Class information for:
Level 1: MYELOKATHEXIS//WHIM SYNDROME//INSERM UMR S996

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
32925 132 41.3 84%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
535 3       TAURINE//CHRONIC GRANULOMATOUS DISEASE//L FORMS 19480
2683 2             NEUTROPHIL EXTRACELLULAR TRAPS//SEVERE CONGENITAL NEUTROPENIA//NETOSIS 3378
32925 1                   MYELOKATHEXIS//WHIM SYNDROME//INSERM UMR S996 132

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MYELOKATHEXIS authKW 3253076 11% 94% 15
2 WHIM SYNDROME authKW 1850632 9% 67% 12
3 INSERM UMR S996 address 693990 2% 100% 3
4 EXCELLENCE MEDICAT INNOVAT THER EUT address 462656 3% 50% 4
5 U819 address 378531 5% 27% 6
6 1500 E MED DRROOM F6515BOX 0238 address 231330 1% 100% 1
7 BLOOD CELL EGRESS authKW 231330 1% 100% 1
8 CS MOTT CHILDRENS HOSP HEMATOL ONCOL address 231330 1% 100% 1
9 CXCL12 STROMAL DERIVED FACTOR 1 SDF 1 authKW 231330 1% 100% 1
10 CXCR4 MUTATION authKW 231330 1% 100% 1

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 2203 39% 0% 52
2 Immunology 449 29% 0% 38
3 Medicine, Research & Experimental 154 14% 0% 18
4 Cell Biology 46 11% 0% 15
5 Pediatrics 14 5% 0% 6
6 Allergy 10 2% 0% 2
7 Pathology 9 3% 0% 4
8 Dermatology 7 2% 0% 3
9 Genetics & Heredity 4 4% 0% 5
10 Infectious Diseases 3 2% 0% 3

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 INSERM UMR S996 693990 2% 100% 3
2 EXCELLENCE MEDICAT INNOVAT THER EUT 462656 3% 50% 4
3 U819 378531 5% 27% 6
4 1500 E MED DRROOM F6515BOX 0238 231330 1% 100% 1
5 CS MOTT CHILDRENS HOSP HEMATOL ONCOL 231330 1% 100% 1
6 EXPT PATHOL CANC UK 231330 1% 100% 1
7 HOP BELLEISLE 231330 1% 100% 1
8 HP 15 231330 1% 100% 1
9 IMCB ELE ON MICROSCOPY SUITE 231330 1% 100% 1
10 IPSITINSERMCNRS 231330 1% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BLOOD 2695 15% 0% 20
2 TRENDS IN IMMUNOLOGY 1609 2% 0% 3
3 BIOLOGY OF SEX DIFFERENCES 1320 1% 1% 1
4 JOURNAL OF LEUKOCYTE BIOLOGY 1190 5% 0% 6
5 EUROPEAN JOURNAL OF HAEMATOLOGY 966 3% 0% 4
6 CURRENT OPINION IN HEMATOLOGY 806 2% 0% 2
7 CLINICAL AND LABORATORY HAEMATOLOGY 622 2% 0% 2
8 BRITISH JOURNAL OF HAEMATOLOGY 611 5% 0% 6
9 IMMUNITY 603 2% 0% 3
10 EXPERT OPINION ON ORPHAN DRUGS 525 1% 0% 1

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 MYELOKATHEXIS 3253076 11% 94% 15 Search MYELOKATHEXIS Search MYELOKATHEXIS
2 WHIM SYNDROME 1850632 9% 67% 12 Search WHIM+SYNDROME Search WHIM+SYNDROME
3 BLOOD CELL EGRESS 231330 1% 100% 1 Search BLOOD+CELL+EGRESS Search BLOOD+CELL+EGRESS
4 CXCL12 STROMAL DERIVED FACTOR 1 SDF 1 231330 1% 100% 1 Search CXCL12+STROMAL+DERIVED+FACTOR+1+SDF+1 Search CXCL12+STROMAL+DERIVED+FACTOR+1+SDF+1
5 CXCR4 MUTATION 231330 1% 100% 1 Search CXCR4+MUTATION Search CXCR4+MUTATION
6 CXCR4 SDF 1 CXCL12 231330 1% 100% 1 Search CXCR4+SDF+1+CXCL12 Search CXCR4+SDF+1+CXCL12
7 G PROTEIN COUPLED RECEPTOR KINASE 3 231330 1% 100% 1 Search G+PROTEIN+COUPLED+RECEPTOR+KINASE+3 Search G+PROTEIN+COUPLED+RECEPTOR+KINASE+3
8 G6PC3 DEFICIENCY 231330 1% 100% 1 Search G6PC3+DEFICIENCY Search G6PC3+DEFICIENCY
9 LEUCOCYTE HOMEOSTASIS 231330 1% 100% 1 Search LEUCOCYTE+HOMEOSTASIS Search LEUCOCYTE+HOMEOSTASIS
10 LEUCOCYTE MOBILIZATION 231330 1% 100% 1 Search LEUCOCYTE+MOBILIZATION Search LEUCOCYTE+MOBILIZATION

