Class information for:
Level 1: EPIDERMOLYSIS BULLOSA//DYSTROPHIC EPIDERMOLYSIS BULLOSA//COL7A1

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
4696 1742 28.4 71%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
336 3       DERMATOLOGY//BEHCETS DISEASE//DERMATOL 37504
861 2             EPIDERMOLYSIS BULLOSA//INTERMEDIATE FILAMENTS//KERATIN 11606
4696 1                   EPIDERMOLYSIS BULLOSA//DYSTROPHIC EPIDERMOLYSIS BULLOSA//COL7A1 1742

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 EPIDERMOLYSIS BULLOSA authKW 3634347 17% 71% 293
2 DYSTROPHIC EPIDERMOLYSIS BULLOSA authKW 1036525 4% 95% 62
3 COL7A1 authKW 702677 2% 95% 42
4 PYLORIC ATRESIA authKW 527260 2% 79% 38
5 TYPE VII COLLAGEN authKW 525895 4% 49% 61
6 RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA authKW 481239 2% 89% 31
7 ANCHORING FIBRILS authKW 412877 2% 67% 35
8 EPIDERMOLYSIS BULLOSA DYSTROPHICA authKW 353461 1% 92% 22
9 JUNCTIONAL EPIDERMOLYSIS BULLOSA authKW 327155 2% 67% 28
10 INHERITED EPIDERMOLYSIS BULLOSA authKW 192799 1% 100% 11

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 87026 53% 1% 931
2 Pediatrics 1577 11% 0% 195
3 Genetics & Heredity 475 8% 0% 143
4 Medicine, Research & Experimental 256 6% 0% 99
5 Pathology 193 4% 0% 64
6 Anesthesiology 155 2% 0% 37
7 Cell & Tissue Engineering 141 1% 0% 16
8 Dentistry, Oral Surgery & Medicine 120 3% 0% 46
9 Surgery 59 6% 0% 96
10 Veterinary Sciences 37 3% 0% 48

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JEFFERSON MOL MED 160578 3% 20% 47
2 ST JOHNS DERMATOL 127466 6% 7% 104
3 EPIDERMOLYSIS BULLOSA REGISTRY 124636 0% 89% 8
4 DERMATOL CUTANEOUS BIOL 123801 4% 10% 68
5 GENET SKIN DIS GRP 84336 1% 25% 19
6 ROBIN EADY DIAGNOST EPIDERMOLYSIS BULLOSA LA 78071 0% 64% 7
7 EPIDERMOLYSIS BULLOSA 70109 0% 100% 4
8 DERMATOL 54378 32% 1% 550
9 BLISTERING DIS 36154 1% 14% 15
10 CINCINNATI CHILDRENS EPIDERMOLYSIS BULLOSA 35054 0% 100% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF INVESTIGATIVE DERMATOLOGY 40970 9% 2% 157
2 DERMATOLOGIC CLINICS 35170 4% 3% 66
3 BRITISH JOURNAL OF DERMATOLOGY 22069 7% 1% 118
4 PEDIATRIC DERMATOLOGY 13271 3% 1% 53
5 ARCHIVES OF DERMATOLOGY 12688 4% 1% 67
6 EXPERIMENTAL DERMATOLOGY 9131 2% 1% 37
7 CLINICAL AND EXPERIMENTAL DERMATOLOGY 6788 3% 1% 44
8 JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY 3522 3% 0% 50
9 JOURNAL OF DERMATOLOGICAL SCIENCE 3097 1% 1% 18
10 INTERNATIONAL JOURNAL OF DERMATOLOGY 3064 2% 0% 36

