Class information for:
Level 1: WYBURN MASON SYNDROME//BONNET DECHAUME BLANC SYNDROME//CONGENITAL RETINAL MACROVESSEL

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
35275 100 17.4 44%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
6 4 GASTROENTEROLOGY & HEPATOLOGY//ONCOLOGY//SURGERY 1371034
391 3       ARTERIOVENOUS MALFORMATION//VERTEBROPLASTY//DURAL ARTERIOVENOUS FISTULA 30586
1471 2             ARTERIOVENOUS MALFORMATION//DURAL ARTERIOVENOUS FISTULA//CEREBRAL ARTERIOVENOUS MALFORMATION 7695
35275 1                   WYBURN MASON SYNDROME//BONNET DECHAUME BLANC SYNDROME//CONGENITAL RETINAL MACROVESSEL 100

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 WYBURN MASON SYNDROME authKW 4041476 15% 88% 15
2 BONNET DECHAUME BLANC SYNDROME authKW 2442850 8% 100% 8
3 CONGENITAL RETINAL MACROVESSEL authKW 1832138 6% 100% 6
4 CONGENITAL ARTERIOVENOUS RETINAL MALFORMATION authKW 916069 3% 100% 3
5 WYBURN MASON authKW 916069 3% 100% 3
6 ANOMALOUS RETINAL VESSEL authKW 610713 2% 100% 2
7 CONGENITAL ARTERIOVENOUS COMMUNICATION OF THE RETINA authKW 610713 2% 100% 2
8 CONGENITAL RETINOCEPHALIC FACIAL VASCULAR MALFORMATION SYNDROME authKW 610713 2% 100% 2
9 RACEMOSE HAEMANGIOMA authKW 610713 2% 100% 2
10 MACROVESSEL authKW 549639 3% 60% 3

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Ophthalmology 7691 74% 0% 74
2 Clinical Neurology 212 21% 0% 21
3 Neuroimaging 154 5% 0% 5
4 Radiology, Nuclear Medicine & Medical Imaging 41 9% 0% 9
5 Surgery 35 12% 0% 12
6 Pediatrics 13 5% 0% 5
7 Primary Health Care 8 1% 0% 1
8 Otorhinolaryngology 6 2% 0% 2
9 Medicine, Research & Experimental 0 2% 0% 2
10 Neurosciences 0 4% 0% 4

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 VA BOSTON OCULAR TELEHLTH 305356 1% 100% 1
2 FDN MONTE TABOR 152677 1% 50% 1
3 HOP INTERCOMMUNAL 25445 1% 8% 1
4 CEREBROVASC NEUROL 15266 1% 5% 1
5 NEURO OPHTHALMOL 13878 1% 5% 1
6 ABT NETZHAUT GLASKORPERCHIRURG 10904 1% 4% 1
7 RETINA VITREOUS SERV 9044 2% 1% 2
8 LUESTHER T MERTZ RETINA 6636 1% 2% 1
9 DEAN MCGEE EYE 2879 1% 1% 1
10 SERV NEURORADIOL DIAGNOST THER EUT 2365 1% 1% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ANNALS OF OPHTHALMOLOGY 5087 6% 0% 6
2 ARQUIVOS BRASILEIROS DE OFTALMOLOGIA 4883 4% 0% 4
3 JOURNAL OF CLINICAL NEURO-OPHTHALMOLOGY 4824 3% 1% 3
4 OPHTHALMIC SURGERY LASERS & IMAGING RETINA 2250 2% 0% 2
5 ALBRECHT VON GRAEFES ARCHIV FUR KLINISCHE UND EXPERIMENTELLE OPHTHALMOLOGIE 1906 1% 1% 1
6 SURVEY OF OPHTHALMOLOGY 1752 3% 0% 3
7 IRANIAN JOURNAL OF OPHTHALMOLOGY 1743 1% 1% 1
8 BMC OPHTHALMOLOGY 1457 2% 0% 2
9 ARCHIVES OF OPHTHALMOLOGY 1322 6% 0% 6
10 KLINISCHE MONATSBLATTER FUR AUGENHEILKUNDE 1228 5% 0% 5

