Class information for:
Level 2: CYSTIC FIBROSIS//CFTR//JOURNAL OF CYSTIC FIBROSIS

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
542 14714 35.7 73%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
597 3       CYSTIC FIBROSIS//CFTR//JOURNAL OF CYSTIC FIBROSIS 14714
542 2             CYSTIC FIBROSIS//CFTR//JOURNAL OF CYSTIC FIBROSIS 14714
1681 1                   CYSTIC FIBROSIS//CFTR GENE//SWEAT TEST 2538
2342 1                   CFTR//CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR//CYSTIC FIBROSIS 2275
2574 1                   CYSTIC FIBROSIS//PULMONARY EXACERBATION//JOURNAL OF CYSTIC FIBROSIS 2205
5897 1                   CYSTIC FIBROSIS//CYSTIC FIBROSIS RELATED DIABETES//JOURNAL OF CYSTIC FIBROSIS 1562
6126 1                   AIRWAY SURFACE LIQUID//SUBMUCOSAL GLANDS//CYST FIBROSIS PULM TREATMENT 1526
11241 1                   CYSTIC FIBROSIS//INFECT CYST FIBROSIS UNIT//ANTI INFLAMMATORY AGENTS ADMINISTRATION DOSAGE ADVERSE EFFECTS 997
11716 1                   DISTAL INTESTINAL OBSTRUCTION SYNDROME//MECONIUM ILEUS//FIBROSING COLONOPATHY 959
14370 1                   CYSTIC FIBROSIS//JOURNAL OF CYSTIC FIBROSIS//REG PAEDIAT CF UNIT 774
16425 1                   CYSTIC FIBROSIS//REFERRAL ADULT CYST FIBROSIS//CHILD DEV EXERCISE 654
21415 1                   AMNIOTIC FLUID ENZYMES//ANAL IMPERFORATION//ANALYTICAL ADAPTATION 419
23621 1                   PANCREATIC DUCT//PANCREATIC DUCT EPITHELIAL CELLS//PANCREATIC DUCT CELLS 340
26631 1                   C10ORF70//INVEST BIOQUIM BUENOS AI BIOL CELULA//MITOCHONDRIAL EXPRESSED GENES 249
32766 1                   EPITHELIAL CELL BIOL//JOINT HUMAN REPROD RELATED DIS//BAK FOONG PILLS 134
36383 1                   HUMAN MOL GENET PROGRAM//CFTR GENE EXPRESSION//CFTR PROMOTER 82

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 CYSTIC FIBROSIS authKW 5113785 32% 52% 4740
2 CFTR authKW 979715 5% 61% 781
3 JOURNAL OF CYSTIC FIBROSIS journal 889708 4% 66% 646
4 CYST FIBROSIS address 529521 3% 53% 486
5 CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR authKW 527909 3% 63% 406
6 PEDIATRIC PULMONOLOGY journal 170171 4% 13% 622
7 PULMONARY EXACERBATION authKW 130669 1% 80% 79
8 CFTR MUTATIONS authKW 123515 0% 83% 72
9 RESPIRATORY SYSTEM WoSSC 121839 24% 2% 3519
10 GREGORY FLEMING JAMES CYST FIBROSIS address 109316 1% 54% 98

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Respiratory System 121839 24% 2% 3519
2 Pediatrics 36169 18% 1% 2607
3 Physiology 11774 11% 0% 1555
4 Critical Care Medicine 5143 4% 1% 586
5 Genetics & Heredity 3525 8% 0% 1147
6 Cell Biology 2683 9% 0% 1308
7 Medicine, General & Internal 1701 7% 0% 980
8 Gastroenterology & Hepatology 1661 4% 0% 591
9 Biochemistry & Molecular Biology 1461 13% 0% 1900
10 Medical Laboratory Technology 1232 2% 0% 261

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CYST FIBROSIS 529521 3% 53% 486
2 GREGORY FLEMING JAMES CYST FIBROSIS 109316 1% 54% 98
3 ADULT CYST FIBROSIS 87270 1% 57% 74
4 CF 76832 1% 48% 78
5 ADULT CYST FIBROSIS UNIT 64609 0% 57% 55
6 CYST FIBROSIS UNIT 64560 0% 47% 67
7 PEDIAT PULMONOL 63462 1% 16% 188
8 CYST FIBROSIS PULM TREATMENT 53898 1% 26% 99
9 CYST FIBROSIS CLIN 48727 0% 56% 42
10 UNIDAD FIBROSIS QUIST 36100 0% 62% 28

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF CYSTIC FIBROSIS 889708 4% 66% 646
2 PEDIATRIC PULMONOLOGY 170171 4% 13% 622
3 PAEDIATRIC RESPIRATORY REVIEWS 22877 1% 14% 81
4 JOURNAL OF PEDIATRICS 13476 2% 2% 301
5 AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY 12938 1% 3% 191
6 AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE 11972 2% 2% 240
7 THORAX 11730 1% 3% 203
8 AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY 9840 1% 3% 157
9 HUMAN GENETICS 9674 1% 2% 196
10 CURRENT OPINION IN PULMONARY MEDICINE 8610 0% 6% 72

