Class information for:
Level 1: PACHYONYCHIA CONGENITA//EPIDERMOLYSIS BULLOSA SIMPLEX//EPIDERMOLYTIC HYPERKERATOSIS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
8104 1292 39.3 81%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
336 3       DERMATOLOGY//BEHCETS DISEASE//DERMATOL 37504
861 2             EPIDERMOLYSIS BULLOSA//INTERMEDIATE FILAMENTS//KERATIN 11606
8104 1                   PACHYONYCHIA CONGENITA//EPIDERMOLYSIS BULLOSA SIMPLEX//EPIDERMOLYTIC HYPERKERATOSIS 1292

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PACHYONYCHIA CONGENITA authKW 1067629 4% 94% 48
2 EPIDERMOLYSIS BULLOSA SIMPLEX authKW 947894 4% 70% 57
3 EPIDERMOLYTIC HYPERKERATOSIS authKW 879844 3% 85% 44
4 KERATIN authKW 519484 14% 12% 185
5 EPIDERMOLYTIC PALMOPLANTAR KERATODERMA authKW 401753 1% 100% 17
6 EPITHELIAL GENET GRP address 363034 3% 39% 39
7 INTERMEDIATE FILAMENTS authKW 338379 11% 10% 147
8 KERATIN 9 authKW 332331 1% 94% 15
9 GENODERMATOSIS authKW 261939 4% 21% 54
10 ICHTHYOSIS BULLOSA OF SIEMENS authKW 236325 1% 100% 10

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Dermatology 41483 43% 0% 555
2 Cell Biology 2598 24% 0% 311
3 Genetics & Heredity 352 8% 0% 106
4 Pathology 140 4% 0% 47
5 Gastroenterology & Hepatology 133 4% 0% 50
6 Biochemistry & Molecular Biology 111 12% 0% 160
7 Ophthalmology 64 3% 0% 33
8 Developmental Biology 49 2% 0% 21
9 Medicine, Research & Experimental 38 3% 0% 42
10 Oncology 37 5% 0% 65

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 EPITHELIAL GENET GRP 363034 3% 39% 39
2 CANC UK CELL STRUCT GRP 181530 1% 59% 13
3 ABT ZELLBIOCHEM 133115 1% 43% 13
4 BONNER FORUM BIOMED 124155 1% 31% 17
5 CRC CELL STRUCT GRP 75623 0% 80% 4
6 CRUK CELL STRUCT GRP 70898 0% 100% 3
7 MOL CELLULAR ANAT 51987 1% 12% 19
8 DERMATOL GENET MED 50266 1% 21% 10
9 BONNER FORUM BIOMED LIMES 47265 0% 100% 2
10 CANC CAMPAIGN CELL STRUCT GRP 47265 0% 100% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF INVESTIGATIVE DERMATOLOGY 40281 10% 1% 134
2 BRITISH JOURNAL OF DERMATOLOGY 8719 5% 1% 64
3 EXPERIMENTAL DERMATOLOGY 8099 2% 1% 30
4 CLINICAL AND EXPERIMENTAL DERMATOLOGY 4839 2% 1% 32
5 JOURNAL OF INVESTIGATIVE DERMATOLOGY SYMPOSIUM PROCEEDINGS 4696 1% 2% 8
6 JOURNAL OF CELL BIOLOGY 4101 4% 0% 53
7 PEDIATRIC DERMATOLOGY 3963 2% 1% 25
8 EUROPEAN JOURNAL OF DERMATOLOGY 2860 1% 1% 18
9 JOURNAL OF DERMATOLOGICAL SCIENCE 2527 1% 1% 14
10 JOURNAL OF CELL SCIENCE 2295 3% 0% 36

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 PACHYONYCHIA CONGENITA 1067629 4% 94% 48 Search PACHYONYCHIA+CONGENITA Search PACHYONYCHIA+CONGENITA
2 EPIDERMOLYSIS BULLOSA SIMPLEX 947894 4% 70% 57 Search EPIDERMOLYSIS+BULLOSA+SIMPLEX Search EPIDERMOLYSIS+BULLOSA+SIMPLEX
3 EPIDERMOLYTIC HYPERKERATOSIS 879844 3% 85% 44 Search EPIDERMOLYTIC+HYPERKERATOSIS Search EPIDERMOLYTIC+HYPERKERATOSIS
4 KERATIN 519484 14% 12% 185 Search KERATIN Search KERATIN
5 EPIDERMOLYTIC PALMOPLANTAR KERATODERMA 401753 1% 100% 17 Search EPIDERMOLYTIC+PALMOPLANTAR+KERATODERMA Search EPIDERMOLYTIC+PALMOPLANTAR+KERATODERMA
6 INTERMEDIATE FILAMENTS 338379 11% 10% 147 Search INTERMEDIATE+FILAMENTS Search INTERMEDIATE+FILAMENTS
7 KERATIN 9 332331 1% 94% 15 Search KERATIN+9 Search KERATIN+9
8 GENODERMATOSIS 261939 4% 21% 54 Search GENODERMATOSIS Search GENODERMATOSIS
9 ICHTHYOSIS BULLOSA OF SIEMENS 236325 1% 100% 10 Search ICHTHYOSIS+BULLOSA+OF+SIEMENS Search ICHTHYOSIS+BULLOSA+OF+SIEMENS
10 BULLOUS CONGENITAL ICHTHYOSIFORM ERYTHRODERMA 219961 1% 85% 11 Search BULLOUS+CONGENITAL+ICHTHYOSIFORM+ERYTHRODERMA Search BULLOUS+CONGENITAL+ICHTHYOSIFORM+ERYTHRODERMA

