Class information for:
Level 1: METACHROMATIC LEUKODYSTROPHY//ARYLSULFATASE A//MULTIPLE SULFATASE DEFICIENCY

Basic class information

Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 ONCOLOGY//CELL BIOLOGY//BIOCHEMISTRY & MOLECULAR BIOLOGY 2934640
497 3       FABRY DISEASE//GAUCHER DISEASE//LYSOSOMAL STORAGE DISEASE 23081
385 2             FABRY DISEASE//GAUCHER DISEASE//LYSOSOMAL STORAGE DISEASE 17453
11487 1                   METACHROMATIC LEUKODYSTROPHY//ARYLSULFATASE A//MULTIPLE SULFATASE DEFICIENCY 1005

Terms with highest relevance score



rank Category termType chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 METACHROMATIC LEUKODYSTROPHY authKW 5043555 19% 83% 194
2 ARYLSULFATASE A authKW 2892318 11% 82% 112
3 MULTIPLE SULFATASE DEFICIENCY authKW 691191 2% 96% 23
4 PSEUDODEFICIENCY authKW 542044 2% 79% 22
5 ARYLSULFATASE A PSEUDODEFICIENCY authKW 311734 1% 76% 13
6 ARYLSULPHATASE A authKW 261317 1% 83% 10
7 ARYLSULFATASE authKW 247523 3% 26% 30
8 FORMYLGLYCINE authKW 230909 1% 82% 9
9 ARYLSULFATASE A DEFICIENCY authKW 219509 1% 100% 7
10 SUMF1 authKW 195382 1% 69% 9

Web of Science journal categories



chi_square_rank Category chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 Genetics & Heredity 2828 23% 0% 229
2 Clinical Neurology 1187 16% 0% 162
3 Biochemistry & Molecular Biology 1119 30% 0% 303
4 Medicine, Research & Experimental 661 11% 0% 107
5 Pediatrics 472 8% 0% 84
6 Medical Laboratory Technology 341 3% 0% 33
7 Neurosciences 155 10% 0% 98
8 Biophysics 130 5% 0% 52
9 Biotechnology & Applied Microbiology 123 6% 0% 62
10 Endocrinology & Metabolism 79 5% 0% 47

Address terms



chi_square_rank term chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 BIOCHEM ABT 2 109040 2% 17% 20
2 CHILD NEUROL DIS UNIT 41810 0% 67% 2
3 BIOCHEM MOL ZELLBIOL 32291 1% 8% 13
4 ADDENBROOKES CAMBRIDGE UNIV HOSP 31358 0% 100% 1
5 ASSOC RECH NEUROCHIM 31358 0% 100% 1
6 BIOL FUNCTAREA FISIOL 31358 0% 100% 1
7 BIOPROMOENSAIA 31358 0% 100% 1
8 BIOSCI BIOTECHNOL BIOSCI 31358 0% 100% 1
9 CHILD NEUROL PATHOL 31358 0% 100% 1
10 CHILDHOOD WHITE MATTER DISORDERS NEUROSCI C 31358 0% 100% 1

Journals



chi_square_rank term chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 JOURNAL OF INHERITED METABOLIC DISEASE 4605 3% 1% 26
2 HUMAN GENETICS 3249 3% 0% 29
3 REVUE ROUMAINE DE BIOCHIMIE 2569 0% 2% 5
4 MOLECULAR GENETICS AND METABOLISM 2186 1% 0% 15
5 HUMAN MUTATION 1941 2% 0% 16
6 CLINICAL GENETICS 1709 2% 0% 17
7 NEUROPEDIATRICS 1499 1% 0% 10
8 MOLECULAR AND CHEMICAL NEUROPATHOLOGY 1483 0% 1% 5
9 AMERICAN JOURNAL OF MEDICAL GENETICS 1401 2% 0% 20
10 HUMAN GENE THERAPY CLINICAL DEVELOPMENT 1374 0% 2% 2

Author Key Words



chi_square_rank term chi_square shrOfCwithTerm shrOfTermInClass termInClass LCSH search Wikipedia search
1 METACHROMATIC LEUKODYSTROPHY 5043555 19% 83% 194 Search METACHROMATIC+LEUKODYSTROPHY Search METACHROMATIC+LEUKODYSTROPHY
2 ARYLSULFATASE A 2892318 11% 82% 112 Search ARYLSULFATASE+A Search ARYLSULFATASE+A
3 MULTIPLE SULFATASE DEFICIENCY 691191 2% 96% 23 Search MULTIPLE+SULFATASE+DEFICIENCY Search MULTIPLE+SULFATASE+DEFICIENCY
4 PSEUDODEFICIENCY 542044 2% 79% 22 Search PSEUDODEFICIENCY Search PSEUDODEFICIENCY
5 ARYLSULFATASE A PSEUDODEFICIENCY 311734 1% 76% 13 Search ARYLSULFATASE+A+PSEUDODEFICIENCY Search ARYLSULFATASE+A+PSEUDODEFICIENCY
6 ARYLSULPHATASE A 261317 1% 83% 10 Search ARYLSULPHATASE+A Search ARYLSULPHATASE+A
7 ARYLSULFATASE 247523 3% 26% 30 Search ARYLSULFATASE Search ARYLSULFATASE
8 FORMYLGLYCINE 230909 1% 82% 9 Search FORMYLGLYCINE Search FORMYLGLYCINE
9 ARYLSULFATASE A DEFICIENCY 219509 1% 100% 7 Search ARYLSULFATASE+A+DEFICIENCY Search ARYLSULFATASE+A+DEFICIENCY
10 SUMF1 195382 1% 69% 9 Search SUMF1 Search SUMF1

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.

Classes with closest relation at Level 1



rank cluster_id2 link
1 16946 KRABBE DISEASE//GLOBOID CELL LEUKODYSTROPHY//PSYCHOSINE
2 18526 SULFATIDE//BIOMED ANAL RADIOISOTOPE//SULFOGLYCOLIPID
3 11715 STEROID SULFATASE//X LINKED ICHTHYOSIS//ESTRONE SULFATASE
4 912 MUCOPOLYSACCHARIDOSIS//MUCOPOLYSACCHARIDOSES//HUNTER SYNDROME
5 17631 PROSAPOSIN//SPHINGOLIPID ACTIVATOR PROTEINS//SAPOSIN
6 10461 SANDHOFF DISEASE//GM2 GANGLIOSIDOSIS//TAY SACHS DISEASE
7 12885 ALEXANDER DISEASE//LEUKODYSTROPHY//ROSENTHAL FIBERS
8 8534 MANNOSE 6 PHOSPHATE//MANNOSE 6 PHOSPHATE RECEPTOR//I CELL DISEASE
9 10500 ADRENOLEUKODYSTROPHY//X LINKED ADRENOLEUKODYSTROPHY//ADRENOMYELONEUROPATHY
10 29591 TOXIC LEUKOENCEPHALOPATHY//CHASING THE DRAGON//LEUCOENCEPHALOPATHY

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