Class information for:
Level 1: CHOREA ACANTHOCYTOSIS//NEUROACANTHOCYTOSIS//MCLEOD SYNDROME

Basic class information

Class id #P Avg. number of
references
Database coverage
of references
19205 516 28.4 67%



Bar chart of Publication_year

Last years might be incomplete

Hierarchy of classes

The table includes all classes above and classes immediately below the current class.



Cluster id Level Cluster label #P
17 4 REPRODUCTIVE BIOLOGY//OBSTETRICS & GYNECOLOGY//VETERINARY SCIENCES 563730
453 3       PRENATAL DIAGNOSIS//NUCHAL TRANSLUCENCY//OBSTETRICS & GYNECOLOGY 25435
1345 2             TRANSFUSION//VOX SANGUINIS//AUTOIMMUNE HEMOLYTIC ANEMIA 8314
19205 1                   CHOREA ACANTHOCYTOSIS//NEUROACANTHOCYTOSIS//MCLEOD SYNDROME 516

Terms with highest relevance score



rank Term termType Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 CHOREA ACANTHOCYTOSIS authKW 2700282 10% 89% 51
2 NEUROACANTHOCYTOSIS authKW 2614482 10% 82% 54
3 MCLEOD SYNDROME authKW 2309304 8% 98% 40
4 CHOREIN authKW 946815 3% 100% 16
5 ACANTHOCYTOSIS authKW 899871 4% 72% 21
6 VPS13A authKW 769287 3% 100% 13
7 XK GENE authKW 532584 2% 100% 9
8 ACANTHOCYTES authKW 384631 3% 50% 13
9 HUNTINGTONS DISEASE LIKE authKW 304332 1% 86% 6
10 KELL BLOOD GROUP authKW 295880 1% 100% 5

Web of Science journal categories



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 Hematology 5474 32% 0% 163
2 Clinical Neurology 2764 32% 0% 167
3 Neurosciences 315 16% 0% 85
4 Genetics & Heredity 114 8% 0% 39
5 Medicine, General & Internal 44 6% 0% 31
6 Psychiatry 39 4% 0% 22
7 Neuroimaging 35 1% 0% 6
8 Immunology 24 5% 0% 27
9 Pathology 21 3% 0% 13
10 Medicine, Research & Experimental 16 3% 0% 17

Address terms



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 HUMAN MOL GENET UNIT 2A3 118352 0% 100% 2
2 ADV OCCLUS PROGRAM 59176 0% 100% 1
3 BIOL GRP SANGUINS 59176 0% 100% 1
4 BIOL MOL MED CHEM 59176 0% 100% 1
5 CARDIOVASCBRANCH 59176 0% 100% 1
6 CNRSU1127UMR 7225UMR S1127 59176 0% 100% 1
7 COLOMBES 59176 0% 100% 1
8 DIAGNOST MED MOL GENOMED 59176 0% 100% 1
9 ENDOCRINE 2 59176 0% 100% 1
10 EXTRPYRAMIDOVYCH ONEMOCNENI 59176 0% 100% 1

Journals



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
1 TRANSFUSION 17802 9% 1% 48
2 VOX SANGUINIS 12684 6% 1% 29
3 REVUE FRANCAISE DE TRANSFUSION ET IMMUNO-HEMATOLOGIE 8515 1% 2% 7
4 MOVEMENT DISORDERS 7612 6% 0% 29
5 BEITRAGE ZUR INFUSIONSTHERAPIE/CONTRIBUTIONS TO INFUSION THERAPY 3216 2% 1% 8
6 JOURNAL OF THE NEUROLOGICAL SCIENCES 2322 4% 0% 20
7 JOURNAL OF THE JAPANESE SOCIETY OF INTERNAL MEDICINE 2190 0% 4% 1
8 ANNALS OF NEUROLOGY 1077 2% 0% 12
9 BRITISH JOURNAL OF HAEMATOLOGY 966 3% 0% 15
10 ARCHIVES OF NEUROLOGY 883 2% 0% 10

Author Key Words



Rank Term Chi square Shr. of publ. in
class containing
term
Class's shr. of
term's tot. occurrences
#P with
term in
class
LCSH search Wikipedia search
1 CHOREA ACANTHOCYTOSIS 2700282 10% 89% 51 Search CHOREA+ACANTHOCYTOSIS Search CHOREA+ACANTHOCYTOSIS
2 NEUROACANTHOCYTOSIS 2614482 10% 82% 54 Search NEUROACANTHOCYTOSIS Search NEUROACANTHOCYTOSIS
3 MCLEOD SYNDROME 2309304 8% 98% 40 Search MCLEOD+SYNDROME Search MCLEOD+SYNDROME
4 CHOREIN 946815 3% 100% 16 Search CHOREIN Search CHOREIN
5 ACANTHOCYTOSIS 899871 4% 72% 21 Search ACANTHOCYTOSIS Search ACANTHOCYTOSIS
6 VPS13A 769287 3% 100% 13 Search VPS13A Search VPS13A
7 XK GENE 532584 2% 100% 9 Search XK+GENE Search XK+GENE
8 ACANTHOCYTES 384631 3% 50% 13 Search ACANTHOCYTES Search ACANTHOCYTES
9 HUNTINGTONS DISEASE LIKE 304332 1% 86% 6 Search HUNTINGTONS+DISEASE+LIKE Search HUNTINGTONS+DISEASE+LIKE
10 KELL BLOOD GROUP 295880 1% 100% 5 Search KELL+BLOOD+GROUP Search KELL+BLOOD+GROUP

Core articles

The table includes core articles in the class. The following variables is taken into account for the relevance score of an article in a cluster c:
(1) Number of references referring to publications in the class.
(2) Share of total number of active references referring to publications in the class.
(3) Age of the article. New articles get higher score than old articles.
(4) Citation rate, normalized to year.



