Class information for:
Level 2: AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//POLYCYSTIC KIDNEY DISEASE//ADPKD

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
2024 5429 31.7 74%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
642 3       POLYCYSTIC KIDNEY DISEASE//AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//HEDGEHOG 12305
2024 2             AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//POLYCYSTIC KIDNEY DISEASE//ADPKD 5429
657 1                   AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE//POLYCYSTIC KIDNEY DISEASE//ADPKD 3203
9164 1                   POLYCYSTIC LIVER DISEASE//LIVER CYSTS//HEPATIC CYST 1182
16565 1                   CAROLIS DISEASE//VON MEYENBURG COMPLEX//BILE DUCT HAMARTOMA 647
22007 1                   PERIRENAL PSEUDOCYST//GLOMERULOCYSTIC KIDNEY DISEASE//JUVENILE NEPHROPATHY 397

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE authKW 1741500 7% 80% 388
2 POLYCYSTIC KIDNEY DISEASE authKW 1599299 9% 61% 465
3 ADPKD authKW 1146309 4% 84% 244
4 POLYCYSTIC LIVER DISEASE authKW 519753 2% 89% 104
5 PKD1 authKW 413372 2% 74% 100
6 AUTOSOMAL RECESSIVE POLYCYSTIC KIDNEY DISEASE authKW 359376 1% 85% 75
7 PKD2 authKW 350872 1% 79% 79
8 CAROLIS DISEASE authKW 347978 1% 76% 81
9 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE ADPKD authKW 327960 1% 83% 70
10 LIVER CYSTS authKW 322499 2% 59% 97

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Urology & Nephrology 52191 29% 1% 1565
2 Gastroenterology & Hepatology 8614 13% 0% 687
3 Pathology 3085 7% 0% 399
4 Transplantation 2251 5% 0% 250
5 Surgery 1678 11% 0% 622
6 Radiology, Nuclear Medicine & Medical Imaging 1277 7% 0% 388
7 Genetics & Heredity 1230 8% 0% 414
8 Veterinary Sciences 1054 6% 0% 324
9 Medicine, General & Internal 737 7% 0% 383
10 Pediatrics 645 5% 0% 259

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 KHA CARI GUIDELINES 67471 0% 100% 12
2 KIDNEY GENET GRP 64820 0% 82% 14
3 RAINBOW CHILDHOOD PKD 54993 0% 65% 15
4 EDUC ANIM MODELS HUMAN DIS 52402 0% 55% 17
5 WESTERN SYDNEY LOCAL HLTH DIST 44069 0% 56% 14
6 GENET TRANSLAT MED 41302 0% 57% 13
7 SHIMIZU KU 39739 1% 14% 49
8 ADPKD 33735 0% 100% 6
9 CHRON DIS CKD 33735 0% 100% 6
10 NEPHROL 33633 11% 1% 622

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY 37277 4% 3% 220
2 KIDNEY INTERNATIONAL 17826 4% 2% 216
3 AMERICAN JOURNAL OF KIDNEY DISEASES 12641 3% 2% 139
4 NEPHROLOGY DIALYSIS TRANSPLANTATION 7845 2% 1% 133
5 AMERICAN JOURNAL OF PHYSIOLOGY-RENAL PHYSIOLOGY 7267 2% 1% 93
6 CLINICAL JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY 6028 1% 2% 55
7 PEDIATRIC NEPHROLOGY 4695 1% 1% 72
8 SEMINARS IN NEPHROLOGY 3328 1% 2% 34
9 BMC NEPHROLOGY 3145 0% 2% 27
10 INTERNATIONAL JOURNAL OF CLINICAL AND EXPERIMENTAL PATHOLOGY 2709 1% 1% 53

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE 1741500 7% 80% 388 Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE
2 POLYCYSTIC KIDNEY DISEASE 1599299 9% 61% 465 Search POLYCYSTIC+KIDNEY+DISEASE Search POLYCYSTIC+KIDNEY+DISEASE
3 ADPKD 1146309 4% 84% 244 Search ADPKD Search ADPKD
4 POLYCYSTIC LIVER DISEASE 519753 2% 89% 104 Search POLYCYSTIC+LIVER+DISEASE Search POLYCYSTIC+LIVER+DISEASE
5 PKD1 413372 2% 74% 100 Search PKD1 Search PKD1
6 AUTOSOMAL RECESSIVE POLYCYSTIC KIDNEY DISEASE 359376 1% 85% 75 Search AUTOSOMAL+RECESSIVE+POLYCYSTIC+KIDNEY+DISEASE Search AUTOSOMAL+RECESSIVE+POLYCYSTIC+KIDNEY+DISEASE
7 PKD2 350872 1% 79% 79 Search PKD2 Search PKD2
8 CAROLIS DISEASE 347978 1% 76% 81 Search CAROLIS+DISEASE Search CAROLIS+DISEASE
9 AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE ADPKD 327960 1% 83% 70 Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE+ADPKD Search AUTOSOMAL+DOMINANT+POLYCYSTIC+KIDNEY+DISEASE+ADPKD
10 LIVER CYSTS 322499 2% 59% 97 Search LIVER+CYSTS Search LIVER+CYSTS

