Class information for:
Level 1: ALTERNATING HEMIPLEGIA OF CHILDHOOD//HOT WATER EPILEPSY//ALTERNATING HEMIPLEGIA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
26562 251 26.4 73%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
11 4 NEUROSCIENCES//CLINICAL NEUROLOGY//NEUROL 1112395
124 3       PARKINSONS DISEASE//MOVEMENT DISORDERS//DEEP BRAIN STIMULATION 67777
1818 2             DYSTONIA//TETRAHYDROBIOPTERIN//WRITERS CRAMP 6225
26562 1                   ALTERNATING HEMIPLEGIA OF CHILDHOOD//HOT WATER EPILEPSY//ALTERNATING HEMIPLEGIA 251

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ALTERNATING HEMIPLEGIA OF CHILDHOOD authKW 3438528 12% 91% 31
2 HOT WATER EPILEPSY authKW 2264642 9% 85% 22
3 ALTERNATING HEMIPLEGIA authKW 2235399 8% 88% 21
4 ATP1A3 authKW 1899370 9% 71% 22
5 RAPID ONSET DYSTONIA PARKINSONISM authKW 1244186 6% 68% 15
6 BATHING EPILEPSY authKW 851583 3% 100% 7
7 RAPID ONSET DYSTONIA PARKINSONISM RDP authKW 506893 2% 83% 5
8 DYT12 authKW 437952 2% 60% 6
9 ALTERNATING HEMIPLEGIA OF CHILDHOOD AHC authKW 364964 1% 100% 3
10 CAPOS SYNDROME authKW 364964 1% 100% 3

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 6094 67% 0% 168
2 Pediatrics 968 22% 0% 55
3 Neurosciences 265 21% 0% 52
4 Genetics & Heredity 42 7% 0% 17
5 Sport Sciences 33 3% 0% 8
6 Nutrition & Dietetics 32 4% 0% 9
7 Psychiatry 11 4% 0% 9
8 Behavioral Sciences 6 2% 0% 4
9 Medicine, General & Internal 2 3% 0% 8
10 Physiology 2 2% 0% 5

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 DUKE HLTH 218976 1% 60% 3
2 MOL EPILEPSY 162205 1% 67% 2
3 CENBIOTECH BIOSTAT SERV 121655 0% 100% 1
4 CHILDRENS HOSP SAN DIEGO MEDSTEM CELL PROGRA 121655 0% 100% 1
5 DIABLO VALLEY CHILD NEUROL 121655 0% 100% 1
6 EEG CHILD NEUROPSYCHIAT UNIT 121655 0% 100% 1
7 GENET UNIT NEUROMETABOL DIS 121655 0% 100% 1
8 GENOME SCI PEDIAT NEUROL 121655 0% 100% 1
9 IMAGERIE MOL DIAGNOST CIBLAGE THER EUT 121655 0% 100% 1
10 MED ETH HUMANITIES MED 121655 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BRAIN & DEVELOPMENT 7536 6% 0% 15
2 JOURNAL OF THE INTERNATIONAL SOCIETY OF SPORTS NUTRITION 7249 2% 1% 5
3 EPILEPTIC DISORDERS 4337 2% 1% 6
4 NEUROPEDIATRICS 3827 3% 0% 8
5 PEDIATRIC NEUROLOGY 3469 4% 0% 11
6 MOVEMENT DISORDERS 2676 5% 0% 12
7 DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY 2078 4% 0% 9
8 SEIZURE 1992 0% 2% 1
9 EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY 1758 2% 0% 4
10 JOURNAL OF CHILD NEUROLOGY 1596 3% 0% 8