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 COHEN, SB , FENNETEAU, O , PLOUVIER, E , ROHRLICH, PS , DALTROFF, G , PLANTIER, I , DUPUY, A , KEROB, D , BEAUPAIN, B , BORDIGONI, P , ET AL (2012) DESCRIPTION AND OUTCOME OF A COHORT OF 8 PATIENTS WITH WHIM SYNDROME FROM THE FRENCH SEVERE CHRONIC NEUTROPENIA REGISTRY.ORPHANET JOURNAL OF RARE DISEASES. VOL. 7. ISSUE . P. - 40 75% 12
2 AL USTWANI, O , KURZROCK, R , WETZLER, M , (2014) GENETICS ON A WHIM.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 164. ISSUE 1. P. 15-23 41 64% 8
3 KAWAI, T , MALECH, HL , (2009) WHIM SYNDROME: CONGENITAL IMMUNE DEFICIENCY DISEASE.CURRENT OPINION IN HEMATOLOGY. VOL. 16. ISSUE 1. P. 20-26 24 48% 74
4 DOTTA, L , TASSONE, L , BADOLATO, R , (2011) CLINICAL AND GENETIC FEATURES OF WARTS, HYPOGAMMAGLOBULINEMIA, INFECTIONS AND MYELOKATHEXIS (WHIM) SYNDROME.CURRENT MOLECULAR MEDICINE. VOL. 11. ISSUE 4. P. 317-325 25 47% 28
5 BOCK, I , DUGUE, F , LOPPINET, E , BELLANNE-CHANTELOT, C , BENET, B , (2014) WHIM SYNDROME: PRESUMPTIVE DIAGNOSIS BASED ON MYELOKATHEXIS ON BONE MARROW SMEAR.ANNALES DE BIOLOGIE CLINIQUE. VOL. 72. ISSUE 1. P. 111 -119 11 85% 1
6 SIEDLAR, M , RUDZKI, Z , STRACH, M , TRZYNA, E , PITUCH-NOWOROLSKA, A , BLAUT-SZLOSARCZYK, A , BUKOWSKA-STRAKOVA, K , LENART, M , GRODZICKI, T , ZEMBALA, M , (2008) FAMILIAL OCCURRENCE OF WARTS, HYPOGAMMAGLOBULINEMIA, INFECTIONS, AND MYELOKATHEXIS (WHIM) SYNDROME.ARCHIVUM IMMUNOLOGIAE ET THERAPIAE EXPERIMENTALIS. VOL. 56. ISSUE 6. P. 419 -425 13 81% 8
7 KELLY, C , CARDONES, AR , GOLD, SH , HWANG, EI , WECHSLER, DS , MALECH, HL , MURPHY, PM , MCDERMOTT, DH , LIU, Q , CHEN, HQ , ET AL (2012) WHIM SYNDROME CAUSED BY A SINGLE AMINO ACID SUBSTITUTION IN THE CARBOXY-TAIL OF CHEMOKINE RECEPTOR CXCR4.BLOOD. VOL. 120. ISSUE 1. P. 181 -189 20 44% 16
8 BALABANIAN, K , BROTIN, E , BIAJOUX, V , BOUCHET-DELBOS, L , LAINEY, E , FENNETEAU, O , BONNET, D , FIETTE, L , EMILIE, D , BACHELERIE, F , (2012) PROPER DESENSITIZATION OF CXCR4 IS REQUIRED FOR LYMPHOCYTE DEVELOPMENT AND PERIPHERAL COMPARTMENTALIZATION IN MICE.BLOOD. VOL. 119. ISSUE 24. P. 5722-5730 20 43% 19
9 DIAZ, GA , GULINO, AV , (2005) WHIM SYNDROME: A DEFECT IN CXCR4 SIGNALING.CURRENT ALLERGY AND ASTHMA REPORTS. VOL. 5. ISSUE 5. P. 350-355 18 53% 34
10 STRYDOM, N , RANKIN, SM , (2013) REGULATION OF CIRCULATING NEUTROPHIL NUMBERS UNDER HOMEOSTASIS AND IN DISEASE.JOURNAL OF INNATE IMMUNITY. VOL. 5. ISSUE 4. P. 304-314 19 37% 26

Classes with closest relation at Level 1



Rank Class id link
1 9288 SEVERE CONGENITAL NEUTROPENIA//CYCLIC NEUTROPENIA//CONGENITAL NEUTROPENIA
2 1531 CXCR4//CXCL12//CXCR7
3 21472 NEUTROPHIL MARGINATION//PULMONARY MICROCIRCULATION//BRONCHIAL TEMPERATURE
4 28787 IDIOPATHIC CD4 T LYMPHOCYTOPENIA//IDIOPATHIC CD4 LYMPHOCYTOPENIA//CD4 LYMPHOCYTOPENIA
5 10814 NEUTROPHILS//POLYMORPHONUCLEAR NEUTROPHIL PMN//NEONATOLEDWARD A DOISY
6 36082 FAILURE OF NEUTROPHIL MIGRATION//NEUTROPHIL MIGRATION FAILURE//NEUTROPHIL MIGRATION INHIBITION
7 3997 HEMATOPOIETIC STEM CELLS//SAKAGUCHI DEV BIOL//RUTH L DAVID S GOTTESMAN STEM CELL REGEN
8 13330 NEUTROPHIL EXTRACELLULAR TRAPS//NETOSIS//NEUTROPHIL EXTRACELLULAR TRAPS NETS
9 15024 FIBROBLASTIC RETICULAR CELLS//INTRAVITAL IMAGING//LYMPHOCYTE BIOL SECT
10 14203 GATA 1//GATA2//EDAG

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