Class information for:
Level 1: SEVERE CONGENITAL NEUTROPENIA//CYCLIC NEUTROPENIA//CONGENITAL NEUTROPENIA

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
9288 1170 34.3 73%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
535 3       TAURINE//CHRONIC GRANULOMATOUS DISEASE//L FORMS 19480
2683 2             NEUTROPHIL EXTRACELLULAR TRAPS//SEVERE CONGENITAL NEUTROPENIA//NETOSIS 3378
9288 1                   SEVERE CONGENITAL NEUTROPENIA//CYCLIC NEUTROPENIA//CONGENITAL NEUTROPENIA 1170

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SEVERE CONGENITAL NEUTROPENIA authKW 2489848 9% 89% 107
2 CYCLIC NEUTROPENIA authKW 852132 3% 82% 40
3 CONGENITAL NEUTROPENIA authKW 603933 3% 64% 36
4 KOSTMANN SYNDROME authKW 601756 2% 82% 28
5 AUTOIMMUNE NEUTROPENIA authKW 533203 3% 55% 37
6 HAX 1 authKW 484888 2% 77% 24
7 HAX1 authKW 460166 2% 77% 23
8 CHRONIC IDIOPATHIC NEUTROPENIA authKW 453856 2% 87% 20
9 G6PC3 authKW 384331 2% 82% 18
10 ELANE authKW 365358 1% 100% 14

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 24493 44% 0% 515
2 Pediatrics 2306 16% 0% 187
3 Oncology 403 12% 0% 135
4 Immunology 285 9% 0% 108
5 Medicine, Research & Experimental 266 7% 0% 79
6 Medicine, General & Internal 183 7% 0% 87
7 Cell Biology 156 8% 0% 93
8 Allergy 108 2% 0% 19
9 Dentistry, Oral Surgery & Medicine 88 3% 0% 32
10 Biochemistry & Molecular Biology 66 11% 0% 130

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SEVERE CHRON NEUTROPENIA INT REGISTRY 117433 1% 75% 6
2 UNIV CRETE 83509 0% 80% 4
3 MOL HEMATOPOIESIS 72250 1% 23% 12
4 MOFID PEDIAT HOSP 52194 0% 100% 2
5 SCNIR 52194 0% 100% 2
6 ABT MOL HAMATOPOESE 34795 0% 67% 2
7 G SALESI WOMENS CHILDRENS HOSP 34795 0% 67% 2
8 SECT PEDIAT LEUKEMIA LYMPHOMA 34795 0% 67% 2
9 3495 BAILEY AVE 26097 0% 100% 1
10 AFFILIATED ZOUPING HOSP 26097 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 BLOOD 11803 11% 0% 125
2 BRITISH JOURNAL OF HAEMATOLOGY 8120 6% 0% 65
3 CURRENT OPINION IN HEMATOLOGY 4447 1% 1% 14
4 AMERICAN JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY 4429 1% 1% 13
5 AMERICAN JOURNAL OF HEMATOLOGY 3913 3% 1% 30
6 ANNALS OF HEMATOLOGY 3409 2% 1% 22
7 JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY 2569 2% 1% 19
8 INTERNATIONAL JOURNAL OF PEDIATRIC HEMATOLOGY/ONCOLOGY 2194 0% 2% 5
9 ACTA HAEMATOLOGICA 2163 1% 0% 17
10 PEDIATRIC BLOOD & CANCER 1842 2% 0% 18

