Class information for:
Level 1: FAHRS DISEASE//FAHRS SYNDROME//SLC20A2

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
17964 573 25.0 57%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
196 3       GENETICS & HEREDITY//FRAGILE X SYNDROME//AMERICAN JOURNAL OF MEDICAL GENETICS 53756
3243 2             PSEUDOHYPOPARATHYROIDISM//FAHRS DISEASE//MENINGIOANGIOMATOSIS 1993
17964 1                   FAHRS DISEASE//FAHRS SYNDROME//SLC20A2 573

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 FAHRS DISEASE authKW 3488698 12% 92% 71
2 FAHRS SYNDROME authKW 1142571 5% 79% 27
3 SLC20A2 authKW 863281 3% 90% 18
4 BASAL GANGLIA CALCIFICATION authKW 818694 5% 59% 26
5 IDIOPATHIC BASAL GANGLIA CALCIFICATION authKW 705294 3% 88% 15
6 PRIMARY FAMILIAL BRAIN CALCIFICATION authKW 431640 2% 90% 9
7 BRAIN CALCIFICATION authKW 427256 4% 38% 21
8 KEIZO ASAMI address 426305 2% 67% 12
9 DIFFUSE NEUROFIBRILLARY TANGLES WITH CALCIFICATION authKW 392399 2% 82% 9
10 IBGC authKW 274057 1% 86% 6

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 5366 42% 0% 242
2 Neuroimaging 1112 6% 0% 32
3 Neurosciences 973 25% 0% 146
4 Psychiatry 959 16% 0% 89
5 Radiology, Nuclear Medicine & Medical Imaging 737 15% 0% 85
6 Medicine, General & Internal 335 13% 0% 72
7 Pathology 162 5% 0% 31
8 Pediatrics 54 4% 0% 25
9 Emergency Medicine 35 1% 0% 7
10 Genetics & Heredity 35 5% 0% 27

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 KEIZO ASAMI 426305 2% 67% 12
2 MED THER EUT MOL THER EUT 87028 1% 23% 7
3 CNR MAJ 72521 1% 19% 7
4 UNIT BIOQUIM 71047 1% 33% 4
5 KEIZO ASAMI LIKA 56836 1% 27% 4
6 ARBEITSBEREICH MRT 53289 0% 100% 1
7 BETH ISRAEL DEACONESS MED DEP NEUROL 53289 0% 100% 1
8 CIENCIAS NEUROL MEDSERV NEUROL 53289 0% 100% 1
9 CONDENSED MATTER PHYS CRYSTALLO MINEROL 53289 0% 100% 1
10 CURSO POS NEUROL 53289 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ACTA NEUROPATHOLOGICA 2038 3% 0% 15
2 JOURNAL OF MOLECULAR NEUROSCIENCE 1947 2% 0% 10
3 NEURORADIOLOGY 1815 2% 0% 13
4 ACTA PAEDIATRICA BELGICA 1330 0% 3% 1
5 JOURNAL OF NEUROLOGY 1246 2% 0% 12
6 FEUILLETS DE RADIOLOGIE 1174 0% 1% 2
7 ITALIAN JOURNAL OF NEUROLOGICAL SCIENCES 1150 1% 0% 5
8 PEDIATRIC NEUROSCIENCE 1124 0% 1% 2
9 ANALES ESPANOLES DE PEDIATRIA 1043 0% 2% 1
10 COMPUTERTOMOGRAPHIE SONOGRAPHIE UND ANDERE NEUE BILDDIAGNOSTISCHE METHODEN 1023 0% 2% 1

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 FAHRS DISEASE 3488698 12% 92% 71 Search FAHRS+DISEASE Search FAHRS+DISEASE
2 FAHRS SYNDROME 1142571 5% 79% 27 Search FAHRS+SYNDROME Search FAHRS+SYNDROME
3 SLC20A2 863281 3% 90% 18 Search SLC20A2 Search SLC20A2
4 BASAL GANGLIA CALCIFICATION 818694 5% 59% 26 Search BASAL+GANGLIA+CALCIFICATION Search BASAL+GANGLIA+CALCIFICATION
5 IDIOPATHIC BASAL GANGLIA CALCIFICATION 705294 3% 88% 15 Search IDIOPATHIC+BASAL+GANGLIA+CALCIFICATION Search IDIOPATHIC+BASAL+GANGLIA+CALCIFICATION
6 PRIMARY FAMILIAL BRAIN CALCIFICATION 431640 2% 90% 9 Search PRIMARY+FAMILIAL+BRAIN+CALCIFICATION Search PRIMARY+FAMILIAL+BRAIN+CALCIFICATION
7 BRAIN CALCIFICATION 427256 4% 38% 21 Search BRAIN+CALCIFICATION Search BRAIN+CALCIFICATION
8 DIFFUSE NEUROFIBRILLARY TANGLES WITH CALCIFICATION 392399 2% 82% 9 Search DIFFUSE+NEUROFIBRILLARY+TANGLES+WITH+CALCIFICATION Search DIFFUSE+NEUROFIBRILLARY+TANGLES+WITH+CALCIFICATION
9 IBGC 274057 1% 86% 6 Search IBGC Search IBGC
10 DIFFUSE NEUROFIBRILLARY TANGLES WITH CALCIFICATION DNTC 266446 1% 100% 5 Search DIFFUSE+NEUROFIBRILLARY+TANGLES+WITH+CALCIFICATION+DNTC Search DIFFUSE+NEUROFIBRILLARY+TANGLES+WITH+CALCIFICATION+DNTC

