Class information for:
Level 1: ADRENOLEUKODYSTROPHY//X LINKED ADRENOLEUKODYSTROPHY//PHYTANIC ACID

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
1912 2429 33.7 71%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
389 3       PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE 30841
1356 2             PEROXISOME//ADRENOLEUKODYSTROPHY//ZELLWEGER SYNDROME 8277
1912 1                   ADRENOLEUKODYSTROPHY//X LINKED ADRENOLEUKODYSTROPHY//PHYTANIC ACID 2429

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ADRENOLEUKODYSTROPHY authKW 2524673 10% 84% 238
2 X LINKED ADRENOLEUKODYSTROPHY authKW 1003627 4% 87% 92
3 PHYTANIC ACID authKW 904214 4% 72% 100
4 PEROXISOMAL DISORDERS authKW 844691 4% 69% 97
5 PEROXISOME authKW 717495 13% 18% 325
6 VERY LONG CHAIN FATTY ACIDS authKW 714032 5% 45% 125
7 REFSUM DISEASE authKW 664887 3% 77% 69
8 ADRENOMYELONEUROPATHY authKW 653030 2% 88% 59
9 ZELLWEGER SYNDROME authKW 522015 4% 46% 90
10 ABCD1 authKW 416144 1% 95% 35

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 5098 21% 0% 508
2 Genetics & Heredity 4219 18% 0% 444
3 Biochemistry & Molecular Biology 3002 32% 0% 768
4 Medicine, Research & Experimental 2716 13% 0% 325
5 Biophysics 1565 10% 0% 246
6 Endocrinology & Metabolism 1491 11% 0% 258
7 Pediatrics 1174 8% 0% 206
8 Neurosciences 881 13% 0% 325
9 Pathology 394 4% 0% 104
10 Neuroimaging 318 2% 0% 38

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 GENET METAB DIS 149104 4% 12% 100
2 NEUROMETAB DIS 131355 1% 58% 18
3 CELL METAB 102266 1% 35% 23
4 EMMA CHILDRENS HOSP GENET METAB DIS 87985 0% 100% 7
5 CLIN CHEM METAB 68430 0% 78% 7
6 DARBY CHILDREN 52371 0% 83% 5
7 NEUROMETABOL DIS 51319 0% 58% 7
8 NEUROPATOL BELLVITGE 50277 0% 100% 4
9 REFSUM DIS CLIN 50277 0% 100% 4
10 KENNEDY KRIEGER 43525 2% 7% 48

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 JOURNAL OF INHERITED METABOLIC DISEASE 78302 7% 4% 168
2 JOURNAL OF LIPID RESEARCH 6144 3% 1% 65
3 MOLECULAR GENETICS AND METABOLISM 4601 1% 1% 34
4 BRAIN & DEVELOPMENT 2864 1% 1% 29
5 NEUROLOGY 2640 3% 0% 68
6 BIOCHIMICA ET BIOPHYSICA ACTA-LIPIDS AND LIPID METABOLISM 2268 1% 1% 14
7 NEUROPEDIATRICS 2202 1% 1% 19
8 JOURNAL OF THE NEUROLOGICAL SCIENCES 2130 2% 0% 42
9 PEDIATRIC NEUROLOGY 1814 1% 1% 25
10 ANNALS OF NEUROLOGY 1810 1% 0% 34

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 ADRENOLEUKODYSTROPHY 2524673 10% 84% 238 Search ADRENOLEUKODYSTROPHY Search ADRENOLEUKODYSTROPHY
2 X LINKED ADRENOLEUKODYSTROPHY 1003627 4% 87% 92 Search X+LINKED+ADRENOLEUKODYSTROPHY Search X+LINKED+ADRENOLEUKODYSTROPHY
3 PHYTANIC ACID 904214 4% 72% 100 Search PHYTANIC+ACID Search PHYTANIC+ACID
4 PEROXISOMAL DISORDERS 844691 4% 69% 97 Search PEROXISOMAL+DISORDERS Search PEROXISOMAL+DISORDERS
5 PEROXISOME 717495 13% 18% 325 Search PEROXISOME Search PEROXISOME
6 VERY LONG CHAIN FATTY ACIDS 714032 5% 45% 125 Search VERY+LONG+CHAIN+FATTY+ACIDS Search VERY+LONG+CHAIN+FATTY+ACIDS
7 REFSUM DISEASE 664887 3% 77% 69 Search REFSUM+DISEASE Search REFSUM+DISEASE
8 ADRENOMYELONEUROPATHY 653030 2% 88% 59 Search ADRENOMYELONEUROPATHY Search ADRENOMYELONEUROPATHY
9 ZELLWEGER SYNDROME 522015 4% 46% 90 Search ZELLWEGER+SYNDROME Search ZELLWEGER+SYNDROME
10 ABCD1 416144 1% 95% 35 Search ABCD1 Search ABCD1