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 WYBURN MASON SYNDROME 4041476 15% 88% 15 Search WYBURN+MASON+SYNDROME Search WYBURN+MASON+SYNDROME
2 BONNET DECHAUME BLANC SYNDROME 2442850 8% 100% 8 Search BONNET+DECHAUME+BLANC+SYNDROME Search BONNET+DECHAUME+BLANC+SYNDROME
3 CONGENITAL RETINAL MACROVESSEL 1832138 6% 100% 6 Search CONGENITAL+RETINAL+MACROVESSEL Search CONGENITAL+RETINAL+MACROVESSEL
4 CONGENITAL ARTERIOVENOUS RETINAL MALFORMATION 916069 3% 100% 3 Search CONGENITAL+ARTERIOVENOUS+RETINAL+MALFORMATION Search CONGENITAL+ARTERIOVENOUS+RETINAL+MALFORMATION
5 WYBURN MASON 916069 3% 100% 3 Search WYBURN+MASON Search WYBURN+MASON
6 ANOMALOUS RETINAL VESSEL 610713 2% 100% 2 Search ANOMALOUS+RETINAL+VESSEL Search ANOMALOUS+RETINAL+VESSEL
7 CONGENITAL ARTERIOVENOUS COMMUNICATION OF THE RETINA 610713 2% 100% 2 Search CONGENITAL+ARTERIOVENOUS+COMMUNICATION+OF+THE+RETINA Search CONGENITAL+ARTERIOVENOUS+COMMUNICATION+OF+THE+RETINA
8 CONGENITAL RETINOCEPHALIC FACIAL VASCULAR MALFORMATION SYNDROME 610713 2% 100% 2 Search CONGENITAL+RETINOCEPHALIC+FACIAL+VASCULAR+MALFORMATION+SYNDROME Search CONGENITAL+RETINOCEPHALIC+FACIAL+VASCULAR+MALFORMATION+SYNDROME
9 RACEMOSE HAEMANGIOMA 610713 2% 100% 2 Search RACEMOSE+HAEMANGIOMA Search RACEMOSE+HAEMANGIOMA
10 MACROVESSEL 549639 3% 60% 3 Search MACROVESSEL Search MACROVESSEL