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ALTERNATING HEMIPLEGIA OF CHILDHOOD 3438528 12% 91% 31 Search ALTERNATING+HEMIPLEGIA+OF+CHILDHOOD Search ALTERNATING+HEMIPLEGIA+OF+CHILDHOOD
2 HOT WATER EPILEPSY 2264642 9% 85% 22 Search HOT+WATER+EPILEPSY Search HOT+WATER+EPILEPSY
3 ALTERNATING HEMIPLEGIA 2235399 8% 88% 21 Search ALTERNATING+HEMIPLEGIA Search ALTERNATING+HEMIPLEGIA
4 ATP1A3 1899370 9% 71% 22 Search ATP1A3 Search ATP1A3
5 RAPID ONSET DYSTONIA PARKINSONISM 1244186 6% 68% 15 Search RAPID+ONSET+DYSTONIA+PARKINSONISM Search RAPID+ONSET+DYSTONIA+PARKINSONISM
6 BATHING EPILEPSY 851583 3% 100% 7 Search BATHING+EPILEPSY Search BATHING+EPILEPSY
7 RAPID ONSET DYSTONIA PARKINSONISM RDP 506893 2% 83% 5 Search RAPID+ONSET+DYSTONIA+PARKINSONISM+RDP Search RAPID+ONSET+DYSTONIA+PARKINSONISM+RDP
8 DYT12 437952 2% 60% 6 Search DYT12 Search DYT12
9 ALTERNATING HEMIPLEGIA OF CHILDHOOD AHC 364964 1% 100% 3 Search ALTERNATING+HEMIPLEGIA+OF+CHILDHOOD+AHC Search ALTERNATING+HEMIPLEGIA+OF+CHILDHOOD+AHC
10 CAPOS SYNDROME 364964 1% 100% 3 Search CAPOS+SYNDROME Search CAPOS+SYNDROME

