Class information for:
Level 1: RIGID SPINE SYNDROME//RIGID SPINE//1ST AFFILIATED HOSP NEUROL

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
36499 80 21.7 39%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
180 3       DUCHENNE MUSCULAR DYSTROPHY//DYSTROPHIN//MUSCULAR DYSTROPHY 56784
1857 2             TITIN//INCLUSION BODY MYOSITIS//NEMALINE MYOPATHY 6073
36499 1                   RIGID SPINE SYNDROME//RIGID SPINE//1ST AFFILIATED HOSP NEUROL 80

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 RIGID SPINE SYNDROME authKW 3117171 18% 58% 14
2 RIGID SPINE authKW 795194 6% 42% 5
3 1ST AFFILIATED HOSP NEUROL address 381696 1% 100% 1
4 CERVICAL EXTENSION CONTRACTURE authKW 381696 1% 100% 1
5 DISORDERED BREATHING DURING SLEEP authKW 381696 1% 100% 1
6 GENETHON URA 1922 address 381696 1% 100% 1
7 HAUPTMANN THANNHAUSER SYNDROME authKW 381696 1% 100% 1
8 HEAD ORTHOPAEDIAT P E address 381696 1% 100% 1
9 HYPERTROPHIC NONOBSTRUCTIVE CARDIOMYOPATHY HNCM authKW 381696 1% 100% 1
10 INTERNAL MEDSERV DOENCAS NEUROMUSCULA address 381696 1% 100% 1

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 1485 59% 0% 47
2 Pediatrics 163 16% 0% 13
3 Neurosciences 90 21% 0% 17
4 Psychiatry 83 13% 0% 10
5 Medicine, General & Internal 46 13% 0% 10
6 Surgery 31 13% 0% 10
7 Rheumatology 29 4% 0% 3
8 Respiratory System 12 4% 0% 3
9 Orthopedics 11 4% 0% 3
10 Anesthesiology 10 3% 0% 2

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 1ST AFFILIATED HOSP NEUROL 381696 1% 100% 1
2 GENETHON URA 1922 381696 1% 100% 1
3 HEAD ORTHOPAEDIAT P E 381696 1% 100% 1
4 INTERNAL MEDSERV DOENCAS NEUROMUSCULA 381696 1% 100% 1
5 METAB DIS SERV 381696 1% 100% 1
6 NEUROPSYCHIAT INVEST UNIT 381696 1% 100% 1
7 PATHOL ANAT SERV HUMAN BIOPATHOL 381696 1% 100% 1
8 SERV BIOCHIMINSERMU582ASSISTANCE PUBL HOP PARI 381696 1% 100% 1
9 UF CARDIO GENET MYOGENET 381696 1% 100% 1
10 KINDERKLIN ATEMWEGSERKRANKUNGEN ALLERGIEN 190847 1% 50% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY 2617 10% 0% 8
2 REVUE NEUROLOGIQUE 2007 6% 0% 5
3 JOURNAL OF NEUROLOGY 1569 6% 0% 5
4 REVUE DU RHUMATISME 1505 4% 0% 3
5 NEUROMUSCULAR DISORDERS 1457 4% 0% 3
6 MUSCLE & NERVE 859 5% 0% 4
7 ARCHIVES FRANCAISES DE PEDIATRIE 838 3% 0% 2
8 HELVETICA PAEDIATRICA ACTA 803 1% 0% 1
9 KLINISCHE NEUROPHYSIOLOGIE 783 1% 0% 1
10 NEUROPEDIATRICS 750 3% 0% 2

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 RIGID SPINE SYNDROME 3117171 18% 58% 14 Search RIGID+SPINE+SYNDROME Search RIGID+SPINE+SYNDROME
2 RIGID SPINE 795194 6% 42% 5 Search RIGID+SPINE Search RIGID+SPINE
3 CERVICAL EXTENSION CONTRACTURE 381696 1% 100% 1 Search CERVICAL+EXTENSION+CONTRACTURE Search CERVICAL+EXTENSION+CONTRACTURE
4 DISORDERED BREATHING DURING SLEEP 381696 1% 100% 1 Search DISORDERED+BREATHING+DURING+SLEEP Search DISORDERED+BREATHING+DURING+SLEEP
5 HAUPTMANN THANNHAUSER SYNDROME 381696 1% 100% 1 Search HAUPTMANN+THANNHAUSER+SYNDROME Search HAUPTMANN+THANNHAUSER+SYNDROME
6 HYPERTROPHIC NONOBSTRUCTIVE CARDIOMYOPATHY HNCM 381696 1% 100% 1 Search HYPERTROPHIC+NONOBSTRUCTIVE+CARDIOMYOPATHY+HNCM Search HYPERTROPHIC+NONOBSTRUCTIVE+CARDIOMYOPATHY+HNCM
7 INTERNALIZED CAPILLARIES 381696 1% 100% 1 Search INTERNALIZED+CAPILLARIES Search INTERNALIZED+CAPILLARIES
8 MUSCULAR DISEASES DIAGNOSIS PATHOLOGY 381696 1% 100% 1 Search MUSCULAR+DISEASES+DIAGNOSIS+PATHOLOGY Search MUSCULAR+DISEASES+DIAGNOSIS+PATHOLOGY
9 NEURO ELECTROMYOGRAPHY 381696 1% 100% 1 Search NEURO+ELECTROMYOGRAPHY Search NEURO+ELECTROMYOGRAPHY
10 RESTRICTIVE RESPIRATORY IMPAIRMENT 381696 1% 100% 1 Search RESTRICTIVE+RESPIRATORY+IMPAIRMENT Search RESTRICTIVE+RESPIRATORY+IMPAIRMENT

