Class information for:
Level 2: HYPER IGE SYNDROME//SEVERE COMBINED IMMUNODEFICIENCY//OMENN SYNDROME

Basic class information

Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
10 4 IMMUNOLOGY//TRANSPLANTATION//RHEUMATOLOGY 1369268
701 3       COMMON VARIABLE IMMUNODEFICIENCY//PRIMARY IMMUNODEFICIENCY//INTRAVENOUS IMMUNOGLOBULIN 7268
3443 2             HYPER IGE SYNDROME//SEVERE COMBINED IMMUNODEFICIENCY//OMENN SYNDROME 1642
12088 1                   SEVERE COMBINED IMMUNODEFICIENCY//OMENN SYNDROME//PRIMARY IMMUNODEFICIENCY 961
20149 1                   HYPER IGE SYNDROME//JOBS SYNDROME//HYPERIMMUNOGLOBULIN E SYNDROME 495
36117 1                   DUBOWITZ SYNDROME//CHOLESTEROL METABOLISM DISORDER//HYPOPLASIA BILATERAL METACARPAL 103
37403 1                   IN 111 WBC//31D8 MAB//ABDOMINAL INFLAMMATORY IMAGING 83

Terms with highest relevance score



rank Category termType chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 HYPER IGE SYNDROME authKW 1439987 6% 77% 98
2 SEVERE COMBINED IMMUNODEFICIENCY authKW 1309765 9% 44% 155
3 OMENN SYNDROME authKW 987023 4% 86% 60
4 JOBS SYNDROME authKW 875771 3% 89% 51
5 HYPERIMMUNOGLOBULIN E SYNDROME authKW 512323 2% 86% 31
6 PRIMARY IMMUNODEFICIENCY authKW 403402 8% 17% 125
7 DOCK8 authKW 386935 2% 81% 25
8 DUBOWITZ SYNDROME authKW 301231 1% 83% 19
9 DOCK8 DEFICIENCY authKW 268694 1% 100% 14
10 SEVERE COMBINED IMMUNODEFICIENCY SCID authKW 221149 1% 52% 22

Web of Science journal categories



chi_square_rank Category chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 Allergy 15402 14% 0% 236
2 Immunology 12982 43% 0% 698
3 Hematology 3269 14% 0% 232
4 Pediatrics 2926 15% 0% 250
5 Transplantation 1034 6% 0% 91
6 Medicine, Research & Experimental 392 7% 0% 114
7 Dermatology 368 4% 0% 67
8 Genetics & Heredity 237 6% 0% 105
9 Medicine, General & Internal 231 7% 0% 117
10 Pathology 144 3% 0% 54

Address terms



chi_square_rank term chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 JEFFREY MODELL DIAGNOST PRIMARY IMMUNOD 147630 1% 77% 10
2 PEDIAT ALLERGY IMMUNOL BLOOD MARROW TRANS 79967 0% 83% 5
3 U429 63866 2% 13% 26
4 IMMUNODEFICIENCY LEIPZIG 61414 0% 80% 4
5 CLIN IMMUNOL TRANSFUS MED MED 57577 0% 100% 3
6 ALLERGY IMMUNOL BLOOD MARROW TRANSPLANTAT 53308 0% 56% 5
7 JEFFREY MODELL DIAG PRIMARY IMMUNODEFICIE 53308 0% 56% 5
8 IMMUNODEFICIENCIES UNIT 49487 0% 37% 7
9 PEDIAT IMMUNOL SERV 44773 0% 33% 7
10 CLIN IMMUNODIAGNOST 43181 0% 75% 3

Journals



chi_square_rank term chi_square shrOfCwithTerm shrOfTermInClass termInClass
1 JOURNAL OF CLINICAL IMMUNOLOGY 37610 4% 3% 71
2 JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY 19480 6% 1% 105
3 CLINICAL IMMUNOLOGY 10481 2% 1% 39
4 IMMUNOLOGY AND ALLERGY CLINICS OF NORTH AMERICA 7355 1% 2% 23
5 CURRENT OPINION IN ALLERGY AND CLINICAL IMMUNOLOGY 4548 1% 1% 16
6 BONE MARROW TRANSPLANTATION 4498 3% 1% 46
7 IMMUNOLOGIC RESEARCH 3391 1% 1% 18
8 BLOOD 3255 5% 0% 78
9 CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY 3248 1% 1% 24
10 INTERNATIONAL JOURNAL OF PEDIATRIC HEMATOLOGY/ONCOLOGY 1611 0% 2% 5

Author Key Words



chi_square_rank term chi_square shrOfCwithTerm shrOfTermInClass termInClass LCSH search Wikipedia search
1 HYPER IGE SYNDROME 1439987 6% 77% 98 Search HYPER+IGE+SYNDROME Search HYPER+IGE+SYNDROME
2 SEVERE COMBINED IMMUNODEFICIENCY 1309765 9% 44% 155 Search SEVERE+COMBINED+IMMUNODEFICIENCY Search SEVERE+COMBINED+IMMUNODEFICIENCY
3 OMENN SYNDROME 987023 4% 86% 60 Search OMENN+SYNDROME Search OMENN+SYNDROME
4 JOBS SYNDROME 875771 3% 89% 51 Search JOBS+SYNDROME Search JOBS+SYNDROME
5 HYPERIMMUNOGLOBULIN E SYNDROME 512323 2% 86% 31 Search HYPERIMMUNOGLOBULIN+E+SYNDROME Search HYPERIMMUNOGLOBULIN+E+SYNDROME
6 PRIMARY IMMUNODEFICIENCY 403402 8% 17% 125 Search PRIMARY+IMMUNODEFICIENCY Search PRIMARY+IMMUNODEFICIENCY
7 DOCK8 386935 2% 81% 25 Search DOCK8 Search DOCK8
8 DUBOWITZ SYNDROME 301231 1% 83% 19 Search DUBOWITZ+SYNDROME Search DUBOWITZ+SYNDROME
9 DOCK8 DEFICIENCY 268694 1% 100% 14 Search DOCK8+DEFICIENCY Search DOCK8+DEFICIENCY
10 SEVERE COMBINED IMMUNODEFICIENCY SCID 221149 1% 52% 22 Search SEVERE+COMBINED+IMMUNODEFICIENCY+SCID Search SEVERE+COMBINED+IMMUNODEFICIENCY+SCID

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.

Classes with closest relation at Level 2



rank cluster_id2 link
1 2075 COMMON VARIABLE IMMUNODEFICIENCY//INTRAVENOUS IMMUNOGLOBULIN//PRIMARY IMMUNODEFICIENCY
2 3276 VELOCARDIOFACIAL SYNDROME//DIGEORGE SYNDROME//22Q112 DELETION SYNDROME
3 3111 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//HEMOPHAGOCYTIC SYNDROME//MACROPHAGE ACTIVATION SYNDROME
4 818 ONCOLYTIC VIRUS//GENE THERAPY//HUMAN GENE THERAPY
5 1495 CHRONIC GRANULOMATOUS DISEASE//FORMYL PEPTIDE RECEPTOR//NADPH OXIDASE
6 79 BONE MARROW TRANSPLANTATION//HEMATOLOGY//BIOLOGY OF BLOOD AND MARROW TRANSPLANTATION
7 1041 GAMMA DELTA T CELLS//THYMUS//INTERLEUKIN 7
8 559 SH2 DOMAIN//BTK//P66SHC
9 911 STAT3//GP130//ONCOSTATIN M
10 3291 MOLLUSCUM CONTAGIOSUM//WELLS SYNDROME//EOSINOPHILIC PUSTULAR FOLLICULITIS

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