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 SWENEY, MT , NEWCOMB, TM , SWOBODA, KJ , (2015) THE EXPANDING SPECTRUM OF NEUROLOGICAL PHENOTYPES IN CHILDREN WITH ATP1A3 MUTATIONS, ALTERNATING HEMIPLEGIA OF CHILDHOOD, RAPID-ONSET DYSTONIA-PARKINSONISM, CAPOS AND BEYOND.PEDIATRIC NEUROLOGY. VOL. 52. ISSUE 1. P. 56 -64 46 72% 18
2 VIOLLET, L , GLUSMAN, G , MURPHY, KJ , NEWCOMB, TM , REYNA, SP , SWENEY, M , NELSON, B , ANDERMANN, F , ANDERMANN, E , ACSADI, G , ET AL (2015) ALTERNATING HEMIPLEGIA OF CHILDHOOD: RETROSPECTIVE GENETIC STUDY AND GENOTYPE-PHENOTYPE CORRELATIONS IN 187 SUBJECTS FROM THE US AHCF REGISTRY.PLOS ONE. VOL. 10. ISSUE 5. P. - 40 85% 9
3 PANAGIOTAKAKI, E , DE GRANDIS, E , STAGNARO, M , HEINZEN, EL , FONS, C , SISODIYA, S , DE VRIES, B , GOUBAU, C , WECKHUYSEN, S , KEMLINK, D , ET AL (2015) CLINICAL PROFILE OF PATIENTS WITH ATP1A3 MUTATIONS IN ALTERNATING HEMIPLEGIA OF CHILDHOOD-A STUDY OF 155 PATIENTS.ORPHANET JOURNAL OF RARE DISEASES. VOL. 10. ISSUE . P. - 32 91% 13
4 HEINZEN, EL , ARZIMANOGLOU, A , BRASHEAR, A , CLAPCOTE, SJ , GURRIERI, F , GOLDSTEIN, DB , JOHANNESSON, SH , MIKATI, MA , NEVILLE, B , NICOLE, S , ET AL (2014) DISTINCT NEUROLOGICAL DISORDERS WITH ATP1A3 MUTATIONS.LANCET NEUROLOGY. VOL. 13. ISSUE 5. P. 503 -514 46 60% 36
5 GERGONT, A , KACINSKI, M , (2014) ALTERNATING HEMIPLEGIA OF CHILDHOOD: NEW DIAGNOSTIC OPTIONS.NEUROLOGIA I NEUROCHIRURGIA POLSKA. VOL. 48. ISSUE 2. P. 130 -135 24 96% 1
6 ROSEWICH, H , THIELE, H , OHLENBUSCH, A , MASCHKE, U , ALTMULLER, J , FROMMOLT, P , ZIM, B , EBINGER, F , SIEMES, H , NURNBERG, P , ET AL (2012) HETEROZYGOUS DE-NOVO MUTATIONS IN ATP1A3 IN PATIENTS WITH ALTERNATING HEMIPLEGIA OF CHILDHOOD: A WHOLE-EXOME SEQUENCING GENE-IDENTIFICATION STUDY.LANCET NEUROLOGY. VOL. 11. ISSUE 9. P. 764 -773 25 69% 76
7 PANAGIOTAKAKI, E , GOBBI, G , NEVILLE, B , EBINGER, F , CAMPISTOL, J , NEVSIMALOVA, S , LAAN, L , CASAER, P , SPIEL, G , GIANNOTTA, M , ET AL (2010) EVIDENCE OF A NON-PROGRESSIVE COURSE OF ALTERNATING HEMIPLEGIA OF CHILDHOOD: STUDY OF A LARGE COHORT OF CHILDREN AND ADULTS.BRAIN. VOL. 133. ISSUE . P. 3598 -3610 21 100% 37
8 ROSEWICH, H , OHLENBUSCH, A , HUPPKE, P , SCHLOTAWA, L , BAETHMANN, M , CARRILHO, I , FIORI, S , LOURENCO, CM , SAWYER, S , STEINFELD, R , ET AL (2014) THE EXPANDING CLINICAL AND GENETIC SPECTRUM OF ATP1A3-RELATED DISORDERS.NEUROLOGY. VOL. 82. ISSUE 11. P. 945 -955 19 90% 24
9 HULLY, M , ROPARS, J , HUBERT, L , BODDAERT, N , RIO, M , BERNARDELLI, M , DESGUERRE, I , CORMIER-DAIRE, V , MUNNICH, A , DE LONLAY, P , ET AL (2017) MOSAICISM IN ATP1A3-RELATED DISORDERS: NOT JUST A THEORETICAL RISK.NEUROGENETICS. VOL. 18. ISSUE 1. P. 23 -28 25 78% 0
10 PACIORKOWSKI, AR , MCDANIEL, SS , JANSEN, LA , TULLY, H , TUTTLE, E , GHONEIM, DH , TUPAL, S , GUNTER, SA , VASTA, V , ZHANG, Q , ET AL (2015) NOVEL MUTATIONS IN ATP1A3 ASSOCIATED WITH CATASTROPHIC EARLY LIFE EPILEPSY, EPISODIC PROLONGED APNEA, AND POSTNATAL MICROCEPHALY.EPILEPSIA. VOL. 56. ISSUE 3. P. 422 -430 22 71% 11

Classes with closest relation at Level 1



Rank Class id link
1 8676 FAMILIAL HEMIPLEGIC MIGRAINE//HEMIPLEGIC MIGRAINE//CACNA1A
2 25904 MOOD DISORDERS PROGRAMMED 1//PROGRAM HLTH SCIHLTH SCI UNIT//AGRN
3 1271 DYSTONIA//WRITERS CRAMP//DYT1
4 32993 DYKE DAVIDOFF MASSON SYNDROME//CEREBRAL HEMIATROPHY//HEMICONVULSION HEMIPLEGIA EPILEPSY SYNDROME
5 5719 NA K ATPASE//SODIUM PUMP//RECH CARDIOL
6 15161 FEBRILE SEIZURES//FEBRILE SEIZURE//FEBRILE CONVULSIONS
7 5865 JUVENILE MYOCLONIC EPILEPSY//IDIOPATHIC GENERALIZED EPILEPSY//REFLEX EPILEPSY
8 15144 PAROXYSMAL KINESIGENIC DYSKINESIA//PRRT2//PAROXYSMAL DYSKINESIA
9 29126 SEIZURE PRECIPITANTS//AURA INTERRUPTION//PRECIPITATION OF SEIZURES
10 3645 ATPASE NA K//NA K ATPASE//CURRENT TOPICS IN MEMBRANES AND TRANSPORT

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