Class information for:
Level 2: PKAN//NBIA//PANTOTHENATE KINASE

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
3395 1632 29.8 63%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
389 3       PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE 30841
3395 2             PKAN//NBIA//PANTOTHENATE KINASE 1632
15543 1                   COENZYME A//PANTOTHENATE KINASE//PANTOTHENATE SYNTHETASE 706
18617 1                   PKAN//NBIA//HALLERVORDEN SPATZ SYNDROME 544
26715 1                   PANTETHEINASE//TEX101//VANIN 247
32715 1                   BETA AMINOALANINE//ANTI HERPES SIMPLEX VIRUS TYPE 1//METHYLENEHYDANTOIN 135

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 PKAN authKW 714751 3% 93% 41
2 NBIA authKW 653171 3% 78% 45
3 PANTOTHENATE KINASE authKW 569131 2% 89% 34
4 HALLERVORDEN SPATZ SYNDROME authKW 551043 2% 82% 36
5 HALLERVORDEN SPATZ DISEASE authKW 520852 2% 80% 35
6 COENZYME A authKW 425954 5% 30% 75
7 PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION authKW 414039 2% 76% 29
8 PLA2G6 authKW 401125 2% 79% 27
9 NEURODEGENERATION WITH BRAIN IRON ACCUMULATION authKW 391559 2% 70% 30
10 PANTETHEINASE authKW 337690 1% 95% 19

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Clinical Neurology 2833 19% 0% 313
2 Biochemistry & Molecular Biology 1489 28% 0% 456
3 Biochemical Research Methods 481 7% 0% 108
4 Neurosciences 338 11% 0% 177
5 Nutrition & Dietetics 296 4% 0% 68
6 Chemistry, Analytical 295 7% 0% 118
7 Biophysics 280 6% 0% 95
8 Chemistry, Medicinal 240 4% 0% 71
9 Pharmacology & Pharmacy 212 9% 0% 151
10 Pediatrics 152 4% 0% 71

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 LEHRSTUHL MIKROBIELLE GENET 101020 1% 60% 9
2 PIERFRANCO LUISA MARIANI STUDY MITOCHONDRIA 65473 0% 50% 7
3 STRUCT FUNCT NUCL ACID 42093 0% 75% 3
4 MICROCITEMIA ANEMIE CONGENITE HAEMATOL 37417 0% 100% 2
5 MOL MED GENET PEDIAT NEUROL 37417 0% 100% 2
6 SCOTTISH STRUCT IL 37417 0% 100% 2
7 ILLING SECT CLIN MOL NEUROGENET 32063 0% 29% 6
8 IMMUNOL PARASITOL 25072 1% 7% 19
9 GENET FUNKT GENOMFOR 24944 0% 67% 2
10 NEUROMUSCULAR NEUROMETAB DISORDERS 24944 0% 67% 2

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 ARTERY 3510 1% 2% 10
2 MOVEMENT DISORDERS 3463 2% 1% 35
3 CURRENT THERAPEUTIC RESEARCH-CLINICAL AND EXPERIMENTAL 1854 1% 0% 22
4 SEMINARS IN PEDIATRIC NEUROLOGY 1565 0% 2% 5
5 ANALYTICAL BIOCHEMISTRY 1482 2% 0% 39
6 JOURNAL OF MICRONUTRIENT ANALYSIS 1214 0% 2% 3
7 PEDIATRIC NEUROLOGY 1104 1% 0% 16
8 NEUROPEDIATRICS 1096 1% 1% 11
9 PARKINSONISM & RELATED DISORDERS 926 1% 0% 11
10 ACTA MEDICA ACADEMIAE SCIENTIARUM HUNGARICAE 920 0% 2% 2

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 PKAN 714751 3% 93% 41 Search PKAN Search PKAN
2 NBIA 653171 3% 78% 45 Search NBIA Search NBIA
3 PANTOTHENATE KINASE 569131 2% 89% 34 Search PANTOTHENATE+KINASE Search PANTOTHENATE+KINASE
4 HALLERVORDEN SPATZ SYNDROME 551043 2% 82% 36 Search HALLERVORDEN+SPATZ+SYNDROME Search HALLERVORDEN+SPATZ+SYNDROME
5 HALLERVORDEN SPATZ DISEASE 520852 2% 80% 35 Search HALLERVORDEN+SPATZ+DISEASE Search HALLERVORDEN+SPATZ+DISEASE
6 COENZYME A 425954 5% 30% 75 Search COENZYME+A Search COENZYME+A
7 PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION 414039 2% 76% 29 Search PANTOTHENATE+KINASE+ASSOCIATED+NEURODEGENERATION Search PANTOTHENATE+KINASE+ASSOCIATED+NEURODEGENERATION
8 PLA2G6 401125 2% 79% 27 Search PLA2G6 Search PLA2G6
9 NEURODEGENERATION WITH BRAIN IRON ACCUMULATION 391559 2% 70% 30 Search NEURODEGENERATION+WITH+BRAIN+IRON+ACCUMULATION Search NEURODEGENERATION+WITH+BRAIN+IRON+ACCUMULATION
10 PANTETHEINASE 337690 1% 95% 19 Search PANTETHEINASE Search PANTETHEINASE