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 FADIC, R , WACLAWIK, AJ , BROOKS, BR , LOTZ, BP , (1997) THE RIGID SPINE SYNDROME DUE TO ACID MALTASE DEFICIENCY.MUSCLE & NERVE. VOL. 20. ISSUE 3. P. 364-366 14 74% 17
2 ARKADER, A , HOSALKAR, H , DORMANS, JP , (2005) SCOLIOSIS CORRECTION IN AN ADOLESCENT WITH A RIGID SPINE SYNDROME - CASE REPORT.SPINE. VOL. 30. ISSUE 20. P. E623-E628 9 90% 1
3 POULTER, GT , GARTON, HJL , BLAKEMORE, LC , HENSINGER, RN , GRAZIANO, GP , FARLEY, FA , (2009) MORTALITY AND MORBIDITY ASSOCIATED WITH CORRECTION OF SEVERE CERVICAL HYPEREXTENSION.SPINE. VOL. 34. ISSUE 4. P. 378-383 13 54% 2
4 TODOROVIC, S , (1989) RIGID SPINE SYNDROME AND PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA IN A 15-YEAR-OLD GIRL.DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY. VOL. 31. ISSUE 6. P. 811-815 14 100% 0
5 JORGENSEN, BG , LAUB, M , KNUDSEN, RH , (1999) ANAESTHETIC IMPLICATIONS OF RIGID SPINE SYNDROME.PAEDIATRIC ANAESTHESIA. VOL. 9. ISSUE 4. P. 352 -355 15 58% 1
6 GIERER, S , PFISTER, R , (2000) ELECTROMYOGRAPHY IN LATE ONSET RIGID SPINE SYNDROME.KLINISCHE NEUROPHYSIOLOGIE. VOL. 31. ISSUE 1. P. 40 -43 9 90% 0
7 STUBGEN, JP , (2008) RIGID SPINE SYNDROME: A NONINVASIVE CARDIAC EVALUATION.PEDIATRIC CARDIOLOGY. VOL. 29. ISSUE 1. P. 45 -49 7 88% 3
8 YANG, MC , CHU, CC , CHERN, MS , CHEN, NH , CHUANG, ML , (2002) RIGID SPINE SYNDROME WITH CHRONIC RESPIRATORY FAILURE.JOURNAL OF THE FORMOSAN MEDICAL ASSOCIATION. VOL. 101. ISSUE 9. P. 650-654 7 88% 1
9 MOGHADASZADEH, B , DESGUERRE, I , TOPALOGLU, H , MUNTONI, FN , PAVEK, S , SEWRY, C , MAYER, M , FARDEAU, M , TOME, FMS , GUICHENEY, P , (1998) IDENTIFICATION OF A NEW LOCUS FOR A PECULIAR FORM OF CONGENITAL MUSCULAR DYSTROPHY WITH EARLY RIGIDITY OF THE SPINE, ON CHROMOSOME 1P35-36.AMERICAN JOURNAL OF HUMAN GENETICS. VOL. 62. ISSUE 6. P. 1439-1445 12 52% 45
10 VANNESTE, JAL , AUGUSTIJN, PB , STAM, FC , (1988) THE RIGID SPINE SYNDROME IN 2 SISTERS.JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY. VOL. 51. ISSUE 1. P. 131-135 12 75% 6

Classes with closest relation at Level 1



Rank Class id link
1 18862 COLLAGEN VI//TYPE VI COLLAGEN//BETHLEM MYOPATHY
2 25641 FHL2//FHL1//REDUCING BODY MYOPATHY
3 1053 LAMIN//LAMINOPATHY//NUCLEAR ENVELOPE
4 19195 MYOFIBRILLAR MYOPATHY//DESMINOPATHY//DESMIN
5 10502 NEMALINE MYOPATHY//CONGENITAL MYOPATHY//CENTRONUCLEAR MYOPATHY
6 6620 CONGENITAL MUSCULAR DYSTROPHY//DYSTROGLYCAN//WALKER WARBURG SYNDROME
7 15871 FACIOSCAPULOHUMERAL MUSCULAR DYSTROPHY//FSHD//DUX4
8 12262 INCLUSION BODY MYOSITIS//SPORADIC INCLUSION BODY MYOSITIS//GNE
9 24556 HIRAYAMA DISEASE//MONOMELIC AMYOTROPHY//CLIPPERS
10 8640 DYSFERLIN//LIMB GIRDLE MUSCULAR DYSTROPHY//SARCOGLYCAN

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