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 KEMP, S , HUFFNAGEL, IC , LINTHORST, GE , WANDERS, RJ , ENGELEN, M , (2016) ADRENOLEUKODYSTROPHY - NEUROENDOCRINE PATHOGENESIS AND REDEFINITION OF NATURAL HISTORY.NATURE REVIEWS ENDOCRINOLOGY. VOL. 12. ISSUE 10. P. 606 -615 112 94% 1
2 FERRER, I , AUBOURG, P , PUJOL, A , (2010) GENERAL ASPECTS AND NEUROPATHOLOGY OF X-LINKED ADRENOLEUKODYSTROPHY.BRAIN PATHOLOGY. VOL. 20. ISSUE 4. P. 817 -830 124 92% 39
3 MOSER, HW , (1993) PEROXISOMAL DISEASES.ADVANCES IN HUMAN GENETICS. VOL. 21. ISSUE . P. 1-& 241 68% 33
4 BERGER, J , DORNINGER, F , FORSS-PETTER, S , KUNZE, M , (2016) PEROXISOMES IN BRAIN DEVELOPMENT AND FUNCTION.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1863. ISSUE 5. P. 934 -955 141 47% 4
5 WANDERS, RJA , POLL-THE, BT , (2017) "ROLE OF PEROXISOMES IN HUMAN LIPID METABOLISM AND ITS IMPORTANCE FOR NEUROLOGICAL DEVELOPMENT".NEUROSCIENCE LETTERS. VOL. 637. ISSUE . P. 11 -17 47 81% 2
6 BERGER, J , FORSS-PETTER, S , EICHLER, FS , (2014) PATHOPHYSIOLOGY OF X-LINKED ADRENOLEUKODYSTROPHY.BIOCHIMIE. VOL. 98. ISSUE . P. 135 -142 75 88% 22
7 BERGER, J , GARTNER, J , (2006) X-LINKED ADRENOLEUKODYSTROPHY: CLINICAL, BIOCHEMICAL AND PATHOGENETIC ASPECTS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1763. ISSUE 12. P. 1721-1732 97 86% 73
8 MOSER, HW , MAHMOOD, A , RAYMOND, GV , (2007) X-LINKED ADRENOLEUKODYSTROPHY.NATURE CLINICAL PRACTICE NEUROLOGY. VOL. 3. ISSUE 3. P. 140 -151 79 92% 116
9 KEMP, S , BERGER, J , AUBOURG, P , (2012) X-LINKED ADRENOLEUKODYSTROPHY: CLINICAL, METABOLIC, GENETIC AND PATHOPHYSIOLOGICAL ASPECTS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE. VOL. 1822. ISSUE 9. P. 1465-1474 75 81% 59
10 DE MUNTER, S , VERHEIJDEN, S , REGAL, L , BAES, M , (2015) PEROXISOMAL DISORDERS: A REVIEW ON CEREBELLAR PATHOLOGIES.BRAIN PATHOLOGY. VOL. 25. ISSUE 6. P. 663 -678 93 71% 4

Classes with closest relation at Level 1



Rank Class id link
1 2721 PEROXISOME//PEROXIN//PEROXISOME BIOGENESIS
2 19665 PLASMALOGEN//ALPHA HYDROXYALDEHYDES//PHOSPHATIDYLETHANOLAMINE PLASMALOGEN
3 30827 DODECANEDIOIC ACID//DIETHYL SEBACATE//AZELAIC ACID
4 23151 SOCIAL SEPARATION STRESS//NEONATAL CHICK//REGULAT METAB BEHAV
5 14230 BETA KETOTHIOLASE DEFICIENCY//MITOCHONDRIAL ACETOACETYL COA THIOLASE//THIOLASE
6 3761 PEROXISOME PROLIFERATOR//PEROXISOME PROLIFERATION//3 THIA FATTY ACIDS
7 27804 ACYL COA THIOESTERASE//ACETYL COA HYDROLASE//ACYL COA HYDROLASE
8 34928 PERRAULT SYNDROME//HOLMES ATAXIA//BOUCHER NEUHAUSER SYNDROME
9 5778 BILE ACIDS//SULFATED BILE ACID//TAURINE CONJUGATE
10 12781 ALEXANDER DISEASE//LEUKODYSTROPHY//ROSENTHAL FIBERS

Go to start page