Class information for: |
Basic class information |
Class id | #P | Avg. number of references |
Database coverage of references |
---|---|---|---|
1912 | 2429 | 33.7 | 71% |
Hierarchy of classes |
The table includes all classes above and classes immediately below the current class. |
Cluster id | Level | Cluster label | #P |
---|---|---|---|
0 | 4 | BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY | 4064930 |
389 | 3 | PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE | 30841 |
1356 | 2 | PEROXISOME//ADRENOLEUKODYSTROPHY//ZELLWEGER SYNDROME | 8277 |
1912 | 1 | ADRENOLEUKODYSTROPHY//X LINKED ADRENOLEUKODYSTROPHY//PHYTANIC ACID | 2429 |
Terms with highest relevance score |
rank | Term | termType | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|---|
1 | ADRENOLEUKODYSTROPHY | authKW | 2524673 | 10% | 84% | 238 |
2 | X LINKED ADRENOLEUKODYSTROPHY | authKW | 1003627 | 4% | 87% | 92 |
3 | PHYTANIC ACID | authKW | 904214 | 4% | 72% | 100 |
4 | PEROXISOMAL DISORDERS | authKW | 844691 | 4% | 69% | 97 |
5 | PEROXISOME | authKW | 717495 | 13% | 18% | 325 |
6 | VERY LONG CHAIN FATTY ACIDS | authKW | 714032 | 5% | 45% | 125 |
7 | REFSUM DISEASE | authKW | 664887 | 3% | 77% | 69 |
8 | ADRENOMYELONEUROPATHY | authKW | 653030 | 2% | 88% | 59 |
9 | ZELLWEGER SYNDROME | authKW | 522015 | 4% | 46% | 90 |
10 | ABCD1 | authKW | 416144 | 1% | 95% | 35 |
Web of Science journal categories |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | Clinical Neurology | 5098 | 21% | 0% | 508 |
2 | Genetics & Heredity | 4219 | 18% | 0% | 444 |
3 | Biochemistry & Molecular Biology | 3002 | 32% | 0% | 768 |
4 | Medicine, Research & Experimental | 2716 | 13% | 0% | 325 |
5 | Biophysics | 1565 | 10% | 0% | 246 |
6 | Endocrinology & Metabolism | 1491 | 11% | 0% | 258 |
7 | Pediatrics | 1174 | 8% | 0% | 206 |
8 | Neurosciences | 881 | 13% | 0% | 325 |
9 | Pathology | 394 | 4% | 0% | 104 |
10 | Neuroimaging | 318 | 2% | 0% | 38 |
Address terms |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | GENET METAB DIS | 149104 | 4% | 12% | 100 |
2 | NEUROMETAB DIS | 131355 | 1% | 58% | 18 |
3 | CELL METAB | 102266 | 1% | 35% | 23 |
4 | EMMA CHILDRENS HOSP GENET METAB DIS | 87985 | 0% | 100% | 7 |
5 | CLIN CHEM METAB | 68430 | 0% | 78% | 7 |
6 | DARBY CHILDREN | 52371 | 0% | 83% | 5 |
7 | NEUROMETABOL DIS | 51319 | 0% | 58% | 7 |
8 | NEUROPATOL BELLVITGE | 50277 | 0% | 100% | 4 |
9 | REFSUM DIS CLIN | 50277 | 0% | 100% | 4 |
10 | KENNEDY KRIEGER | 43525 | 2% | 7% | 48 |
Journals |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
---|---|---|---|---|---|
1 | JOURNAL OF INHERITED METABOLIC DISEASE | 78302 | 7% | 4% | 168 |
2 | JOURNAL OF LIPID RESEARCH | 6144 | 3% | 1% | 65 |
3 | MOLECULAR GENETICS AND METABOLISM | 4601 | 1% | 1% | 34 |
4 | BRAIN & DEVELOPMENT | 2864 | 1% | 1% | 29 |
5 | NEUROLOGY | 2640 | 3% | 0% | 68 |
6 | BIOCHIMICA ET BIOPHYSICA ACTA-LIPIDS AND LIPID METABOLISM | 2268 | 1% | 1% | 14 |
7 | NEUROPEDIATRICS | 2202 | 1% | 1% | 19 |
8 | JOURNAL OF THE NEUROLOGICAL SCIENCES | 2130 | 2% | 0% | 42 |
9 | PEDIATRIC NEUROLOGY | 1814 | 1% | 1% | 25 |
10 | ANNALS OF NEUROLOGY | 1810 | 1% | 0% | 34 |
Author Key Words |
Rank | Term | Chi square | Shr. of publ. in class containing term |
Class's shr. of term's tot. occurrences |
#P with term in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | ADRENOLEUKODYSTROPHY | 2524673 | 10% | 84% | 238 | Search ADRENOLEUKODYSTROPHY | Search ADRENOLEUKODYSTROPHY |