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 CHAMCHEU, JC , SIDDIQUI, IA , SYED, DN , ADHAMI, VM , LIOVIC, M , MUKHTAR, H , (2011) KERATIN GENE MUTATIONS IN DISORDERS OF HUMAN SKIN AND ITS APPENDAGES.ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS. VOL. 508. ISSUE 2. P. 123 -137 94 68% 56
2 SMITH, FJD , (2003) THE MOLECULAR GENETICS OF KERATIN DISORDERS.AMERICAN JOURNAL OF CLINICAL DERMATOLOGY. VOL. 4. ISSUE 5. P. 347-364 105 80% 81
3 ARIN, MJ , (2009) THE MOLECULAR BASIS OF HUMAN KERATIN DISORDERS.HUMAN GENETICS. VOL. 125. ISSUE 4. P. 355-373 99 74% 24
4 PAN, XO , HOBBS, RP , COULOMBE, PA , (2013) THE EXPANDING SIGNIFICANCE OF KERATIN INTERMEDIATE FILAMENTS IN NORMAL AND DISEASED EPITHELIA.CURRENT OPINION IN CELL BIOLOGY. VOL. 25. ISSUE 1. P. 47 -56 70 71% 60
5 STRNAD, P , GULDIKEN, N , HELENIUS, TO , MISIOREK, JO , NYSTROM, JH , LAHDENIEMI, IAK , SILVANDER, JSG , KUSCUOGLU, D , TOIVOLA, DM , (2016) SIMPLE EPITHELIAL KERATINS.INTERMEDIATE FILAMENT PROTEINS. VOL. 568. ISSUE . P. 351 -388 87 66% 0
6 COULOMBE, PA , LEE, CH , (2012) DEFINING KERATIN PROTEIN FUNCTION IN SKIN EPITHELIA: EPIDERMOLYSIS BULLOSA SIMPLEX AND ITS AFTERMATH.JOURNAL OF INVESTIGATIVE DERMATOLOGY. VOL. 132. ISSUE 3. P. 763-775 80 66% 33
7 PORTER, RM , LANE, EB , (2003) PHENOTYPES, GENOTYPES AND THEIR CONTRIBUTION TO UNDERSTANDING KERATIN FUNCTION.TRENDS IN GENETICS. VOL. 19. ISSUE 5. P. 278-285 65 93% 108
8 KIRFEL, J , MAGIN, TM , REICHELT, J , (2003) KERATINS: A STRUCTURAL SCAFFOLD WITH EMERGING FUNCTIONS.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 60. ISSUE 1. P. 56-71 92 59% 99
9 KARANTZA, V , (2011) KERATINS IN HEALTH AND CANCER: MORE THAN MERE EPITHELIAL CELL MARKERS.ONCOGENE. VOL. 30. ISSUE 2. P. 127 -138 70 50% 97
10 TAKAHASHI, K , COULOMBE, PA , MIYACHI, Y , (1999) USING TRANSGENIC MODELS TO STUDY THE PATHOGENESIS OF KERATIN-BASED INHERITED SKIN DISEASES.JOURNAL OF DERMATOLOGICAL SCIENCE. VOL. 21. ISSUE 2. P. 73 -95 88 73% 11

Classes with closest relation at Level 1



Rank Class id link
1 3411 INTERMEDIATE FILAMENTS//VIMENTIN//SYNEMIN
2 29102 M65//M30//CYTOKERATIN 18
3 24159 FAT10//MALLORY BODIES//MALLORY DENK BODIES MDBS
4 14769 KID SYNDROME//MAL DE MELEDA//PALMOPLANTAR KERATODERMA
5 20731 PLECTIN//PLAKIN//DYSTONIN
6 4696 EPIDERMOLYSIS BULLOSA//DYSTROPHIC EPIDERMOLYSIS BULLOSA//COL7A1
7 14100 SJOGREN LARSSON SYNDROME//LAMELLAR ICHTHYOSIS//HARLEQUIN ICHTHYOSIS
8 5837 CYTOKERATIN//KERATIN//HAMSTER CHEEK POUCH EPITHELIUM
9 9187 MONILETHRIX//HAIRLESS GENE//ATRICHIA
10 24594 DYSCHROMATOSIS SYMMETRICA HEREDITARIA//DOWLING DEGOS DISEASE//DSRAD GENE

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