Class information for:
Level 2: SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
4001 687 26.2 67%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
535 3       TAURINE//CHRONIC GRANULOMATOUS DISEASE//L FORMS 19480
4001 2             SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME 687
19077 1                   SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME 523
30755 1                   POTENT ANTIMICROBIALS//MORFOMETRIA MORFOL CARDIOVASC//HYDROSELENITE 164

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 SHWACHMAN DIAMOND SYNDROME authKW 2975591 12% 83% 81
2 SBDS authKW 870807 3% 85% 23
3 SHWACHMAN SYNDROME authKW 580760 2% 93% 14
4 PANCREATIC STEATOSIS authKW 272230 1% 88% 7
5 FATTY PANCREAS authKW 217782 1% 70% 7
6 LIPOMATOUS PSEUDOHYPERTROPHY authKW 185190 1% 83% 5
7 SBDS GENE authKW 177784 1% 100% 4
8 SCHWACHMAN DIAMOND SYNDROME authKW 177784 1% 100% 4
9 PANCREATIC LIPOMATOSIS authKW 142226 1% 80% 4
10 SHWACHMAN DIAMOND authKW 142226 1% 80% 4

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 1383 14% 0% 98
2 Gastroenterology & Hepatology 1039 12% 0% 85
3 Pediatrics 1013 14% 0% 96
4 Radiology, Nuclear Medicine & Medical Imaging 589 12% 0% 85
5 Endocrinology & Metabolism 334 10% 0% 66
6 Nutrition & Dietetics 162 5% 0% 32
7 Pathology 108 4% 0% 29
8 Oncology 84 8% 0% 54
9 Chemistry, Medicinal 78 4% 0% 27
10 Genetics & Heredity 44 5% 0% 33

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 MORFOMETRIA MORFOL CARDIOVASC 128031 2% 26% 11
2 GASTROENTEROL NUTR PAEDIAT 88892 0% 100% 2
3 MORPHOMETRY CARDIOVASC MORPHOL 55762 1% 16% 8
4 MORPHOMETRY METAB CARDIOVASC DIS 53107 1% 17% 7
5 PROGRAM INTEGRAT BIOL 51842 1% 17% 7
6 MARROW FAILURE MYELODYSPLASIA PROGRAM 47403 1% 27% 4
7 BIOCHIM HP 44446 0% 100% 1
8 BIOMED MORPHOMETRY CARDIOVASC MORPHOL 44446 0% 100% 1
9 BONE JOINT DISSNP 44446 0% 100% 1
10 CLIN EXPT MEDGASTROENTEROL HEPATOL SERV 44446 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PANCREATOLOGY 2302 1% 1% 8
2 PANCREAS 2157 2% 0% 14
3 INTERNATIONAL JOURNAL OF PANCREATOLOGY 1724 1% 1% 6
4 PEDIATRIC BLOOD & CANCER 1398 2% 0% 12
5 RHEUMATOLOGY AND REHABILITATION 1364 0% 2% 2
6 JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION 1208 2% 0% 14
7 BRITISH JOURNAL OF HAEMATOLOGY 820 2% 0% 16
8 CHEMISTRY OF HETEROCYCLIC COMPOUNDS 685 1% 0% 5
9 JAPANESE JOURNAL OF PHARMACOLOGY 636 1% 0% 8
10 MORFOLOGIA NORMAL Y PATOLOGICA SECCION B-ANATOMIA PATOLOGICA 591 0% 1% 1

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 SHWACHMAN DIAMOND SYNDROME 2975591 12% 83% 81 Search SHWACHMAN+DIAMOND+SYNDROME Search SHWACHMAN+DIAMOND+SYNDROME
2 SBDS 870807 3% 85% 23 Search SBDS Search SBDS
3 SHWACHMAN SYNDROME 580760 2% 93% 14 Search SHWACHMAN+SYNDROME Search SHWACHMAN+SYNDROME
4 PANCREATIC STEATOSIS 272230 1% 88% 7 Search PANCREATIC+STEATOSIS Search PANCREATIC+STEATOSIS
5 FATTY PANCREAS 217782 1% 70% 7 Search FATTY+PANCREAS Search FATTY+PANCREAS
6 LIPOMATOUS PSEUDOHYPERTROPHY 185190 1% 83% 5 Search LIPOMATOUS+PSEUDOHYPERTROPHY Search LIPOMATOUS+PSEUDOHYPERTROPHY
7 SBDS GENE 177784 1% 100% 4 Search SBDS+GENE Search SBDS+GENE
8 SCHWACHMAN DIAMOND SYNDROME 177784 1% 100% 4 Search SCHWACHMAN+DIAMOND+SYNDROME Search SCHWACHMAN+DIAMOND+SYNDROME
9 PANCREATIC LIPOMATOSIS 142226 1% 80% 4 Search PANCREATIC+LIPOMATOSIS Search PANCREATIC+LIPOMATOSIS
10 SHWACHMAN DIAMOND 142226 1% 80% 4 Search SHWACHMAN+DIAMOND Search SHWACHMAN+DIAMOND