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 EPIDERMOLYSIS BULLOSA 3634347 17% 71% 293 Search EPIDERMOLYSIS+BULLOSA Search EPIDERMOLYSIS+BULLOSA
2 DYSTROPHIC EPIDERMOLYSIS BULLOSA 1036525 4% 95% 62 Search DYSTROPHIC+EPIDERMOLYSIS+BULLOSA Search DYSTROPHIC+EPIDERMOLYSIS+BULLOSA
3 COL7A1 702677 2% 95% 42 Search COL7A1 Search COL7A1
4 PYLORIC ATRESIA 527260 2% 79% 38 Search PYLORIC+ATRESIA Search PYLORIC+ATRESIA
5 TYPE VII COLLAGEN 525895 4% 49% 61 Search TYPE+VII+COLLAGEN Search TYPE+VII+COLLAGEN
6 RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA 481239 2% 89% 31 Search RECESSIVE+DYSTROPHIC+EPIDERMOLYSIS+BULLOSA Search RECESSIVE+DYSTROPHIC+EPIDERMOLYSIS+BULLOSA
7 ANCHORING FIBRILS 412877 2% 67% 35 Search ANCHORING+FIBRILS Search ANCHORING+FIBRILS
8 EPIDERMOLYSIS BULLOSA DYSTROPHICA 353461 1% 92% 22 Search EPIDERMOLYSIS+BULLOSA+DYSTROPHICA Search EPIDERMOLYSIS+BULLOSA+DYSTROPHICA
9 JUNCTIONAL EPIDERMOLYSIS BULLOSA 327155 2% 67% 28 Search JUNCTIONAL+EPIDERMOLYSIS+BULLOSA Search JUNCTIONAL+EPIDERMOLYSIS+BULLOSA
10 INHERITED EPIDERMOLYSIS BULLOSA 192799 1% 100% 11 Search INHERITED+EPIDERMOLYSIS+BULLOSA Search INHERITED+EPIDERMOLYSIS+BULLOSA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 FINE, JD , MELLERIO, JE , (2009) EXTRACUTANEOUS MANIFESTATIONS AND COMPLICATIONS OF INHERITED EPIDERMOLYSIS BULLOSA PART I. EPITHELIAL ASSOCIATED TISSUES.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 61. ISSUE 3. P. 367 -384 99 80% 55
2 EL HACHEM, M , ZAMBRUNO, G , BOURDON-LANOY, E , CIASULLI, A , BUISSON, C , HADJ-RABIA, S , DIOCIAIUTI, A , GOUVEIA, CF , HERNANDEZ-MARTIN, A , LAGUNA, RD , ET AL (2014) MULTICENTRE CONSENSUS RECOMMENDATIONS FOR SKIN CARE IN INHERITED EPIDERMOLYSIS BULLOSA.ORPHANET JOURNAL OF RARE DISEASES. VOL. 9. ISSUE . P. - 76 87% 8
3 MEDEIROS, GX , RIET-CORREA, F , (2015) EPIDERMOLYSIS BULLOSA IN ANIMALS: A REVIEW.VETERINARY DERMATOLOGY. VOL. 26. ISSUE 1. P. 3 -+ 62 84% 5
4 VARKI, R , SADOWSKI, S , UITTO, J , PFENDNER, E , (2007) EPIDERMOLYSIS BULLOSA. II. TYPE VII COLLAGEN MUTATIONS AND PHENOTYPE-GENOTYPE CORRELATIONS IN THE DYSTROPHIC SUBTYPES.JOURNAL OF MEDICAL GENETICS. VOL. 44. ISSUE 3. P. 181-192 58 94% 94
5 DANG, NN , MURRELL, DF , (2008) MUTATION ANALYSIS AND CHARACTERIZATION OF COL7A1 MUTATIONS IN DYSTROPHIC EPIDERMOLYSIS BULLOSA.EXPERIMENTAL DERMATOLOGY. VOL. 17. ISSUE 7. P. 553-568 56 93% 83
6 MELLERIO, JE , FINE, JD , GEORGE, R , GOLDBERG, D , HALMOS, GB , HARRIES, M , JONKMAN, MF , LUCKY, A , MARTINEZ, AE , MAUBEC, E , ET AL (2016) MANAGEMENT OF CUTANEOUS SQUAMOUS CELL CARCINOMA IN PATIENTS WITH EPIDERMOLYSIS BULLOSA: BEST CLINICAL PRACTICE GUIDELINES.BRITISH JOURNAL OF DERMATOLOGY. VOL. 174. ISSUE 1. P. 56 -67 44 79% 6
7 MURAT-SUSIC, S , HUSAR, K , SKERLEV, M , MARINOVIC, B , BABIC, I , (2011) INHERITED EPIDERMOLYSIS BULLOSA - THE SPECTRUM OF COMPLICATIONS.ACTA DERMATOVENEROLOGICA CROATICA. VOL. 19. ISSUE 4. P. 255-263 55 96% 5
8 HAS, C , BRUCKNER-TUDERMAN, L , (2014) THE GENETICS OF SKIN FRAGILITY.ANNUAL REVIEW OF GENOMICS AND HUMAN GENETICS, VOL 15. VOL. 15. ISSUE . P. 245 -268 68 61% 10
9 RAMIREZ, MN , MURRELL, DF , FINE, JD , (2013) MANAGEMENT OF EPIDERMOLYSIS BULLOSA.EXPERT OPINION ON ORPHAN DRUGS. VOL. 1. ISSUE 4. P. 279 -293 59 77% 1
10 FINE, JD , MELLERIO, JE , (2009) EXTRACUTANEOUS MANIFESTATIONS AND COMPLICATIONS OF INHERITED EPIDERMOLYSIS BULLOSA PART II. OTHER ORGANS.JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY. VOL. 61. ISSUE 3. P. 387 -402 56 74% 49

Classes with closest relation at Level 1



Rank Class id link
1 20731 PLECTIN//PLAKIN//DYSTONIN
2 8104 PACHYONYCHIA CONGENITA//EPIDERMOLYSIS BULLOSA SIMPLEX//EPIDERMOLYTIC HYPERKERATOSIS
3 22520 SKIN GENE THERAPY//MOUSE GROWTH HORMONE//LITTLE MICE
4 971 BULLOUS PEMPHIGOID//EPIDERMOLYSIS BULLOSA ACQUISITA//CICATRICIAL PEMPHIGOID
5 14100 SJOGREN LARSSON SYNDROME//LAMELLAR ICHTHYOSIS//HARLEQUIN ICHTHYOSIS
6 36200 ACRAL PEELING SKIN SYNDROME//KERATOLYTIC WINTER ERYTHEMA//PEELING SKIN SYNDROME
7 2796 LAMININ//BASEMENT MEMBRANE//LAMININ 5
8 37384 KERATOSIS LICHENOIDES CHRONICA//LICHEN MONILIFORMIS//LICHEN RUBER ACUMINATUS VERRUCOSUS ET RETICULARIS
9 19553 APLASIA CUTIS CONGENITA//ADAMS OLIVER SYNDROME//CUTIS MARMORATA TELANGIECTATICA CONGENITA
10 34185 FLIGHTLESS I//TTYH1//TTYH2

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