Class information for:
Level 1: DYSTROPHIN//DUCHENNE MUSCULAR DYSTROPHY//BECKER MUSCULAR DYSTROPHY

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
1302 2729 34.8 79%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
180 3       DUCHENNE MUSCULAR DYSTROPHY//DYSTROPHIN//MUSCULAR DYSTROPHY 56784
991 2             DUCHENNE MUSCULAR DYSTROPHY//DYSTROPHIN//MUSCULAR DYSTROPHY 10483
1302 1                   DYSTROPHIN//DUCHENNE MUSCULAR DYSTROPHY//BECKER MUSCULAR DYSTROPHY 2729

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 DYSTROPHIN authKW 2570928 20% 42% 550
2 DUCHENNE MUSCULAR DYSTROPHY authKW 1008886 15% 23% 401
3 BECKER MUSCULAR DYSTROPHY authKW 909485 5% 57% 142
4 DYSTROPHIN GENE authKW 523020 2% 78% 60
5 UTROPHIN authKW 458473 3% 44% 93
6 DP71 authKW 351391 1% 90% 35
7 DMD authKW 324155 3% 32% 92
8 DYSTROPHIN RELATED PROTEIN authKW 280097 1% 96% 26
9 DYSTROBREVIN authKW 223959 1% 65% 31
10 DUCHENNE BECKER MUSCULAR DYSTROPHY authKW 214605 1% 71% 27

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Genetics & Heredity 14110 30% 0% 829
2 Clinical Neurology 7148 23% 0% 632
3 Neurosciences 3254 22% 0% 596
4 Biochemistry & Molecular Biology 1142 21% 0% 565
5 Cell Biology 967 11% 0% 313
6 Pediatrics 514 6% 0% 156
7 Pathology 332 4% 0% 104
8 Biophysics 239 5% 0% 123
9 Medicine, Research & Experimental 200 4% 0% 120
10 Medical Laboratory Technology 172 2% 0% 43

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 GRP MUSCLES PATHOL 78312 0% 100% 7
2 OREGON CHILD HLTH 46612 0% 83% 5
3 PHYSIOL INTERACT EA701 44750 0% 100% 4
4 EA 701 BIOL 33562 0% 100% 3
5 MOLEC MED MOLEC GENET GRP 33562 0% 100% 3
6 EMI 99 18 29830 0% 67% 4
7 PHYSIOPATHOL CELLULAIRE MOL RETINE 28454 1% 18% 14
8 INSERM U300 27963 0% 50% 5
9 CHEM NUTRIENT DATA OUTPUT 22375 0% 100% 2
10 CHILD HLTH VIETNAM 22375 0% 100% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 NEUROMUSCULAR DISORDERS 68383 4% 5% 120
2 JOURNAL OF MEDICAL GENETICS 17705 4% 2% 96
3 HUMAN GENETICS 13923 4% 1% 100
4 AMERICAN JOURNAL OF MEDICAL GENETICS 7273 3% 1% 76
5 MUSCLE & NERVE 5985 2% 1% 62
6 HUMAN MOLECULAR GENETICS 5678 3% 1% 71
7 HUMAN MUTATION 5387 2% 1% 44
8 CLINICAL GENETICS 4782 2% 1% 47
9 AMERICAN JOURNAL OF HUMAN GENETICS 4757 2% 1% 59
10 JOURNAL OF THE NEUROLOGICAL SCIENCES 4306 2% 1% 63

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 DYSTROPHIN 2570928 20% 42% 550 Search DYSTROPHIN Search DYSTROPHIN
2 DUCHENNE MUSCULAR DYSTROPHY 1008886 15% 23% 401 Search DUCHENNE+MUSCULAR+DYSTROPHY Search DUCHENNE+MUSCULAR+DYSTROPHY
3 BECKER MUSCULAR DYSTROPHY 909485 5% 57% 142 Search BECKER+MUSCULAR+DYSTROPHY Search BECKER+MUSCULAR+DYSTROPHY
4 DYSTROPHIN GENE 523020 2% 78% 60 Search DYSTROPHIN+GENE Search DYSTROPHIN+GENE
5 UTROPHIN 458473 3% 44% 93 Search UTROPHIN Search UTROPHIN
6 DP71 351391 1% 90% 35 Search DP71 Search DP71
7 DMD 324155 3% 32% 92 Search DMD Search DMD
8 DYSTROPHIN RELATED PROTEIN 280097 1% 96% 26 Search DYSTROPHIN+RELATED+PROTEIN Search DYSTROPHIN+RELATED+PROTEIN
9 DYSTROBREVIN 223959 1% 65% 31 Search DYSTROBREVIN Search DYSTROBREVIN
10 DUCHENNE BECKER MUSCULAR DYSTROPHY 214605 1% 71% 27 Search DUCHENNE+BECKER+MUSCULAR+DYSTROPHY Search DUCHENNE+BECKER+MUSCULAR+DYSTROPHY

