Class information for:
Level 1: ALAGILLE SYNDROME//ARTERIOHEPATIC DYSPLASIA//PAUCITY OF INTERLOBULAR BILE DUCTS

Basic class information
Class id #P Avg. number of
references		 Database coverage
of references
20402 462 22.2 67%


Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes
The table includes all classes above and classes immediately below the current class.


Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
212 3       GASTROENTEROLOGY & HEPATOLOGY//LAPAROSCOPIC CHOLECYSTECTOMY//PRIMARY BILIARY CIRRHOSIS 51420
2293 2             BILIARY ATRESIA//CHOLEDOCHAL CYST//ALAGILLE SYNDROME 4563
20402 1                   ALAGILLE SYNDROME//ARTERIOHEPATIC DYSPLASIA//PAUCITY OF INTERLOBULAR BILE DUCTS 462

Terms with highest relevance score


rank Term termType Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 ALAGILLE SYNDROME authKW 7061859 32% 72% 148
2 ARTERIOHEPATIC DYSPLASIA authKW 939984 3% 89% 16
3 PAUCITY OF INTERLOBULAR BILE DUCTS authKW 469992 2% 89% 8
4 JAG1 authKW 440592 4% 33% 20
5 BILE DUCT PAUCITY authKW 359836 2% 78% 7
6 BUTTERFLY VERTEBRA authKW 302132 2% 57% 8
7 POSTERIOR EMBRYOTOXON authKW 294409 2% 64% 7
8 JAG1 GENE authKW 264371 1% 100% 4
9 JAG1 MUTATION authKW 198279 1% 100% 3
10 ALAGILLE authKW 148707 1% 75% 3

Web of Science journal categories


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 Pediatrics 3009 28% 0% 130
2 Gastroenterology & Hepatology 2048 21% 0% 95
3 Genetics & Heredity 1235 22% 0% 103
4 Nutrition & Dietetics 251 7% 0% 31
5 Transplantation 249 5% 0% 24
6 Radiology, Nuclear Medicine & Medical Imaging 108 7% 0% 33
7 Ophthalmology 98 5% 0% 21
8 Surgery 42 7% 0% 34
9 Pathology 37 3% 0% 15
10 Dermatology 34 3% 0% 12

Address terms


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 U347 73592 2% 16% 7
2 ABRAMSON 1010 66093 0% 100% 1
3 ANESTHESIA PERIOPERAT CRIT CARE MED 66093 0% 100% 1
4 CANC GENET NIH 66093 0% 100% 1
5 CLIN DEMARCHI 66093 0% 100% 1
6 CNRS UP A8090 66093 0% 100% 1
7 CNRS URA 620 STRUCT MUTAGENESE CHROMOSOMIQUES 66093 0% 100% 1
8 DIPARTIMENTO FISIOPATOL MED CHIRURG TR IAN 66093 0% 100% 1
9 DIPARTIMENTO PEDIAT ADOLESCENZA 66093 0% 100% 1
10 DIPARTIMENTO PEDIAT CARDIOCHIRURG CARDIOPATIE C 66093 0% 100% 1

Journals


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION 8377 6% 0% 30
2 AMERICAN JOURNAL OF MEDICAL GENETICS 2424 4% 0% 18
3 ACTA PAEDIATRICA BELGICA 1650 0% 3% 1
4 HEPATOLOGY 1405 3% 0% 16
5 JOURNAL OF MEDICAL GENETICS 1366 2% 0% 11
6 HUMAN MUTATION 1335 2% 0% 9
7 AMERICAN JOURNAL OF MEDICAL GENETICS PART A 1131 2% 0% 10
8 SEMINARS IN LIVER DISEASE 780 1% 0% 4
9 PEDIATRIC TRANSPLANTATION 713 1% 0% 5
10 CLINICAL DYSMORPHOLOGY 528 1% 0% 3

Author Key Words


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class		 LCSH search Wikipedia search
1 ALAGILLE SYNDROME 7061859 32% 72% 148 Search ALAGILLE+SYNDROME Search ALAGILLE+SYNDROME
2 ARTERIOHEPATIC DYSPLASIA 939984 3% 89% 16 Search ARTERIOHEPATIC+DYSPLASIA Search ARTERIOHEPATIC+DYSPLASIA
3 PAUCITY OF INTERLOBULAR BILE DUCTS 469992 2% 89% 8 Search PAUCITY+OF+INTERLOBULAR+BILE+DUCTS Search PAUCITY+OF+INTERLOBULAR+BILE+DUCTS
4 JAG1 440592 4% 33% 20 Search JAG1 Search JAG1
5 BILE DUCT PAUCITY 359836 2% 78% 7 Search BILE+DUCT+PAUCITY Search BILE+DUCT+PAUCITY
6 BUTTERFLY VERTEBRA 302132 2% 57% 8 Search BUTTERFLY+VERTEBRA Search BUTTERFLY+VERTEBRA
7 POSTERIOR EMBRYOTOXON 294409 2% 64% 7 Search POSTERIOR+EMBRYOTOXON Search POSTERIOR+EMBRYOTOXON
8 JAG1 GENE 264371 1% 100% 4 Search JAG1+GENE Search JAG1+GENE
9 JAG1 MUTATION 198279 1% 100% 3 Search JAG1+MUTATION Search JAG1+MUTATION
10 ALAGILLE 148707 1% 75% 3 Search ALAGILLE Search ALAGILLE

Core articles
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.