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 PISTACCHI, M , GIOULIS, M , SANSON, F , MARSALA, SZ , (2016) FAHR'S SYNDROME AND CLINICAL CORRELATION: A CASE SERIES AND LITERATURE REVIEW.FOLIA NEUROPATHOLOGICA. VOL. 54. ISSUE 3. P. 282 -294 45 87% 0
2 SALEEM, S , ASLAM, HM , ANWAR, M , ANWAR, S , SALEEM, M , SALEEM, A , REHMANI, MAK , (2013) FAHR'S SYNDROME: LITERATURE REVIEW OF CURRENT EVIDENCE.ORPHANET JOURNAL OF RARE DISEASES. VOL. 8. ISSUE . P. - 36 88% 17
3 SAVINO, E , SOAVI, C , CAPATTI, E , BORRELLI, M , VIGNA, GB , PASSARO, A , ZULIANI, G , (2016) BILATERAL STRIO-PALLIDO-DENTATE CALCINOSIS (FAHR'S DISEASE): REPORT OF SEVEN CASES AND REVISION OF LITERATURE.BMC NEUROLOGY. VOL. 16. ISSUE . P. - 30 83% 1
4 KIMURA, T , MIURA, T , AOKI, K , SAITO, S , HONDO, H , KONNO, T , UCHIYAMA, A , IKEUCHI, T , TAKAHASHI, H , KAKITA, A , (2016) FAMILIAL IDIOPATHIC BASAL GANGLIA CALCIFICATION: HISTOPATHOLOGIC FEATURES OF AN AUTOPSIED PATIENT WITH AN SLC20A2 MUTATION.NEUROPATHOLOGY. VOL. 36. ISSUE 4. P. 365 -371 27 90% 1
5 CASANOVA, MF , ARAQUE, JM , (2003) MINERALIZATION OF THE BASAL GANGLIA: IMPLICATIONS FOR NEUROPSYCHIATRY, PATHOLOGY AND NEUROIMAGING.PSYCHIATRY RESEARCH. VOL. 121. ISSUE 1. P. 59-87 69 49% 30
6 MANYAM, BV , (2005) WHAT IS AND WHAT IS NOT FAHR'S DISEASE'.PARKINSONISM & RELATED DISORDERS. VOL. 11. ISSUE 2. P. 73-80 42 64% 119
7 WESTENBERGER, A , KLEIN, C , (2014) THE GENETICS OF PRIMARY FAMILIAL BRAIN CALCIFICATIONS.CURRENT NEUROLOGY AND NEUROSCIENCE REPORTS. VOL. 14. ISSUE 10. P. - 25 76% 5
8 WALLINGFORD, MC , CHIA, JJ , LEAF, EM , BORGEIA, S , CHAVKIN, NW , SAWANGMAKE, C , MARRO, K , COX, TC , SPEER, MY , GIACHELLI, CM , (2017) SLC20A2 DEFICIENCY IN MICE LEADS TO ELEVATED PHOSPHATE LEVELS IN CERBROSPINAL FLUID AND GLYMPHATIC PATHWAY-ASSOCIATED ARTERIOLAR CALCIFICATION, AND RECAPITULATES HUMAN IDIOPATHIC BASAL GANGLIA CALCIFICATION.BRAIN PATHOLOGY. VOL. 27. ISSUE 1. P. 64 -76 15 58% 2
9 BONAZZA, S , LA MORGIA, C , MARTINELLI, P , CAPELLARI, S , (2011) STRIO-PALLIDO-DENTATE CALCINOSIS: A DIAGNOSTIC APPROACH IN ADULT PATIENTS.NEUROLOGICAL SCIENCES. VOL. 32. ISSUE 4. P. 537-545 30 65% 14
10 LEMOS, RR , RAMOS, EM , LEGATI, A , NICOLAS, G , JENKINSON, EM , LIVINGSTON, JH , CROW, YJ , CAMPION, D , COPPOLA, G , OLIVEIRA, JRM , (2015) UPDATE AND MUTATIONAL ANALYSIS OF SLC20A2: A MAJOR CAUSE OF PRIMARY FAMILIAL BRAIN CALCIFICATION.HUMAN MUTATION. VOL. 36. ISSUE 5. P. 489 -495 23 68% 11

Classes with closest relation at Level 1



Rank Class id link
1 23941 HDR SYNDROME//HYPOPARATHYROIDISM//KENNY CAFFEY SYNDROME
2 33060 MENINGIOANGIOMATOSIS//CALCIFYING PSEUDONEOPLASM//CAPNON
3 15670 AICARDI GOUTIERES SYNDROME//TREX1//RIBONUCLEASE H
4 11696 PSEUDOHYPOPARATHYROIDISM//ALBRIGHT HEREDITARY OSTEODYSTROPHY//ALBRIGHTS HEREDITARY OSTEODYSTROPHY
5 36814 ALPHA KETOGLUTARIC ACID DEHYDROGENASE//ALPHA KETOGLUTARIC ACIDURIA//CHOROID PLEXUS CALCIFICATIONS
6 15144 PAROXYSMAL KINESIGENIC DYSKINESIA//PRRT2//PAROXYSMAL DYSKINESIA
7 23052 OCCIPITAL CALCIFICATIONS//GLUTEN ATAXIA//GLUTEN SENSITIVITY
8 17613 STURGE WEBER SYNDROME//CHOROIDAL HEMANGIOMA//CIRCUMSCRIBED CHOROIDAL HEMANGIOMA
9 26888 MILIARY BRAIN METASTASES//CARCINOMATOUS ENCEPHALITIS//BRAIN METASTASES
10 16357 HEMICHOREA//HEMIBALLISM//HOLMES TREMOR

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