Class information for:
Level 1: BROWN VIALETTO VAN LAERE SYNDROME//RIBOFLAVIN//RIBOFLAVIN DEFICIENCY

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
17425 600 28.7 47%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
631 3       KYNURENINE//NEOPTERIN//INDOLEAMINE 2 3 DIOXYGENASE 12928
1475 2             THIAMINE//THIAMINE DEFICIENCY//WERNICKES ENCEPHALOPATHY 7673
17425 1                   BROWN VIALETTO VAN LAERE SYNDROME//RIBOFLAVIN//RIBOFLAVIN DEFICIENCY 600

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BROWN VIALETTO VAN LAERE SYNDROME authKW 1020132 4% 95% 21
2 RIBOFLAVIN authKW 473090 19% 8% 115
3 RIBOFLAVIN DEFICIENCY authKW 434255 3% 53% 16
4 PONTOBULBAR PALSY authKW 356237 1% 100% 7
5 RIBOFLAVIN TRANSPORTER authKW 305346 1% 100% 6
6 RIBOFLAVIN TRANSPORT authKW 261724 1% 86% 6
7 MADRAS MOTOR NEURON DISEASE authKW 212044 1% 83% 5
8 RIBOFLAVIN STATUS authKW 207799 1% 58% 7
9 FAZIO LONDE DISEASE authKW 203564 1% 100% 4
10 SLC52A2 authKW 203564 1% 100% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Nutrition & Dietetics 14878 42% 0% 249
2 Tropical Medicine 210 3% 0% 18
3 Clinical Neurology 141 8% 0% 49
4 Medicine, Research & Experimental 141 7% 0% 41
5 Pediatrics 88 5% 0% 31
6 Physiology 45 4% 0% 24
7 Agriculture, Dairy & Animal Science 38 2% 0% 14
8 Medical Laboratory Technology 34 2% 0% 9
9 Endocrinology & Metabolism 33 4% 0% 25
10 Pharmacology & Pharmacy 22 6% 0% 38

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 UCI LONG BEACH VA MED PROGRAM 101782 0% 100% 2
2 AUDIOVESTIBULAR UNIT 50891 0% 100% 1
3 CA ABT GYNAKOL GEBURTSHILFE 50891 0% 100% 1
4 CATEDRA MIROBIOL SUPER 50891 0% 100% 1
5 CLIN EXPT PHYSIOPATHOL 50891 0% 100% 1
6 COLERAINE HOSP 50891 0% 100% 1
7 DIS CONTROL PREVENTCOMMISSIONED CORPS 50891 0% 100% 1
8 ELDERLY REHABIL UNIT 50891 0% 100% 1
9 GEN PHYSL BIOCHEM 50891 0% 100% 1
10 INT EMERGENCY REFUGEE HLTH 50891 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HUMAN NUTRITION-CLINICAL NUTRITION 40290 3% 5% 15
2 INTERNATIONAL JOURNAL FOR VITAMIN AND NUTRITION RESEARCH 15268 4% 1% 24
3 BRITISH JOURNAL OF NUTRITION 5537 5% 0% 31
4 AMERICAN JOURNAL OF CLINICAL NUTRITION 4224 6% 0% 33
5 JOURNAL OF NUTRITION 3681 5% 0% 31
6 NUTRITION RESEARCH 3525 3% 0% 18
7 DRUG-NUTRIENT INTERACTIONS 2541 0% 3% 2
8 ANNALS OF NUTRITION AND METABOLISM 2387 2% 0% 10
9 BIOMEDICINE EXPRESS 1782 0% 2% 2
10 JOURNAL OF NUTRITIONAL SCIENCE AND VITAMINOLOGY 1230 1% 0% 8

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 BROWN VIALETTO VAN LAERE SYNDROME 1020132 4% 95% 21 Search BROWN+VIALETTO+VAN+LAERE+SYNDROME Search BROWN+VIALETTO+VAN+LAERE+SYNDROME
2 RIBOFLAVIN 473090 19% 8% 115 Search RIBOFLAVIN Search RIBOFLAVIN
3 RIBOFLAVIN DEFICIENCY 434255 3% 53% 16 Search RIBOFLAVIN+DEFICIENCY Search RIBOFLAVIN+DEFICIENCY
4 PONTOBULBAR PALSY 356237 1% 100% 7 Search PONTOBULBAR+PALSY Search PONTOBULBAR+PALSY
5 RIBOFLAVIN TRANSPORTER 305346 1% 100% 6 Search RIBOFLAVIN+TRANSPORTER Search RIBOFLAVIN+TRANSPORTER
6 RIBOFLAVIN TRANSPORT 261724 1% 86% 6 Search RIBOFLAVIN+TRANSPORT Search RIBOFLAVIN+TRANSPORT
7 MADRAS MOTOR NEURON DISEASE 212044 1% 83% 5 Search MADRAS+MOTOR+NEURON+DISEASE Search MADRAS+MOTOR+NEURON+DISEASE
8 RIBOFLAVIN STATUS 207799 1% 58% 7 Search RIBOFLAVIN+STATUS Search RIBOFLAVIN+STATUS
9 FAZIO LONDE DISEASE 203564 1% 100% 4 Search FAZIO+LONDE+DISEASE Search FAZIO+LONDE+DISEASE
10 SLC52A2 203564 1% 100% 4 Search SLC52A2 Search SLC52A2