2 | X LINKED ADRENOLEUKODYSTROPHY | 1003627 | 4% | 87% | 92 | Search X+LINKED+ADRENOLEUKODYSTROPHY | Search X+LINKED+ADRENOLEUKODYSTROPHY |
3 | PHYTANIC ACID | 904214 | 4% | 72% | 100 | Search PHYTANIC+ACID | Search PHYTANIC+ACID |
4 | PEROXISOMAL DISORDERS | 844691 | 4% | 69% | 97 | Search PEROXISOMAL+DISORDERS | Search PEROXISOMAL+DISORDERS |
5 | PEROXISOME | 717495 | 13% | 18% | 325 | Search PEROXISOME | Search PEROXISOME |
6 | VERY LONG CHAIN FATTY ACIDS | 714032 | 5% | 45% | 125 | Search VERY+LONG+CHAIN+FATTY+ACIDS | Search VERY+LONG+CHAIN+FATTY+ACIDS |
7 | REFSUM DISEASE | 664887 | 3% | 77% | 69 | Search REFSUM+DISEASE | Search REFSUM+DISEASE |
8 | ADRENOMYELONEUROPATHY | 653030 | 2% | 88% | 59 | Search ADRENOMYELONEUROPATHY | Search ADRENOMYELONEUROPATHY |
9 | ZELLWEGER SYNDROME | 522015 | 4% | 46% | 90 | Search ZELLWEGER+SYNDROME | Search ZELLWEGER+SYNDROME |
10 | ABCD1 | 416144 | 1% | 95% | 35 | Search ABCD1 | Search ABCD1 |
Core articles |
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c: (1) Number of references referring to publications in the class. (2) Share of total number of active references referring to publications in the class. (3) Age of the article. New articles get higher score than old articles. (4) Citation rate, normalized to year. |
Rank | Reference | # ref. in cl. |
Shr. of ref. in cl. |
Citations |
---|---|---|---|---|
1 | KEMP, S , HUFFNAGEL, IC , LINTHORST, GE , WANDERS, RJ , ENGELEN, M , (2016) ADRENOLEUKODYSTROPHY - NEUROENDOCRINE PATHOGENESIS AND REDEFINITION OF NATURAL HISTORY.NATURE REVIEWS ENDOCRINOLOGY. VOL. 12. ISSUE 10. P. 606 -615 | 112 | 94% | 1 |
2 | FERRER, I , AUBOURG, P , PUJOL, A , (2010) GENERAL ASPECTS AND NEUROPATHOLOGY OF X-LINKED ADRENOLEUKODYSTROPHY.BRAIN PATHOLOGY. VOL. 20. ISSUE 4. P. 817 -830 | 124 | 92% | 39 |
3 | MOSER, HW , (1993) PEROXISOMAL DISEASES.ADVANCES IN HUMAN GENETICS. VOL. 21. ISSUE . P. 1-& | 241 | 68% | 33 |
4 | BERGER, J , DORNINGER, F , FORSS-PETTER, S , KUNZE, M , (2016) PEROXISOMES IN BRAIN DEVELOPMENT AND FUNCTION.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1863. ISSUE 5. P. 934 -955 | 141 | 47% | 4 |
5 | WANDERS, RJA , POLL-THE, BT , (2017) "ROLE OF PEROXISOMES IN HUMAN LIPID METABOLISM AND ITS IMPORTANCE FOR NEUROLOGICAL DEVELOPMENT".NEUROSCIENCE LETTERS. VOL. 637. ISSUE . P. 11 -17 | 47 | 81% | 2 |
6 | BERGER, J , FORSS-PETTER, S , EICHLER, FS , (2014) PATHOPHYSIOLOGY OF X-LINKED ADRENOLEUKODYSTROPHY.BIOCHIMIE. VOL. 98. ISSUE . P. 135 -142 | 75 | 88% | 22 |
7 | BERGER, J , GARTNER, J , (2006) X-LINKED ADRENOLEUKODYSTROPHY: CLINICAL, BIOCHEMICAL AND PATHOGENETIC ASPECTS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1763. ISSUE 12. P. 1721-1732 | 97 | 86% | 73 |
8 | MOSER, HW , MAHMOOD, A , RAYMOND, GV , (2007) X-LINKED ADRENOLEUKODYSTROPHY.NATURE CLINICAL PRACTICE NEUROLOGY. VOL. 3. ISSUE 3. P. 140 -151 | 79 | 92% | 116 |
9 | KEMP, S , BERGER, J , AUBOURG, P , (2012) X-LINKED ADRENOLEUKODYSTROPHY: CLINICAL, METABOLIC, GENETIC AND PATHOPHYSIOLOGICAL ASPECTS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE. VOL. 1822. ISSUE 9. P. 1465-1474 | 75 | 81% | 59 |
10 | DE MUNTER, S , VERHEIJDEN, S , REGAL, L , BAES, M , (2015) PEROXISOMAL DISORDERS: A REVIEW ON CEREBELLAR PATHOLOGIES.BRAIN PATHOLOGY. VOL. 25. ISSUE 6. P. 663 -678 | 93 | 71% | 4 |
Classes with closest relation at Level 1 |