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 MUNTONI, F , TORELLI, S , FERLINI, A , (2003) DYSTROPHIN AND MUTATIONS: ONE GENE, SEVERAL PROTEINS, MULTIPLE PHENOTYPES.LANCET NEUROLOGY. VOL. 2. ISSUE 12. P. 731-740 117 85% 310
2 TADAYONI, R , RENDON, A , SORIA-JASSO, LE , CISNEROS, B , (2012) DYSTROPHIN DP71: THE SMALLEST BUT MULTIFUNCTIONAL PRODUCT OF THE DUCHENNE MUSCULAR DYSTROPHY GENE.MOLECULAR NEUROBIOLOGY. VOL. 45. ISSUE 1. P. 43-60 99 80% 20
3 HAENGGI, T , FRITSCHY, JM , (2006) ROLE OF DYSTROPHIN AND UTROPHIN FOR ASSEMBLY AND FUNCTION OF THE DYSTROPHIN GLYCOPROTEIN COMPLEX IN NON-MUSCLE TISSUE.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 63. ISSUE 14. P. 1614-1631 137 63% 81
4 PERRONNET, C , VAILLEND, C , (2010) DYSTROPHINS, UTROPHINS, AND ASSOCIATED SCAFFOLDING COMPLEXES: ROLE IN MAMMALIAN BRAIN AND IMPLICATIONS FOR THERAPEUTIC STRATEGIES.JOURNAL OF BIOMEDICINE AND BIOTECHNOLOGY. VOL. . ISSUE . P. - 125 63% 34
5 AHN, AH , KUNKEL, LM , (1993) THE STRUCTURAL AND FUNCTIONAL DIVERSITY OF DYSTROPHIN.NATURE GENETICS. VOL. 3. ISSUE 4. P. 283-291 111 71% 487
6 BOHM, SV , ROBERTS, RG , (2009) EXPRESSION OF MEMBERS OF THE DYSTROPHIN, DYSTROBREVIN, AND DYSTROTELIN SUPERFAMILY.CRITICAL REVIEWS IN EUKARYOTIC GENE EXPRESSION. VOL. 19. ISSUE 2. P. 89-108 95 77% 2
7 ROBERTS, RG , (1995) DYSTROPHIN, ITS GENE, AND THE DYSTROPHINOPATHIES.ADVANCES IN GENETICS, VOL 33. VOL. 33. ISSUE . P. 177-231 141 71% 22
8 FERLINI, A , NERI, M , GUALANDI, F , (2013) THE MEDICAL GENETICS OF DYSTROPHINOPATHIES: MOLECULAR GENETIC DIAGNOSIS AND ITS IMPACT ON CLINICAL PRACTICE.NEUROMUSCULAR DISORDERS. VOL. 23. ISSUE 1. P. 4-14 67 80% 14
9 RAE, MG , O'MALLEY, D , (2016) COGNITIVE DYSFUNCTION IN DUCHENNE MUSCULAR DYSTROPHY: A POSSIBLE ROLE FOR NEUROMODULATORY IMMUNE MOLECULES.JOURNAL OF NEUROPHYSIOLOGY. VOL. 116. ISSUE 3. P. 1304 -1315 94 49% 0
10 LOVE, DR , BYTH, BC , TINSLEY, JM , BLAKE, DJ , DAVIES, KE , (1993) DYSTROPHIN AND DYSTROPHIN-RELATED PROTEINS - A REVIEW OF PROTEIN AND RNA STUDIES.NEUROMUSCULAR DISORDERS. VOL. 3. ISSUE 1. P. 5 -21 92 88% 46

Classes with closest relation at Level 1



Rank Class id link
1 3773 MDX MOUSE//DUCHENNE MUSCULAR DYSTROPHY//MDX
2 17872 EXON SKIPPING//MC LOCKWOOD MUSCULAR DYSTROPHY//NEUROMUSCULAR ALS
3 37057 PRE ANALYTICAL PROCESS//OCCUPAT HLTH PREVENT REINTEGRAT//SCI QUAL HLTH CARE
4 30643 GLYCEROL KINASE DEFICIENCY//COMPLEX GLYCEROL KINASE DEFICIENCY//KOHLSCHUTTER TONZ SYNDROME
5 8640 DYSFERLIN//LIMB GIRDLE MUSCULAR DYSTROPHY//SARCOGLYCAN
6 8253 DUCHENNE MUSCULAR DYSTROPHY//DUCHENNE//MUSCULAR DYSTROPHY
7 6620 CONGENITAL MUSCULAR DYSTROPHY//DYSTROGLYCAN//WALKER WARBURG SYNDROME
8 13599 REHABIL INFANTIL//MUSCLE & NERVE//ANGULATED FIBERS
9 35818 HYPERCKEMIA//ASYMPTOMATIC CK ELEVATION//IDIOPATHIC HYPER CK EMIA
10 5454 AGRIN//NEUROMUSCULAR JUNCTION//ACETYLCHOLINE RECEPTOR

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