Class information for:
Level 3: PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
389 30841 34.9 68%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
389 3       PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE 30841
1356 2             PEROXISOME//ADRENOLEUKODYSTROPHY//ZELLWEGER SYNDROME 8277
1504 2             CARNITINE//L CARNITINE//TRIMETAZIDINE 7543
2144 2             JOURNAL OF INHERITED METABOLIC DISEASE//NEWBORN SCREENING//METHYLMALONIC ACIDEMIA 5035
2805 2             BIOTIN//BIOTINIDASE DEFICIENCY//BIOTINIDASE 3081
2868 2             PYRUVATE DEHYDROGENASE COMPLEX//NONKETOTIC HYPERGLYCINEMIA//DIHYDROLIPOAMIDE DEHYDROGENASE 2878
3076 2             PEPTIDE DEFORMYLASE//ENOYL ACP REDUCTASE//ACYL CARRIER PROTEIN 2395
3395 2             PKAN//NBIA//PANTOTHENATE KINASE 1632

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 PEROXISOME authKW 712037 4% 62% 1155
2 CARNITINE authKW 349077 2% 57% 625
3 JOURNAL OF INHERITED METABOLIC DISEASE journal 278934 4% 25% 1132
4 L CARNITINE authKW 256365 2% 53% 489
5 TRIMETAZIDINE authKW 229125 1% 80% 291
6 ADRENOLEUKODYSTROPHY authKW 203441 1% 85% 241
7 RANOLAZINE authKW 160546 1% 80% 204
8 ZELLWEGER SYNDROME authKW 137904 1% 85% 165
9 BIOTIN authKW 133294 1% 29% 460
10 NEWBORN SCREENING authKW 129063 1% 34% 388

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 Biochemistry & Molecular Biology 36510 31% 1% 9580
2 Genetics & Heredity 15491 11% 1% 3260
3 Medicine, Research & Experimental 13033 9% 1% 2692
4 Biophysics 9900 8% 1% 2316
5 Endocrinology & Metabolism 9344 8% 1% 2429
6 Pediatrics 7891 6% 1% 1997
7 Cell Biology 4581 8% 0% 2545
8 Nutrition & Dietetics 3707 4% 1% 1084
9 Cardiac & Cardiovascular System 3190 5% 0% 1637
10 Medical Laboratory Technology 2604 2% 1% 549

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 GENET METAB DIS 74171 1% 30% 252
2 UNIT MOL MED 34841 0% 39% 90
3 ABT SYST BIOCHEM 34148 0% 89% 39
4 CLIN CHEM PEDIAT 17795 0% 48% 38
5 AFDELING FARMACOL 17071 0% 79% 22
6 BIOLHIGASHI KU 17071 0% 79% 22
7 PEDIAT 16014 7% 1% 2276
8 CELL METAB 15534 0% 49% 32
9 PEDIAT CLIN CHEM 14960 0% 63% 24
10 ORGAN ACID SECT 14878 0% 94% 16

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
1 JOURNAL OF INHERITED METABOLIC DISEASE 278934 4% 25% 1132
2 MOLECULAR GENETICS AND METABOLISM 60699 1% 14% 440
3 BIOCHEMICAL JOURNAL 11693 2% 2% 612
4 JOURNAL OF BIOLOGICAL CHEMISTRY 7211 4% 1% 1177
5 PEDIATRIC RESEARCH 6490 1% 3% 253
6 EUROPEAN JOURNAL OF PEDIATRICS 5606 1% 3% 212
7 CLINICA CHIMICA ACTA 5341 1% 2% 254
8 BRAIN & DEVELOPMENT 4300 0% 4% 129
9 BIOCHIMICA ET BIOPHYSICA ACTA 4197 1% 1% 375
10 EUROPEAN JOURNAL OF BIOCHEMISTRY 3563 1% 1% 285

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with term
in class
LCSH search Wikipedia search
1 PEROXISOME 712037 4% 62% 1155 Search PEROXISOME Search PEROXISOME
2 CARNITINE 349077 2% 57% 625 Search CARNITINE Search CARNITINE
3 L CARNITINE 256365 2% 53% 489 Search L+CARNITINE Search L+CARNITINE
4 TRIMETAZIDINE 229125 1% 80% 291 Search TRIMETAZIDINE Search TRIMETAZIDINE
5 ADRENOLEUKODYSTROPHY 203441 1% 85% 241 Search ADRENOLEUKODYSTROPHY Search ADRENOLEUKODYSTROPHY
6 RANOLAZINE 160546 1% 80% 204 Search RANOLAZINE Search RANOLAZINE
7 ZELLWEGER SYNDROME 137904 1% 85% 165 Search ZELLWEGER+SYNDROME Search ZELLWEGER+SYNDROME
8 BIOTIN 133294 1% 29% 460 Search BIOTIN Search BIOTIN
9 NEWBORN SCREENING 129063 1% 34% 388 Search NEWBORN+SCREENING Search NEWBORN+SCREENING
10 PEROXIN 125734 0% 96% 133 Search PEROXIN Search PEROXIN