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 BURROUGHS, L , WOOLFREY, A , SHIMAMURA, A , (2009) SHWACHMAN-DIAMOND SYNDROME: A REVIEW OF THE CLINICAL PRESENTATION,, MOLECULAR PATHOGENESIS, DIAGNOSIS, AND TREATMENT.HEMATOLOGY-ONCOLOGY CLINICS OF NORTH AMERICA. VOL. 23. ISSUE 2. P. 233-+ 55 85% 41
2 DROR, Y , (2005) SHWACHMAN-DIAMOND SYNDROME.PEDIATRIC BLOOD & CANCER. VOL. 45. ISSUE 7. P. 892-901 58 82% 56
3 DROR, Y , DONADIEU, J , KOGLMEIER, J , DODGE, J , TOIVIAINEN-SALO, S , MAKITIE, O , KERR, E , ZEIDLER, C , SHIMAMURA, A , SHAH, N , ET AL (2011) DRAFT CONSENSUS GUIDELINES FOR DIAGNOSIS AND TREATMENT OF SHWACHMAN-DIAMOND SYNDROME.ANNALS MEETING REPORTS. VOL. 1242. ISSUE . P. 40-55 48 84% 24
4 SHIMAMURA, A , (2006) SHWACHMAN-DIAMOND SYNDROME.SEMINARS IN HEMATOLOGY. VOL. 43. ISSUE 3. P. 178 -188 52 81% 37
5 CATANZARO, R , CUFFARI, B , ITALIA, A , MAROTTA, F , (2016) EXPLORING THE METABOLIC SYNDROME: NONALCOHOLIC FATTY PANCREAS DISEASE.WORLD JOURNAL OF GASTROENTEROLOGY. VOL. 22. ISSUE 34. P. 7660 -7675 79 45% 0
6 DROR, Y , FREEDMAN, MH , (2002) SHWACHMAN-DIAMOND SYNDROME.BRITISH JOURNAL OF HAEMATOLOGY. VOL. 118. ISSUE 3. P. 701 -713 47 84% 83
7 DONADIEU, J , FENNETEAU, O , BEAUPAIN, B , BEAUFILS, S , BELLANGER, F , MAHLAOUI, N , LAMBILLIOTTE, A , ALADJIDI, N , BERTRAND, Y , MIALOU, V , ET AL (2012) CLASSIFICATION OF AND RISK FACTORS FOR HEMATOLOGIC COMPLICATIONS IN A FRENCH NATIONAL COHORT OF 102 PATIENTS WITH SHWACHMAN-DIAMOND SYNDROME.HAEMATOLOGICA-THE HEMATOLOGY JOURNAL. VOL. 97. ISSUE 9. P. 1312 -1319 38 81% 20
8 MYERS, KC , DAVIES, SM , SHIMAMURA, A , (2013) CLINICAL AND MOLECULAR PATHOPHYSIOLOGY OF SHWACHMAN-DIAMOND SYNDROME: AN UPDATE.HEMATOLOGY-ONCOLOGY CLINICS OF NORTH AMERICA. VOL. 27. ISSUE 1. P. 117-+ 36 77% 13
9 SMITS, MM , VAN GEENEN, EJM , (2011) THE CLINICAL SIGNIFICANCE OF PANCREATIC STEATOSIS.NATURE REVIEWS GASTROENTEROLOGY & HEPATOLOGY. VOL. 8. ISSUE 3. P. 169 -177 54 50% 30
10 SCHABALLIE, H , RENARD, M , VERMYLEN, C , SCHEERS, I , REVENCU, N , REGAL, L , CASSIMAN, D , SEVENANTS, L , HOFFMAN, I , CORVELEYN, A , ET AL (2013) MISDIAGNOSIS AS ASPHYXIATING THORACIC DYSTROPHY AND CMV-ASSOCIATED HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS IN SHWACHMAN-DIAMOND SYNDROME.EUROPEAN JOURNAL OF PEDIATRICS. VOL. 172. ISSUE 5. P. 613-622 30 91% 3

Classes with closest relation at Level 2



Rank Class id link
1 2683 NEUTROPHIL EXTRACELLULAR TRAPS//SEVERE CONGENITAL NEUTROPENIA//NETOSIS
2 2652 LACTOSE INTOLERANCE//LACTOSE MALABSORPTION//HYDROGEN BREATH TEST
3 1696 NONALCOHOLIC FATTY LIVER DISEASE//NON ALCOHOLIC FATTY LIVER DISEASE//NONALCOHOLIC STEATOHEPATITIS
4 1020 NUCLEOLUS//RIBOSOME BIOGENESIS//SNORNA
5 217 PANCREATIC CANCER//CHRONIC PANCREATITIS//PANCREATICODUODENECTOMY
6 3799 OSTEOCLAST LIKE GIANT CELLS//BINUCLEATED LYMPHOCYTES//ENTOSIS
7 3476 MESENTERIC PANNICULITIS//SCLEROSING MESENTERITIS//EPIPLOIC APPENDAGITIS
8 2698 HETEROTOPIC PANCREAS//ECTOPIC PANCREAS//HETEROTOPIC GASTRIC MUCOSA
9 542 CYSTIC FIBROSIS//CFTR//JOURNAL OF CYSTIC FIBROSIS
10 1169 ACUTE PANCREATITIS//PANCREATITIS//SEVERE ACUTE PANCREATITIS

Go to start page