Class information for:
Level 1: WEST SYNDROME//INFANTILE SPASMS//HYPSARRHYTHMIA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
10778 1036 29.5 64%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
11 4 NEUROSCIENCES//CLINICAL NEUROLOGY//NEUROL 1112395
143 3       EPILEPSY//EPILEPSIA//EPILEPSY & BEHAVIOR 64226
41 2             EPILEPSY//EPILEPSIA//EPILEPSY & BEHAVIOR 31060
10778 1                   WEST SYNDROME//INFANTILE SPASMS//HYPSARRHYTHMIA 1036

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 WEST SYNDROME authKW 4592709 25% 61% 254
2 INFANTILE SPASMS authKW 4527015 29% 51% 299
3 HYPSARRHYTHMIA authKW 1390590 7% 69% 68
4 EPILEPTIC SPASMS authKW 878338 4% 65% 46
5 OHTAHARA SYNDROME authKW 398446 3% 52% 26
6 ACTH THERAPY authKW 267932 1% 91% 10
7 EARLY MYOCLONIC ENCEPHALOPATHY authKW 207525 1% 54% 13
8 EARLY INFANTILE EPILEPTIC ENCEPHALOPATHY authKW 206295 1% 50% 14
9 BRAIN & DEVELOPMENT journal 190400 15% 4% 153
10 SUPPRESSION BURST PATTERN authKW 180519 1% 88% 7

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 31932 75% 0% 779
2 Pediatrics 7824 30% 0% 313
3 Neurosciences 358 13% 0% 136
4 Psychiatry 116 5% 0% 51
5 Neuroimaging 12 1% 0% 6
6 Medicine, General & Internal 3 3% 0% 28
7 Medicine, Research & Experimental 1 2% 0% 18
8 Pathology 1 1% 0% 11
9 Education, Special 1 0% 0% 2
10 Behavioral Sciences -0 0% 0% 5

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 COMM TOKYO CH TER 58945 0% 100% 2
2 EPILEPSY INFORMAT SERV 39296 0% 67% 2
3 FDN MONDINO 39296 0% 67% 2
4 CHILD NEUROL 37126 6% 2% 66
5 PETER KELLAWAY SECT NEUROPHYSIOL 34217 1% 19% 6
6 PEDIAT NEUROL 33029 8% 1% 88
7 ABORATE CLIN GRP PEDIAT NEUROL 29473 0% 100% 1
8 ALBERT E EIN MED BRONX 29473 0% 100% 1
9 ARABKIR MED COMPLEX 29473 0% 100% 1
10 BRAIN PEDIAT EPILEPSY CLINSEVERANCE CHI 29473 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BRAIN & DEVELOPMENT 190400 15% 4% 153
2 EPILEPSIA 76557 15% 2% 152
3 JOURNAL OF CHILD NEUROLOGY 30621 7% 1% 71
4 PEDIATRIC NEUROLOGY 29401 6% 2% 65
5 EPILEPSY RESEARCH 16774 5% 1% 47
6 EPILEPTIC DISORDERS 10528 2% 2% 19
7 NEUROPEDIATRICS 9783 3% 1% 26
8 JOURNAL OF EPILEPSY 7404 1% 3% 10
9 JAPANESE JOURNAL OF PSYCHIATRY AND NEUROLOGY 5807 1% 1% 14
10 GASLINI 4910 0% 17% 1

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 WEST SYNDROME 4592709 25% 61% 254 Search WEST+SYNDROME Search WEST+SYNDROME
2 INFANTILE SPASMS 4527015 29% 51% 299 Search INFANTILE+SPASMS Search INFANTILE+SPASMS
3 HYPSARRHYTHMIA 1390590 7% 69% 68 Search HYPSARRHYTHMIA Search HYPSARRHYTHMIA
4 EPILEPTIC SPASMS 878338 4% 65% 46 Search EPILEPTIC+SPASMS Search EPILEPTIC+SPASMS
5 OHTAHARA SYNDROME 398446 3% 52% 26 Search OHTAHARA+SYNDROME Search OHTAHARA+SYNDROME
6 ACTH THERAPY 267932 1% 91% 10 Search ACTH+THERAPY Search ACTH+THERAPY
7 EARLY MYOCLONIC ENCEPHALOPATHY 207525 1% 54% 13 Search EARLY+MYOCLONIC+ENCEPHALOPATHY Search EARLY+MYOCLONIC+ENCEPHALOPATHY
8 EARLY INFANTILE EPILEPTIC ENCEPHALOPATHY 206295 1% 50% 14 Search EARLY+INFANTILE+EPILEPTIC+ENCEPHALOPATHY Search EARLY+INFANTILE+EPILEPTIC+ENCEPHALOPATHY
9 SUPPRESSION BURST PATTERN 180519 1% 88% 7 Search SUPPRESSION+BURST+PATTERN Search SUPPRESSION+BURST+PATTERN
10 VIGABATRIN 140708 5% 9% 52 Search VIGABATRIN Search VIGABATRIN