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 SEVERE CONGENITAL NEUTROPENIA 2489848 9% 89% 107 Search SEVERE+CONGENITAL+NEUTROPENIA Search SEVERE+CONGENITAL+NEUTROPENIA
2 CYCLIC NEUTROPENIA 852132 3% 82% 40 Search CYCLIC+NEUTROPENIA Search CYCLIC+NEUTROPENIA
3 CONGENITAL NEUTROPENIA 603933 3% 64% 36 Search CONGENITAL+NEUTROPENIA Search CONGENITAL+NEUTROPENIA
4 KOSTMANN SYNDROME 601756 2% 82% 28 Search KOSTMANN+SYNDROME Search KOSTMANN+SYNDROME
5 AUTOIMMUNE NEUTROPENIA 533203 3% 55% 37 Search AUTOIMMUNE+NEUTROPENIA Search AUTOIMMUNE+NEUTROPENIA
6 HAX 1 484888 2% 77% 24 Search HAX+1 Search HAX+1
7 HAX1 460166 2% 77% 23 Search HAX1 Search HAX1
8 CHRONIC IDIOPATHIC NEUTROPENIA 453856 2% 87% 20 Search CHRONIC+IDIOPATHIC+NEUTROPENIA Search CHRONIC+IDIOPATHIC+NEUTROPENIA
9 G6PC3 384331 2% 82% 18 Search G6PC3 Search G6PC3
10 ELANE 365358 1% 100% 14 Search ELANE Search ELANE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 ZEIDLER, C , GERMESHAUSEN, M , KLEIN, C , WELTE, K , (2009) CLINICAL IMPLICATIONS OF ELA2-, HAX1-, AND G-CSF-RECEPTOR (CSF3R) MUTATIONS IN SEVERE CONGENITAL NEUTROPENIA.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 144. ISSUE 4. P. 459 -467 52 95% 45
2 TOUW, IP , (2015) GAME OF CLONES: THE GENOMIC EVOLUTION OF SEVERE CONGENITAL NEUTROPENIA.HEMATOLOGY-AMERICAN SOCIETY OF HEMATOLOGY EDUCATION PROGRAM. VOL. . ISSUE . P. 1 -7 47 94% 3
3 GERMESHAUSEN, M , BALLMAIER, M , WELTE, K , (2007) INCIDENCE OF CSF3R MUTATIONS IN SEVERE CONGENITAL NEUTROPENIA AND RELEVANCE FOR LEUKEMOGENESIS: RESULTS OF A LONG-TERM SURVEY.BLOOD. VOL. 109. ISSUE 1. P. 93-99 49 96% 92
4 WARD, AC , (2007) THE ROLE OF THE GRANULOCYTE COLONY-STIMULATING FACTOR RECEPTOR (G-CSF-R) IN DISEASE.FRONTIERS IN BIOSCIENCE-LANDMARK. VOL. 12. ISSUE . P. 608-618 73 74% 15
5 WELTE, K , ZEIDLER, C , (2009) SEVERE CONGENITAL NEUTROPENIA.HEMATOLOGY-ONCOLOGY CLINICS OF NORTH AMERICA. VOL. 23. ISSUE 2. P. 307-+ 51 85% 19
6 CONNELLY, JA , CHOI, SW , LEVINE, JE , (2012) HEMATOPOIETIC STEM CELL TRANSPLANTATION FOR SEVERE CONGENITAL NEUTROPENIA.CURRENT OPINION IN HEMATOLOGY. VOL. 19. ISSUE 1. P. 44-51 41 89% 13
7 SKOKOWA, J , GERMESHAUSEN, M , ZEIDLER, C , WELTE, K , (2007) SEVERE CONGENITAL NEUTROPENIA: INHERITANCE AND PATHOPHYSIOLOGY.CURRENT OPINION IN HEMATOLOGY. VOL. 14. ISSUE 1. P. 22-28 39 93% 31
8 PAPADAKI, HA , PONTIKOGLOU, C , (2008) PATHOPHYSIOLOGIC MECHANISMS, CLINICAL FEATURES AND TREATMENT OF IDIOPATHIC NEUTROPENIA.EXPERT REVIEW OF HEMATOLOGY. VOL. 1. ISSUE 2. P. 217-229 60 62% 6
9 VAN DE VOSSE, E , VERHARD, EM , TOOL, AJT , DE VISSER, AW , KUIJPERS, TW , HIEMSTRA, PS , VAN DISSEL, JT , (2011) SEVERE CONGENITAL NEUTROPENIA IN A MULTIGENERATIONAL FAMILY WITH A NOVEL NEUTROPHIL ELASTASE (ELANE) MUTATION.ANNALS OF HEMATOLOGY. VOL. 90. ISSUE 2. P. 151-158 39 89% 2
10 PALMBLAD, J , PAPADAKI, HA , (2008) CHRONIC IDIOPATHIC NEUTROPENIAS AND SEVERE CONGENITAL NEUTROPENIA.CURRENT OPINION IN HEMATOLOGY. VOL. 15. ISSUE 1. P. 8-14 40 89% 10

Classes with closest relation at Level 1



Rank Class id link
1 32925 MYELOKATHEXIS//WHIM SYNDROME//INSERM UMR S996
2 20937 CYCLIC THROMBOCYTOPENIA//CYCLICAL NEUTROPENIA//ACQUIRED AMEGAKARYOCYTIC THROMBOCYTOPENIA
3 24980 FELTYS SYNDROME//ANTINEUTROPHIL CYTOPLASMIC ANTIBODY ASSOCIATED SYSTEMIC VASCULITIS//ASYMPTOMATIC FELTYS SYNDROME
4 30554 GFI1B//GFI1//ZELLBIOL TUMORFOR
5 2206 G CSF//GM CSF//GRANULOCYTE COLONY STIMULATING FACTOR
6 13443 TRALI//TRANSFUSION RELATED ACUTE LUNG INJURY//HUMAN NEUTROPHIL ANTIGENS
7 19077 SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME
8 25338 GRANULOCYTE COLONY STIMULATING FACTOR//HYPOXIA ISCHEMIA HI//G CSF
9 19697 4C4//BLOOD LITHIUM//REPROD ENDOCRINE PHYSIOL
10 13304 CORD BLOOD NEUTROPHILS//INFECTION DRUG THERAPY MORTALITY//MED HOWARD HUGHES S

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