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 LOPASCHUK, GD , USSHER, JR , FOLMES, CDL , JASWAL, JS , STANLEY, WC , (2010) MYOCARDIAL FATTY ACID METABOLISM IN HEALTH AND DISEASE.PHYSIOLOGICAL REVIEWS. VOL. 90. ISSUE 1. P. 207 -258 296 49% 421
2 HUEMER, M , DIODATO, D , SCHWAHN, B , SCHIFF, M , BANDEIRA, A , BENOIST, JF , BURLINA, A , CERONE, R , COUCE, ML , GARCIA-CAZORLA, A , ET AL (2017) GUIDELINES FOR DIAGNOSIS AND MANAGEMENT OF THE COBALAMIN-RELATED REMETHYLATION DISORDERS CBLC, CBLD, CBLE, CBLF, CBLG, CBLJ AND MTHFR DEFICIENCY.JOURNAL OF INHERITED METABOLIC DISEASE. VOL. 40. ISSUE 1. P. 21 -48 165 87% 1
3 KIM, PK , HETTEMA, EH , (2015) MULTIPLE PATHWAYS FOR PROTEIN TRANSPORT TO PEROXISOMES.JOURNAL OF MOLECULAR BIOLOGY. VOL. 427. ISSUE 6. P. 1176 -1190 171 96% 26
4 KUNAU, WH , DOMMES, V , SCHULZ, H , (1995) BETA-OXIDATION OF FATTY ACIDS IN MITOCHONDRIA, PEROXISOMES, AND BACTERIA: A CENTURY OF CONTINUED PROGRESS.PROGRESS IN LIPID RESEARCH. VOL. 34. ISSUE 4. P. 267 -342 430 66% 292
5 WELLER, S , GOULD, SJ , VALLE, D , (2003) PEROXISOME BIOGENESIS DISORDERS.ANNUAL REVIEW OF GENOMICS AND HUMAN GENETICS. VOL. 4. ISSUE . P. 165 -211 244 96% 108
6 BAUMGARTNER, MR , HORSTER, F , DIONISI-VICI, C , HALILOGLU, G , KARALL, D , CHAPMAN, KA , HUEMER, M , HOCHULI, M , ASSOUN, M , BALLHAUSEN, D , ET AL (2014) PROPOSED GUIDELINES FOR THE DIAGNOSIS AND MANAGEMENT OF METHYLMALONIC AND PROPIONIC ACIDEMIA.ORPHANET JOURNAL OF RARE DISEASES. VOL. 9. ISSUE . P. - 198 79% 28
7 BERGER, J , DORNINGER, F , FORSS-PETTER, S , KUNZE, M , (2016) PEROXISOMES IN BRAIN DEVELOPMENT AND FUNCTION.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1863. ISSUE 5. P. 934 -955 201 67% 4
8 WATERHAM, HR , FERDINANDUSSE, S , WANDERS, RJA , (2016) HUMAN DISORDERS OF PEROXISOME METABOLISM AND BIOGENESIS.BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH. VOL. 1863. ISSUE 5. P. 922 -933 129 82% 10
9 FRASER, JL , VENDITTI, CP , (2016) METHYLMALONIC AND PROPIONIC ACIDEMIAS: CLINICAL MANAGEMENT UPDATE.CURRENT OPINION IN PEDIATRICS. VOL. 28. ISSUE 6. P. 682 -693 183 92% 0
10 ECKERT, JH , ERDMANN, R , (2003) PEROXISOME BIOGENESIS.REVIEWS OF PHYSIOLOGY, BIOCHEMISTRY AND PHARMACOLOGY, VOL 147 2003. VOL. 147. ISSUE . P. 75-121 222 91% 63

Classes with closest relation at Level 3



Rank Class id link
1 630 HEPATIC ENCEPHALOPATHY//ASYMMETRIC DIMETHYLARGININE//HYPERAMMONEMIA
2 66 LEPTIN//ADIPONECTIN//ENDOCRINOLOGY & METABOLISM
3 230 P GLYCOPROTEIN//FMO3//TRIMETHYLAMINURIA
4 631 KYNURENINE//NEOPTERIN//INDOLEAMINE 2 3 DIOXYGENASE
5 271 MITOCHONDRIA//MITOCHONDRIAL GENOME//MITOCHONDRIAL DNA PART A
6 278 CORYNEBACTERIUM GLUTAMICUM//ACTA CRYSTALLOGRAPHICA SECTION D-BIOLOGICAL CRYSTALLOGRAPHY//BIOCHEMISTRY & MOLECULAR BIOLOGY
7 551 FABRY DISEASE//GAUCHER DISEASE//LYSOSOMAL STORAGE DISEASE
8 502 HOMOCYSTEINE//FOLATE//FOLIC ACID
9 285 ERDOSTEINE//PEROXIREDOXIN//GLUTATHIONE
10 387 DOCOSAHEXAENOIC ACID//CONJUGATED LINOLEIC ACID//FISH OIL

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