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 TIBUSSEK, D , KLEPPER, J , KORINTHENBERG, R , KURLEMANN, G , RATING, D , WOHLRAB, G , WOLFF, M , SCHMITT, B , (2016) TREATMENT OF INFANTILE SPASMS: REPORT OF THE INTERDISCIPLINARY GUIDELINE COMMITTEE COORDINATED BY THE GERMAN-SPEAKING SOCIETY FOR NEUROPEDIATRICS.NEUROPEDIATRICS. VOL. 47. ISSUE 3. P. 139 -150 109 79% 0
2 PELLOCK, JM , HRACHOVY, R , SHINNAR, S , BARAM, TZ , BETTIS, D , DLUGOS, DJ , GAILLARD, WD , GIBSON, PA , HOLMES, GL , NORDLI, DR , ET AL (2010) INFANTILE SPASMS: A U.S. CONSENSUS REPORT.EPILEPSIA. VOL. 51. ISSUE 10. P. 2175 -2189 60 64% 119
3 TSAO, CY , (2009) CURRENT TRENDS IN THE TREATMENT OF INFANTILE SPASMS.NEUROPSYCHIATRIC DISEASE AND TREATMENT. VOL. 5. ISSUE . P. 289 -299 71 69% 19
4 HRACHOVY, RA , FROST, JD , (2003) INFANTILE EPILEPTIC ENCEPHALOPATHY WITH HYPSARRHYTHMIA (INFANTILE SPASMS/WEST SYNDROME).JOURNAL OF CLINICAL NEUROPHYSIOLOGY. VOL. 20. ISSUE 6. P. 408-425 68 78% 61
5 RIIKONEN, R , (2014) RECENT ADVANCES IN THE PHARMACOTHERAPY OF INFANTILE SPASMS.CNS DRUGS. VOL. 28. ISSUE 4. P. 279 -290 56 61% 12
6 WONG, M , TREVATHAN, E , (2001) INFANTILE SPASMS.PEDIATRIC NEUROLOGY. VOL. 24. ISSUE 2. P. 89 -98 56 84% 64
7 MACKAY, MT , WEISS, SK , ADAMS-WEBBER, T , ASHWAL, S , STEPHENS, D , BALLABAN-GILL, K , BARAM, TZ , DUCHOWNY, M , HIRTZ, D , PELLOCK, JM , ET AL (2004) PRACTICE PARAMETER: MEDICAL TREATMENT OF INFANTILE SPASMS - REPORT OF THE AMERICAN ACADEMY OF NEUROLOGY AND THE CHILD NEUROLOGY SOCIETY.NEUROLOGY. VOL. 62. ISSUE 10. P. 1668-1681 45 82% 177
8 MACKAY, M , WEISS, S , SNEAD, OC , (2002) TREATMENT OF INFANTILE SPASMS: AN EVIDENCE-BASED APPROACH.EPILEPSY, INFANTILE SPASMS, AND DEVELOPMENTAL ENCEPHALOPATHY. VOL. 49. ISSUE . P. 157 -184 59 79% 26
9 GO, CY , MACKAY, MT , WEISS, SK , STEPHENS, D , ADAMS-WEBBER, T , ASHWAL, S , SNEAD, OC , (2012) EVIDENCE-BASED GUIDELINE UPDATE: MEDICAL TREATMENT OF INFANTILE SPASMS REPORT OF THE GUIDELINE DEVELOPMENT SUBCOMMITTEE OF THE AMERICAN ACADEMY OF NEUROLOGY AND THE PRACTICE COMMITTEE OF THE CHILD NEUROLOGY SOCIETY.NEUROLOGY. VOL. 78. ISSUE 24. P. 1974-1980 31 89% 76
10 STAFSTROM, CE , ARNASON, BGW , BARAM, TZ , CATANIA, A , CORTEZ, MA , GLAUSER, TA , PRANZATELLI, MR , RIIKONEN, R , ROGAWSKI, MA , SHINNAR, S , ET AL (2011) TREATMENT OF INFANTILE SPASMS: EMERGING INSIGHTS FROM CLINICAL AND BASIC SCIENCE PERSPECTIVES.JOURNAL OF CHILD NEUROLOGY. VOL. 26. ISSUE 11. P. 1411-1421 53 64% 18

Classes with closest relation at Level 1



Rank Class id link
1 15080 VIGABATRIN//GAMMA VINYL GABA//VISUAL FIELD CONSTRICTION
2 23232 RUFINAMIDE//CLOBAZAM//LENNOX GASTAUT SYNDROME
3 23193 CORPUS CALLOSOTOMY//CALLOSOTOMY//DROP ATTACKS
4 13456 HEMISPHERECTOMY//HEMIMEGALENCEPHALY//HEMISPHEROTOMY
5 20804 PYRIDOXINE DEPENDENT EPILEPSY//PYRIDOXINE DEPENDENT SEIZURES//ALDH7A1
6 3699 DRAVET SYNDROME//SCN1A//GEFS
7 14954 HIGH FREQUENCY OSCILLATIONS//FAST RIPPLES//SEIZURE ONSET ZONE
8 13564 EPILEPTOGENESIS//NEURO PATHOL//EMERGENCY ACUTA
9 7373 LANDAU KLEFFNER SYNDROME//ROLANDIC EPILEPSY//PANAYIOTOPOULOS SYNDROME
10 15144 PAROXYSMAL KINESIGENIC DYSKINESIA//PRRT2//PAROXYSMAL DYSKINESIA

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