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref. in
cl.
Shr. of ref. in
cl.
Citations
1 LEONARDI, R , ZHANG, YM , ROCK, CO , JACKOWSKI, S , (2005) COENZYME A: BACK IN ACTION.PROGRESS IN LIPID RESEARCH. VOL. 44. ISSUE 2-3. P. 125 -153 106 64% 193
2 SPRY, C , KIRK, K , SALIBA, KJ , (2008) COENZYME A BIOSYNTHESIS: AN ANTIMICROBIAL DRUG TARGET.FEMS MICROBIOLOGY REVIEWS. VOL. 32. ISSUE 1. P. 56 -106 100 61% 85
3 LEVI, S , FINAZZI, D , (2014) NEURODEGENERATION WITH BRAIN IRON ACCUMULATION: UPDATE ON PATHOGENIC MECHANISMS.FRONTIERS IN PHARMACOLOGY. VOL. 5. ISSUE . P. - 88 54% 24
4 SCHNEIDER, SA , (2016) NEURODEGENERATION WITH BRAIN IRON ACCUMULATION.CURRENT NEUROLOGY AND NEUROSCIENCE REPORTS. VOL. 16. ISSUE 1. P. - 63 77% 0
5 KURIAN, MA , HAYFLICK, SJ , (2013) PANTOTHENATE KINASE-ASSOCIATED NEURODEGENERATION (PKAN) AND PLA2G6-ASSOCIATED NEURODEGENERATION (PLAN): REVIEW OF TWO MAJOR NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA) PHENOTYPES.METAL RELATED NEURODEGENERATIVE DISEASE. VOL. 110. ISSUE . P. 49-71 51 89% 16
6 SCHNEIDER, SA , DUSEK, P , HARDY, J , WESTENBERGER, A , JANKOVIC, J , BHATIA, KP , (2013) GENETICS AND PATHOPHYSIOLOGY OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).CURRENT NEUROPHARMACOLOGY. VOL. 11. ISSUE 1. P. 59 -79 83 50% 30
7 ARBER, CE , LI, A , HOULDEN, H , WRAY, S , (2016) REVIEW: INSIGHTS INTO MOLECULAR MECHANISMS OF DISEASE IN NEURODEGENERATION WITH BRAIN IRON ACCUMULATION: UNIFYING THEORIES.NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY. VOL. 42. ISSUE 3. P. 220 -241 65 46% 7
8 WEBB, ME , SMITH, AG , (2011) PANTOTHENATE BIOSYNTHESIS IN HIGHER PLANTS.BIOSYNTHESIS OF VITAMINS IN PLANTS: VITAMINS A, B1, B2, B3, B5, PT A. VOL. 58. ISSUE . P. 203 -255 74 59% 5
9 SCHNEIDER, SA , BHATIA, KP , (2012) SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION.SEMINARS IN PEDIATRIC NEUROLOGY. VOL. 19. ISSUE 2. P. 57 -66 56 69% 24
10 SCHNEIDER, SA , ZORZI, G , NARDOCCI, N , (2013) PATHOPHYSIOLOGY AND TREATMENT OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION IN THE PEDIATRIC POPULATION.CURRENT TREATMENT OPTIONS IN NEUROLOGY. VOL. 15. ISSUE 5. P. 652 -667 56 67% 6

Classes with closest relation at Level 2



Rank Class id link
1 3076 PEPTIDE DEFORMYLASE//ENOYL ACP REDUCTASE//ACYL CARRIER PROTEIN
2 3898 CYSTINOSIS//NEPHROPATHIC CYSTINOSIS//SALLA DISEASE
3 2596 ACTA CRYSTALLOGRAPHICA SECTION D-BIOLOGICAL CRYSTALLOGRAPHY//ACTA CRYSTALLOGRAPHICA SECTION A//ACTA CRYSTALLOGRAPHICA SECTION D-STRUCTURAL BIOLOGY
4 1818 DYSTONIA//TETRAHYDROBIOPTERIN//WRITERS CRAMP
5 1475 THIAMINE//THIAMINE DEFICIENCY//WERNICKES ENCEPHALOPATHY
6 1356 PEROXISOME//ADRENOLEUKODYSTROPHY//ZELLWEGER SYNDROME
7 1504 CARNITINE//L CARNITINE//TRIMETAZIDINE
8 2144 JOURNAL OF INHERITED METABOLIC DISEASE//NEWBORN SCREENING//METHYLMALONIC ACIDEMIA
9 3232 GRASS SICKNESS//EQUINE GRASS SICKNESS//DEGENERATIVE MYELOPATHY
10 1711 SPINOCEREBELLAR ATAXIA//HEREDITARY SPASTIC PARAPLEGIA//FRIEDREICHS ATAXIA

Go to start page