Rank Reference # ref.
in cl.
Shr. of ref. in
cl.
Citations
1 DANEK, A , JUNG, HH , MELONE, MAB , RAMPOLDI, L , BROCCOLI, V , WALKER, RH , (2005) NEUROACANTHOCYTOSIS: NEW DEVELOPMENTS IN A NEGLECTED GROUP OF DEMENTING DISORDERS.JOURNAL OF THE NEUROLOGICAL SCIENCES. VOL. 229. ISSUE . P. 171 -186 63 66% 43
2 LEE, S , (2007) THE VALUE OF DNA ANALYSIS FOR ANTIGENS OF THE KELL AND KX BLOOD GROUP SYSTEMS.TRANSFUSION. VOL. 47. ISSUE 1. P. 32S-39S 47 87% 16
3 ZHANG, LH , WANG, SP , LIN, JW , (2013) CLINICAL AND MOLECULAR RESEARCH OF NEUROACANTHOCYTOSIS.NEURAL REGENERATION RESEARCH. VOL. 8. ISSUE 9. P. 833 -842 52 69% 0
4 WALKER, RH , JUNG, HH , DOBSON-STONE, C , RAMPOLDI, L , SANO, A , TISON, F , DANEK, A , (2007) NEUROLOGIC PHENOTYPES ASSOCIATED WITH ACANTHOCYTOSIS.NEUROLOGY. VOL. 68. ISSUE 2. P. 92-98 55 67% 45
5 RAMPOLDI, L , DANEK, A , MONACO, AP , (2002) CLINICAL FEATURES AND MOLECULAR BASES OF NEUROACANTHOCYTOSIS.JOURNAL OF MOLECULAR MEDICINE-JMM. VOL. 80. ISSUE 8. P. 475 -491 77 53% 64
6 JUNG, HH , DANEK, A , FREY, BM , (2007) MCLEOD SYNDROME: A NEUROHAEMATOLOGICAL DISORDER.VOX SANGUINIS. VOL. 93. ISSUE 2. P. 112-121 43 81% 16
7 DANEK, A , RUBIO, JP , RAMPOLDI, L , HO, MF , DOBSON-STONE, C , TISON, F , SYMMANS, WA , OECHSNER, M , KALCKREUTH, W , WATT, JM , ET AL (2001) MCLEOD NEUROACANTHOCYTOSIS: GENOTYPE AND PHENOTYPE.ANNALS OF NEUROLOGY. VOL. 50. ISSUE 6. P. 755-764 42 89% 87
8 WALKER, RH , DANEK, A , UTTNER, I , OFFNER, R , REID, M , LEE, S , (2007) MCLEOD PHENOTYPE WITHOUT THE MCLEOD SYNDROME.TRANSFUSION. VOL. 47. ISSUE 2. P. 299 -305 39 87% 9
9 STEVENSON, VL , HARDIE, RJ , (2001) ACANTHOCYTOSIS AND NEUROLOGICAL DISORDERS.JOURNAL OF NEUROLOGY. VOL. 248. ISSUE 2. P. 87 -94 46 82% 27
10 JUNG, HH , DANEK, A , WALKER, RH , (2011) NEUROACANTHOCYTOSIS SYNDROMES.ORPHANET JOURNAL OF RARE DISEASES. VOL. 6. ISSUE . P. - 32 82% 30

Classes with closest relation at Level 1



Rank Class id link
1 18617 PKAN//NBIA//HALLERVORDEN SPATZ SYNDROME
2 10696 WEAK D//RH BLOOD GROUP//RH BLOOD GROUP SYSTEM
3 6793 ALLOIMMUNIZATION//TRANSFUSION//ANTIBODY SCREENING
4 16076 GLYCOPHORIN//GLYCOPHORIN C//GERBICH
5 4166 FETAL ANEMIA//INTRAUTERINE TRANSFUSION//FETOMATERNAL HEMORRHAGE
6 1749 HUNTINGTONS DISEASE//PREDICTIVE TESTING//JUVENILE HUNTINGTON DISEASE
7 21780 DARC//DUFFY BLOOD GROUP//DUFFY ANTIGEN
8 14477 ENDOTHELIN CONVERTING ENZYME//NEPRILYSIN//PHOSPHORAMIDON
9 26340 COHEN SYNDROME//CHORIORETINAL DYSPLASIA//COH1
10 2557 SPINOCEREBELLAR ATAXIA//MACHADO JOSEPH DISEASE//SCA2

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