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 POWERS, HJ , (2003) RIBOFLAVIN (VITAMIN B-2) AND HEALTH.AMERICAN JOURNAL OF CLINICAL NUTRITION. VOL. 77. ISSUE 6. P. 1352 -1360 50 57% 236
2 MANOLE, A , FRATTA, P , HOULDEN, H , (2014) RECENT ADVANCES IN BULBAR SYNDROMES: GENETIC CAUSES AND DISEASE MECHANISMS.CURRENT OPINION IN NEUROLOGY. VOL. 27. ISSUE 5. P. 506 -514 37 62% 4
3 JAEGER, B , BOSCH, AM , (2016) CLINICAL PRESENTATION AND OUTCOME OF RIBOFLAVIN TRANSPORTER DEFICIENCY: MINI REVIEW AFTER FIVE YEARS OF EXPERIENCE.JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 39. ISSUE 4. P. 559 -564 23 88% 1
4 BOSCH, AM , STROEK, K , ABELING, NG , WATERHAM, HR , IJLST, L , WANDERS, RJA , (2012) THE BROWN-VIALETTO-VAN LAERE AND FAZIO LONDE SYNDROME REVISITED: NATURAL HISTORY, GENETICS, TREATMENT AND FUTURE PERSPECTIVES.ORPHANET JOURNAL OF RARE DISEASES. VOL. 7. ISSUE . P. - 23 92% 26
5 FOLEY, AR , MENEZES, MP , PANDRAUD, A , GONZALEZ, MA , AL-ODAIB, A , ABRAMS, AJ , SUGANO, K , YONEZAWA, A , MANZUR, AY , BURNS, J , ET AL (2014) TREATABLE CHILDHOOD NEURONOPATHY CAUSED BY MUTATIONS IN RIBOFLAVIN TRANSPORTER RFVT2.BRAIN. VOL. 137. ISSUE . P. 44-56 22 81% 21
6 SATHASIVAM, S , (2008) BROWN-VIALETTO-VAN LAERE SYNDROME.ORPHANET JOURNAL OF RARE DISEASES. VOL. 3. ISSUE . P. - 23 88% 31
7 SUBRAMANIAN, VS , LAMBRECHT, N , LYTLE, C , SAID, HM , (2016) CONDITIONAL (INTESTINAL-SPECIFIC) KNOCKOUT OF THE RIBOFLAVIN TRANSPORTER-3 (RFVT-3) IMPAIRS RIBOFLAVIN ABSORPTION.AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY. VOL. 310. ISSUE 4. P. G285 -G293 21 72% 1
8 YOSHIMATSU, H , YONEZAWA, A , YAO, Y , SUGANO, K , NAKAGAWA, S , OMURA, T , MATSUBARA, K , (2014) FUNCTIONAL INVOLVEMENT OF RFVT3/SLC52A3 IN INTESTINAL RIBOFLAVIN ABSORPTION.AMERICAN JOURNAL OF PHYSIOLOGY-GASTROINTESTINAL AND LIVER PHYSIOLOGY. VOL. 306. ISSUE 2. P. G102-G110 22 73% 5
9 INTOH, A , SUZUKI, N , KOSZKA, K , EGGAN, K , (2016) SLC52A3, A BROWN-VIALETTO-VAN LAERE SYNDROME CANDIDATE GENE IS ESSENTIAL FOR MOUSE DEVELOPMENT, BUT DISPENSABLE FOR MOTOR NEURON DIFFERENTIATION.HUMAN MOLECULAR GENETICS. VOL. 25. ISSUE 9. P. 1814 -1823 18 78% 0
10 BARILE, M , GIANCASPERO, TA , BRIZIO, C , PANEBIANCO, C , INDIVERI, C , GALLUCCIO, M , VERGANI, L , EBERINI, I , GIANAZZA, E , (2013) BIOSYNTHESIS OF FLAVIN COFACTORS IN MAN: IMPLICATIONS IN HEALTH AND DISEASE.CURRENT PHARMACEUTICAL DESIGN. VOL. 19. ISSUE 14. P. 2649 -2675 54 26% 10

Classes with closest relation at Level 1



Rank Class id link
1 26280 RIBOFLAVIN CARRIER PROTEIN//RIBOFLAVIN BINDING PROTEIN//CHICKEN RIBOFLAVIN CARRIER PROTEIN
2 9029 VITAMIN B 6//VITAMIN B 6 STATUS//VITAMIN B 6 DEFICIENCY
3 14851 ASHBYA GOSSYPII//RIBOFLAVIN BIOSYNTHESIS//RIBOFLAVIN SYNTHASE
4 25058 DRUG METAB MOL TOXICOL S//KUVIN TROP DIS//P VINCKEI PETTERI
5 10670 WATER SOLUBLE VITAMINS//RIBOFLAVIN//THIAMINE
6 21807 BENFOTIAMINE//SLC19A2//SLC19A3
7 37634 TABLE OF FOOD COMPOSITION//BEANS AND CORN TORTILLAS//BONE MASS AND DENSITY
8 30336 EVOLUTIONARY IMMUNOBIOL//PERITONEAL INFLAMMATION//ZYMOSAN
9 24556 HIRAYAMA DISEASE//MONOMELIC AMYOTROPHY//CLIPPERS
10 25989 PROSTATE STEM CELL ANTIGEN//PSCA//PLCE1

Go to start page