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 TORRES, VE , HARRIS, PC , PIRSON, Y , (2007) AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE.LANCET. VOL. 369. ISSUE 9569. P. 1287 -1301 165 87% 361
2 HAPPE, H , PETERS, DJM , (2014) TRANSLATIONAL RESEARCH IN ADPKD: LESSONS FROM ANIMAL MODELS.NATURE REVIEWS NEPHROLOGY. VOL. 10. ISSUE 10. P. 587 -601 148 83% 10
3 CHEBIB, FT , SUSSMAN, CR , WANG, XF , HARRIS, PC , TORRES, VE , (2015) VASOPRESSIN AND DISRUPTION OF CALCIUM SIGNALLING IN POLYCYSTIC KIDNEY DISEASE.NATURE REVIEWS NEPHROLOGY. VOL. 11. ISSUE 8. P. 451 -464 137 76% 15
4 CALVET, JP , GRANTHAM, JJ , (2001) THE GENETICS AND PHYSIOLOGY OF POLYCYSTIC KIDNEY DISEASE.SEMINARS IN NEPHROLOGY. VOL. 21. ISSUE 2. P. 107 -123 182 88% 106
5 TORRES, VE , HARRIS, PC , (2009) AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE: THE LAST 3 YEARS.KIDNEY INTERNATIONAL. VOL. 76. ISSUE 2. P. 149 -168 126 77% 221
6 ONG, ACM , HARRIS, PC , (2015) A POLYCYSTIN-CENTRIC VIEW OF CYST FORMATION AND DISEASE: THE POLYCYSTINS REVISITED.KIDNEY INTERNATIONAL. VOL. 88. ISSUE 4. P. 699 -710 137 73% 15
7 SAIGUSA, T , BELL, PD , (2015) MOLECULAR PATHWAYS AND THERAPIES IN AUTOSOMAL-DOMINANT POLYCYSTIC KIDNEY DISEASE.PHYSIOLOGY. VOL. 30. ISSUE 3. P. 195 -207 133 86% 5
8 HORIE, S , MOCHIZUKI, T , MUTO, S , HANAOKA, K , FUKUSHIMA, Y , NARITA, I , NUTAHARA, K , TSUCHIYA, K , TSURUYA, K , KAMURA, K , ET AL (2016) EVIDENCE-BASED CLINICAL PRACTICE GUIDELINES FOR POLYCYSTIC KIDNEY DISEASE 2014.CLINICAL AND EXPERIMENTAL NEPHROLOGY. VOL. 20. ISSUE 4. P. 493 -509 152 78% 0
9 MEKAHLI, D , PARYS, JB , BULTYNCK, G , MISSIAEN, L , DE SMEDT, H , (2013) POLYCYSTINS AND CELLULAR CA2+ SIGNALING.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 70. ISSUE 15. P. 2697-2712 138 86% 6
10 SCHRIER, RW , TORRA, R , TORRES, VE , WATNICK, T , WHEELER, DC , CHAPMAN, AB , DEVUYST, O , ECKARDT, KU , GANSEVOORT, RT , HARRIS, T , ET AL (2015) AUTOSOMAL-DOMINANT POLYCYSTIC KIDNEY DISEASE (ADPKD): EXECUTIVE SUMMARY FROM A KIDNEY DISEASE: IMPROVING GLOBAL OUTCOMES (KDIGO) CONTROVERSIES CONFERENCE.KIDNEY INTERNATIONAL. VOL. 88. ISSUE 1. P. 17 -27 97 87% 24

Classes with closest relation at Level 2



Rank Class id link
1 1658 HEDGEHOG//GLI//CILIOPATHY
2 2113 CHOLANGIOCARCINOMA//GALLBLADDER CANCER//BILIARY TRACT CANCER
3 2293 BILIARY ATRESIA//CHOLEDOCHAL CYST//ALAGILLE SYNDROME
4 1316 FOCAL NODULAR HYPERPLASIA//GD EOB DTPA//GADOXETIC ACID
5 2675 HYDATID CYST//HYDATID DISEASE//ECHINOCOCCOSIS
6 3747 BASALOID SQUAMOUS CELL CARCINOMA//ADENOSQUAMOUS CARCINOMA//BARTHOLINS GLAND
7 668 VESICOURETERAL REFLUX//VESICO URETERAL REFLUX//HYDRONEPHROSIS
8 1854 ANGIOMYOLIPOMA//TUBEROUS SCLEROSIS//TUBEROUS SCLEROSIS COMPLEX
9 1495 KIDNEY DEVELOPMENT//FETAL PROGRAMMING//URETERIC BUD
10 2510 HEPATECTOMY//LIVER RESECTION//LAPAROSCOPIC LIVER RESECTION

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