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
LCSH search Wikipedia search
1 CYSTIC FIBROSIS 5113785 32% 52% 4740 Search CYSTIC+FIBROSIS Search CYSTIC+FIBROSIS
2 CFTR 979715 5% 61% 781 Search CFTR Search CFTR
3 CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR 527909 3% 63% 406 Search CYSTIC+FIBROSIS+TRANSMEMBRANE+CONDUCTANCE+REGULATOR Search CYSTIC+FIBROSIS+TRANSMEMBRANE+CONDUCTANCE+REGULATOR
4 PULMONARY EXACERBATION 130669 1% 80% 79 Search PULMONARY+EXACERBATION Search PULMONARY+EXACERBATION
5 CFTR MUTATIONS 123515 0% 83% 72 Search CFTR+MUTATIONS Search CFTR+MUTATIONS
6 CYSTIC FIBROSIS RELATED DIABETES 108357 0% 93% 56 Search CYSTIC+FIBROSIS+RELATED+DIABETES Search CYSTIC+FIBROSIS+RELATED+DIABETES
7 CFTR GENE 104540 0% 75% 67 Search CFTR+GENE Search CFTR+GENE
8 SWEAT TEST 99665 0% 70% 69 Search SWEAT+TEST Search SWEAT+TEST
9 IVACAFTOR 80333 0% 82% 47 Search IVACAFTOR Search IVACAFTOR
10 CHLORIDE CHANNEL 77304 1% 17% 220 Search CHLORIDE+CHANNEL Search CHLORIDE+CHANNEL

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 TURCK, D , BRAEGGER, CP , COLOMBO, C , DECLERCQ, D , MORTON, A , PANCHEVA, R , ROBBERECHT, E , STERN, M , STRANDVIK, B , WOLFE, S , ET AL (2016) ESPEN-ESPGHAN-ECFS GUIDELINES ON NUTRITION CARE FOR INFANTS, CHILDREN, AND ADULTS WITH CYSTIC FIBROSIS.CLINICAL NUTRITION. VOL. 35. ISSUE 3. P. 557 -577 163 85% 6
2 CUTTING, GR , (2015) CYSTIC FIBROSIS GENETICS: FROM MOLECULAR UNDERSTANDING TO CLINICAL APPLICATION.NATURE REVIEWS GENETICS. VOL. 16. ISSUE 1. P. 45 -56 115 83% 66
3 GIBSON, RL , BURNS, JL , RAMSEY, BW , (2003) PATHOPHYSIOLOGY AND MANAGEMENT OF PULMONARY INFECTIONS IN CYSTIC FIBROSIS.AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE. VOL. 168. ISSUE 8. P. 918-951 224 52% 793
4 RATJEN, F , BELL, SC , ROWE, SM , GOSS, CH , QUITTNER, AL , BUSH, A , (2015) CYSTIC FIBROSIS.NATURE REVIEWS DISEASE PRIMERS. VOL. 1. ISSUE . P. - 184 72% 6
5 CALLEBAUT, I , HOFFMANN, B , LEHN, P , MORNON, JP , (2017) MOLECULAR MODELLING AND MOLECULAR DYNAMICS OF CFTR.CELLULAR AND MOLECULAR LIFE SCIENCES. VOL. 74. ISSUE 1. P. 3 -22 164 83% 0
6 RIORDAN, JR , (2008) CFTR FUNCTION AND PROSPECTS FOR THERAPY.ANNUAL REVIEW OF BIOCHEMISTRY. VOL. 77. ISSUE . P. 701-726 133 77% 280
7 VEIT, G , AVRAMESCU, RG , CHIANG, AN , HOUCK, SA , CAI, ZW , PETERS, KW , HONG, JS , POLLARD, HB , GUGGINO, WB , BALCH, WE , ET AL (2016) FROM CFTR BIOLOGY TOWARD COMBINATORIAL PHARMACOTHERAPY: EXPANDED CLASSIFICATION OF CYSTIC FIBROSIS MUTATIONS.MOLECULAR BIOLOGY OF THE CELL. VOL. 27. ISSUE 3. P. 424 -433 77 91% 14
8 ELBORN, JS , (2016) CYSTIC FIBROSIS.LANCET. VOL. 388. ISSUE 10059. P. 2519 -2531 97 82% 9
9 LOPES-PACHECO, M , (2016) CFTR MODULATORS: SHEDDING LIGHT ON PRECISION MEDICINE FOR CYSTIC FIBROSIS.FRONTIERS IN PHARMACOLOGY. VOL. 7. ISSUE . P. - 158 80% 0
10 BOMBIERI, C , CLAUSTRES, M , DE BOECK, K , DERICHS, N , DODGE, J , GIRODON, E , SERMET, I , SCHWARZ, M , TZETIS, M , WILSCHANSKI, M , ET AL (2011) RECOMMENDATIONS FOR THE CLASSIFICATION OF DISEASES AS CFTR-RELATED DISORDERS.JOURNAL OF CYSTIC FIBROSIS. VOL. 10. ISSUE . P. S86-S102 117 84% 98

Classes with closest relation at Level 2



Rank Class id link
1 2652 LACTOSE INTOLERANCE//LACTOSE MALABSORPTION//HYDROGEN BREATH TEST
2 910 QUORUM SENSING//PSEUDOMONAS AERUGINOSA//N ACYL HOMOSERINE LACTONE
3 1141 INTRACELLULAR PH//NA H EXCHANGER//AMERICAN JOURNAL OF PHYSIOLOGY
4 1698 MUC1//MUCIN//MUC5AC
5 2003 MYOTONIC DYSTROPHY//MYOTONIA//MYOTONIC DYSTROPHY TYPE 1
6 4001 SHWACHMAN DIAMOND SYNDROME//SBDS//SHWACHMAN SYNDROME
7 1653 PRIMARY CILIARY DYSKINESIA//KARTAGENERS SYNDROME//DYNEIN
8 1881 LUNG TRANSPLANTATION//BRONCHIOLITIS OBLITERANS SYNDROME//JOURNAL OF HEART AND LUNG TRANSPLANTATION
9 1248 ALDOSTERONE//GITELMAN SYNDROME//BARTTER SYNDROME
10 2298 VENTILATOR ASSOCIATED PNEUMONIA//NOSOCOMIAL PNEUMONIA//ENDOTRACHEAL SUCTIONING

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