Rank Reference # ref.
in cl.		 Shr. of ref. in
cl.		 Citations
1 TURNPENNY, PD , ELLARD, S , (2012) ALAGILLE SYNDROME: PATHOGENESIS, DIAGNOSIS AND MANAGEMENT.EUROPEAN JOURNAL OF HUMAN GENETICS. VOL. 20. ISSUE 3. P. 251 -257 41 84% 51
2 KAMATH, BM , LOOMES, KM , PICCOLI, DA , (2010) MEDICAL MANAGEMENT OF ALAGILLE SYNDROME.JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION. VOL. 50. ISSUE 6. P. 580 -586 44 75% 15
3 KAMATH, BM , SPINNER, NB , ROSENBLUM, ND , (2013) RENAL INVOLVEMENT AND THE ROLE OF NOTCH SIGNALLING IN ALAGILLE SYNDROME.NATURE REVIEWS NEPHROLOGY. VOL. 9. ISSUE 7. P. 409-418 44 66% 4
4 CHO, JM , OH, SH , KIM, HJ , KIM, JS , KIM, KM , KIM, GH , YU, E , LEE, BH , YOO, HW , (2015) CLINICAL FEATURES, OUTCOMES, AND GENETIC ANALYSIS IN KOREAN CHILDREN WITH ALAGILLE SYNDROME.PEDIATRICS INTERNATIONAL. VOL. 57. ISSUE 4. P. 552 -557 27 90% 2
5 EMERICK, KM , RAND, EB , GOLDMUNTZ, E , KRANTZ, ID , SPINNER, NB , PICCOLI, DA , (1999) FEATURES OF ALAGILLE SYNDROME IN 92 PATIENTS: FREQUENCY AND RELATION TO PROGNOSIS.HEPATOLOGY. VOL. 29. ISSUE 3. P. 822 -829 32 84% 199
6 KAMATH, BM , SCHWARZ, KB , HADZIC, N , (2010) ALAGILLE SYNDROME AND LIVER TRANSPLANTATION.JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION. VOL. 50. ISSUE 1. P. 11 -15 29 83% 17
7 CIOCCA, M , ALVAREZ, F , (2012) ALAGILLE SYNDROME.ARCHIVOS ARGENTINOS DE PEDIATRIA. VOL. 110. ISSUE 6. P. 509-515 26 87% 1
8 PICCOLI, DA , SPINNER, NB , (2001) ALAGILLE SYNDROME AND THE JAGGED1 GENE.SEMINARS IN LIVER DISEASE. VOL. 21. ISSUE 4. P. 525-534 35 80% 58
9 LIN, HC , HOANG, PL , HUTCHINSON, A , CHAO, G , GERFEN, J , LOOMES, KM , KRANTZ, I , KAMATH, BM , SPINNER, NB , (2012) ALAGILLE SYNDROME IN A VIETNAMESE COHORT: MUTATION ANALYSIS AND ASSESSMENT OF FACIAL FEATURES.AMERICAN JOURNAL OF MEDICAL GENETICS PART A. VOL. 158A. ISSUE 5. P. 1005 -1013 24 89% 3
10 SUBRAMANIAM, P , KNISELY, A , PORTMANN, B , QURESHI, SA , ACLIMANDOS, WA , KARANI, JB , BAKER, AJ , (2011) DIAGNOSIS OF ALAGILLE SYNDROME-25 YEARS OF EXPERIENCE AT KING'S COLLEGE HOSPITAL.JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION. VOL. 52. ISSUE 1. P. 84 -89 24 86% 15

Classes with closest relation at Level 1


Rank Class id link
1 33440 TRISOMY 20P//TRISOMY 6P//NEURENSIN 2
2 6437 BILIARY ATRESIA//PORTOENTEROSTOMY//KASAI OPERATION
3 26933 HAJDU CHENEY SYNDROME//ACROOSTEOLYSIS//SERPENTINE FIBULA POLYCYSTIC KIDNEY SYNDROME
4 9748 INTRAHEPATIC CHOLESTASIS OF PREGNANCY//PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS//ABCB11
5 11708 DLL4//VASC PATTERNING//DELTA LIKE LIGAND 4
6 26264 KABUKI SYNDROME//KABUKI MAKE UP SYNDROME//NIIKAWA KUROKI SYNDROME
7 29024 TRISOMY 10Q//MONOSOMY 10Q//DISTAL 10Q TRISOMY
8 31161 CARPAL COALITION//FAMILIAL CARPAL TUNNEL SYNDROME//MELBOURNE PEDIAT HAND
9 13482 CONGENITAL SCOLIOSIS//EARLY ONSET SCOLIOSIS//GROWING RODS
10 3238 NOTCH//NEUROGENIC GENES//SUPPRESSOR OF HAIRLESS

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