Class information for:
Level 1: PKAN//NBIA//HALLERVORDEN SPATZ SYNDROME

Basic class information
Class id #P Avg. number of
references		 Database coverage
of references
18617 544 30.1 74%


Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes
The table includes all classes above and classes immediately below the current class.


Cluster id Level Cluster label #P
0 4 BIOCHEMISTRY & MOLECULAR BIOLOGY//CELL BIOLOGY//ONCOLOGY 4064930
389 3       PEROXISOME//CARNITINE//JOURNAL OF INHERITED METABOLIC DISEASE 30841
3395 2             PKAN//NBIA//PANTOTHENATE KINASE 1632
18617 1                   PKAN//NBIA//HALLERVORDEN SPATZ SYNDROME 544

Terms with highest relevance score


rank Term termType Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 PKAN authKW 2041085 7% 91% 40
2 NBIA authKW 1959692 8% 78% 45
3 HALLERVORDEN SPATZ SYNDROME authKW 1653272 7% 82% 36
4 HALLERVORDEN SPATZ DISEASE authKW 1562697 6% 80% 35
5 PLA2G6 authKW 1203483 5% 79% 27
6 NEURODEGENERATION WITH BRAIN IRON ACCUMULATION authKW 1174797 6% 70% 30
7 PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION authKW 1076795 5% 71% 27
8 PANK2 authKW 901197 3% 94% 17
9 NEUROFERRITINOPATHY authKW 790694 3% 78% 18
10 INFANTILE NEUROAXONAL DYSTROPHY authKW 718458 3% 80% 16

Web of Science journal categories


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 Clinical Neurology 9547 57% 0% 311
2 Neurosciences 1383 31% 0% 166
3 Pediatrics 691 13% 0% 71
4 Genetics & Heredity 403 13% 0% 68
5 Pathology 345 8% 0% 42
6 Neuroimaging 278 3% 0% 16
7 Radiology, Nuclear Medicine & Medical Imaging 78 6% 0% 32
8 Psychiatry 51 5% 0% 25
9 Biochemistry & Molecular Biology 36 12% 0% 63
10 Geriatrics & Gerontology 8 1% 0% 5

Address terms


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 PIERFRANCO LUISA MARIANI STUDY MITOCHONDRIA 144328 1% 43% 6
2 MICROCITEMIA ANEMIE CONGENITE HAEMATOL 112260 0% 100% 2
3 MOL MED GENET PEDIAT NEUROL 112260 0% 100% 2
4 ILLING SECT CLIN MOL NEUROGENET 96214 1% 29% 6
5 NEUROMUSCULAR NEUROMETAB DISORDERS 74839 0% 67% 2
6 OSPED REG MICROCITEMIA 74839 0% 67% 2
7 ADVOCATE CHRIST HOSP MED 56130 0% 100% 1
8 ALBRECHT KOSSEL NEUROREGULAT 56130 0% 100% 1
9 ANIM MED SURGERY 56130 0% 100% 1
10 CATTEDRO UO NEUROL 56130 0% 100% 1

Journals


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class
1 MOVEMENT DISORDERS 10527 6% 1% 35
2 SEMINARS IN PEDIATRIC NEUROLOGY 4715 1% 2% 5
3 PEDIATRIC NEUROLOGY 3376 3% 0% 16
4 NEUROPEDIATRICS 3330 2% 1% 11
5 PARKINSONISM & RELATED DISORDERS 2822 2% 0% 11
6 BRAIN & DEVELOPMENT 2596 2% 0% 13
7 EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY 1822 1% 1% 6
8 INTERNATIONAL REVIEW OF NEUROBIOLOGY 1703 1% 1% 6
9 ACTA NEUROPATHOLOGICA 1610 2% 0% 13
10 NEUROLOGY 1496 4% 0% 24

Author Key Words


Rank Term Chi square Shr. of publ. in
class containing
term		 Class's shr. of
term's tot. occurrences		 #P with
term in
class		 LCSH search Wikipedia search
1 PKAN 2041085 7% 91% 40 Search PKAN Search PKAN
2 NBIA 1959692 8% 78% 45 Search NBIA Search NBIA
3 HALLERVORDEN SPATZ SYNDROME 1653272 7% 82% 36 Search HALLERVORDEN+SPATZ+SYNDROME Search HALLERVORDEN+SPATZ+SYNDROME
4 HALLERVORDEN SPATZ DISEASE 1562697 6% 80% 35 Search HALLERVORDEN+SPATZ+DISEASE Search HALLERVORDEN+SPATZ+DISEASE
5 PLA2G6 1203483 5% 79% 27 Search PLA2G6 Search PLA2G6
6 NEURODEGENERATION WITH BRAIN IRON ACCUMULATION 1174797 6% 70% 30 Search NEURODEGENERATION+WITH+BRAIN+IRON+ACCUMULATION Search NEURODEGENERATION+WITH+BRAIN+IRON+ACCUMULATION
7 PANTOTHENATE KINASE ASSOCIATED NEURODEGENERATION 1076795 5% 71% 27 Search PANTOTHENATE+KINASE+ASSOCIATED+NEURODEGENERATION Search PANTOTHENATE+KINASE+ASSOCIATED+NEURODEGENERATION
8 PANK2 901197 3% 94% 17 Search PANK2 Search PANK2
9 NEUROFERRITINOPATHY 790694 3% 78% 18 Search NEUROFERRITINOPATHY Search NEUROFERRITINOPATHY
10 INFANTILE NEUROAXONAL DYSTROPHY 718458 3% 80% 16 Search INFANTILE+NEUROAXONAL+DYSTROPHY Search INFANTILE+NEUROAXONAL+DYSTROPHY

Core articles
The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.