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 SCHMIDT, D , PACHE, M , SCHUMACHER, M , (2008) THE CONGENITAL UNILATERAL RETINOCEPHALIC VASCULAR MALFORMATION SYNDROME (BONNET-DECHAUME-BLANC SYNDROME OR WYBURN-MASON SYNDROME): REVIEW OF THE LITERATURE.SURVEY OF OPHTHALMOLOGY. VOL. 53. ISSUE 3. P. 227-249 29 67% 21
2 QIN, XJ , HUANG, C , LAI, K , (2014) RETINAL VEIN OCCLUSION IN RETINAL RACEMOSE HEMANGIOMA: A CASE REPORT AND LITERATURE REVIEW OF OCULAR COMPLICATIONS IN THIS RARE RETINAL VASCULAR DISORDER.BMC OPHTHALMOLOGY. VOL. 14. ISSUE . P. - 20 71% 2
3 DAYANI, PN , SADUN, AA , (2007) A CASE REPORT OF WYBURN-MASON SYNDROME AND REVIEW OF THE LITERATURE.NEURORADIOLOGY. VOL. 49. ISSUE 5. P. 445-456 16 89% 21
4 SCHMIDT, D , (2009) CONGENITAL RETINOCEPHALIC FACIAL VASCULAR MALFORMATION SYNDROME.OPHTHALMOLOGE. VOL. 106. ISSUE 1. P. 61 -68 9 90% 2
5 PETROPOULOS, IK , PETKOU, D , THEOULAKIS, PE , KORDELOU, A , POURNARAS, CJ , KATSIMPRIS, JM , (2008) CONGENITAL RETINAL MACROVESSELS: DESCRIPTION OF THREE CASES AND REVIEW OF THE LITERATURE.KLINISCHE MONATSBLATTER FUR AUGENHEILKUNDE. VOL. 225. ISSUE 5. P. 469-472 7 100% 2
6 RECK, SD , ZACKS, DN , EIBSCHITZ-TSIMHONI, M , (2005) RETINAL AND INTRACRANIAL ARTERIOVENOUS MALFORMATIONS: WYBURN-MASON SYNDROME.JOURNAL OF NEURO-OPHTHALMOLOGY. VOL. 25. ISSUE 3. P. 205-208 8 89% 16
7 GHASEMZADEH, F , ALEMZADEH, SH , BARKHORDARI, HR , REZAEIAN, E , (2010) CONGENITAL MACULAR MACROVESSELS: A CASE REPORT AND REVIEW OF THE LITERATURE.IRANIAN JOURNAL OF OPHTHALMOLOGY. VOL. 22. ISSUE 3. P. 61-65 6 100% 0
8 JIARAKONGMUN, P , ALVAREZ, A , RODESCH, G , LASJAUNIAS, P , (2002) CLINICAL COURSE AND ANGIOARCHITECTURE OF CEREBROFACIAL ARTERIOVENOUS METAMERIC SYNDROMES - THREE DEMONSTRATIVE CASES AND LITERATURE REVIEW.INTERVENTIONAL NEURORADIOLOGY. VOL. 8. ISSUE 3. P. 251-264 9 82% 1
9 CALLAHAN, AB , SKONDRA, D , KRZYSTOLIK, M , YONEKAWA, Y , ELIOTT, D , (2015) WYBURN-MASON SYNDROME ASSOCIATED WITH CUTANEOUS REACTIVE ANGIOMATOSIS AND CENTRAL RETINAL VEIN OCCLUSION.OPHTHALMIC SURGERY LASERS & IMAGING RETINA. VOL. 46. ISSUE 7. P. 760 -762 6 86% 0
10 ONDER, HI , ALISAN, S , TUNC, M , (2015) SEROUS RETINAL DETACHMENT AND CYSTOID MACULAR EDEMA IN A PATIENT WITH WYBURN-MASON SYNDROME.SEMINARS IN OPHTHALMOLOGY. VOL. 30. ISSUE 2. P. 154 -156 5 100% 1

Classes with closest relation at Level 1



Rank Class id link
1 17613 STURGE WEBER SYNDROME//CHOROIDAL HEMANGIOMA//CIRCUMSCRIBED CHOROIDAL HEMANGIOMA
2 15431 TERSONS SYNDROME//SUBMACULAR HEMORRHAGE//SUBRETINAL HEMORRHAGE
3 29593 CONJUNCTIVOCHALASIS//SUPERIOR LIMBIC KERATOCONJUNCTIVITIS//CONJUNCTIVAL RESECTION
4 1481 ARTERIOVENOUS MALFORMATION//CEREBRAL ARTERIOVENOUS MALFORMATION//ARTERIOVENOUS MALFORMATIONS
5 25607 SINUS PERICRANII//CIRSOID ANEURYSM//SCALP ARTERIOVENOUS MALFORMATION
6 24469 BLUE RUBBER BLEB NEVUS SYNDROME//BEAN SYNDROME//BRBNS
7 24573 EPITHELIAL DOWNGROWTH//IRIS CYST//VITREOUS CYST
8 19028 COATS DISEASE//IDIOPATHIC MACULAR TELANGIECTASIA//MACULAR TELANGIECTASIA
9 27512 INTRAVASCULAR PAPILLARY ENDOTHELIAL HYPERPLASIA//PAPILLARY ENDOTHELIAL HYPERPLASIA//MASSONS TUMOR
10 12813 CENTRAL RETINAL ARTERY OCCLUSION//RETINAL ARTERY OCCLUSION//AMAUROSIS FUGAX

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