE SURGICAL REPAIR OF HALF-NOSE.JOURNAL OF PLASTIC RECONSTRUCTIVE AND AESTHETIC SURGERY. VOL. 63. ISSUE 1. P. 15 -21 19 83% 0
10 ANTONELI, MZ , GIACHETI, CM , GENARO, KF , ZORZETTO, NL , RICHIERI-COSTA, A , (2011) FRONTONASAL DYSPLASIA: CLINICAL EVALUATION ON AUDIOLOGICAL AND BRAINSTEM ELECTROPHYSIOLOGICAL PROFILES.BRAZILIAN JOURNAL OF OTORHINOLARYNGOLOGY. VOL. 77. ISSUE 5. P. 611-615 16 94% 0

Classes with closest relation at Level 1



Rank Class id link
1 32361 PARIETAL FORAMINA//FORAMINA PARIETALIA PERMAGNA//POTOCKI SHAFFER SYNDROME
2 26136 INTRACRANIAL LIPOMA//LIPOMA//INTERHEMISPHERIC LIPOMA
3 27158 ACROCALLOSAL SYNDROME//VICI SYNDROME//GREIG CEPHALOPOLYSYNDACTYLY SYNDROME
4 24795 FRASER SYNDROME//CRYPTOPHTHALMOS//FRAS1
5 17315 AMNIOTIC BAND SYNDROME//LIMB BODY WALL COMPLEX//AMNIOTIC BANDS
6 16610 GOLDENHAR SYNDROME//HEMIFACIAL MICROSOMIA//OCULOAURICULOVERTEBRAL SPECTRUM
7 12166 HOLOPROSENCEPHALY//TGIF//CYCLOPIA
8 30049 INTERPUPILLARY DISTANCE//EXOPHTHALMOMETRY//HERTEL EXOPHTHALMOMETER
9 21083 TREACHER COLLINS SYNDROME//MANDIBULOFACIAL DYSOSTOSIS//ACROFACIAL DYSOSTOSIS
10 20350 NASAL GLIOMA//NASAL DERMOID//GLIAL HETEROTOPIA

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