Rank Reference # ref.
in cl.		 Shr. of ref. in
cl.		 Citations
1 LEVI, S , FINAZZI, D , (2014) NEURODEGENERATION WITH BRAIN IRON ACCUMULATION: UPDATE ON PATHOGENIC MECHANISMS.FRONTIERS IN PHARMACOLOGY. VOL. 5. ISSUE . P. - 81 50% 24
2 KURIAN, MA , HAYFLICK, SJ , (2013) PANTOTHENATE KINASE-ASSOCIATED NEURODEGENERATION (PKAN) AND PLA2G6-ASSOCIATED NEURODEGENERATION (PLAN): REVIEW OF TWO MAJOR NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA) PHENOTYPES.METAL RELATED NEURODEGENERATIVE DISEASE. VOL. 110. ISSUE . P. 49-71 51 89% 16
3 SCHNEIDER, SA , (2016) NEURODEGENERATION WITH BRAIN IRON ACCUMULATION.CURRENT NEUROLOGY AND NEUROSCIENCE REPORTS. VOL. 16. ISSUE 1. P. - 62 76% 0
4 SCHNEIDER, SA , DUSEK, P , HARDY, J , WESTENBERGER, A , JANKOVIC, J , BHATIA, KP , (2013) GENETICS AND PATHOPHYSIOLOGY OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).CURRENT NEUROPHARMACOLOGY. VOL. 11. ISSUE 1. P. 59 -79 83 50% 30
5 SCHNEIDER, SA , BHATIA, KP , (2012) SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION.SEMINARS IN PEDIATRIC NEUROLOGY. VOL. 19. ISSUE 2. P. 57 -66 56 69% 24
6 SCHNEIDER, SA , ZORZI, G , NARDOCCI, N , (2013) PATHOPHYSIOLOGY AND TREATMENT OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION IN THE PEDIATRIC POPULATION.CURRENT TREATMENT OPTIONS IN NEUROLOGY. VOL. 15. ISSUE 5. P. 652 -667 56 67% 6
7 SCHNEIDER, SA , BHATIA, KP , (2013) EXCESS IRON HARMS THE BRAIN: THE SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).JOURNAL OF NEURAL TRANSMISSION. VOL. 120. ISSUE 4. P. 695 -703 55 63% 14
8 ARBER, CE , LI, A , HOULDEN, H , WRAY, S , (2016) REVIEW: INSIGHTS INTO MOLECULAR MECHANISMS OF DISEASE IN NEURODEGENERATION WITH BRAIN IRON ACCUMULATION: UNIFYING THEORIES.NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY. VOL. 42. ISSUE 3. P. 220 -241 58 41% 7
9 SCHNEIDER, SA , HARDY, J , BHATIA, KP , (2012) SYNDROMES OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA): AN UPDATE ON CLINICAL PRESENTATIONS, HISTOLOGICAL AND GENETIC UNDERPINNINGS, AND TREATMENT CONSIDERATIONS.MOVEMENT DISORDERS. VOL. 27. ISSUE 1. P. 42 -53 50 63% 45
10 KURIAN, MA , MCNEILL, A , LIN, JP , MAHER, ER , (2011) CHILDHOOD DISORDERS OF NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA).DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY. VOL. 53. ISSUE 5. P. 394 -404 39 83% 34

Classes with closest relation at Level 1


Rank Class id link
1 19205 CHOREA ACANTHOCYTOSIS//NEUROACANTHOCYTOSIS//MCLEOD SYNDROME
2 15543 COENZYME A//PANTOTHENATE KINASE//PANTOTHENATE SYNTHETASE
3 37662 NALCN//ABNORMAL RESPIRATORY RHYTHM//ADDIC MENTAL HLTH
4 8891 SUSCEPTIBILITY WEIGHTED IMAGING//QUANTITATIVE SUSCEPTIBILITY MAPPING//BRAIN IRON
5 12765 CERULOPLASMIN//ACERULOPLASMINEMIA//FERROXIDASE
6 37447 ATHETOID CEREBRAL PALSY//BREACH RATE//CERVICAL OPERATION
7 34608 GIANT AXONAL NEUROPATHY//GIGAXONIN//GAN MUTATIONS
8 14726 DEGENERATIVE MYELOPATHY//ABIOTROPHY//CEREBELLAR ABIOTROPHY
9 26478 GAPO SYNDROME//ICHTHYOSIS FOLLICULARIS//IFAP SYNDROME
10 1271 DYSTONIA//WRITERS CRAMP//DYT1

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